More than 50 years with a complete heart block

We have described several cases of complete heart block on the background of rheumatism ("Ter. arch", 1955), and both favorable and unfavorable clinical course. In all cases, an electrocardiographic break was noted in the passage of the pulse from the atria to the ventricles, when the atria and ventricles contract independently of each other. Some authors believe that the life expectancy of patients with complete atrioventricular heart block of rheumatic etiology does not exceed 2-3 years.

Transient Congenital Complete Heart Block: A Case Report

Children ◽

10.3390/children8090790 ◽

2021 ◽

Vol 8 (9) ◽

pp. 790

Author(s):

Ying-Tzu Ju ◽

Yu-Jen Wei ◽

Ming-Ling Hsieh ◽

Jieh-Neng Wang ◽

Jing-Ming Wu

Keyword(s):

Heart Block ◽

Rare Case ◽

Complete Heart Block ◽

Normal Sinus Rhythm ◽

Structural Heart Disease ◽

Normal Heart ◽

Normal Sinus ◽

Congenital Complete Heart Block ◽

Congenital complete heart block is defined as a complete atrioventricular block occurring prenatally, at birth, or within the first month of life. Congenital complete heart block has a high mortality rate, and in infants with normal heart morphology, it is often associated with maternal connective tissue disease. In these latter cases, neonatal congenital complete heart block is usually irreversible. We present a rare case of a female neonate who had bradycardia noted at a gestational age of 37 weeks. Her mother had no autoimmune disease history. She had no structural heart disease, and the serology surveys for autoantibodies including SSA/Ro and SSB/La were all negative. Without intervention or medication, her congenital complete heart block completely recovered to a normal sinus rhythm within 5 days. The cause of the transient congenital complete heart block was unknown in this case.

Complete Heart Block, Severe Right Ventricular Dysfunction in a Child with COVID-19 Infection

10.1017/s1047951121004248 ◽

2021 ◽

pp. 1-10

Author(s):

Sezen Gulumser Sisko ◽

Sezen Ugan Atik ◽

Cem Karadeniz ◽

Alper Guzeltas ◽

Yakup Ergul

Keyword(s):

Atrioventricular Block ◽

Heart Block ◽

Ventricular Dysfunction ◽

Complete Heart Block ◽

Pacemaker Implantation ◽

Right Ventricular Dysfunction ◽

Right Heart Failure ◽

Right Heart ◽

Abstract A young child presented with hepatomegaly, ascites, and bradycardia in the setting of coronavirus disease-2019. Permanent complete atrioventricular block and severe right heart failure were diagnosed. He was treated with surgical epicardial pacemaker implantation. This report is the first description of coronavirus disease-2019–induced permanent complete atrioventricular block in a child.

Late complete heart block post-tetralogy of Fallot repair: a possible new predicting, precipitating factor and review of related cases

BMJ Case Reports ◽

10.1136/bcr-2018-228642 ◽

2019 ◽

Vol 12 (4) ◽

pp. e228642

Author(s):

Rayan Hejazi ◽

Marwan Balubaid ◽

Jameel Alata ◽

Rahaf Waggass

Keyword(s):

Tetralogy Of Fallot ◽

Heart Block ◽

Complete Heart Block ◽

Corrective Surgery ◽

Patient Assessment ◽

Severe Tricuspid Regurgitation ◽

Atrioventricular Dissociation ◽

Complete Atrioventricular ◽

Tetralogy Of Fallot Repair

Tetralogy of Fallot (TOF) is the most common form of cyanotic congenital heart disease beyond the age of 3 months. Complete heart block (CHB) is rare but a serious sequalae post-repair of TOF. We present a case of an 18-month-old child who developed late CHB after around 1 year of the corrective surgery of the congenital anomaly. On the regular follow-up visit, the patient assessment was unremarkable. However, there was bradycardia, 55 beats/min. The ECG showed complete atrioventricular dissociation. Echocardiogram was done and demonstrated severe tricuspid regurgitation (TR). The patient required a permanent pacemaker and he is currently well. We are presenting this case as a late unexpected CHB, with a possibility of progressive right-side dilatation as a contributing factor to CHB due to severe TR.

Successful management of fetal hydrops due to congenitally complete atrioventricular block

10.1017/s1047951103000787 ◽

2003 ◽

Vol 13 (4) ◽

pp. 380-383 ◽

Cited By ~ 8

Author(s):

Jacintha Sivarajah ◽

Ian C. Huggon ◽

Eric Rosenthal

Keyword(s):

Preterm Delivery ◽

Atrioventricular Block ◽

Heart Block ◽

Complete Heart Block ◽

Successful Management ◽

Fetal Hydrops ◽

At 32 weeks, a fetus was found to be hydropic with congenitally complete heart block in an asymptomatic mother who was positive to anti-Ro antibodies. Maternal therapy with oral salbutamol was successful in prolonging gestation for a period of 3 weeks so that preterm delivery was delayed until the 35th week of gestation. Following treatment with inotropes and diuretics, a permanent transvenous pacemaker was implanted at 8 weeks of age. The child is now thriving at 20 months of age.

Circulatory support for prolonged electro-mechanical standstill in fulminant pediatric myocarditis

The International Journal of Artificial Organs ◽

10.1177/0391398820972708 ◽

2020 ◽

pp. 039139882097270

Author(s):

Shriprasad R Deshpande ◽

Renee C Willett ◽

Karthik Ramakrishnan ◽

Syed Murfad Peer ◽

Pranava Sinha

Keyword(s):

Cardiac Dysfunction ◽

Heart Block ◽

Pediatric Patients ◽

Clinical Course ◽

Complete Heart Block ◽

Fulminant Myocarditis ◽

Circulatory Support ◽

Poor Survival ◽

Hemodynamic Compromise ◽

Biventricular Assist Devices

Pediatric patients with fulminant myocarditis can rarely present with complete heart block with severe hemodynamic compromise, cardiac arrest and require circulatory support. Additionally, patients with cardiac dysfunction that require extracorporeal membrane oxygenation (ECMO) support sometimes develop cardiac stun or standstill. These factors are associated with extremely poor survival. We present a case of fulminant myocarditis presenting with dense heart block, no ventricular electrical activity resuscitated with ECMO that developed prolonged cardiac standstill. We present the clinical course, management including ECMO followed by biventricular assist devices, pacing and review supporting literature. We hope that the case will highlight challenges in management and decision making in such patients.

The Clinical Course of Acquired Complete Heart Block in Children with Acute Myocarditis

Pediatric Cardiology ◽

10.1007/s00246-002-0402-2 ◽

2003 ◽

Vol 24 (5) ◽

pp. 495-497 ◽

Cited By ~ 43

Author(s):

D. Epstein ◽

M. J. Silka ◽

A. S. Batra

Keyword(s):

Heart Block ◽

Clinical Course ◽

Complete Heart Block ◽

Acute Myocarditis

Complete heart block as a cause of syncope in hypertrocphic cardiomyopathy

10.1017/s1047951100010933 ◽

1994 ◽

Vol 4 (1) ◽

pp. 79-81 ◽

Cited By ~ 1

Author(s):

Juan Calderón-Colmenero ◽

Mario Baltazares ◽

Alfonso Buendía

Keyword(s):

Hypertrophic Cardiomyopathy ◽

Atrioventricular Block ◽

Right Bundle Branch Block ◽

Heart Block ◽

Complete Heart Block ◽

Conduction Delay ◽

Bundle Branch Block ◽

The Relationship ◽

SummaryWe report a 12-year-old boy with hypertrophic cardiomyopathy presenting with syncope. His electrocardiogram showed first-degree atrioventricular block, complete right bundle branch block, conduction delay in the anterior fascicle of the left bundle branch, and intermittent complete atrioventricular block. We detected hypertrophic cardiomyopathy in the mother. The relationship between the diseases is discussed, and interpreted in the light of previous descriptions.

An unusual course of anti-Ro antibody-mediated fetal complete heart block

10.1017/s1047951117001937 ◽

2017 ◽

Vol 28 (1) ◽

pp. 171-174

Author(s):

Claudia Renaud ◽

Edgar Jaeggi ◽

Varsha Thakur

Keyword(s):

Heart Block ◽

Complete Heart Block ◽

Favourable Outcome ◽

Fetal Hydrops ◽

Congenital Complete Atrioventricular Block ◽

Immune Mediated ◽

Predicting Outcome ◽

Ectopic Beats ◽

AbstractFetal hydrops is a serious complication of immune-mediated congenital complete atrioventricular block. We present the case of a fetus with severe hydrops and profound bradycardia and an unusual favourable outcome. This case enhances the importance of considering the contribution of ventricular ectopic beats to the cardiac output when counselling and predicting outcome of complete heart block.

Transient Complete Heart Block after Percutaneous Transcatheter ASD Device Closure

International Journal of Research and Review ◽

10.52403/ijrr.20211115 ◽

2021 ◽

Vol 8 (11) ◽

pp. 113-116

Author(s):

Revanth Vulli ◽

Nagabhushan Doddakal ◽

VikasKadiyala .

Keyword(s):

Atrial Septal Defect ◽

Heart Block ◽

Septal Defect ◽

Complete Heart Block ◽

Case Reports ◽

Rare Complication ◽

Device Closure ◽

Small Children ◽

Transcatheter Device ◽

Transcatheter device closure of atrial septal defect (ASD) is associated with increased complications in small children in device size ≥ 19mm or indexed size ≥ 0.18 mm/cm and weight≤ 15 kg. Complete atrioventricular heart block (CHB) is reported as a rare complication of ASD device closure. We report the case of a 7year-old boy, 23kg weight, underwent device closure of ASD and subsequently developed CHB next day after the procedure which was completely resolved by day 3 with steroid treatment. Similar case reports were rarely reported in the literature. Keywords: atrial septal defect, complete heart block, device/height ratio.

Persistent Fetal Sinus Bradycardia Associated with Maternal Anti-SSA/Ro and Anti-SSB/La Antibodies

The Journal of Rheumatology ◽

10.3899/jrheum.110720 ◽

2011 ◽

Vol 38 (12) ◽

pp. 2682-2685 ◽

Cited By ~ 14

Author(s):

PRIYA CHOCKALINGAM ◽

EDGAR T. JAEGGI ◽

LUKAS A. RAMMELOO ◽

MONIQUE C. HAAK ◽

PHEBE N. ADAMA van SCHELTEMA ◽

...

Keyword(s):

Heart Block ◽

Cardiac Involvement ◽

Clinical Course ◽

Complete Heart Block ◽

Sinus Bradycardia ◽

Sinus Node ◽

Good Prognosis ◽

Sinus Arrest ◽

Congenital Complete Heart Block ◽

Myocardial Involvement

Objective.To study the clinical course and outcome of fetal sinus bradycardia (SB) due to maternal antibody-induced sinus node dysfunction.Methods.We reviewed the maternal, prenatal, and postnatal findings of fetuses with SB associated with elevated maternal anti-SSA/Ro and anti-SSB/La antibodies.Results.Of the 6 cases diagnosed prenatally, 3 had isolated SB persisting after birth and had a good prognosis. Three fetuses with SB and severe myocardial involvement (congenital complete heart block and/or endocardial fibroelastosis) succumbed in utero in spite of treatment. Postmortem histopathology in 1 fetus showed inflammatory destruction of the sinus and atrioventricular nodes. SB was detected incidentally in a 7-year-old girl. She had intermittent heart block with progressive sinus arrest requiring permanent pacemaker.Conclusion.Fetal SB associated with maternal autoantibodies may persist in childhood, with a good prognosis in the absence of widespread cardiac involvement.