Inappropriate shock delivery by an implantable cardioverter-defibrillator due to electrical interference with a refrigerator in a 4-year-old child

2021 ◽  
pp. 1-3
Author(s):  
Sezen Gulumser Sisko ◽  
Hasan Candas Kafali ◽  
Yakup Ergul
Keyword(s):  
Ventricular Fibrillation ◽  
Implantable Cardioverter Defibrillator ◽  
Inappropriate Shock ◽  
Long Qt ◽  
Shock Delivery ◽  
Cardioverter Defibrillator ◽  
Qt Syndrome ◽  
Implantable Cardioverter Defibrillator Shock ◽  
Defibrillator Shock ◽  
Electrical Interference

Abstract We report a patient with long QT syndrome who received an inappropriate implantable cardioverter-defibrillator shock due to electrical interference from a refrigerator. This electrical interference was mistakenly detected as an episode of ventricular fibrillation and ended with an inappropriate delivery of shock without any warning symptoms before.

Abstract 17128: Primary Prevention With Implantable Cardioverter Defibrillator in High-risk Long-QT Syndrome Patients

Circulation ◽  
2015 ◽  
Vol 132 (suppl_3) ◽  
Author(s):  
Yitschak Biton ◽  
Spencer Rosero ◽  
Arthur J Moss ◽  
Ilan Goldenberg ◽  
Scott Mcnitt ◽  
...  
Keyword(s):  
Primary Prevention ◽  
High Risk ◽  
Implantable Cardioverter Defibrillator ◽  
Long Qt Syndrome ◽  
Inappropriate Shock ◽  
Long Qt ◽  
Cardioverter Defibrillator ◽  
Increased Risk ◽  
Β Blockers ◽  
Qt Syndrome

Background: Implantable cardioverter defibrillator (ICD) is currently indicated for the treatment of long QT syndrome (LQTS) patients who survived aborted cardiac arrest. However, data regarding the role of ICD in primary prevention in patients with LQTS is scarce. Methods: The study population comprised 212 LQTS patients (65% genotype positive) from the Rochester LQTS Registry who had ICD implantation for primary prevention. Cox regression model was used to identify clinical variables that were associated with appropriate shock and inappropriate shock. The efficacy of β-blockers was determined using a time-dependent analysis. Results: During a median follow up time of 9.2±4.9 years the cumulative event rates of appropriate shocks and inappropriate shocks were 23% and 34% respectively. In the entire cohort appropriate shock was associated with QTc ≥ 550 msec (HR=3.94; CI 2.08-7.46; p<0.001) and prior syncope on β-blockers (HR=1.92;(CI 1.01-3.65, p=0.047), β-blockers trended to be protective (HR=0.52; CI 0.26-1.07; p=0.075). Importantly, prior syncope was only important if it happened while on β-blockers. Inappropriate shock was significantly associated with age below 15 at implantation (HR=1.94; CI 1.11-3.38; p=0.019). In patients with positive genotype, appropriate shock was associated with QTc ≥ 550 msec (HR=5.37; CI 2.38-12.10; p<0.001), implantation age ≤ 15 years (HR=2.77; CI 1.08-7.11; p=0.034), LQT2 vs. LQT1 (HR=2.47; CI 0.93-6.52; p=0.069), and multiple mutations vs. LQT1 (HR=2.87; CI 0.88-9.42; p=0.081); β-blockers were significantly protective (HR=0.23, CI 0.09-0.59, p=0.002). Conclusions: Among LQTS patients in whom ICD is implanted for primary prevention, QTc duration and history of syncope while on β-blockers therapy are associated increased risk for appropriate shock. β-blocker treatment remains important in this high-risk group. Those with an ICD implanted before age 15 were at a higher risk of receiving an inappropriate shock.

scholarly journals Outcome by Sex in Patients With Long QT Syndrome With an Implantable Cardioverter Defibrillator

2020 ◽  
Vol 9 (19) ◽  
Author(s):  
Arwa Younis ◽  
Mehmet K. Aktas ◽  
Spencer Rosero ◽  
Valentina Kutyifa ◽  
Bronislava Polonsky ◽  
...  
Keyword(s):  
Ventricular Tachycardia ◽  
Ventricular Fibrillation ◽  
Implantable Cardioverter Defibrillator ◽  
Long Qt Syndrome ◽  
Syndrome Type ◽  
Long Qt ◽  
Cardioverter Defibrillator ◽  
Life Threatening ◽  
Qt Syndrome

Background Sex differences in outcome have been reported in patients with congenital long QT syndrome. We aimed to report on the incidence of time‐dependent life‐threatening events in male and female patients with long QT syndrome with an implantable cardioverter defibrillator (ICD). Methods and Results A total of 60 patients with long QT syndrome received an ICD for primary or secondary prevention indications. Life‐threatening events were evaluated from the date of ICD implant and included ICD shocks for ventricular tachycardia, ventricular fibrillation, or death. ICDs were implanted in 219 women (mean age 38±13 years), 46 girls (12±5 years), 55 men (43±17 years), and 40 boys (11±4 years). Mean follow‐up post‐ICD implantation was 14±6 years for females and 12±6 years for males. At 15 years of follow‐up, the cumulative probability of life‐threatening events was 27% in females and 34% in males (log‐rank P =0.26 for the overall difference). In the multivariable Cox model, sex was not associated with significant differences in risk first appropriate ICD shock (hazard ratio, 0.83 female versus male; 95% CI, 0.52–1.34; P =0.47). Results were similar when stratified by age and by genotype: long QT syndrome type 1 (LQT1), long QT syndrome type 2 (LQT2), and long QT syndrome type 3 (LQT3). Incidence of inappropriate ICD shocks was higher in males versus females (4.2 versus 2.7 episodes per 100 patient‐years; P =0.018), predominantly attributed to atrial fibrillation. The first shock did not terminate ventricular tachycardia/ventricular fibrillation in 48% of females and 62% of males ( P =0.25). Conclusions In patients with long QT syndrome with an ICD, the risk and rate of life‐threatening events did not significantly differ between males and females regardless of ICD indications or genotype. In a substantial proportion of patients with long QT syndrome, first shock did not terminate ventricular tachycardia/ventricular fibrillation.

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