Spontaneously Ruptured Dural Ectasia in a Patient with Marfan Syndrome: a Case Report and Discussion of the Challenges Faced

2021 ◽  
Vol 4 (1) ◽  
Author(s):  
Ifigeneia Gioti ◽  
Dimitrios Nikolaides ◽  
Constantinos Picolas ◽  
Konstantinos Faropoulos
Keyword(s):  
Case Report ◽  
Marfan Syndrome ◽  
Dural Ectasia

scholarly journals Marfan syndrome and symptomatic dural ectasia: A case report and literature review

2014 ◽  
Vol 11 (2) ◽  
pp. 83-85
Author(s):  
Si Nae Eom ◽  
Dong Chan Kim ◽  
Kwang Nam Kim ◽  
Sung Hye Kim
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Marfan Syndrome ◽  
Dural Ectasia

scholarly journals Marfan syndrome and symptomatic dural ectasia: A case report and literature review

2014 ◽  
Vol 11 (2) ◽  
pp. 103
Author(s):  
Si Nae Eom ◽  
Dong Chan Kim ◽  
Kwang Nam Kim ◽  
Sung Hye Kim
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Marfan Syndrome ◽  
Dural Ectasia

Dystrophic Lumbar Kyphoscoliosis Associated with Giant Dural Ectasia in a 19-Year-Old Patient with Neurofibromatosis Type 1. Case Report

2020 ◽  
Vol 2 (10) ◽  
pp. 1926-1930
Author(s):  
Nicolas Plais ◽  
Peter H. Connolly ◽  
Renaud Lafage ◽  
Debra Jacobs ◽  
Virginie Lafage ◽  
...  
Keyword(s):  
Case Report ◽  
Neurofibromatosis Type 1 ◽  
Neurofibromatosis Type ◽  
Dural Ectasia

scholarly journals Stanford type B aortic dissection associated with pregnancy in patients with Marfan syndrome—A case report and review of the literature

2010 ◽  
Vol 1 (3) ◽  
pp. e180-e183 ◽  
Author(s):  
Hiroshi Nishino ◽  
Kenji Suda ◽  
Akitaka Kuramaoto ◽  
Yoshihiro Honda ◽  
Kiyoko Takemiya ◽  
...  
Keyword(s):  
Case Report ◽  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Type B ◽  
Review Of The Literature ◽  
Type B Aortic Dissection ◽  
Stanford Type B

Sacral erosion and insufficiency fracture secondary to dural ectasia in patient with Marfan syndrome

2016 ◽  
Vol 16 (5) ◽  
pp. e301-e302
Author(s):  
Hossein Elgafy ◽  
Nicholas Peters ◽  
Robert M. Wetzel
Keyword(s):  
Marfan Syndrome ◽  
Insufficiency Fracture ◽  
Dural Ectasia

scholarly journals A Case Report of Marfan Syndrome with Literature Review

2015 ◽  
Vol 4 (4) ◽  
pp. 269
Author(s):  
Hemanth Kumar Kalla ◽  
Swarna Kumari ◽  
CH Rama rao ◽  
MKR Parthasarathy ◽  
S Surya prakash Reddy ◽  
...  
Keyword(s):  
Case Report ◽  
Connective Tissue ◽  
Marfan Syndrome ◽  
Clinical Signs ◽  
Connective Tissue Disorder ◽  
Multiple Organ ◽  
Review Of The Literature ◽  
Organ Systems ◽  
Loin Pain ◽  
Routine Physical Examination

Marfan syndrome(MFS) is a connective tissue disorder that affects multiple organ systems. Cardiovascular, ocular, and skeletal abnormalities are cardinal features of the syndrome. Its incidence is among the highest of any heritable disorder.Most patients who have Marfan syndrome are usually diagnosed incidentally when they present for a routine physical examination for various reasons. The purpose of this paper is to provide a review of the literature, as well as describe a 22-year-old male with MFS and right hydroureteronephrosis diagnosed incidentally when he attended our hospital for complaints of fever and right loin pain. This case report emphasizes importance of “Revised Ghent criteria” for the diagnosis of MFS and highlights various clinical signs of MFS<strong>.</strong>

scholarly journals Concurrent End-Stage Cardiomyopathy and Aortic Disease in Patients with Marfan Syndrome: A Case Report and Literature Review

2021 ◽  
Author(s):  
Timothy Smith ◽  
Jose Sleiman ◽  
Nikita Zadneulitca ◽  
Cedric Sheffield ◽  
Viviana Navas ◽  
...  
Keyword(s):  
Heart Failure ◽  
Case Report ◽  
Literature Review ◽  
Marfan Syndrome ◽  
Aortic Disease ◽  
Connective Tissue Disorder ◽  
Orthotopic Heart Transplantation ◽  
Bentall Procedure ◽  
Life Saving ◽  
End Stage

Abstract Background: Marfan syndrome (MFS) is a connective tissue disorder that can lead to aortic disease, arrhythmias and heart failure. Many centers are reluctant to offer orthotopic heart transplantation (OHT) for patients with MFS with concurrent aortic disease due to complexity of the surgery and perceived inferior results when compared to patients without MFS. Methods: We present a case of a patient with MFS with previous Bentall procedure who underwent successful OHT, accompanied by a literature review on OHT performed for patients with MFS. Results and Conclusions: Patients with MFS who underwent OHT had no difference in mortality compared to patients without MFS. Even though OHT is technically more challenging when combined with concurrent intervention for aortic disease, it should be considered as a life-saving operation for patients with MFS.

scholarly journals Marfan Syndrome: A Case Report

2020 ◽  
Vol 9 (3) ◽  
pp. 136-142
Author(s):  
Mediha Gönenç Ortaköylü ◽  
Tuğçe Özen ◽  
Belma Akbaba Bağcı ◽  
Esma Seda Akalın Karaca
Keyword(s):  
Case Report ◽  
Marfan Syndrome
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