scholarly journals Superficial siderosis of the central nervous system: an unusual cause of sensorineural hearing loss

2010 ◽  
Vol 68 (3) ◽  
pp. 469-471 ◽  
Author(s):  
Ana Claudia Rodrigues de Cerqueira ◽  
Antônio Egídio Nardi ◽  
José Marcelo Ferreira Bezerra
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Superficial Siderosis ◽  
The Central Nervous System

Superficial Siderosis of the Central Nervous System: A Neglected Cause of Sensorineural Hearing Loss

1992 ◽  
Vol 107 (1) ◽  
pp. 69-77 ◽  
Author(s):  
Steven M. Parnes ◽  
Susan A. Weaver
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Imaging Techniques ◽  
Cranial Nerves ◽  
Sensorineural Hearing ◽  
Superficial Siderosis ◽  
System A ◽  
The Central Nervous System

Superficial siderosis of the central nervous system is a rare, often unrecognized condition in which there is a deposition of intracellular and extracellular hemosiderin in the leptomeninges, subpial tissue, spinal cord, and cranial nerves as a result of chronic bleeding in the subarachnoid space. On the basis of our cases and a review of the literature, the majority of patients manifest sensorineural hearing loss in addition to cerebellar dysfunction, pyramidal tract signs, and progressive mental deterioration. Recent imaging techniques—particularly CT and MRI—can define the presence of iron deposition, confirming the diagnosis ante mortem. From post mortem specimens, histologic sections demonstrate severe damage to the eighth nerve, with microglial metabolism of iron. Cases will be presented to illustrate these points.

scholarly journals Superficial siderosis of the central nervous system: an usual cause of sensorineural hearing loss

2013 ◽  
Vol 79 (2) ◽  
pp. 257
Author(s):  
Diana Cunha Ribeiro ◽  
Joana Nunes ◽  
Ana Cláudia Ribeiro ◽  
Felisberto Maricato ◽  
Carlos Ribeiro
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Superficial Siderosis ◽  
The Central Nervous System

scholarly journals A Case of Progressive Sensorineural Hearing Loss Caused by Superficial Siderosis of Central Nervous System.

1999 ◽  
Vol 42 (4) ◽  
pp. 254-258
Author(s):  
Tadashi Wada ◽  
Hitoshi Satoh ◽  
Noriko Tsuchiya ◽  
Toshiyuki Fujisaki ◽  
Sugata Takahasih
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Superficial Siderosis

Superficial siderosis of the central nervous system: a case with an unruptured intracranial aneurysm

1995 ◽  
Vol 109 (6) ◽  
pp. 549-552 ◽  
Author(s):  
Ming-Tang Lai ◽  
Takuya Ohmichi ◽  
Koji Yuen ◽  
Kentaro Egusa ◽  
Satoshi Yorizane ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Intracranial Aneurysm ◽  
Sensorineural Hearing Loss ◽  
Superficial Siderosis ◽  
Unruptured Intracranial Aneurysm ◽  
System A ◽  
The Central Nervous System ◽  
Important Sign

AbstractWe present a case of superficial siderosis (SS) of the central nervous system (CNS) with an unruptured intracranial aneurysm to illustrate that the commonly encountered unexplainable progressive sensorineural hearing loss (SNHL) can be an important sign for the early awareness of this rare disorder. The literature on SS is reviewed and the pathogenesis of SS is discussed.

Superficial siderosis of the central nervous system after brachial plexus injury

1994 ◽  
Vol 80 (5) ◽  
pp. 931-934 ◽  
Author(s):  
Virginio Bonito ◽  
Cristina Agostinis ◽  
Stefano Ferraresi ◽  
Carlo Alberto Defanti
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Brachial Plexus ◽  
Brachial Plexus Injury ◽  
Superficial Siderosis ◽  
Content Type ◽  
Initial Symptoms ◽  
The Central Nervous System ◽  
Fine Print

✓ Superficial siderosis is a rare condition characterized by deposition of hemosiderin in the leptomeninges and in the subpial layers of the brain and spinal cord. It is associated with cerebrospinal fluid abnormalities consistent with recurrent bleeding into the subarachnoid space. The usual symptoms are hearing loss, ataxia, spastic paraparesis, sensory and sphincter deficits, and mental deterioration. A case is presented of severe superficial siderosis of the central nervous system in a 51-year-old man who had suffered a brachial plexus injury at the age of 20 years. The diagnosis was made by means of magnetic resonance imaging 16 years after the initial symptoms, which comprised bilateral hearing loss and anosmia. Subarachnoid bleeding was due to traumatic pseudomeningocele of the brachial plexus, a very unusual cause of superficial siderosis. This case is interesting insofar as the surgical treatment prevented further bleeding and possibly progression of the disease.

Hearing loss and vertigo in superficial siderosis of the central nervous system

2004 ◽  
Vol 25 (2) ◽  
pp. 142-149 ◽  
Author(s):  
Dominique Vibert ◽  
Rudolf Häusler ◽  
Karl-Olof Lövblad ◽  
Gerhard Schroth
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Superficial Siderosis ◽  
The Central Nervous System
Sign in / Sign up

Export Citation Format

Share Document