scholarly journals Graham-Little Piccardi Lassueur Syndrome: case report

2012 ◽  
Vol 87 (5) ◽  
pp. 775-777 ◽  
Author(s):  
Raquel Bissacotti Steglich ◽  
Renata Elise Tonoli ◽  
Giselle Martins Pinto ◽  
Fernanda Melo Müller ◽  
Isabelle Maffei Guarenti ◽  
...  
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Hair Follicles ◽  
Rare Disorder ◽  
Rare Syndrome ◽  
Scarring Alopecia ◽  
History Of

A 33-year-old woman presented with a 3-year history of progressive alopecia of the scalp. Past treatment with hydroxicloroquine did not show improvement. Physical examination revealed multiple areas of alopecia with atrophic aspect of the scalp, and axillary and pubic hypotrichosis. Dermoscopy showed hyperkeratosis and accentuation of follicular ostia. Anatomopathological examination revealed decrease in the number of hair follicles, upper perifollicular infiltrate and areas with fibrosis. The Piccardi-Lassueur-Graham-Little syndrome is a rare disorder, characterized by the triad of multifocal scarring alopecia of the scalp, keratotic follicular eruption and hypotrichosis of axillary and pubic regions. Management is a challenge and many medications tried have controversial results. We report a case of this rare syndrome which improved with corticoids.

scholarly journals Extensive nasopharyngeal angiofibroma – case report

1970 ◽  
Vol 15 (2) ◽  
pp. 75-77
Author(s):  
M Alamgir Chowdhury ◽  
Mousumi Malakar ◽  
SM Golam Rabbani ◽  
Naseem Yasmeen ◽  
Shahidul Islam
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Nasal Cavity ◽  
Neck Region ◽  
Lateral Rhinotomy ◽  
Male Population ◽  
Vascular Neoplasm ◽  
Nasopharyngeal Angiofibroma ◽  
Recurrent Epistaxis ◽  
History Of

Juvenile nasopharyngeal angiofibroma is a benign vascular neoplasm, but it is locally aggressive. This accounts for less than 0.5% of all the neoplasm in the head & neck region in the male population only. Here we report a case of 10-year-old boy with a blackish red smooth polypoidal mass in the nasal cavity, with history of recurrent epistaxis. On physical examination it was suspected as nasopharyngeal angiofibroma. We removed it totally by lateral rhinotomy approach. And the diagnosis was nasopharyngeal angiofibroma on histopathology. Key words: Angiofibroma; Nasopharyngeal. DOI: 10.3329/bjo.v15i2.5061 Bangladesh J Otorhinolaryngol 2009; 15(2): 75-77

scholarly journals Recurrence of Avellino Corneal Dystrophy Following Penetrating Keratoplasty: A Case Report

2021 ◽  
Vol 59 (236) ◽  
Author(s):  
Rachana Singh Rana ◽  
Leena Bajracharya ◽  
Reeta Gurung
Keyword(s):  
Case Report ◽  
Penetrating Keratoplasty ◽  
Autosomal Dominant ◽  
Corneal Dystrophy ◽  
Rare Disorder ◽  
Epithelial Defect ◽  
Autosomal Dominant Fashion ◽  
History Of

Granular – lattice (Avellino) corneal dystrophy is inherited in an autosomal dominant fashion which affects stroma of the cornea with recurrent erosions and decreased vision due to clouding of cornea in later stage. We reported a case of 53-year old woman presented with pain and blurring of vision of left eye for 10 days with history of right eye deep anterior lamellar dystrophy and Left eye penetrating keratoplasty 5years back for Avellino dystrophy. On examination right eye graft was clear and left eye showed circular edges of irregular epithelium with patchy stains and epithelial defect suggestive of recurrence of dystrophy. A patient with recurrent corneal erosions and opacity in cornea has to be examined carefully so as not to overlook Avellino corneal dystrophy. Being a rare disorder this case has been reported to draw the attention of ophthalmologists about its recurrence following keratoplasty.

scholarly journals Compound Presentation: A Case Report of One of the Rarest Varieties- Vertex, Hand, and Feet Presentation

2021 ◽  
Vol 8 (2) ◽  
Author(s):  
Sium AF ◽  
◽  
Tilahun A ◽  
Mersha A ◽  
Yihun S ◽  
...  
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Cesarean Delivery ◽  
Conservative Management ◽  
Similar Type ◽  
Cervical Dilation ◽  
Compound A ◽  
Case Summary ◽  
Spontaneous Correction ◽  
History Of

Background: Compound presentation occurs in approximately 1/700 deliveries. Being the rarest type, there is scarce literature about the recommended management for vertex-hand-feet variety of compound presentation. We report a similar type of compound presentation. Case Summary: A 25 years-old primigravida who claimed to be 9 months ammenorric presented with a history of pushing down pain of 12 hours duration with associated history of passage of liquor of 4 hours duration. Up on physical examination she was in active first of labor at cervical dilation of 5 centimeters and the presentation was compound- a vertex-hand-feet variety. Cesarean delivery was done after two hours of conservative management and the outcome was an alive 2300grams male neonates with no perinatal or maternal complication. Conclusion: In the rarest variety of compound presentation, which is a vertex, hand, and feet type, spontaneous correction is unusual if the fetus is alive and interference is usually necessary.

scholarly journals Idiopathic Hypertrophic Pachymeningitis: A Case Report from Bangladesh

2018 ◽  
Vol 3 (2) ◽  
pp. 110-112
Author(s):  
Meera Momtaz Sabeka ◽  
Md Nazrul Islam
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Optic Atrophy ◽  
Severe Headache ◽  
Imaging Studies ◽  
Hypertrophic Pachymeningitis ◽  
History Of ◽  
Diagnostic Clue ◽  
Work Up ◽  
Rule Out

A 52 years old lady presented with sudden severe headache with the history of similar intense headache twenty years back which ended up with left sided blindness. Her physical examination was unremarkable except optic atrophy of the left eye. Investigation included biochemical work up, imaging studies and CSF study. The MRI of brain with contrast gave the key diagnostic clue with characteristic findings of hypertrophic pachymeningitis. Other investigations helped to rule out possible etiologies and the diagnosis idiopathic hypertrophic pachymeningitis was finally made. The patient has been treated with steroid and enjoyed improvement in her yearlong symptoms.Journal of National Institute of Neurosciences Bangladesh, 2017;3(2): 110-112

scholarly journals Unusual Clinical Manifestations of Chronic Discoid Lupus Erythematosus

2014 ◽  
Vol 6 (2) ◽  
pp. 69-72
Author(s):  
Ljubka Miteva ◽  
Valentina Broshtilova ◽  
Robert A. Schwartz
Keyword(s):  
Physical Examination ◽  
Alopecia Areata ◽  
Lupus Erythematosus ◽  
Clinical Manifestations ◽  
Clinical History ◽  
Discoid Lupus Erythematosus ◽  
Histopathological Analysis ◽  
Scarring Alopecia ◽  
History Of ◽  
Scalp Lesions

Abstract A 22-year-old woman with a 3-year history of discoid lupus erythematosus presented with two circumscribed patches of non-scarring alopecia, clinically simulating alopecia areata. Histopathological analysis of scalp lesions revealed discoid lupus erythematosus. Based on the clinical history, physical examination, and histological and immunological findings, we distinguished our case from a true combination of alopecia areata and typical chronic discoid lupus erythematosus.

scholarly journals PeutzJeghers syndrome: A case report and literature review

2014 ◽  
Vol 4 (8) ◽  
pp. 677-679
Author(s):  
A Lakhey ◽  
H Shakya
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Physical Examination ◽  
Rectal Bleeding ◽  
Buccal Mucosa ◽  
Autosomal Dominant ◽  
Hamartomatous Polyps ◽  
Pigmented Lesions ◽  
History Of ◽  
Peutz Jeghers Syndrome

Peutz–Jeghers Syndrome is an autosomal dominant inheritedhamartomatous polyp. We present a case of a 5-year-old young boywith a history of per rectal bleeding and mass protruding out of the anus. Physical examination revealed presence of mucocutaneous pigmented lesions over the tongue, and few hamartomatous polyps protruding out of the rectum suggesting Peutz–Jeghers syndrome. The presence in early infancy of small, well-demarcated and dark-brown to blue-black lentigines on the lips,buccal mucosa and perioral skin, should alert the clinician to Peutz–Jeghers Syndrome.DOI: http://dx.doi.org/10.3126/jpn.v4i8.11597 Journal of Pathology of Nepal; Vol.4,No. 8 (2014) 677-679

scholarly journals Fixation Rotator cuff repair of shoulder by Patch augmentation technique. A Case Report

2021 ◽  
Vol 9 (8) ◽  
pp. 1814-1818
Author(s):  
Mohammed Yaseen Azher
Keyword(s):  
Case Report ◽  
Rotator Cuff ◽  
Physical Examination ◽  
Range Of Motion ◽  
Rotator Cuff Repair ◽  
Left Shoulder ◽  
Synthetic Graft ◽  
History Of ◽  
Cuff Repair

Abstract: Rotator cuff repair has excellent outcomes for many patients but continues to be suboptimal for large, retracted tears, and revision procedures. In certain circumstances, augmentation may be explored to aid healing. This is a case study. A 61-yearold man with a 3-month history of left shoulder arthroscopic subacromal decompression with bursectomy, acromioplasty, rotator cuff repair with patch augmentation, strengthening with bio synthetic graft fleece, and ACJ excision. After a physical examination, the left shoulder was found to have active forward elevation of 130 degrees and passive forward elevation of 150 degrees, pain in the periscapular region, rotator cuff strength of 4/5, and distal neurovascular integrity. Finally, the patient is pleased with the results of the operation, and he now has a decent functional range of motion, although he still has weak muscles and severe scapular discomfort

scholarly journals Congenital Hypotrichosis Simplex: A Case Report

2019 ◽  
Vol 43 (1) ◽  
pp. 59-61
Author(s):  
Maria Kibtiar ◽  
Romana Akther ◽  
Mohammed Mahbubul Islam ◽  
Shahana A Rahman
Keyword(s):  
Case Report ◽  
Child Health ◽  
Physical Examination ◽  
Scalp Hair ◽  
Rare Disorder ◽  
Detailed History

Congenital hypotrichosis simplex of scalp is a rare disorder which only affect the scalp hair. Rest of the hair bearing areas are spared. In this disorder the scalp hair are absent or sparse. We describe a 5 month old boy presented with no growth of scalp hair since birth in this case report. After taking detailed history, a thorough physical examination was done. Other causes of alopecia were ruled out and finally the child was diagnosed as a case of Congenital Hypotrichosis Simplex (CHS). Bangladesh J Child Health 2019; VOL 43 (1) :59-61

scholarly journals A Giant Lymphangioma Circumscriptum on the Anterior Axilla: A Case Report

2003 ◽  
Vol 11 (3) ◽  
pp. 157-159
Author(s):  
Ibrahim Askar ◽  
Nihal Kilinc ◽  
Sema Aytekin
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Male Patient ◽  
Histopathological Examination ◽  
Postoperative Result ◽  
History Of ◽  
Lymphangioma Circumscriptum ◽  
Thin Walled ◽  
Large Muscle

Lymphangioma is a rare benign proliferative lymphatic lesion that appears in chronic lymphedematous states in a variety of settings. Lymphangioma circumscriptum consists of clinically thin-walled, translucent vesicles appearing in groups most commonly located on the axilla, chest, mouth, and tongue. A 12-year-old male patient had been suffering from itching, pink-red colored, translucent vesicular lesions overlying the anterior axilla since birth. The lesions had slowly grown in size and number over the years. The patient had no history of trauma, or cellulites. The physical examination revealed clusters of pink-red colored vesicles, which released a clear exudate when punctured. The lesion was 50×120 mm in size. The lesion was totally excised and repaired with Z-plasty. Histopathological examination revealed slight epidermal acanthosis and enlarged lymph in the upper dermis, impinging directly onto the epidermis. These lymphatics were lined only by endothelium. The lower dermis and subcutis contained abnormally large muscle-coated vessels containing a proteinaceous fluid. Six months later, there was no recurrence and a cosmetically and functionally acceptable postoperative result was obtained.

scholarly journals Feline plasm cell pododermatitis: case report

2020 ◽  
Vol 14 (4) ◽  
pp. 220-225
Author(s):  
Adriane Strack ◽  
Luana Moretto ◽  
Carla Di Concilio ◽  
Francielli Cordeiro Zimermann ◽  
Adriano Tony Ramos ◽  
...  
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Present Report ◽  
Clinical History ◽  
Histopathological Diagnosis ◽  
Veterinary Clinic ◽  
Immune Mediated ◽  
Mixed Breed ◽  
History Of

Feline Plasmacytic Pododermatitis is an uncommon dermatological disorder that affects one or multiple paw pads and leads to swelling, ulceration, hemorrhage, scaling, erythema, and striation. Its etiopathogenesis is poorly understood, however, an immune-mediated basis is strongly suggested. A two-year-old neutered, mixed breed, male cat was referred to the Veterinary Clinic of the Federal University of Santa Catarina (UFSC), Curitibanos Campus, with a brief clinical history of progressive lesions on palmar and plantar pads for one month. On physical examination, the patient had enlarged popliteal and inguinal lymph nodes, and paw pads with thin, swollen, hyperemic, erythematous, and purple color skin with multiple white striations. Histopathological diagnosis confirmed plasmacytic pododermatitis, and glucocorticoid therapy with prednisolone was prescribed. In the present report, the patient's clinical follow-up was compromised, as the tutor did not perform the prescribed treatment and did not return with the animal for further evaluations.

Sign in / Sign up

Export Citation Format

Share Document