Obstruction to Left Coronary Artery Blood Flow Secondary to Obliteration of the Coronary Ostium in Supravalvular Aortic Stenosis

1988 ◽  
Vol 45 (1) ◽  
pp. 16-20 ◽  
Author(s):  
Monica M. Martin ◽  
John H. Lemmer ◽  
Elizabeth Shaffer ◽  
Macdonald Dick ◽  
Edward L. Bove
Keyword(s):  
Blood Flow ◽  
Coronary Artery ◽  
Aortic Stenosis ◽  
Left Coronary Artery ◽  
Supravalvular Aortic Stenosis ◽  
Coronary Ostium ◽  
Artery Blood Flow

scholarly journals A rare combination of cardiovascular anomaly: Supravalvular aortic stenosis and congenital absence of right coronary artery

2021 ◽  
Author(s):  
Yunfei Ling ◽  
Song Jiayi ◽  
Tiange Li ◽  
Ke Lin
Keyword(s):  
Blood Flow ◽  
Cardiopulmonary Bypass ◽  
Coronary Artery ◽  
Aortic Stenosis ◽  
Right Coronary Artery ◽  
Aortic Root ◽  
Supravalvular Aortic Stenosis ◽  
Cardiac Symptoms ◽  
Cardiovascular Ct ◽  
Cardiovascular Anomaly

We reported a case of a 3-month-old infant presented with supravalvular aortic stenosis with congenital right coronary artery deficiency. According to cardiovascular CT results, Doty technique was adopted to restore the aortic root geometry under cardiopulmonary bypass. An angioplasty was performed to establish right coronary blood flow at the same time. The patient had no abnormal cardiac symptoms after surgery.

scholarly journals A family with a newelastingene mutation: broad clinical spectrum, including sudden cardiac death

2010 ◽  
Vol 21 (1) ◽  
pp. 62-65 ◽  
Author(s):  
André Jakob ◽  
Sheila Unger ◽  
Raoul Arnold ◽  
Jochen Grohmann ◽  
Cornelia Kraus ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Sudden Cardiac Death ◽  
Aortic Stenosis ◽  
General Anaesthesia ◽  
Cardiac Death ◽  
Left Coronary Artery ◽  
Vascular Malformations ◽  
The Other ◽  
Supravalvular Aortic Stenosis ◽  
New Mutation

AbstractSupravalvular aortic stenosis is associated with the Williams–Beuren syndrome, but it also occurs in a non-syndromatic congenital form. Anelastingene mutation of chromosome 7q11.23 is responsible in both cases. The vascular features are identical. These patients have a higher risk of sudden death, particularly when undergoing diagnostic or surgical procedures. We report the account of a family with a new mutation in theelastingene. Screening over three generations revealed eight affected individuals. The cardiac and vascular malformations ranged from mild asymptomatic supravalvular aortic stenosis and isolated dysplastic atrioventricular valves to diffuse arterial hypoplasia. Two infants presented arteries affected at multiple locations, including the left coronary artery. Both died of sudden cardiac death and myocardial ischaemia, one while under general anaesthesia for cardiac catheterisation, and the other perioperatively. We discuss the pathophysiological aspects in these patients that deserve consideration before any general anaesthesia is administered.

scholarly journals Atresia of the proximal left coronary artery associated with supravalvular aortic stenosis

1974 ◽  
Vol 67 (2) ◽  
pp. 266-271 ◽  
Author(s):  
Hugh D. Allen ◽  
James H. Moller ◽  
Augustin Formanek ◽  
Demetre Nicoloff
Keyword(s):  
Coronary Artery ◽  
Aortic Stenosis ◽  
Left Coronary Artery ◽  
Supravalvular Aortic Stenosis

ORIGIN OF THE LEFT CORONARY ARTERY FROM THE PULMONARY ARTERY WITHOUT COLLATERAL CIRCULATION

PEDIATRICS ◽  
1963 ◽  
Vol 32 (4) ◽  
pp. 588-593
Author(s):  
Robert M. Armer ◽  
Harris B. Shumacker ◽  
Paul R. Lurie ◽  
Charles Fisch
Keyword(s):  
Coronary Artery ◽  
Pulmonary Artery ◽  
Collateral Circulation ◽  
Left Coronary Artery ◽  
Main Pulmonary Artery ◽  
Coronary Ostium ◽  
Coronary Insufficiency ◽  
Electrocardiographic Findings ◽  
Patch Graft ◽  
Painful Shock

A 4-month-old infant with repeated painful shock-like episodes was shown by the progression of electrocardiographic findings to have coronary insufficiency and finally a myocardial infarction. Selective cineangio-cardiography demonstrated anomalous origin of the left coronary artery from the main pulmonary artery with flow from the pulmonary artery to the myocardium. Preparations for surgical transplantation to the aorta were being made when the infant died. The feasibility of the proposed operation was demonstrated post mortem. A segment of the main pulmonary artery was excised with the coronary ostium at its base and converted into a tube which was anastomosed to the aorta. The defect in the pulmonary artery was repaired with a patch graft of Dacron.

Coronary Artery Vasomotion and Post-Stenotic Coronary Artery Blood Flow after Intracoronary Lacidipine in Patients with Ischaemic Heart Disease

Drugs ◽  
1999 ◽  
Vol 57 (Supplement 1) ◽  
pp. 19-26
Author(s):  
Corrado Vassanelli ◽  
Giuliana Menegatti ◽  
Alberto Marini ◽  
Federico Beltrame ◽  
Jonata Molinari ◽  
...  
Keyword(s):  
Blood Flow ◽  
Heart Disease ◽  
Coronary Artery ◽  
Ischaemic Heart Disease ◽  
Artery Blood Flow
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