An unusual complication following a shoulder relocation attempt in a case of Larsen syndrome: Deep soft tissue laceration of the arm

AbstractObjective:To describe the first published case of superficial angiomyxoma with an epithelial component occurring in the retropharynx.Method:Case report of a patient with swallowing difficulties caused by a rare case of superficial angiomyxoma in the retropharynx.Results:Superficial angiomyxoma is a distinct entity among the dermal myxomatous lesions. Superficial angiomyxoma is poorly circumscribed, and local recurrence is common unless the tumour is excised with clear margins. Distinctive histological features include a myxoid mass composed of spindle and stellate-shaped cells and occasional multinucleated cells. There is prominent vasculature and a mixed inflammatory infiltrate in the stroma, particularly by neutrophil polymorphs. Epithelial structures are seen in about one-third of cases. A case of retropharyngeal tumour with morphological features of superficial angiomyxoma is reported. The tumour cells, including multinucleated ones, were negative for soft tissue differentiation markers. The inflammatory cells included lymphocytes, histiocytes and neutrophil polymorphs.Conclusion:This case demonstrates that a cutaneous type of angiomyxoma with epithelial-lined structures can occur in deep soft tissue, such as the retropharynx.

Download Full-text

Epithelioid Leiomyosarcoma of the External Deep Soft Tissue

Archives of Pathology & Laboratory Medicine ◽

10.5858/2002-126-0468-eloted ◽

2002 ◽

Vol 126 (4) ◽

pp. 468-470 ◽

Cited By ~ 2

Author(s):

Tetsuji Yamamoto ◽

Rieko Minami ◽

Chiho Ohbayashi ◽

Mayumi Inaba

Keyword(s):

Soft Tissue ◽

Tumor Cells ◽

Epithelial Membrane Antigen ◽

Spindle Cell ◽

Smooth Muscle Actin ◽

S100 Protein ◽

Immunohistochemical Analysis ◽

Deep Soft Tissue ◽

Cell Component ◽

Spindle Cell Component

Abstract Epithelioid leiomyosarcoma in the external deep soft tissue is extremely rare. Most epithelioid leiomyosarcomas occur in the uterus. We present a case of epithelioid leiomyosarcoma occurring in the muscle of the thigh of a 78-year-old man. Histologically, the tumor predominantly consisted of round or polygonal cells arranged in sheets with a focal spindle cell component. Immunohistochemical analysis revealed that the tumor cells expressed vimentin, α-smooth muscle actin, and α-sarcomeric actin. The tumor was negative for desmin, S100 protein, glial fibrillary acidic protein, pan-keratin, epithelial membrane antigen, CAM 5.2, HMB-45, leukocyte common antigen, factor VIII–associated antigen, and CD34. Electron microscopically, some tumor cells contained abundant actin-type filaments in their cytoplasm.

Download Full-text

Epithelioid Leiomyosarcoma of the External Deep Soft Tissue

Archives of Pathology & Laboratory Medicine ◽

10.5858/2003-127-0402c-eloted ◽

2003 ◽

Vol 127 (4) ◽

pp. 402-404

Author(s):

Brian Eyden

Keyword(s):

Soft Tissue ◽

Deep Soft Tissue

Download Full-text

Low-grade fibromyxoid sarcoma: A rare case in an unusual location

SAGE Open Medical Case Reports ◽

10.1177/2050313x20944315 ◽

2020 ◽

Vol 8 ◽

pp. 2050313X2094431

Author(s):

Diandra Perez ◽

Ola El-Zammar ◽

Brando Cobanov ◽

Rana Naous

Keyword(s):

Young Adults ◽

Soft Tissue ◽

Rare Case ◽

Primary Site ◽

Low Grade ◽

Deep Soft Tissue ◽

Unusual Location ◽

Fibromyxoid Sarcoma ◽

Intrathoracic Mass

Low-grade fibromyxoid sarcoma, also known as Evans tumor, is a low-grade sarcoma that most commonly arises in the deep soft tissue of the proximal extremities or trunk in young adults. It is very rare in the viscera as a primary site, with only a few cases reported in the literature. Here, we present a case of Evans tumor occurring in an unusual and rarely reported location; an intrathoracic mass arising from the diaphragmatic pleura.

Download Full-text