scholarly journals An Approach to the Identification of Anomalies and Etiologies in Neonates with Identified or Suspected VACTERL (Vertebral Defects, Anal Atresia, Tracheo-Esophageal Fistula with Esophageal Atresia, Cardiac Anomalies, Renal Anomalies, and Limb Anomalies) Association

2014 ◽  
Vol 164 (3) ◽  
pp. 451-457.e1 ◽  
Author(s):  
Benjamin D. Solomon ◽  
Linda A. Baker ◽  
Kelly A. Bear ◽  
Bridget K. Cunningham ◽  
Philip F. Giampietro ◽  
...  
Keyword(s):  
Esophageal Atresia ◽  
Esophageal Fistula ◽  
Anal Atresia ◽  
Renal Anomalies ◽  
Cardiac Anomalies ◽  
Limb Anomalies ◽  
Vertebral Defects

scholarly journals THE POSSIBILITIES OF MUSEUM STUDYING OF VACTERL SYNDROME

2017 ◽  
Vol 3 (4) ◽  
pp. 201-205
Author(s):  
V.V. Gargin ◽  
Yu.V. Kurchanova ◽  
Yu.I. Ivanteeva
Keyword(s):  
Museum Collection ◽  
Esophageal Fistula ◽  
Pathological Anatomy ◽  
Anal Atresia ◽  
Renal Anomalies ◽  
Museum Exhibits ◽  
Perinatal Pathology ◽  
National Medical ◽  
Vertebral Anomalies ◽  
Medical University

The article deals with VACTERL association, particularly non randomly associated birth defects, typically defined by the presence of at least three of the following congenital malformations: vertebral anomalies, anal atresia, cardiac malformations, tracheo-esophageal fistula, renal anomalies, and limb abnormalities. Museum collection of the Department of Pathological Anatomy of Kharkiv National Medical University, which devoted to prenatal and perinatal pathology, has numerous museum exhibits representing this pathology. The specimens help to discuss pathological anatomy of each of these defects.KeyWords:  fetus, VACTERL, congenital defect.Курчанова Ю.В., Івантеєва Ю.І., Гаргін В.В.МОЖЛИВОСТІ МУЗЕЙНОГО ВИВЧЕННЯ СИНДРОМУ VACTERLСтатья посвящена синдрому VACTERL - закономерно объединенным врожденным патологиям развития. Для постановки синдрома необходимо присутствие не менее трех из следующих дефектов: аномалии позвоночника, анальная атрезия, пороки сердца, трахеопищеводный свищ, почечные аномалии и аномалии конечностей. Музейная коллекция кафедры патологической анатомии ХНМУ, посвященная пре- и перинатальной патологии, имеет множество учебных макропрепаратов, которые описывают синдром VACTERL. На их примере мы обсудим каждый характерный дефект развития.Ключевые слова: плод, VACTERL, врожденный дефект Курчанова Ю.В., Ивантеева Ю.И., Гаргин В.В.ВОЗМОЖНОСТИ МУЗЕЙНОГО ИЗУЧЕНИЯ СИНДРОМА VACTERLСтаття присвячена синдрому VACTERL - закономірно об'єднаним вродженим патологіям розвитку. Для постановки синдрому необхідна наявність не менше трьох з наступних дефектів: аномалії хребта, анальна атрезія, пороки серця, трахеостравоходний свищ, ниркові аномалії і аномалії кінцівок. Музейна колекція кафедри патологічної анатомії ХНМУ, присвячена пре- і перинатальній патології, має велику кількість навчальних макропрепаратів, які описують синдром VACTERL. На їхньому прикладі ми обговоримо кожен характерний дефект розвитку.Ключові слова: плід, VACTERL, вроджений дефект

Surgeon-Level Variation in Outcome following Esophageal Atresia Repair Is Not Explained by Volume

2020 ◽  
Author(s):  
Elizabeth O'Connor ◽  
Bruce Jaffray
Keyword(s):  
Esophageal Atresia ◽  
Sequential Analysis ◽  
Predictors Of Outcome ◽  
Renal Anomalies ◽  
Explanatory Variables ◽  
Regional Center ◽  
Confounding Variables ◽  
Objective Outcome ◽  
Surgeon Performance ◽  
Case Mortality

Abstract Introduction To assess whether there is a difference in operative outcome for esophageal atresia (EA) depending on a surgeon's seniority as defined by years in consultant practice or number of cases performed. In addition a Clavien–Dindo score was used to sequentially analyze the outcome of each surgeon's EA procedure. Materials and Methods All repairs performed over 22 years in an English regional center were analyzed. Outcomes were: death, anastomotic leak, need for dilatation, need for more than three dilatations, need for fundoplication, and a Clavien–Dindo adverse outcome of ≥3b. Possible explanatory variables were: number of prior repairs by the surgeon, surgeon's years of consultant experience. We also examined the effect of variables intrinsic to the infant as possible confounding variables and as independent predictors of outcome. Results A total of 190 repairs were performed or supervised by 12 consultants. There was no significant association between consultant experience and any objective outcome. However, sequential analysis suggests there is variation between surgeons in the incidence of Clavien–Dindo events of ≥3b. Performance showed deterioration in one case. Mortality was explicable by cardiac and renal anomalies. Conclusion There are surgeon-level variations in outcomes for the procedure of EA repair, but they are not explained by volume. Surgeon performance can deteriorate. Our study would not support the concept that patient outcomes could be improved by concentrating the provision of this surgery to fewer hospitals or surgeons.

Esophageal atresia and tracheo-esophageal fistula

2017 ◽  
Vol 26 (2) ◽  
pp. 67-71 ◽  
Author(s):  
David C. van der Zee ◽  
Stefaan H.A. Tytgat ◽  
Maud Y.A. van Herwaarden
Keyword(s):  
Esophageal Atresia ◽  
Esophageal Fistula

TRACHEO-ESOPHAGEAL FISTULA WITHOUT ESOPHAGEAL ATRESIA—CONGENITAL AND RECURRENT

PEDIATRICS ◽  
1956 ◽  
Vol 18 (6) ◽  
pp. 935-942
Author(s):  
William K. Sieber ◽  
Bertram R. Girdany
Keyword(s):  
Aqueous Solution ◽  
Esophageal Atresia ◽  
Early Recognition ◽  
Esophageal Fistula ◽  
Clinical Problems

The clinical problems presented by 10 infants with congenital and recurrent tracheo-esophageal fistulas are discussed. A roentgenographic technique of identification of tracheo-esophageal fistulas, using the aqueous solution Dionosil®, is described. The intermittent patency of the fistula is stressed. Recurrent tracheo-esophageal fistula may be a complication in infants operated upon for esophageal atresia with tracheo-esophageal fistula. The results in this series demonstrate the urgency of early recognition and prompt therapy.

Esophageal atresia and tracheo-esophageal fistula

2003 ◽  
pp. 337-352 ◽  
Author(s):  
Paul Losty ◽  
Colin Baillie
Keyword(s):  
Esophageal Atresia ◽  
Esophageal Fistula
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