Abstract
Background Right atrial diverticulum is a rare congenital condition which causes the right atrium enlargement. The squeals of this condition can vary from cardiac abnormalities to respiratory distress and systemic thromboembolism, hence Identifying these patients can prevent life-threatening outcomes. Prenatal diagnosis has the benefit of better following up and managing patients to prevent later subsequences. Case presentation Echocardiography of the neonate 3 days after birth showed a massive right atrium with a diverticulum measuring 2.09*2.27 cm connected laterally to the right atrium without any clot in it. A fibromuscular strand was seen at the entry of the diverticulum through the right atrium.CT-Angiography 16 days after birth showed a massive right atrium with a diverticulum in the right hemithorax and confirmed the diagnosis.The patient underwent on low dose aspirin therapy to prevent thromboembolism.After 16 months the patient goes on well this condition without cardiac or respiratory symptoms and echocardiography showed the diverticulum size increased to 3.5*2.5 cm without any clot in it.Surgical resection has not proceeded yet because the patient has been asymptomatic until now.ConclusionBecause of the rarity of this condition, management of these patients is highly dependent on the symptoms they show, and also early diagnosis can prevent further medical squeals. Low doses aspirin is suggested to prevent the formation of thrombosis. Surgical resection can be done in patients with serious cardiac or respiratory abnormality, It is important to do not misdiagnosis this condition with a right atrial aneurysm which involves whole layers of the atrial wall. Although outcomes of both conditions are almost the same, using a proper term to establish an accurate diagnosis preferred.