Cranial hyperostosis and hearing loss (A new syndrome?)

1986 ◽  
Vol 100 (10) ◽  
pp. 1187-1193
Author(s):  
W. H. Moesker ◽  
R. A. Tange
Keyword(s):  
Hearing Loss ◽  
Differential Diagnosis ◽  
Facial Paralysis ◽  
Middle Ear ◽  
Musculoskeletal Disease ◽  
Mother And Daughter ◽  
Skeletal Disorder ◽  
Hereditary Conditions

SummaryWe present two patients, mother and daughter, with a skeletal disorder of the skull, hearing loss and in one of them recurrent facial paralysis. In one patient middle ear exploration was performed. The malleus and incus were found to be fixed in the epitympanum.The differential diagnosis is discussed. We reviewed all known hereditary conditions with hearing loss and musculoskeletal disease but we could not accept any of these diagnoses for our patients.

Facial Paralysis in Children: Differential Diagnosis

1981 ◽  
Vol 89 (5) ◽  
pp. 841-848 ◽  
Author(s):  
Mark May ◽  
Thomas J. Fria ◽  
Frank Blumenthal ◽  
Hugh Curtin
Keyword(s):  
Hearing Loss ◽  
Differential Diagnosis ◽  
Herpes Zoster ◽  
Facial Paralysis ◽  
Positive Family History ◽  
Pseudobulbar Palsy ◽  
Slow Progression ◽  
Facial Edema ◽  
Physical Findings ◽  
Fissured Tongue

The differential diagnosis in 170 patients between birth and 18 years of age is reviewed. There are a number of obvious physical findings and historical features that allow one to make a diagnosis rather quickly. Pain, vesicles, a red pinna, vertigo, and sensorineural hearing loss suggest herpes zoster oticus. Slow progression beyond three weeks, recurrent facial paralysis involving the same side, facial twitching, weakness, or no return of function after six months indicate a neoplasm. Bilateral simultaneous facial paralysis indicates a cause other than Bell's palsy, such as Guillain-Barré syndrome, pseudobulbar palsy, sarcoidosis, and leukemia. Recurrent facial paralysis associated with a fissured tongue, facial edema, and a positive family history should suggest Melkersson-Rosenthal syndrome.

scholarly journals Childhood Middle Ear Tuberculosis–A Rare Case Report

1970 ◽  
Vol 27 (2) ◽  
pp. 93-94
Author(s):  
PK Swain ◽  
SA Mallik ◽  
A Thapalial
Keyword(s):  
Hearing Loss ◽  
Differential Diagnosis ◽  
Case Report ◽  
Middle Ear ◽  
Facial Nerve Paralysis ◽  
Review Of The Literature ◽  
Key Words Tuberculosis ◽  
Nerve Paralysis ◽  
Rare Case Report ◽  
Middle Ear Cleft

Tuberculosis rarely affects the middle ear cleft; the disease is a curiosity and not often considered in the differential diagnosis of otorrhea. The diagnosis is thus made too late, with resulting complications such as irreversible hearing loss and facial nerve paralysis. A case report with review of the literature is presented, emphasizing that tuberculosis should be considered in the differential diagnosis of chronic ear infection in children. In our case direct nosocomial spread of tuebrculous bacilli has been attributed. Key words: Tuberculosis; otitis media, hearing loss & facial paralysis.   doi:10.3126/jnps.v27i2.1589 J. Nepal Paediatr. Soc. Vol.27(2) p.93-94

Facial Paralysis: Traumatic Neuromas Vs. Facial Nerve Neoplasms

1988 ◽  
Vol 98 (1) ◽  
pp. 53-59 ◽  
Author(s):  
Carl Snyderman ◽  
Mark May ◽  
Michael A. Berman ◽  
Hugh D. Curtin
Keyword(s):  
Differential Diagnosis ◽  
Facial Nerve ◽  
Facial Paralysis ◽  
Middle Ear ◽  
Clinical Presentation ◽  
Neural Tissue ◽  
Diagnosis And Treatment ◽  
Radiographic Appearance ◽  
Middle Ear Disease

Traumatic neuromas (TN) are benign proliferations of neural tissue that may occur without disruption of the facial nerve. The clinical presentation, as well as the radiographic appearance, may suggest neoplastic involvement of the facial nerve. Histologically, they may closely resemble neurilemomas (Schwannomas) or neurofibromas. Three cases of TN of the facial nerve associated with facial paralysis are presented here. Unlike previously reported cases, these tumors were not associated with chronic inflammatory middle ear disease. TN must be considered in the differential diagnosis and treatment of facial paralysis.

scholarly journals Malignant Mucosal Melanoma of the Eustachian Tube With Extension Into the Ipsilateral External Ear Canal: A Case Report and Review of the Literature

2020 ◽  
pp. 014556132090481
Author(s):  
Lifeng Li ◽  
Nyall R. London ◽  
Xiaohong Chen
Keyword(s):  
Hearing Loss ◽  
Differential Diagnosis ◽  
Eustachian Tube ◽  
Middle Ear ◽  
Mucosal Melanoma ◽  
External Ear ◽  
Review Of The Literature ◽  
Ear Canal ◽  
External Ear Canal ◽  
External Canal

Mucosal melanoma arising in the middle ear or eustachian tube is uncommon. We present a patient with hearing loss and otalgia found to have mucosal melanoma which occurred in the eustachian tube with extension into the middle ear cavity and external ear canal. Otologic clinics was consulted and biopsy of the mass located at the external canal was performed to ascertain the pathological diagnosis. The patient refused immunotherapy and surgery instead of undergoing radiotherapy and died from hepatic metastasis 8 months later. The mucosal melanoma originated from the eustachian tube with extension into the external ear canal is exceedingly rare, and the differential diagnosis should be considered for tumors in external ear canal.

scholarly journals Pintail Comb Injury as a Rare Cause of Penetrating Temporal Bone Trauma With Facial Paralysis

2020 ◽  
pp. 014556132096893
Author(s):  
Dylan Jacob Cooper ◽  
Stanley Pelosi
Keyword(s):  
Hearing Loss ◽  
Case Report ◽  
Facial Nerve ◽  
Tympanic Membrane ◽  
Temporal Bone ◽  
Facial Paralysis ◽  
Middle Ear ◽  
Complete Resolution ◽  
Bone Trauma ◽  
Nerve Dysfunction

We present a case of novel penetrating temporal bone trauma with a pintail comb causing facial paralysis. We describe a 42-year-old woman with acute facial paralysis, hearing loss, and dizziness following accidental tympanic membrane puncture. The patient underwent middle ear exploration with tympanoplasty and was found to have an intact but severely edematous facial nerve. The patient demonstrated less than 90% degeneration under electroneuronography and was treated medically without decompression, and by 6 months had exhibited complete resolution of facial nerve dysfunction with normal hearing. This case report highlights a unique cause of penetrating temporal bone trauma and supports the utility of electroneuronography in predicting the likelihood of recovery and need for decompression in patients where the facial nerve has obvious signs of trauma but remains grossly intact.

Air Conduction, Bone Conduction, and Soft Tissue Conduction Audiograms in Normal Hearing and Simulated Hearing Losses

2015 ◽  
Vol 26 (01) ◽  
pp. 101-108 ◽  
Author(s):  
Cahtia Adelman ◽  
Adi Cohen ◽  
Adi Regev-Cohen ◽  
Shai Chordekar ◽  
Rachel Fraenkel ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Differential Diagnosis ◽  
Soft Tissue ◽  
Middle Ear ◽  
Bone Conduction ◽  
Auditory Stimulation ◽  
Threshold Shift ◽  
N Application ◽  
Similar Threshold ◽  
Air Conduction

Background: In order to differentiate between a conductive hearing loss (CHL) and a sensorineural hearing loss (SNHL) in the hearing-impaired individual, we compared thresholds to air conduction (AC) and bone conduction (BC) auditory stimulation. The presence of a gap between these thresholds (an air-bone gap) is taken as a sign of a CHL, whereas similar threshold elevations reflect an SNHL. This is based on the assumption that BC stimulation directly excites the inner ear, bypassing the middle ear. However, several of the classic mechanisms of BC stimulation such as ossicular chain inertia and the occlusion effect involve middle ear structures. An additional mode of auditory stimulation, called soft tissue conduction (STC; also called nonosseous BC) has been demonstrated, in which the clinical bone vibrator elicits hearing when it is applied to soft tissue sites on the head, neck, and thorax. Purpose: The purpose of this study was to assess the relative contributions of threshold determinations to stimulation by STC, in addition to AC and osseous BC, to the differential diagnosis between a CHL and an SNHL. Research Design: Baseline auditory thresholds were determined in normal participants to AC (supra-aural earphones), BC (B71 bone vibrator at the mastoid, with 5 N application force), and STC (B71 bone vibrator) to the submental area and to the submandibular triangle with 5 N application force) stimulation in response to 0.5, 1.0, 2.0, and 4.0 kHz tones. A CHL was then simulated in the participants by means of an ear plug. Separately, an SNHL was simulated in these participants with 30 dB effective masking. Study sample: Study sample consisted of 10 normal-hearing participants (4 males; 6 females, aged 20–30 yr). Data Collection and Analysis: AC, BC, and STC thresholds were determined in the initial normal state and in the presence of each of the simulations. Results: The earplug-induced CHL simulation led to a mean AC threshold elevation of 21–37 dB (depending on frequency), but not of BC and STC thresholds. The masking-induced SNHL led to a mean elevation of AC, BC, and STC thresholds (23–36 dB, depending on frequency). In each type of simulation, the BC threshold shift was similar to that of the STC threshold shift. Conclusions: These results, which show a similar threshold shift for STC and for BC as a result of these simulations, together with additional clinical and laboratory findings, provide evidence that BC thresholds likely represent the threshold of the nonosseous BC (STC) component of multicomponent BC at the BC stimulation site, and thereby succeed in clinical practice to contribute to the differential diagnosis. This also provides evidence that STC (nonosseous BC) stimulation at low intensities probably does not involve components of the middle ear, represents true cochlear function, and therefore can also contribute to a differential diagnosis (e.g., in situations where the clinical bone vibrator cannot be applied to the mastoid or forehead with a 5 N force, such as in severe skull fracture).

The Effect of Sensori-Neural Hearing Loss on Threshold-Duration Functions

1968 ◽  
Vol 11 (4) ◽  
pp. 842-852 ◽  
Author(s):  
H. N. Wright
Keyword(s):  
Hearing Loss ◽  
Differential Diagnosis ◽  
Time Constant ◽  
Present Series ◽  
Auditory Disorders ◽  
Threshold Duration

Previous findings on the threshold for tones as a function of their duration have suggested that such functions may be systematically affected by sensori-neural hearing losses of cochlear origin. The present series of investigations was designed to explore this relation further and to determine also whether the amount of hearing loss present has any effect upon the results which are obtained. Preliminary studies were also carried out on a conductively impaired listener to indicate whether hearing losses of this type affect the threshold-duration function. The results indicate that the threshold-duration function is systematically affected by sensori-neural hearing losses of cochlear origin. This effect is manifested by a progressive shortening of the time constant relating threshold to duration and is not uniquely related to the amount of hearing loss present. The results obtained from the conductively impaired listener suggested that this type of hearing loss has no effect on the threshold-duration function, thereby implying that such functions may contribute significantly to the differential diagnosis of auditory disorders.

Sign in / Sign up

Export Citation Format

Share Document