scholarly journals Hydrometrocolpos secondary to persistent urogenital sinus and transverse vaginal septum: a rare congenital anomaly

2021 ◽  
Vol 8 (3) ◽  
pp. 70-73
Author(s):  
Karamvir Chandel ◽  
Tulika Singh ◽  
Veenu Singla ◽  
Rashmi Bagga
Keyword(s):  
Congenital Anomaly ◽  
Urogenital Sinus ◽  
Vaginal Septum ◽  
Rare Congenital Anomaly ◽  
Transverse Vaginal Septum ◽  
Persistent Urogenital Sinus

scholarly journals Complex mullarian duct abnormality in a young female: a theraputic dilemma

2017 ◽  
Vol 6 (8) ◽  
pp. 3673
Author(s):  
Mukta Agarwal ◽  
Bhawana Tiwary ◽  
Prajnanika Gurung
Keyword(s):  
Lower Abdominal Pain ◽  
Rare Condition ◽  
Young Female ◽  
Urogenital Sinus ◽  
Incomplete Fusion ◽  
Primary Amenorrhea ◽  
Vaginal Septum ◽  
Primary Amenorrhoea ◽  
Transverse Vaginal Septum ◽  
Mullerian Ducts

Genital outflow tract obstruction is a rare cause of primary amenorrhoea. Cervical agenesis is a very rare condition often associated with atresia of vagina. Clinical diagnosis is usually difficult before surgery. Transverse vaginal septum or vaginal agenesis is also a rare condition that results from incomplete fusion between vaginal components of the mullerian ducts and urogenital sinus. If the septum is complete, the menstrual flow will be obstructed causing primary amenorrhoea. The septum is basically a membrane of fibrous connective tissue with both muscular and vascular components formed anywhere along the vagina during embryological development. Here we present a case of 18 year old female who presented with primary amenorrhea, cyclical lower abdominal pain and menouria since 5 years. There was no history of attainment of menarche. The clinical examination revealed a small, blind ending lower vagina with a tough transverse membrane separating the lower portion from the upper genital tract. The ultrasound examination revealed a normal size uterus with hematometra. The magnetic resonance imaging of pelvis confirmed the presence of hematometra and transverse vaginal septum. Transverse vaginal septum resection followed by abdomino-perineal cervicoplasty was done in this patient.

scholarly journals A case of transverse vaginal septum causing obstructed labour

2020 ◽  
Vol 10 (1) ◽  
pp. 350
Author(s):  
Saratu Bello ◽  
Ukwu Eze ◽  
Adoke Umar
Keyword(s):  
Urogenital Sinus ◽  
Antenatal Visit ◽  
Health Seeking ◽  
Obstructed Labor ◽  
Vaginal Septum ◽  
Rare Finding ◽  
Transverse Vaginal Septum ◽  
Seeking Behavior ◽  
Mullerian Ducts ◽  
Rule Out

Transverse vaginal septum (TVS) is a congenital mullerian malformation resulting from failure of fusion or canalization of the urogenital sinus and the mullerian ducts. This results in amenorrhea, inability to consummate marriage and primary infertility if left untreated.  It is a rare finding in pregnancy and labor. However, due to ignorance, poor health seeking behavior and poverty in our setting the diagnosis of transverse vaginal septum may only be encountered in labor. We describe an 18 year old primigravida at term presented with history and findings of obstructed labor due to transverse vaginal septum (low-type) with a small central aperture first diagnosed in labor. This report is aimed at alerting clinicians that all primigravidae should have a routine pelvic examination during their antenatal visit to rule-out lower genital abnormalities.

scholarly journals Spectrum of Etiologies Causing Hydrometrocolpos

2013 ◽  
Vol 2 (1) ◽  
pp. 5
Author(s):  
Ayşenur Cerrah Celayir ◽  
Gökmen Kurt ◽  
Ceyhan Şahin ◽  
Inanç Cici
Keyword(s):  
Treatment Options ◽  
Urogenital Sinus ◽  
Vaginal Septum ◽  
Imperforate Hymen ◽  
Incision And Drainage ◽  
Persistent Cloaca ◽  
Transverse Vaginal Septum ◽  
Initial Procedure ◽  
Cloacal Malformations

Background: Hydrometrocolpos (HMC) develops as a result of vaginal outflow obstruction and the accumulation of secretions. It might be secondary to persistent cloaca, urogenital sinus, some syndromes, presence of the vaginal septum, vaginal atresia, and imperforate hymen. Each of them has different treatment options and follow-up protocols. This study was performed to identify the etiology and the related management of patients with HMC.Materials and Methods: A descriptive series of patients with HMC managed in our hospital between 2004 and 2011 is being presented. The medical record of these patients was analyzed for etiology, management, and outcome.Results: Eight patients with HMC were managed during 7 years at our department. Underlying etiologies included urogenital sinus (n=3), and 1 each of imperforate hymen, transverse vaginal septum, Herlyn-Werner-Wunderlich syndrome, persistent cloaca, and a variant of the cloaca. Four patients were prenatally diagnosed. The patient with imperforate hymen was managed successfully with incision and drainage. Abdominal vaginostomy was done in three patients with urogenital sinus as initial procedure. In patient with persistent cloaca, a colostomy and abdominal vaginostomy were performed. Patient with cloaca variant died due to persistent acidosis and salt wasting.Conclusion: HMC may have different etiological factors which may dictate different surgical management. Etiology of HMC can be as simple as imperforate hymen to the most severe cloacal malformations.

scholarly journals Management of Recurrent Stricture Formation after Transverse Vaginal Septum Excision

2015 ◽  
Vol 2015 ◽  
pp. 1-5 ◽  
Author(s):  
Ridhima Gupta ◽  
Joseph D. Bozzay ◽  
David L. Williams ◽  
Robert T. DePond ◽  
Pickens A. Gantt
Keyword(s):  
Urogenital Sinus ◽  
Primary Amenorrhea ◽  
Stricture Formation ◽  
Multiple Congenital Anomalies ◽  
Initial Examination ◽  
Vaginal Septum ◽  
Recurrent Stricture ◽  
Unicornuate Uterus ◽  
Transverse Vaginal Septum ◽  
Mullerian Ducts

Background. A transverse vaginal septum (TVS) is a rare obstructing anomaly, caused due to improper fusion of Müllerian ducts and urogenital sinus during embryogenesis.Case. A 15-year-old girl presented with primary amenorrhea. She had multiple congenital anomalies. Initial examination and imaging investigation revealed the presence of a unicornuate uterus and a TVS. The TVS was excised; however the patient was unable to perform vaginal dilation postoperatively leading to recurrent stricture formation. She underwent multiple surgeries for excision of the stricture. The patient was eventually evaluated every day in the clinic until she was able to demonstrate successful vaginal dilatation in the presence of a clinician.Summary and Conclusion. Properly guided regular and intensive vaginal dilation after TVS excision may decrease the need of reoperations due to recurrent stricture formation.

scholarly journals Cor triatriatum dexter, a very rare congenital anomaly presented in a complex pathological context – case presentation

2014 ◽  
Vol 60 (4) ◽  
pp. 160-162
Author(s):  
Liliana Gozar ◽  
Cristina Blesneac ◽  
Rodica Toganel
Keyword(s):  
Congenital Anomaly ◽  
Cytomegalovirus Infection ◽  
Cor Triatriatum ◽  
Anatomical Feature ◽  
Renal Anomalies ◽  
Anatomical Variant ◽  
Case Presentation ◽  
Congenital Cytomegalovirus ◽  
Rare Congenital Anomaly ◽  
Cor Triatriatum Dexter

Abstract Background Cor triatriatum dexter is an extremely rare congenital anomaly, and in most cases, without hemodynamic significance. Congenital cytomegalovirus infection is the most common viral infection, the majority of infected infants being asymptomatic and only 5-15% being symptomatic in the neonatal period. Case report We present the case of a female infant, aged 3 months. Clinical examination reveals cranial and facial anomalies. The karyotype was normal. Laboratory tests revealed the presence of anti-CMV antibodies in urine. Imaging studies showed cerebral and renal anomalies. Echocardiographic exam revealed a congenital anatomical feature without hemodynamic significance - cor triatriatum dexter. Conclusions although cytomegalovirus infection is mostly asymptomatic, it can present as a complex pathological association, in which a congenital cardiac anatomical feature without hemodynamic significance, considered by some authors as an anatomical variant, can appear

scholarly journals Congenital anomalies causing hemato/hydrocolpos: imaging findings, treatments, and outcomes

2021 ◽  
Author(s):  
Keizo Tanitame ◽  
Nobuko Tanitame ◽  
Saiko Urayama ◽  
Kazuhiro Ohtsu
Keyword(s):  
Correct Diagnosis ◽  
Late Complications ◽  
Diagnosis And Treatment ◽  
Imaging Findings ◽  
Vaginal Septum ◽  
Renal Anomaly ◽  
Imperforate Hymen ◽  
Adequate Knowledge ◽  
Transverse Vaginal Septum ◽  
Urogenital Anomalies

AbstractHemato/hydrocolpos due to congenital urogenital anomalies are rare conditions discovered in neonatal, infant, and adolescent girls. Diagnosis is often missed or delayed owing to its rare incidence and nonspecific symptoms. If early correct diagnosis and treatment cannot be performed, late complications such as tubal adhesion, pelvic endometriosis, and infertility may develop. Congenital urogenital anomalies causing hemato/hydrocolpos are mainly of four types: imperforate hymen, distal vaginal agenesis, transverse vaginal septum, and obstructed hemivagina and ipsilateral renal anomaly, and clinicians should have adequate knowledge about these anomalies. This article aimed to review the diagnosis and treatment of these urogenital anomalies by describing embryology, clinical presentation, imaging findings, surgical management, and postoperative outcomes.

scholarly journals Roberts uterus: a rare congenital anomaly

2017 ◽  
Vol 6 (12) ◽  
pp. 5657
Author(s):  
Nagendra Sardeshpande ◽  
Pratima Chipalkatti ◽  
Jainesh Doctor
Keyword(s):  
Congenital Anomaly ◽  
Abdominal Pain ◽  
Adnexal Mass ◽  
Lower Abdominal Pain ◽  
Uterine Horn ◽  
Transabdominal Ultrasound ◽  
Septate Uterus ◽  
Bicornuate Uterus ◽  
Rare Congenital Anomaly ◽  
Hysteroscopic Resection

A 23-year-old girl presented with severe cyclical lower abdominal pain during menstruation since menarche, which had increased since the last 4 years. Transabdominal ultrasound showed adnexal mass with no internal vascularity; MRI reported it as bicornuate uterus with one non-communicating right uterine horn with haematometra. On hysteroscopy there was evidence of septate uterus communicating only to the left ostia. Ultrasonography-guided hysteroscopic resection of septa with drainage of haematometra was done. Patient is presently asymptomatic.

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