Pseudoaneurysm of the sinus of Valsalva caused by infective endocarditis in a 7-year-old child with congenital heart disease

2021 ◽  
pp. 1-3
Author(s):  
Wataru Kashimada ◽  
Tao Fujioka ◽  
Jotaro Kobayashi
Keyword(s):  
Congenital Heart Disease ◽  
Infective Endocarditis ◽  
Aortic Valve ◽  
Trisomy 21 ◽  
Congenital Heart ◽  
Septal Defect ◽  
Subaortic Stenosis ◽  
Sinus Of Valsalva ◽  
History Of ◽  
Patch Closure

Abstract We report a case of a pseudoaneurysm in the sinus of Valsalva, secondary to infective endocarditis in a child with trisomy 21. The patient had a history of subaortic stenosis, bicuspid aortic valve, and ventricular septal defect. Patch closure of the ostium of the pseudoaneurysm and aortic valve replacement was performed. The patient was discharged without severe complications.

Reconstruction of a Previously Repaired Aortic Valve Destroyed by Infective Endocarditis: Case Report

2016 ◽  
Vol 8 (3) ◽  
pp. 408-410
Author(s):  
Tomas Chalela ◽  
Viktor Hraska
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Case Report ◽  
Infective Endocarditis ◽  
Aortic Valve ◽  
Congenital Heart ◽  
Congenital Aortic Stenosis ◽  
Life Threatening ◽  
History Of ◽  
Uncommon Condition

Infective endocarditis (IE) is an uncommon condition among patients with congenital heart disease, however it can be life threatening. The usual management includes replacement of the affected valve, especially in patients with aortic valve compromise, and is even more common in previously repaired valves. In this case report, we describe the successful reconstruction of an aortic root destroyed by IE, in a patient with history of ballooning of a congenital aortic stenosis.

Aortic Valve Repair for Adult Congenital Heart Disease

Circulation ◽  
2000 ◽  
Vol 102 (suppl_3) ◽  
Author(s):  
Vivek Rao ◽  
Glen S. Van Arsdell ◽  
Tirone E. David ◽  
Anthony Azakie ◽  
William G. Williams
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Aortic Valve ◽  
Congenital Heart ◽  
Septal Defect ◽  
Aortic Valve Repair ◽  
Subaortic Stenosis ◽  
Valve Repair ◽  
Aortic Valve Leaflets

Background —Aortic valve–preserving procedures have resulted in excellent outcomes in selected patients, particularly those with normal aortic valve leaflets and dilated aortic roots. However, several congenital heart lesions are associated with abnormal aortic valve leaflets. The long-term results of aortic valve repair for these lesions are not well defined. Methods and Results —We reviewed the clinical records of 54 adult (age >18 years) patients who underwent repair of congenital abnormalities of the aortic valve between 1976 and September 1999. Follow-up data were available on 52 (96%) patients (mean 50±67 months, range 1 to 266). Patients underwent repair at a mean age of 34±14 years with associated diagnoses of subaortic stenosis (n=10), ventricular septal defect with prolapsing aortic valve (n=17), bicuspid aortic valve (n=23), sinus of Valsalva aneurysm (n=10), and bacterial endocarditis (n=2). There was 1 operative death (1.9%) and 3 late deaths. Survival at 5 and 10 years was 98±2% and 74±12%, respectively. Freedom from reoperation was 74±9% and 51±15% at 5 and 10 years, respectively. The presence of a ventricular septal defect predicted failure of valve repair (59% versus 22%, P =0.01). A bicuspid aortic valve, subaortic stenosis, or the requirement for mitral valve surgery did not affect outcomes. Conclusions —Aortic valve repair in adult patients with congenital heart disease can be performed with minimal morbidity and mortality rates. The medium-term results of repair are acceptable, regardless of valvular or associated pathology. However, only 31 patients (57%) demonstrated long-term competence of the aortic valve, suggesting that most adult patients with congenital aortic valve disease will eventually require aortic valve replacement.

scholarly journals Surgical repair of perimembranous ventricular septal defect and aortic regurgitation in an adult patient with Laubry-Pezzi syndrome.

2020 ◽  
pp. 15-17
Keyword(s):  
Congenital Heart Disease ◽  
Aortic Valve ◽  
Ventricular Septal Defect ◽  
Congenital Heart ◽  
Septal Defect ◽  
Surgical Repair ◽  
Aortic Valve Insufficiency ◽  
Perimembranous Ventricular Septal Defect ◽  
Venturi Effect ◽  
Valve Insufficiency

Laubry-Pezzi syndrome is a congenital heart disease that consist in a prolapse of aortic valve cusping into a subjacent ventricular septal defect due to Venturi effect. It results in progressive aortic valve insufficiency. The perimembranous type is the most common due to the proximity of the aortic annulus to such defects. The aim of this report is to highlight the specificity of the diagnosis and the surgical management of this syndrome in adult patients.

Infective Endocarditis

1982 ◽  
Vol 3 (7) ◽  
pp. 226-230
Author(s):  
Jane W. Newburger ◽  
Alexander S. Nadas
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Infective Endocarditis ◽  
Congenital Heart ◽  
Septal Defect ◽  
Structural Heart Disease ◽  
Prolonged Treatment ◽  
Predisposing Factor ◽  
Prosthetic Valves ◽  
Flow Through

Infective endocarditis is one of the most serious complications of structural heart disease. It occurs primarily in children and adolescents with preexisting anatomic abnormalities of the heart, with an incidence that varies with the specific cardiac lesion. An identifiable potential source of bacteremia precedes infective endocarditis in approximately one fifth of cases in children. The high mortality (19% to 25%), morbidity, and prolonged treatment course of infective endocarditis make its diagnosis, management, and prevention a matter of great importance to pediatricians. PREDISPOSING FACTORS Structural Heart Disease Cardiac malformations are the major predisposing factor to infective endocarditis. Although rheumatic heart disease has gradually declined as a substrate for endocarditis, the increased survival of children with congenital heart disease in the past two decades has increased the number and age of children susceptible to infective endocarditis. In general, lesions leading to a high velocity of blood flow through a heart valve, septal defect, or blood vessel are associated with increased susceptibility to endocarditis (Table 1). Children at highest risk are those with cyanotic congenital heart disease (eg, tetralogy of Fallot), ventricular septal defect with aortic regurgitation, left-sided valvar regurgitation or obstruction, prosthetic valves, and recent cardiac surgery. Endocarditis is exceedingly uncommon in individuals with isolated atrial septal defect secundum and with mild pulmonic valve stenosis.

Cardiovascular

2019 ◽  
pp. 1-34
Author(s):  
Tanya M. Monaghan ◽  
James D. Thomas
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Infective Endocarditis ◽  
Aortic Valve Disease ◽  
Congenital Heart ◽  
Septal Defect ◽  
Ductus Arteriosus ◽  
Coarctation Of The Aorta ◽  
Valve Disease ◽  
Prosthetic Valves

This chapter is about cardiovascular medicine, and covers mitral regurgitation, mitral stenosis, aortic regurgitation, aortic stenosis, mixed mitral valve disease, mixed aortic valve disease, tricuspid regurgitation, prosthetic valves, ventricular septal defect, atrial septal defect, hypertrophic cardiomyopathy, coarctation of the aorta, persistent ductus arteriosus, Fallot’s tetralogy, dextrocardia, infective endocarditis, and congenital heart disease diagrams.

scholarly journals Sinus of Valsalva Aneurysm and Infective Endocarditis Involving a Bicuspid Aortic Valve in an Infant With Trisomy 21

2018 ◽  
Vol 8 (3) ◽  
pp. 763-768
Author(s):  
Nicole A. Croom ◽  
Nicole Therrien ◽  
Michael Chambliss ◽  
Philip C. Ursell
Keyword(s):  
Infective Endocarditis ◽  
Aortic Valve ◽  
Bicuspid Aortic Valve ◽  
Trisomy 21 ◽  
Aortic Wall ◽  
Febrile Illness ◽  
Valve Leaflet ◽  
Sinus Of Valsalva ◽  
Sinus Of Valsalva Aneurysm

A 19-month-old girl with trisomy 21 and a congenitally bicuspid aortic valve died following a short febrile illness. Autopsy disclosed pericarditis, epimyocardial abscess, infective endocarditis, and a sinus of Valsalva aneurysm. Microscopy demonstrated continuity between the aortic wall and valve leaflet, consistent with an acquired aneurysm. Abnormal hemodynamics associated with the valve malformation likely facilitated endocarditis.

scholarly journals Comorbidities in children with Down syndrome: experience in a tertiary care hospital of Bangladesh

2021 ◽  
Vol 11 (3) ◽  
pp. 191-196
Author(s):  
Fahmida Zabeen ◽  
Fauzia Mohsin ◽  
Eva Jesmin ◽  
Sharmin Mahbuba ◽  
M Quamrul Hassan
Keyword(s):  
Congenital Heart Disease ◽  
Down Syndrome ◽  
Heart Disease ◽  
Trisomy 21 ◽  
Congenital Heart ◽  
Thyroid Dysfunction ◽  
Septal Defect ◽  
Tertiary Care ◽  
Care Hospital ◽  
Children With Down Syndrome

Background: Down syndrome or trisomy 21 is one of the most common chromosomal disorders with moderate intellectual disability. In addition to mental retardation, this syndrome is associated with different congenital anomalies and characteristic dysmorphic features. Affected individuals are more susceptible to congenital heart disease and digestive anomalies, pulmonary complications, immune and endocrine system disorders. While several international studies have shown association of co-morbidities with trisomy 21, there is insufficient data available in Bangladesh.The present study aimed to evaluate the associated co-morbidities in children with Down syndrome. Methods: A cross-sectional study was conducted among pediatric cases with Down syndrome who attended the endocrine outpatient department (OPD) of BIRDEM General Hospital from June 2006 to December 2016. The cases were diagnosed either by Karyotyping or by characteristic phenotypes.The clinical and laboratory data of the patients were collected from outpatient history records for analysis. Results: There were total 42 children with Down syndrome, with mean age 4.2 years at assessment and female predominance (1.47:1). Thyroid dysfunction was the most common (69%) followed by congenital heart disease (57%). Among the thyroid disorders, acquired hypothyroidism was found in 55% cases, congenital hypothyroidism in 41% cases and only one had hyperthyroidism. Isolated patent ductus arteriosus (PDA) and atrial septal defect (ASD) comprised the commonest single congenital heart disease found in 53% and combined atrioventricular septal defect was the commonest among complex congenital cardiac defect observed in our study. Both thyroid dysfunction and congenital heart disease were found more in female children with Down syndrome than their male counterpart and it was found statistically significant. Fifty percent of our Down syndrome cases were referred from other healthcare centers to address developmental delay. Conclusion: Hypothyroidism and congenital heart disease are frequently associated in Down syndrome children in Bangladesh. This calls for developing awareness among health professionals to diagnose comorbidities at an early stage and to form recommendations for long term follow up. BIRDEM Med J 2021; 11(3): 191-196

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