Unguarded mitral orifice associated with hypoplastic left heart syndrome

2014 ◽  
Vol 25 (5) ◽  
pp. 1002-1005 ◽  
Author(s):  
Jennifer A. Su ◽  
John Ho ◽  
Pierre C. Wong
Keyword(s):  
Mitral Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Current Literature ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Valve Orifice ◽  
Mitral Orifice ◽  
Rare Malformation ◽  
Left Heart Syndrome

AbstractIn the spectrum of mitral valve anomalies, unguarded mitral orifice is an exceedingly rare malformation, with only four cases described in the current literature. All previously reported cases have been associated with discordant atrioventricular connections. We describe the first known case of unguarded mitral valve orifice, in the setting of atrioventricular concordance, in a newborn with hypoplastic left heart syndrome.

scholarly journals Improvement in right ventricular function by mitral valve closure in hypoplastic left heart syndrome

2021 ◽  
Author(s):  
Dai Asada ◽  
Yoko Kawai ◽  
Yoshinobu Maeda ◽  
Masaaki Yamagishi
Keyword(s):  
Mitral Valve ◽  
Right Ventricular ◽  
Ventricular Function ◽  
Hypoplastic Left Heart Syndrome ◽  
Right Ventricular Function ◽  
Left Ventricular ◽  
Valve Closure ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Abstract A male neonate presented with the aortic/mitral stenotic variant of hypoplastic left heart syndrome, wherein the suprasystemic left ventricular pressure and relatively large left ventricle had shifted the intraventricular septum. Despite bilateral pulmonary artery banding, the stroke volume was difficult to maintain owing to the compressed right ventricle, causing heart failure symptoms. Percutaneous balloon aortic valvuloplasty decreased the left ventricular pressure, restoring the right ventricular function. Norwood procedure with mitral valve closure after catheter intervention reduced the left ventricular size and improved the right ventricular function. This paper refers to the potential of mitral valve closure for hypoplastic left heart syndrome.

scholarly journals Comparison of Childhood Outcome by Mitral Valve and Aortic Valve Subtypes of Typical Hypoplastic Left Heart Syndrome

2018 ◽  
Vol 34 (1) ◽  
pp. 3-9
Author(s):  
Hirofumi Fukunaga ◽  
Makoto Nakamura ◽  
Shiro Ishikawa ◽  
Yoshihiko Kodama ◽  
Koichi Sagawa ◽  
...  
Keyword(s):  
Mitral Valve ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

First-Trimester Diagnosis of Hypoplastic Left Heart Syndrome: A Case Report

2021 ◽  
Vol 37 (2) ◽  
pp. 185-192
Author(s):  
Emily Hildebrand
Keyword(s):  
Case Report ◽  
Mitral Valve ◽  
Aortic Valve ◽  
Early Detection ◽  
Hypoplastic Left Heart Syndrome ◽  
First Trimester ◽  
Cardiac Anomaly ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Hypoplastic left heart syndrome (HLHS) comprises a spectrum of left-sided heart anomalies resulting from left outflow or inflow obstruction. Obstruction most often occurs at the levels of the aortic valve and/or mitral valve due to stenosis or atresia. HLHS is a lethal cardiac anomaly if not treated within the first week of life. Knowledge of sonographic features could aid in early detection, which results in better planning and management of pregnancy. This report presents a case in which HLHS was discovered during a routine dating and viability sonogram, performed at 12 weeks’ gestation.

scholarly journals Factors associated with increased atrial septum thickness in infants with Hypoplastic Left Heart Syndrome (HLHS)

2020 ◽  
Vol 99 (1) ◽  
pp. 80-83
Author(s):  
Bárbara Justo Carvalho ◽  
Vera Demarchi Aiello
Keyword(s):  
Mitral Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Pulmonary Trunk ◽  
Atrial Septum ◽  
Therapeutic Interventions ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Significant Difference ◽  
The Mean ◽  
Left Heart Syndrome

Introduction: In the usual procedures performed on newborns affect by Hypoplastic Left Heart Syndrome (HLHS), phenotypic variations influence the success of the treatment, especially the characteristics related to the atrial septum and foramen ovale (FO) in case of catheter septostomy. Objectives: To analyze macroscopics features of the atrial septum of hearts with HLHS in order to define and guide therapeutic procedures on this structure. Methods: 18 hearts of deceased patients diagnosed with HLHS were evaluated for FO patency and size, bulging of its blade, atresia or patency of the mitral valve and caliber of the ascending aorta and pulmonary trunk. Histological sections of the atrial septum were made for measurements of maximum and minimum thickness of the lamina. Results: The mean age of the patients was 34.5 days (57% male), with a mean atrial septal thickness of 1.90 mm (0.63 - 4.09 mm). The mean diameter of the pulmonary trunk and aorta were 1.16 cm and 0.22 cm, respectively. FO was patent in 39% of cases. The mitral valve was atresic in 21% of the specimens. There was a significant difference in the thickness of the atrial septum in cases with patent or closed FO, being greater in cases where the FO was closed (p = 0.047). The ratio FO/age presented a statistically significant negative correlation with atrial septum thickness (r = -0.76 and p <0.05). Conclusions: The results indicate that the patency and size of the oval foramen have repercussions on the thickness of the atrial septum, suggesting that this factor may limit the success of therapeutic interventions, especially catheter septostomy.

Coronary Arterial Abnormalities in Hypoplastic Left Heart Syndrome: Pathologic Characteristics of Archived Specimens

2020 ◽  
Vol 32 (3) ◽  
pp. 531-538
Author(s):  
Elizabeth H. Stephens ◽  
Dipankar Gupta ◽  
Mark Bleiweis ◽  
Carl L. Backer ◽  
Robert H. Anderson ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Archived Specimens ◽  
Left Heart Syndrome
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