scholarly journals Partial anomalous pulmonary venous connection detected during right pneumonectomy

2019 ◽  
Vol 30 (3) ◽  
pp. 497-498
Author(s):  
Bülent Mustafa Yenigün ◽  
Gökhan Kocaman ◽  
Ayşegül Gürsoy Çoruh ◽  
Rıfat Murat Akal
Keyword(s):  
Lung Cancer ◽  
Congenital Anomaly ◽  
Case Report ◽  
Surgical Treatment ◽  
Septal Defect ◽  
Lung Resection ◽  
Rare Congenital Anomaly ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection ◽  
Lung Resections

Abstract Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital anomaly. Generally, it is seen on the right side and is associated with an atrial septal defect. Herein, we present a case of a 50-year-old male patient with a supracardiac type PAPVC detected during pneumonectomy for a right hilar mass. This is the second case report in the literature presenting surgical treatment of both lung cancer and PAPVC using pneumonectomy. Thoracic surgeons should be aware of this anomaly when they are planning to perform a major lung resection. If PAPVC and lung cancer are in the same lobe, anatomical lung resections including pneumonectomy can be safely performed.

scholarly journals Late diagnosis of total anomalous connection of pulmonary veins during the puerperium

2019 ◽  
Vol 2 (2) ◽  
pp. 4-8
Author(s):  
Susan Pumacayo-Cárdenas
Keyword(s):  
Congenital Anomaly ◽  
Cardiac Magnetic Resonance ◽  
Magnetic Resonance ◽  
Physical Examination ◽  
Septal Defect ◽  
Pulmonary Veins ◽  
Heart Murmur ◽  
Rare Congenital Anomaly ◽  
Hands And Feet ◽  
Anomalous Pulmonary Venous Connection

The total anomalous pulmonary venous connection (TAPVC) is a rare congenital anomaly. We present a case of a 36-year-old woman, in the postpartum period during the physical examination there was a heart murmur and beating in hands and feet. Cardiac magnetic resonance reported supracardiac TAPVC and large atrial septal defect. The survival of these patients is very uncommon in adults and even worse during pregnancy.

scholarly journals The Ruptured Pericardial Cyst to the Right Atrium: A Case Report

2020 ◽  
Author(s):  
Freidoun SABZI ◽  
Reza FARAJI
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Chest Pain ◽  
Right Atrium ◽  
Imaging Modality ◽  
Physical Exam ◽  
Right Atrial ◽  
Rare Congenital Anomaly ◽  
Pericardial Cysts ◽  
The Right

The pericardial cysts (PC) are rare congenital anomaly. They are usually asymptomatic or incidentally found during surgery or by an imaging modality. We report a 35-yr-old man referred to Imam Ali Hospital, Kermanshah, western Iran in 2017, with palpitation, chest pain and dyspnea and physical exam revealed sign and symptoms of right atrial compression and tamponade.

scholarly journals Infective endocarditis of an asymptomatic congenital aorta-right atrial tunnel: a case report

2020 ◽  
Vol 4 (2) ◽  
pp. 1-5
Author(s):  
Eustaquio Maria Onorato ◽  
Anna Maria Costante ◽  
Daniele Andreini ◽  
Antonio L Bartorelli
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Surgical Treatment ◽  
Infective Endocarditis ◽  
Multimodality Imaging ◽  
Right Atrial ◽  
Rare Congenital Anomaly ◽  
Non Invasive ◽  
Case Summary ◽  
Asymptomatic Patients

Abstract Background Aorta-right atrial tunnel (ARAT) is a rare congenital anomaly whose aetiology and incidence are unknown. It might represent a diagnostic and therapeutic challenge requiring a combination of imaging modalities and an integrated teamwork. Case summary We report a case of a 23-year-old man with an asymptomatic ARAT complicated by infective endocarditis, diagnosed with non-invasive multimodality imaging, and successfully treated with a catheter-based approach. Discussion Aorta-right atrial tunnel closure in asymptomatic patients is still a matter of debate. Considering the risk of serious complications surgical treatment might be recommended soon after diagnosis. In selected cases, catheter-based closure might represent a safe, effective, and less invasive alternative to traditional surgical approach.

Bilateral scimitar syndrome

2004 ◽  
Vol 14 (4) ◽  
pp. 447-449 ◽  
Author(s):  
Mohamed Kabbani ◽  
Naser Haider ◽  
Riyadh Abu-Sulaiman
Keyword(s):  
Congenital Anomaly ◽  
Rare Variant ◽  
Scimitar Syndrome ◽  
Rare Congenital Anomaly ◽  
Horseshoe Lung ◽  
The Right ◽  
Pulmonary Cyst ◽  
Anomalous Pulmonary Venous Connection

Scimitar syndrome is a rare congenital anomaly that affects classically the right lung and the heart. We present a rare variant that involves both lungs in association with totally anomalous pulmonary venous connection, horseshoe lung, and right pulmonary cyst.

CONGENITAL METACARPAL SYNOSTOSIS TREATED BY DOUBLE BONE BLOCKS TECHNIQUE: A CASE REPORT FROM THAILAND

Hand Surgery ◽  
2005 ◽  
Vol 10 (01) ◽  
pp. 131-134 ◽  
Author(s):  
Surut Jianmongkol ◽  
Tala Thammaroj ◽  
Kitiwan Vipulakorn
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Surgical Techniques ◽  
Rare Condition ◽  
Rare Congenital Anomaly

Congenital metacarpal synostosis is a rare congenital anomaly in the hand, especially in our area. There were several reports of surgical techniques for correction deformities. We report this rare condition in our hospital and treatment with the metacarpal osteotomy and double bone blocks technique of grafting.

scholarly journals SURGICAL TREATMENT OF ANOMALIES OF FIXATION OF THE COLON IN CHILDREN

2020 ◽  
Vol 19 (4) ◽  
pp. 32-36
Author(s):  
O. Bodnar
Keyword(s):  
Congenital Anomaly ◽  
Surgical Treatment ◽  
Clinical Symptoms ◽  
Clinical Manifestations ◽  
Results Of Treatment ◽  
Left Diaphragm ◽  
Comparative Group ◽  
The Right ◽  
Paroxysmal Pain ◽  
Over Time

Pyrrhic disease is a congenital anomaly that occurs during embryogenesis due to the fixation of the splenic angle of the colon by a short and highly located left transverse-diaphragmatic ligament, creating a sharp bend and forming a "wellbore". In this case the passage of feces on a cross colon becomes difficult, there is also its sagging to a small pelvis. This pathology is characterized by paroxysmal pain (aggravated by exercise and after eating) and prolonged constipation, which progresses over time. Hilaiditis syndrome is a rather rare pathology in which there is an interposition of the hepatic angle of the colon between the liver and the diaphragm. There are permanent and intermittent localizations. The work generalizes the experience of evaluation of clinical manifestations and remote results of treatment of children with chronic colostasis caused by fixation abnormalities of the colon. 58 children were detected to have Payre’s disease, with Cyilaiditi’s syndrome – 3 children. 24 patients with Payre’s disease and 2 Cyilaiditi’s syndrome were operated on. To assess the effectiveness of surgery, children were divided into two groups: I group – comparative and II group - experienced. In I group (n=12 children) – the analysis of surgical treatment was performed traditionally. In II group (n=14 children) – the analysis of surgical treatment was conducted by means of the methods proposed. Traditional surgical treatment of Payre’s disease in children was followed by relapse of chronic constipation in 45,45%, pain in 50%, flatulence in 33,33% and failure of the ileocoecal closing apparatus in 100% of children. Unsatisfactory outcomes of surgical treatment of Cyilaiditi’s syndrome was observed in a child from the comparative group. Relapse of clinical symptoms to a lesser degree than before the surgery was found in 1 child from the experienced group. To treat Payre’s disease the following operation is proposed: intersection of the left diaphragm-colon ligament, resection of transverse colon and colofixation of the left bending of the colon. To treat Cyilaiditi’s syndrome (in case of dolichoascendocolon) the following operation is suggested: hepatopexy, resection of the right bending of the colon with ascending transversal anastomosis “end to end”, fixing of right bending of the colon. Their reasonability is being proved.

scholarly journals Rare presentation of incomplete male urethral duplication: A case report and review of literature

2021 ◽  
Vol 9 (1) ◽  
pp. 292-296
Author(s):  
Orgeness J Mbwambo ◽  
Alex Mremi ◽  
Mohamed Mbarouk ◽  
Jasper Mbwambo ◽  
Frank Bright ◽  
...  
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Postoperative Period ◽  
Surgical Removal ◽  
Urethral Duplication ◽  
Review Of Literature ◽  
Rare Presentation ◽  
Rare Congenital Anomaly ◽  
Accessory Urethra

Urethral duplication is a rare congenital anomaly affecting mainly males. Here, we report a case of urethral duplication in a 19 years old male presented as a scrotal sinus discharging pus for 1 year. Surgical removal of accessory urethra was done and postoperative period was uneventful.

scholarly journals Novel technique of repairing right partial anomalous pulmonary venous connection with intact atrial septum using in situ interatrial septum as a flap in a 68-year-old-woman: a case report

2020 ◽  
Vol 15 (1) ◽  
Author(s):  
Atsushi Morishita ◽  
Ikuo Hagino ◽  
Hideyuki Tomioka ◽  
Seiichiro Katahira ◽  
Takeshi Hoshino ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Right Atrium ◽  
Septal Defect ◽  
Surgical Repair ◽  
Interatrial Septum ◽  
Pulmonary Artery Hypertension ◽  
Right Heart ◽  
Intact Atrial Septum ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection

Abstract Background Partial anomalous pulmonary venous connection draining into the right atrium with an intact atrial septum is a very rare clinical entity in the adult population. Partial anomalous pulmonary venous connection must be suspected as a differential diagnosis when the cause of right heart enlargement and pulmonary artery hypertension is unknown. Case presentation This study describes the surgical case of an isolated right partial anomalous pulmonary venous connection to the right atrium in a 68-year-old woman, who underwent tricuspid ring annuloplasty and right-sided maze procedure simultaneously. She had complaints of gradually progressing dyspnea on exertion. However, a diagnosis could not be established despite consultations at multiple hospitals for over a year. Right heart catheterization revealed severe pulmonary artery hypertension with a mean pulmonary artery pressure of 46 mmHg, step-up phenomenon of oxygen saturation at the mid-level of the right atrium with a pulmonary-to-systemic blood flow ratio of 2.4, and a pulmonary vascular resistance of 3.1 Wood Units. As medical treatment with pulmonary artery vasodilator therapy did not improve her symptoms, she underwent surgical repair. An atrial septal defect was created surgically with a curvilinear tongue-shaped cut. The right anomalous pulmonary veins were rerouted through the surgically created atrial septal defect into the left atrium with a baffle comprised of the interatrial septum flap, kept in continuity with the anterior margin and sutured while mobilizing the enlarged right atrium. The patient had an uneventful postoperative course and remains asymptomatic. Conclusions The described surgical technique could be considered an effective alternative for patients undergoing surgical repair for a partial anomalous pulmonary venous connection isolated to the right atrium. The indication for surgery must be judged on a case-by-case basis in these patients with prevalent systemic-to-pulmonary shunting.

scholarly journals Incidental Finding of Annular Pancreas in a Routine Cadaveric Dissection: Case Report

2019 ◽  
Vol 36 (04) ◽  
pp. 299-302
Author(s):  
Mythraeyee Prasad ◽  
Theresa Susan Kuriakose ◽  
Sipra Rout
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Duodenal Obstruction ◽  
Clinical Symptoms ◽  
Incidental Finding ◽  
Age Groups ◽  
Annular Pancreas ◽  
Present Case Report ◽  
Rare Congenital Anomaly ◽  
Variable Presentation

AbstractAnnular pancreas is a rare congenital anomaly that results from the malrotation of the ventral pancreatic bud. The presentation of annular pancreas varies: it can be asymptomatic or present clinical symptoms of duodenal obstruction that can affect all age groups, from newborns to adults. In the present case report, we describe a complete type of annular pancreas at the level of the second part of the duodenum, which was an incidental finding in a prosected specimen. This anomaly has significant clinical relevance to clinicians and radiologists due to its variable presentation. The embryological, clinical and radiological aspects of this congenital anomaly are discussed in detail in the present article.

Sign in / Sign up

Export Citation Format

Share Document