Allograft stapes surgery for conductive hearing loss in patients with ossicular chain anomalies

1996 ◽  
Vol 253 (4-5) ◽  
Author(s):  
T. Minatogawa ◽  
H. Iritani ◽  
K. Ishida ◽  
M.N. Node
Keyword(s):  
Hearing Loss ◽  
Conductive Hearing Loss ◽  
Ossicular Chain ◽  
Stapes Surgery ◽  
Conductive Hearing

Ossicular Discontinuity and Exostoses in Proteus Syndrome: A Case Report

2005 ◽  
Vol 114 (3) ◽  
pp. 242-246
Author(s):  
Joni K. Doherty ◽  
Dennis R. Maceri
Keyword(s):  
Hearing Loss ◽  
High Frequency ◽  
Conductive Hearing Loss ◽  
Ossicular Chain ◽  
Typical Feature ◽  
Proteus Syndrome ◽  
Frequency Range ◽  
Pure Tone Average ◽  
Ossicular Chain Reconstruction ◽  
Conductive Hearing

Proteus syndrome (PS) is a rare hamartomatous disorder characterized by mosaic overgrowth of multiple tissues that manifests early in life and is progressive. The presence of unilateral external auditory canal exostoses in a patient who is not a swimmer or surfer is suggestive of PS. However, hearing loss is not a typical feature. Here, we describe exostoses and ossicular discontinuity with conductive hearing loss in a patient with PS. The treatment consisted of canalplasty and ossicular chain reconstruction. A postoperative reduction was demonstrated in the patient's air-bone gap, from 21 dB to 13 dB for the pure tone average (four frequencies) and from 41 dB to 15 dB in the high-frequency range (6,000 to 8,000 Hz). Causes of ossicular discontinuity are discussed. Routine annual audiometric and otolaryngological evaluation should be considered in all patients with temporal bone inyolvement of PS.

Fixation of the Anterior Mallear Ligament: Diagnosis and Consequences for Hearing Results in Stapes Surgery

2003 ◽  
Vol 112 (4) ◽  
pp. 348-355 ◽  
Author(s):  
Alexander Huber ◽  
Takuji Koike ◽  
Vel Nandapalan ◽  
Hiroshi Wada ◽  
Ugo Fisch
Keyword(s):  
Finite Element ◽  
Hearing Loss ◽  
Vibration Amplitude ◽  
Conductive Hearing Loss ◽  
Stapes Surgery ◽  
Hearing Results ◽  
Functional Failure ◽  
Human Temporal Bone ◽  
Manual Palpation ◽  
Conductive Hearing

In the search for possible causes of unfavorable results after stapes surgery, the study reported here focused on the anterior mallear ligament, since it has been previously reported that partial mallear fixation (PMF) leads to functional failure in 38% of cases of stapes revision surgery. The aims of the study were to identify effective methods for the diagnosis of PMF and experimentally assess the conductive hearing loss that results from PMF. The study included vibration amplitude measurements of the ossicles by laser Doppler interferometry (LDI) in 19 patients and 5 fresh human temporal bone (TB) specimens. Analysis of their dynamic behavior was performed by finite element modeling (FEM). Similar, significant changes of manubrium vibration patterns for PMF were found by FEM calculations, in TB experiments, and in patients. We could identify PMF either before operation, using LDI, or during operation, by manual palpation. In the TB experiments and FEM calculations, the attenuation of the stapes displacement due to an isolated PMF was approximately 10 dB and frequency-dependent. Untreated anterior mallear ligament fixation produced a persistent air-bone gap of approximately 10 dB after stapedioplasty.

scholarly journals A Start Codon Variant in NOG Underlies Symphalangism and Ossicular Chain Malformations Affecting Both the Incus and the Stapes

2019 ◽  
Vol 2019 ◽  
pp. 1-5
Author(s):  
Nathan R. Lindquist ◽  
Eric N. Appelbaum ◽  
Anushree Acharya ◽  
Jeffrey T. Vrabec ◽  
Suzanne M. Leal ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Conductive Hearing Loss ◽  
Ossicular Chain ◽  
Start Codon ◽  
Imaging Data ◽  
Hearing Thresholds ◽  
Stapes Footplate ◽  
Multiple Abnormalities ◽  
Protein Variants ◽  
Conductive Hearing

We performed exome sequencing to evaluate the underlying molecular cause of a patient with bilateral conductive hearing loss due to multiple ossicular abnormalities as well as symphalangism of the fifth digits. This leads to the identification of a novel heterozygous start codon variant in the NOG gene (c.2T>C:p.Met1?) that hinders normal translation of the noggin protein. Variants in NOG lead to a spectrum of otologic, digit, and joint abnormalities, a combination suggested to be referred to as NOG‐related‐symphalangism spectrum disorder (NOG‐SSD). Conductive hearing loss from such variants may stem from stapes footplate ankylosis, fixation of the malleoincudal joint, or fixation of the incus short process. In this case, the constellation of both stapes and incus fixation, an exceptionally tall stapes suprastructure, thickened long process of the incus, and enlarged incus body was encountered, leading to distinct challenges during otologic surgery to improve hearing thresholds. This case highlights multiple abnormalities to the ossicular chain in a patient with a start codon variant in NOG. We provide detailed imaging data on these malformations as well as surgical considerations and outcomes.

Rosen mobilization of the stapes: does it have a place in modern otology?

2006 ◽  
Vol 120 (12) ◽  
pp. 1067-1071 ◽  
Author(s):  
G Thiel ◽  
R Mills
Keyword(s):  
Hearing Loss ◽  
Conductive Hearing Loss ◽  
Stapes Surgery ◽  
Hearing Gain ◽  
Stapes Fixation ◽  
Conductive Hearing

We describe two patients with stapes fixation, in both of whom Rosen mobilization seemed to be the most prudent surgical choice. In both cases, a useful hearing gain was achieved initially. In the patient with otosclerosis, the conductive hearing loss recurred and a stapedectomy was subsequently carried out. In the patient with congenital stapes fixation, the hearing gain was maintained for two years eight months. We believe that this technique still has a place in stapes surgery in rare instances.

Inversion of the stapedial reflex in ossicular chain lesions

1986 ◽  
Vol 100 (4) ◽  
pp. 399-403 ◽  
Author(s):  
Steen Gimsing
Keyword(s):  
Hearing Loss ◽  
Soft Tissue ◽  
Conductive Hearing Loss ◽  
External Auditory Meatus ◽  
Ossicular Chain ◽  
Traumatic Origin ◽  
Stapedial Reflex ◽  
Conductive Hearing

AbstractIn ears with minor conductive hearing loss of traumatic origin, it is sometimes possible to invert the deflection of the stapedial reflex by application of a small underpressure in the external auditory meatus of the injured ear (probe ear). This inversion can be explained by an ossicular discontinuity bridge by soft tissue.

Patterns of hearing loss in non-explosive blast injury of the ear

1997 ◽  
Vol 111 (12) ◽  
pp. 1137-1141 ◽  
Author(s):  
Gilead Berger ◽  
Yehuda Finkelstein ◽  
Shabtai Avraham ◽  
Mordehai Himmelfarb
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Conductive Hearing Loss ◽  
Bone Conduction ◽  
Ossicular Chain ◽  
Blast Injury ◽  
Sensorineural Hearing ◽  
Single Frequency ◽  
A Prospective Study ◽  
Conductive Hearing

AbstractA prospective study of hearing loss in 120 cases with non-explosive blast injury of the ear, gathered over a six-year period, is presented. Thirty-three (27.5 per cent) patients had normal hearing, 57 (47.5 per cent) conductive hearing loss, 29 (24.2 per cent) mixed loss and one (0.8 per cent) had pure sensorineural loss. The severity of conductive hearing loss correlated with the size of the eardrum perforation; only a marginal difference was found between water and air pressure injuries, with respect to this type of hearing loss. Of all locations, perforations involving the posterior-inferior quadrant of the eardrum were associated with the largest air-bone gap. Audiometric assessment revealed that none of the patients suffered ossicular chain damage. Three patterns of sensorineural hearing loss were identified: a dip at a single frequency, two separate dips, and abnormality of bone conduction in several adjacent high frequencies. Involvement of several frequencies was associated with a more severe hearing loss than a dip in a single frequency. Healing of the perforation was always accompanied by closure of the air-bone gap, while the recovery of the sensorineural hearing loss was less favourable.

Findings at exploratory tympanotomy for conductive hearing loss

2009 ◽  
Vol 123 (10) ◽  
pp. 1087-1089 ◽  
Author(s):  
G Robertson ◽  
R Mills
Keyword(s):  
Hearing Loss ◽  
Diagnostic Tests ◽  
Conductive Hearing Loss ◽  
Ossicular Chain ◽  
Number Of Patients ◽  
Conductive Hearing

AbstractIntroduction:Despite advances in imaging and other diagnostic tests, it is often impossible to establish with confidence a pre-operative diagnosis in a patient with a conductive hearing loss.Methods:We studied a series of 340 exploratory tympanotomies for conductive hearing loss carried out by a single surgeon.Results:The most common operative diagnosis was otosclerosis (n = 164, 48.2 per cent). Ossicular discontinuity was found more commonly than previously reported (n = 103, 30.3 per cent). A small but significant number of patients were found to have cholesteatoma (n = 7.2 per cent).Conclusions:This information is of value when discussing potential findings at surgery for conductive hearing loss. While otosclerosis is the commonest finding in such cases, a significant number of patients have defects of the ossicular chain.

Stapes surgery for post-traumatic conductive hearing loss: how we do it

2009 ◽  
Vol 34 (1) ◽  
pp. 64-66 ◽  
Author(s):  
Y.K. Shabana ◽  
M. Abu-Samra ◽  
M.R. Ghonim
Keyword(s):  
Hearing Loss ◽  
Conductive Hearing Loss ◽  
Stapes Surgery ◽  
Post Traumatic ◽  
Conductive Hearing

scholarly journals Penetrating Middle Ear Trauma: A Report of 2 Cases

2005 ◽  
Vol 84 (1) ◽  
pp. 32-35 ◽  
Author(s):  
Michael C. Neuenschwander ◽  
Ellen S. Deutsch ◽  
Anthony Cornetta ◽  
Thomas O. Willcox
Keyword(s):  
Hearing Loss ◽  
Physical Examination ◽  
Middle Ear ◽  
Conductive Hearing Loss ◽  
Penetrating Trauma ◽  
Ossicular Chain ◽  
The Other ◽  
Ear Injury ◽  
The Right ◽  
Conductive Hearing

Penetrating middle ear injury can result in hearing loss, vertigo, and facial nerve injury. We describe the cases of 2 children with penetrating trauma to the right ear that resulted in ossicular chain disruption; one injury was caused by cotton-tipped swabs and the other by a wooden matchstick. Symptoms in both children included hearing loss and otalgia; in addition, one child experienced ataxia and the other vertigo. Physical examination in both cases revealed a perforation in the posterosuperior quadrant of the tympanic membrane and visible ossicles. Audiometry identified a moderate conductive hearing loss in one child and a mild sensorineural hearing loss in the other. Both children underwent middle ear exploration and reduction of a subluxed stapes. We discuss the diagnosis, causes, and management of penetrating middle ear trauma. To reduce the morbidity associated with these traumas, otologic surgeons should act promptly and be versatile in choosing methods of repairing ossicular chain injuries.

scholarly journals Endoscopic Ear Surgery for the Management of Traumatic Ossicular Disruption with Intact Tympanic Membrane

2020 ◽  
Author(s):  
Chunlin Zhang ◽  
Dan Long ◽  
Yuan Deng ◽  
Mei Ynag ◽  
Dandan Guo ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Retrospective Study ◽  
Conductive Hearing Loss ◽  
Ossicular Chain ◽  
Endoscopic Ear Surgery ◽  
Ear Surgery ◽  
Temporal Bone Fracture ◽  
Hearing Outcomes ◽  
Conductive Hearing ◽  
Facial Function

Abstract Background Traumatic ossicular disruption (TOD) usually had a severe conductive hearing loss, the exploratory tympanotomy is critical for the diagnosis and improve hearing. Endoscopic ear surgery (EES) is becoming popular in the last decade, we conducted a retrospective study to explore the efficacy of EES for management of TOD and the accompanied injuries.Methods A retrospective study was performed on 18 ears (16 patients) of TOD with intact TM from May 2017 to Jun 2019 in our department. EES was conducted to check the ossicular chain anomalies, and to perform the ossiculoplasty and facial nerve (FN) decompression depending on the intraoperative findings. Hearing outcomes and surgical complications were assessed at 6 months postoperatively. Results The incus injury was the most common type of TOD, which was observed in 14 ears (77.8%), stapes suprastructure fracture was observed in 4 ears (22.2%). FN injury was found in 4 out of 13 ears with temporal bone fracture (TBF), the injury sites were mainly located in the perigeniculate area and the tympanic segment of FN. It showed the postoperative average pure-tone average (PTA) gain was 22.9 ± 9.5 dB, and the average ABG closure was 22.2 ± 8.3 dB, ABG closure to 20 dB or less and ABG closure to 10 dB or less were achieved in 18 ears (100%) and 14 ears (77.8%), respectively. The facial function achieved favorable recovery of House-Brackmann (H-B) grade Ⅰ (3 ears) and grade Ⅱ (1 ear) in all the 4 cases in 6 months after surgery. No iatrogenic FN paralysis and significant sensorineural hearing loss were observed. Conclusions ESS was effective in diagnosis and management of TOD and the accompanied otologic injuries, such as FN paralysis, it showed favorable surgical outcomes. ESS provides an alternative method to manage TOD with the advantage of excellent vision and less invasion.

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