Two-Stage Total Cardioaortic Replacement for End-Stage Heart and Aortic Disease in Marfan Syndrome: Case Report and Review of the Literature

2009 ◽  
Vol 28 (9) ◽  
pp. 958-963 ◽  
Author(s):  
Keshava Rajagopal ◽  
Joseph G. Rogers ◽  
Andrew J. Lodge ◽  
Jeffrey G. Gaca ◽  
Richard L. McCann ◽  
...  
Author(s):  
Timothy Smith ◽  
Jose Sleiman ◽  
Nikita Zadneulitca ◽  
Cedric Sheffield ◽  
Viviana Navas ◽  
...  

Abstract Background: Marfan syndrome (MFS) is a connective tissue disorder that can lead to aortic disease, arrhythmias and heart failure. Many centers are reluctant to offer orthotopic heart transplantation (OHT) for patients with MFS with concurrent aortic disease due to complexity of the surgery and perceived inferior results when compared to patients without MFS. Methods: We present a case of a patient with MFS with previous Bentall procedure who underwent successful OHT, accompanied by a literature review on OHT performed for patients with MFS. Results and Conclusions: Patients with MFS who underwent OHT had no difference in mortality compared to patients without MFS. Even though OHT is technically more challenging when combined with concurrent intervention for aortic disease, it should be considered as a life-saving operation for patients with MFS.


The Foot ◽  
2021 ◽  
pp. 101796
Author(s):  
Elias S. Vasiliadis ◽  
Christos Vlachos ◽  
Angelos Antoniades ◽  
Eftychios Papagrigorakis ◽  
Matthaios Bakalakos ◽  
...  

2010 ◽  
Vol 1 (3) ◽  
pp. e180-e183 ◽  
Author(s):  
Hiroshi Nishino ◽  
Kenji Suda ◽  
Akitaka Kuramaoto ◽  
Yoshihiro Honda ◽  
Kiyoko Takemiya ◽  
...  

2015 ◽  
Vol 4 (4) ◽  
pp. 269
Author(s):  
Hemanth Kumar Kalla ◽  
Swarna Kumari ◽  
CH Rama rao ◽  
MKR Parthasarathy ◽  
S Surya prakash Reddy ◽  
...  

Marfan syndrome(MFS) is a connective tissue disorder that affects multiple organ systems. Cardiovascular, ocular, and skeletal abnormalities are cardinal features of the syndrome. Its incidence is among the highest of any heritable disorder.Most patients who have Marfan syndrome are usually diagnosed incidentally when they present for a routine physical examination for various reasons. The purpose of this paper is to provide a review of the literature, as well as describe a 22-year-old male with MFS and right hydroureteronephrosis diagnosed incidentally when he attended our hospital for complaints of fever and right loin pain. This case report emphasizes importance of “Revised Ghent criteria” for the diagnosis of MFS and highlights various clinical signs of MFS<strong>.</strong>


2017 ◽  
Vol 56 (6) ◽  
pp. 729-732 ◽  
Author(s):  
Tomoaki Takata ◽  
Hiroki Chikumi ◽  
Shota Morishita ◽  
Shintaro Hamada ◽  
Shotaro Hoi ◽  
...  

2015 ◽  
Vol 4 (4) ◽  
pp. 269
Author(s):  
Hemanth Kumar Kalla ◽  
Swarna Kumari ◽  
CH Rama rao ◽  
MKR Parthasarathy ◽  
S Surya prakash Reddy ◽  
...  

Marfan syndrome(MFS) is a connective tissue disorder that affects multiple organ systems. Cardiovascular, ocular, and skeletal abnormalities are cardinal features of the syndrome. Its incidence is among the highest of any heritable disorder.Most patients who have Marfan syndrome are usually diagnosed incidentally when they present for a routine physical examination for various reasons. The purpose of this paper is to provide a review of the literature, as well as describe a 22-year-old male with MFS and right hydroureteronephrosis diagnosed incidentally when he attended our hospital for complaints of fever and right loin pain. This case report emphasizes importance of “Revised Ghent criteria” for the diagnosis of MFS and highlights various clinical signs of MFS<strong>.</strong>


Nephron ◽  
2020 ◽  
Vol 144 (7) ◽  
pp. 358-362
Author(s):  
James A.D. Shand ◽  
Howard C. Potter ◽  
Helen L. Pilmore ◽  
Tim Cundy ◽  
Rinki Murphy

2019 ◽  
Vol 126 ◽  
pp. 581-587 ◽  
Author(s):  
Konstantinos Paterakis ◽  
Alexandros Brotis ◽  
Maria Bakopoulou ◽  
Christos Rountas ◽  
Efthymios Dardiotis ◽  
...  

Sign in / Sign up

Export Citation Format

Share Document