First-Trimester Diagnosis of Hypoplastic Left Heart Syndrome: A Case Report

2021 ◽  
Vol 37 (2) ◽  
pp. 185-192
Author(s):  
Emily Hildebrand
Keyword(s):  
Case Report ◽  
Mitral Valve ◽  
Aortic Valve ◽  
Early Detection ◽  
Hypoplastic Left Heart Syndrome ◽  
First Trimester ◽  
Cardiac Anomaly ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Hypoplastic left heart syndrome (HLHS) comprises a spectrum of left-sided heart anomalies resulting from left outflow or inflow obstruction. Obstruction most often occurs at the levels of the aortic valve and/or mitral valve due to stenosis or atresia. HLHS is a lethal cardiac anomaly if not treated within the first week of life. Knowledge of sonographic features could aid in early detection, which results in better planning and management of pregnancy. This report presents a case in which HLHS was discovered during a routine dating and viability sonogram, performed at 12 weeks’ gestation.

scholarly journals Comparison of Childhood Outcome by Mitral Valve and Aortic Valve Subtypes of Typical Hypoplastic Left Heart Syndrome

2018 ◽  
Vol 34 (1) ◽  
pp. 3-9
Author(s):  
Hirofumi Fukunaga ◽  
Makoto Nakamura ◽  
Shiro Ishikawa ◽  
Yoshihiko Kodama ◽  
Koichi Sagawa ◽  
...  
Keyword(s):  
Mitral Valve ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

scholarly journals Prenatal Diagnosis and Successful Palliation of Absent Aortic Valve with Hypoplastic Left Heart Syndrome: A Case Report and Review of Literature

2019 ◽  
Vol 09 (02) ◽  
pp. e121-e126
Author(s):  
Amna Qasim ◽  
Chelsea Johnson ◽  
Muhammad Aly ◽  
Ashraf Aly
Keyword(s):  
Prenatal Diagnosis ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Main Pulmonary Artery ◽  
Aortic Insufficiency ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Absent Aortic Valve ◽  
Aortic Valve Leaflets ◽  
Left Heart Syndrome

Introduction Congenital absence of the aortic valve leaflets is a rare association with hypoplastic left heart syndrome (HLHS). Case A 37-year-old pregnant woman was referred for fetal evaluation of possible HLHS at 22 weeks of gestation. The fetal echocardiogram (ECHO) was remarkable for a hypoplastic left atrium, nearly atretic mitral valve, small left ventricle, and a hypoplastic aortic valve with severe aortic insufficiency. A female infant was born at term and postnatal ECHO confirmed the above findings. In addition, there was complete absence of the aortic valve leaflets. The patient underwent Norwood's procedure at day 5 of life with atrial septectomy, over-sewing of the aortic valve annulus, and a 4 mm Sano's shunt between the right ventricle and the main pulmonary artery. She tolerated this surgery well and subsequently underwent a bidirectional Glenn's procedure at 8 months of life. Conclusion Prenatal diagnosis of absent aortic valve should be suspected in the presence of severe aortic insufficiency in the fetal ECHO. Early postnatal intervention is critical as those patients are likely to deteriorate quickly. The over-sewing of the aortic valve may be important to prevent coronary steal and myocardial hypoperfusion which could potentially be detrimental.

scholarly journals Improvement in right ventricular function by mitral valve closure in hypoplastic left heart syndrome

2021 ◽  
Author(s):  
Dai Asada ◽  
Yoko Kawai ◽  
Yoshinobu Maeda ◽  
Masaaki Yamagishi
Keyword(s):  
Mitral Valve ◽  
Right Ventricular ◽  
Ventricular Function ◽  
Hypoplastic Left Heart Syndrome ◽  
Right Ventricular Function ◽  
Left Ventricular ◽  
Valve Closure ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Abstract A male neonate presented with the aortic/mitral stenotic variant of hypoplastic left heart syndrome, wherein the suprasystemic left ventricular pressure and relatively large left ventricle had shifted the intraventricular septum. Despite bilateral pulmonary artery banding, the stroke volume was difficult to maintain owing to the compressed right ventricle, causing heart failure symptoms. Percutaneous balloon aortic valvuloplasty decreased the left ventricular pressure, restoring the right ventricular function. Norwood procedure with mitral valve closure after catheter intervention reduced the left ventricular size and improved the right ventricular function. This paper refers to the potential of mitral valve closure for hypoplastic left heart syndrome.

scholarly journals Fontan operation for hypoplastic left heart syndrome with absent aortic valve

2004 ◽  
Vol 128 (2) ◽  
pp. 315-316 ◽  
Author(s):  
Narutoshi Hibino ◽  
Yorikazu Harada ◽  
Takeshi Hiramatsu ◽  
Satoshi Yasukochi ◽  
Gengi Satomi
Keyword(s):  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Absent Aortic Valve ◽  
Left Heart Syndrome

Unguarded mitral orifice associated with hypoplastic left heart syndrome

2014 ◽  
Vol 25 (5) ◽  
pp. 1002-1005 ◽  
Author(s):  
Jennifer A. Su ◽  
John Ho ◽  
Pierre C. Wong
Keyword(s):  
Mitral Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Current Literature ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Valve Orifice ◽  
Mitral Orifice ◽  
Rare Malformation ◽  
Left Heart Syndrome

AbstractIn the spectrum of mitral valve anomalies, unguarded mitral orifice is an exceedingly rare malformation, with only four cases described in the current literature. All previously reported cases have been associated with discordant atrioventricular connections. We describe the first known case of unguarded mitral valve orifice, in the setting of atrioventricular concordance, in a newborn with hypoplastic left heart syndrome.

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