A common mutation of the long-chain hydroxyacyl-Co-A dehydrogenase enzyme of mitochondrial fatty acid beta-oxidation is not associated with non-alcoholic steatohepatitis

Dehydrogenase Enzyme ◽

A common mutation of the long-chain hydroxyacyl-Co-A dehydrogenase enzyme of mitochondrial fatty acid beta-oxidation is not associated with non-alcoholic steatohepatitis

Gastroenterology ◽

10.1016/s0016-5085(01)82697-4 ◽

2001 ◽

Vol 120 (5) ◽

pp. A543-A543

Author(s):

R MERRIMAN ◽

B BACON ◽

E BRUNT ◽

B TETRI ◽

M PETERS ◽

...

Keyword(s):

Fatty Acid ◽

Common Mutation ◽

Beta Oxidation ◽

Alcoholic Steatohepatitis ◽

Dehydrogenase Enzyme ◽

Non-alcoholic steatohepatitis and a common mutation in the long-chain hydroxyacyl-coenzyme a dehydrogenase enzyme of mitochondrial fatty acid B-oxidation

Gastroenterology ◽

10.1016/s0016-5085(00)85728-5 ◽

2000 ◽

Vol 118 (4) ◽

pp. A899

Author(s):

Raphael B. Merriman ◽

Marion G. Peters ◽

Arnold W. Strauss

Keyword(s):

Fatty Acid ◽

Coenzyme A ◽

Common Mutation ◽

Alcoholic Steatohepatitis ◽

Dehydrogenase Enzyme ◽

A mouse model of Long-Chain 3-Ketoacyl-CoA Thiolase deficlency of mitochondrial fatty acid beta-oxidation is associated with low body mass, cold intoterance and hepatic steatosis

Gastroenterology ◽

10.1016/s0016-5085(01)80526-6 ◽

2001 ◽

Vol 120 (5) ◽

pp. A107-A107

Author(s):

R MERRIMAN ◽

W QIN ◽

A STRAUSS

Keyword(s):

Fatty Acid ◽

Mouse Model ◽

Hepatic Steatosis ◽

Body Mass ◽

Beta Oxidation ◽

A mouse model of Long-Chain 3-Ketoacyl-CoA Thiolase deficlency of mitochondrial fatty acid beta-oxidation is associated with low body mass, cold intoterance and hepatic steatosis

Gastroenterology ◽

10.1016/s0016-5085(08)80526-4 ◽

2001 ◽

Vol 120 (5) ◽

pp. A107

Author(s):

Raphael B. Merriman ◽

Wenning Qin ◽

Arnold W. Strauss

Keyword(s):

Fatty Acid ◽

Mouse Model ◽

Hepatic Steatosis ◽

Body Mass ◽

Beta Oxidation ◽

Rat very-long-chain acyl-CoA dehydrogenase, a novel mitochondrial acyl-CoA dehydrogenase gene product, is a rate-limiting enzyme in long-chain fatty acid beta-oxidation system. cDNA and deduced amino acid sequence and distinct specificities of the cDNA-expressed protein.

Journal of Biological Chemistry ◽

10.1016/s0021-9258(17)32278-0 ◽

1994 ◽

Vol 269 (29) ◽

pp. 19088-19094

Author(s):

T. Aoyama ◽

I. Ueno ◽

T. Kamijo ◽

T. Hashimoto

Keyword(s):

Fatty Acid ◽

Chain Fatty Acid ◽

Beta Oxidation ◽

Long Chain Fatty Acid ◽

Dehydrogenase Gene ◽

Chain Acyl ◽

Rate Limiting ◽

Oxidation System ◽

The enzymology of mitochondrial fatty acid beta-oxidation and its application to follow-up analysis of positive neonatal screening results

Journal of Inherited Metabolic Disease ◽

10.1007/s10545-010-9104-8 ◽

2010 ◽

Vol 33 (5) ◽

pp. 479-494 ◽

Cited By ~ 113

Author(s):

Ronald J. A. Wanders ◽

Jos P. N. Ruiter ◽

Lodewijk IJlst ◽

Hans R. Waterham ◽

Sander M. Houten

Keyword(s):

Fatty Acid ◽

Neonatal Screening ◽

Beta Oxidation ◽

Fatty Acid Beta Oxidation

Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders.

Journal of Clinical Investigation ◽

10.1172/jci113271 ◽

1987 ◽

Vol 80 (6) ◽

pp. 1778-1783 ◽

Cited By ~ 74

Author(s):

R J Wanders ◽

C W van Roermund ◽

M J van Wijland ◽

R B Schutgens ◽

J Heikoop ◽

...

Keyword(s):

Fatty Acids ◽

Fatty Acid ◽

Zellweger Syndrome ◽

Long Chain Fatty Acids ◽

Beta Oxidation ◽

Peroxisomal Disorders ◽

Cultured Skin ◽

Long Chain ◽

Peroxisomal Fatty Acid

Clinical and biological features at diagnosis in mitochondrial fatty acid beta-oxidation defects: a French pediatric study of 187 patients

Journal of Inherited Metabolic Disease ◽

10.1007/s10545-012-9542-6 ◽

2012 ◽

Vol 36 (5) ◽

pp. 795-803 ◽

Cited By ~ 52

Author(s):

Julien Baruteau ◽

Philippe Sachs ◽

Pierre Broué ◽

Michèle Brivet ◽

Hendy Abdoul ◽

...

Keyword(s):

Fatty Acid ◽

Beta Oxidation ◽

Biological Features ◽

Pediatric Study ◽

Fatty Acid Beta Oxidation

Long-chain fatty acyl-CoA synthetase 1 promotes prostate cancer progression by elevation of lipogenesis and fatty acid beta-oxidation

Oncogene ◽

10.1038/s41388-021-01667-y ◽

2021 ◽

Author(s):

Yongjie Ma ◽

Junyi Zha ◽

XiangKun Yang ◽

Qianjin Li ◽

Qingfu Zhang ◽

...

Keyword(s):

Prostate Cancer ◽

Fatty Acid ◽

Cancer Progression ◽

Fatty Acyl ◽

Prostate Cancer Progression ◽

Beta Oxidation ◽

Acylcarnitine profiles in fibroblasts from patients with respiratory chain defects can resemble those from patients with mitochondrial fatty acid [beta ]-oxidation disorders

Metabolism ◽

10.1053/meta.2002.30521 ◽

2002 ◽

Vol 51 (3) ◽

pp. 366-371 ◽

Cited By ~ 33

Author(s):

Keow Giak Sim ◽

Kevin Carpenter ◽

Judith Hammond ◽

John Christodoulou ◽

Bridget Wilcken

Keyword(s):

Fatty Acid ◽

Respiratory Chain ◽

Beta Oxidation ◽

Chain Defects ◽

Respiratory Chain Defects