Disturbed hepatic carbohydrate management during high metabolic demand in medium-chain acyl-CoA dehydrogenase (MCAD)-deficient mice

10.1002/hep.22284 ◽

2008 ◽

Vol 47 (6) ◽

pp. 1894-1904 ◽

Author(s):

Hilde Herrema ◽

Terry G. J. Derks ◽

Theo H. van Dijk ◽

Vincent W. Bloks ◽

Albert Gerding ◽

...

Keyword(s):

Metabolic Demand ◽

Medium Chain ◽

Deficient Mice ◽

High Metabolic Demand

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Pre-exercise medium-chain triglyceride application prevents acylcarnitine accumulation in skeletal muscle from very-long-chain acyl-CoA-dehydrogenase-deficient mice

Journal of Inherited Metabolic Disease ◽

10.1007/s10545-010-9105-7 ◽

2010 ◽

Vol 33 (3) ◽

pp. 237-246 ◽

Author(s):

Sonja Primassin ◽

Sara Tucci ◽

Diran Herebian ◽

Annette Seibt ◽

Lars Hoffmann ◽

...

Keyword(s):

Skeletal Muscle ◽

Medium Chain Triglyceride ◽

Medium Chain ◽

Deficient Mice ◽

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Medium-chain triglycerides impair lipid metabolism and induce hepatic steatosis in very long-chain acyl-CoA dehydrogenase (VLCAD)-deficient mice

Molecular Genetics and Metabolism ◽

10.1016/j.ymgme.2010.05.005 ◽

2010 ◽

Vol 101 (1) ◽

pp. 40-47 ◽

Author(s):

Sara Tucci ◽

Sonja Primassin ◽

Frank Ter Veld ◽

Ute Spiekerkoetter

Keyword(s):

Lipid Metabolism ◽

Hepatic Steatosis ◽

Medium Chain Triglycerides ◽

Medium Chain ◽

Deficient Mice ◽

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De novofatty acid biosynthesis and elongation in very long-chain acyl-CoA dehydrogenase-deficient mice supplemented with odd or even medium-chain fatty acids

FEBS Journal ◽

10.1111/febs.13418 ◽

2015 ◽

Vol 282 (21) ◽

pp. 4242-4253 ◽

Author(s):

Sara Tucci ◽

Sidney Behringer ◽

Ute Spiekerkoetter

Keyword(s):

Fatty Acids ◽

Acid Biosynthesis ◽

Medium Chain ◽

Medium Chain Fatty Acids ◽

Deficient Mice ◽

Chain Fatty Acids

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Cardiac tissue citric acid cycle intermediates in exercised very long‐chain acyl‐CoA dehydrogenase‐deficient mice fed triheptanoin or medium‐chain triglyceride

Journal of Inherited Metabolic Disease ◽

10.1002/jimd.12284 ◽

2020 ◽

Vol 43 (6) ◽

pp. 1232-1242 ◽

Author(s):

Garen Gaston ◽

Jon A. Gangoiti ◽

Shelley Winn ◽

Benjamin Chan ◽

Bruce A. Barshop ◽

...

Keyword(s):

Citric Acid ◽

Cardiac Tissue ◽

Citric Acid Cycle ◽

Medium Chain Triglyceride ◽

Medium Chain ◽

Deficient Mice ◽

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Faculty Opinions recommendation of Basal mitophagy occurs independently of PINK1 in mouse tissues of high metabolic demand.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.732477092.793542878 ◽

2018 ◽

Author(s):

Xinnan Wang ◽

Roeland Vanhauwaert

Keyword(s):

Metabolic Demand ◽

Mouse Tissues ◽

High Metabolic Demand

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Purification and properties of short chain acyl-CoA, medium chain acyl-CoA, and isovaleryl-CoA dehydrogenases from human liver.

Journal of Biological Chemistry ◽

10.1016/s0021-9258(18)47514-x ◽

1987 ◽

Vol 262 (17) ◽

pp. 7982-7989

Author(s):

G Finocchiaro ◽

M Ito ◽

K Tanaka

Keyword(s):

Human Liver ◽

Short Chain ◽

Medium Chain ◽

Purification And Properties ◽

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13C- and 15N-NMR Studies of Medium-Chain Acyl-CoA Dehydrogenase from Porcine Kidney

Flavins and Flavoproteins 1993 ◽

10.1515/9783110885774-051 ◽

1994 ◽

pp. 293-302

Keyword(s):

15N Nmr ◽

Porcine Kidney ◽

Nmr Studies ◽

Medium Chain ◽

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Purification and characterization of short-chain, medium-chain, and long-chain acyl-CoA dehydrogenases from rat liver mitochondria. Isolation of the holo- and apoenzymes and conversion of the apoenzyme to the holoenzyme.

Journal of Biological Chemistry ◽

10.1016/s0021-9258(20)71245-7 ◽

1985 ◽

Vol 260 (2) ◽

pp. 1311-1325 ◽

Author(s):

Y Ikeda ◽

K Okamura-Ikeda ◽

K Tanaka

Keyword(s):

Rat Liver ◽

Liver Mitochondria ◽

Rat Liver Mitochondria ◽

Purification And Characterization ◽

Medium Chain ◽

Acyl Coa Dehydrogenases ◽

Mitochondria Isolation ◽

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Impaired tetramer assembly of variant medium-chain acyl-coenzyme A dehydrogenase with a glutamate or aspartate substitution for lysine 304 causing instability of the protein.

Journal of Biological Chemistry ◽

10.1016/s0021-9258(18)35708-9 ◽

1992 ◽

Vol 267 (36) ◽

pp. 26004-26010

Author(s):

I Yokota ◽

T Saijo ◽

J Vockley ◽

K Tanaka

Keyword(s):

Medium Chain ◽

Acyl Coenzyme A

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The human medium chain acyl-CoA dehydrogenase gene promoter consists of a complex arrangement of nuclear receptor response elements and Sp1 binding sites.

Journal of Biological Chemistry ◽

10.1016/s0021-9258(18)57572-4 ◽

1995 ◽

Vol 270 (41) ◽

pp. 24622

Author(s):

Teresa C. Leone ◽

Sharon Cresci ◽

M. Eric Carter ◽

Zhifang Zhang ◽

Deepak S. Lala ◽

...

Keyword(s):

Nuclear Receptor ◽

Binding Sites ◽

Gene Promoter ◽

Response Elements ◽

Medium Chain ◽

Receptor Response ◽

Dehydrogenase Gene ◽

Complex Arrangement

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