Cortical Auditory Evoked Potentials in Auditory Neuropathy Spectrum Disorder: Clinical Implications

2011 ◽  
Vol 21 (1) ◽  
pp. 31-37 ◽  
Author(s):  
Garrett Cardon ◽  
Anu Sharma

Standard clinical audiologic assessments have proven useful in the detection and diagnosis of auditory neuropathy spectrum disorder (ANSD). However, beyond initial diagnosis, clinicians have fewer tools to appropriately manage infants and young children with ANSD. While cortical auditory evoked potentials (CAEP) are not currently used routinely in the management of children with ANSD, mounting evidence suggests that they are not only recordable in this population, but that they may provide useful information regarding treatment and behavioral outcomes in children with ANSD. The report discusses the potential clinical utility of CAEPs in children with ANSD, using a case illustration.

2018 ◽  
Vol 83 (4) ◽  
pp. 15 ◽  
Author(s):  
M. R. Lalayants ◽  
N. B. Brazhkina ◽  
E. N. Geptner ◽  
A. V. Kruglov ◽  
V. V. Barrlyak ◽  
...  

2007 ◽  
Vol 18 (05) ◽  
pp. 380-390 ◽  
Author(s):  
Wendy Pearce ◽  
Maryanne Golding ◽  
Harvey Dillon

Infants with auditory neuropathy and possible hearing impairment are being identified at very young ages through the implementation of hearing screening programs. The diagnosis is commonly based on evidence of normal cochlear function but abnormal brainstem function. This lack of normal brainstem function is highly problematic when prescribing amplification in young infants because prescriptive formulae require the input of hearing thresholds that are normally estimated from auditory brainstem responses to tonal stimuli. Without this information, there is great uncertainty surrounding the final fitting. Cortical auditory evoked potentials may, however, still be evident and reliably recorded to speech stimuli presented at conversational levels. The case studies of two infants are presented that demonstrate how these higher order electrophysiological responses may be utilized in the audiological management of some infants with auditory neuropathy. Los niños con neuropatía auditiva y posibles posibles trastornos auditivos están siendo identificados a edades tempranas con la implementación de programas de tamizaje auditivo. El diagnóstico se basa en la evidencia de una función coclear normal pero de una función anormal del tallo cerebral. Esta falta de función normal de tallo cerebral es muy problemática cuando se trata de prescribir amplificación en niños pequeños, porque las fórmulas de prescripción requieren el insumo de los umbrales auditivos que se estiman normalmente a partir de las respuestas del tallo cerebral ante estímulos tonales. Sin esta información, existe una gran incertidumbre en cuanto a la adaptación final. Los potenciales evocados auditivos corticales pueden, sin embargo, registrarse con confiabilidad a partir de estímulos de lenguaje presentados a niveles de intensidad para la conversación. Se presenta el estudio de dos casos de niños, que demuestran como estas respuestas electrofisiológicas de orden mayor pueden utilizarse en el manejo audiológico de algunos niños con neuropatía auditiva.


2021 ◽  
pp. 1-13
Author(s):  
Katherine Myers ◽  
Nannette Nicholson

Objective The aim of this mini-systematic review was to evaluate the evidence reporting speech, language, and auditory behavioral outcome measures for children with a diagnosis of auditory neuropathy spectrum disorder (ANSD) who received cochlear implants (CIs) prior to 3 years of age. Method A mini-systematic review of the literature supporting evidence-based practices was performed. Two databases were searched utilizing a search strategy derived from the PICO (patient, intervention, comparison, outcome) framework. Peer-reviewed articles published between 2009 and 2019 evaluating children with a diagnosis of ANSD who were implanted prior to 3 years of age with a range of speech, language, and auditory behavioral outcomes were included. Four articles meeting inclusion criteria were critically appraised for reputable research design and risks of bias. Each of the four studies was assigned a level of evidence for effectiveness and quality assessment rating. Results Evidence supports cochlear implantation as an appropriate intervention for children with ANSD. Improvements in outcome performance were observed in all the included studies. Children with ANSD fit with CIs can achieve outcomes similar to children with sensorineural hearing loss and CIs, despite the heterogeneity of ANSD. Conclusion These findings have implications for clinical practice and for future research with current CI technology for facilitating parent education, counseling, and realistic expectations for children with ANSD and CIs.


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