Glial nuclear aggregates of superoxide dismutase-1 are regularly present in patients with amyotrophic lateral sclerosis

Acta Neuropathologica ◽

10.1007/s00401-011-0805-3 ◽

2011 ◽

Vol 121 (5) ◽

pp. 623-634 ◽

Author(s):

Karin Forsberg ◽

Peter M. Andersen ◽

Stefan L. Marklund ◽

Thomas Brännström

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Superoxide Dismutase 1 ◽

Lateral Sclerosis

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Transgenic mouse model for familial amyotrophic lateral sclerosis with superoxide dismutase-1 mutation

Neuropathology ◽

10.1046/j.1440-1789.2001.00361.x ◽

2001 ◽

Vol 21 (1) ◽

pp. 82-92 ◽

Author(s):

Noriyuki Shibata

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Mouse Model ◽

Transgenic Mouse ◽

Transgenic Mouse Model ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Lateral Sclerosis

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Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superoxide dismutase 1 mutant

Proceedings of the National Academy of Sciences ◽

10.1073/pnas.94.14.7606 ◽

1997 ◽

Vol 94 (14) ◽

pp. 7606-7611 ◽

Author(s):

L. I. Bruijn ◽

M. F. Beal ◽

M. W. Becher ◽

J. B. Schulz ◽

P. C. Wong ◽

...

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Hydroxyl Radicals ◽

Tyrosine Nitration ◽

Superoxide Dismutase 1 ◽

Familial Als ◽

Lateral Sclerosis

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Superoxide dismutase 1 mutants related to amyotrophic lateral sclerosis induce endoplasmic stress in neuro2a cells

Journal of Neurochemistry ◽

10.1111/j.1471-4159.2007.05053.x ◽

2008 ◽

Vol 104 (4) ◽

pp. 993-1005 ◽

Author(s):

Yeo Kyoung Oh ◽

Ki Soon Shin ◽

Junying Yuan ◽

Shin Jung Kang

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Superoxide Dismutase 1 ◽

Neuro2a Cells ◽

Lateral Sclerosis

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New consensus research on neuropathological aspects of familial amyotrophic lateral sclerosis with superoxide dismutase 1 (SOD1) gene mutations: Inclusions containing SOD1 in neurons and astrocytes

Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders ◽

10.1080/14660820050515160 ◽

2000 ◽

Vol 1 (3) ◽

pp. 163-184 ◽

Author(s):

Shinsuke Kato ◽

Miki Takikawa ◽

Kenji Nakashima ◽

Asao Hirano ◽

Don W Cleveland ◽

...

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Gene Mutations ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Sod1 Gene ◽

Lateral Sclerosis

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Neuropathology of familial amyotrophic lateral sclerosis patients with superoxide dismutase 1 gene mutation

Neuropathology ◽

10.1111/j.1440-1789.1998.tb00132.x ◽

1998 ◽

Vol 18 (4) ◽

pp. 363-369 ◽

Author(s):

Asao Hirano

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Gene Mutation ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Lateral Sclerosis

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Phenotype of Transgenic Mice Carrying a Very Low Copy Number of the Mutant Human G93A Superoxide Dismutase-1 Gene Associated with Amyotrophic Lateral Sclerosis

PLoS ONE ◽

10.1371/journal.pone.0099879 ◽

2014 ◽

Vol 9 (6) ◽

pp. e99879 ◽

Author(s):

Jeffrey S. Deitch ◽

Guillermo M. Alexander ◽

Andrew Bensinger ◽

Steven Yang ◽

Juliann T. Jiang ◽

...

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Transgenic Mice ◽

Copy Number ◽

Superoxide Dismutase 1 ◽

Low Copy Number ◽

Lateral Sclerosis

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MRI detects early hindlimb muscle atrophy in Gly93Ala superoxide dismutase-1 (G93A SOD1) transgenic mice, an animal model of familial amyotrophic lateral sclerosis

NMR in Biomedicine ◽

10.1002/nbm.861 ◽

2004 ◽

Vol 17 (1) ◽

pp. 28-32 ◽

Author(s):

Keith J. Brooks ◽

Mark D. W. Hill ◽

Paul D. Hockings ◽

David G. Reid

Keyword(s):

Animal Model ◽

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Transgenic Mice ◽

Muscle Atrophy ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Hindlimb Muscle ◽

G93a Sod1 ◽

Lateral Sclerosis

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Correction to: the Cysteine (Cys) Residues Cys-6 and Cys-111 in Mutant Superoxide Dismutase 1 (SOD1) A4V Are Required for Induction of Endoplasmic Reticulum Stress in Amyotrophic Lateral Sclerosis

Journal of Molecular Neuroscience ◽

10.1007/s12031-020-01617-5 ◽

2020 ◽

Vol 70 (9) ◽

pp. 1369-1369

Author(s):

Emma R. Perri ◽

Sonam Parakh ◽

Marta Vidal ◽

Prachi Mehta ◽

Yi Ma ◽

...

Keyword(s):

Endoplasmic Reticulum ◽

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Endoplasmic Reticulum Stress ◽

Superoxide Dismutase 1 ◽

Lateral Sclerosis

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Novel behavioural characteristics of the superoxide dismutase 1 G93A ( SOD1 G93A ) mouse model of amyotrophic lateral sclerosis include sex‐dependent phenotypes

Genes Brain & Behavior ◽

10.1111/gbb.12604 ◽

2019 ◽

Vol 19 (2) ◽

Author(s):

Fabian Kreilaus ◽

Stefan Guerra ◽

Rebecca Masanetz ◽

Victoria Menne ◽

Justin Yerbury ◽

...

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Mouse Model ◽

Superoxide Dismutase 1 ◽

Behavioural Characteristics ◽

G93a Sod1 ◽

Lateral Sclerosis ◽

Sod1 G93a Mouse

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Familial Amyotrophic Lateral Sclerosis with a Novel G85S Mutation of Superoxide Dismutase 1 Gene: Clinical Features of Lower Motor Neuron Disease

Internal Medicine ◽

10.2169/internalmedicine.49.2720 ◽

2010 ◽

Vol 49 (2) ◽

pp. 183-186 ◽

Author(s):

Takanori Takazawa ◽

Ken Ikeda ◽

Takehisa Hirayama ◽

Kiyokazu Kawabe ◽

Yoshikazu Nakamura ◽

...

Keyword(s):

Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase ◽

Motor Neuron ◽

Motor Neuron Disease ◽

Clinical Features ◽

Lower Motor Neuron ◽

Familial Amyotrophic Lateral Sclerosis ◽

Superoxide Dismutase 1 ◽

Lower Motor Neuron Disease ◽

Lateral Sclerosis

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