scholarly journals Partial anomalous drainage of pulmonary venous to the inferior vena cava (scimitar syndrome): the part of radiated methods of research in primary diagnostic and control of surgical treatment

2020 ◽  
Vol 7 (3) ◽  
pp. 45-54
Author(s):  
I. V. Basek ◽  
A. A. Benken ◽  
V. K. Grebennik ◽  
I. K/ Ismail-zade ◽  
E. I. Nikolaichuk
Keyword(s):  
Surgical Treatment ◽  
Inferior Vena Cava ◽  
Congenital Malformation ◽  
Inferior Vena ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Scimitar Syndrome ◽  
Duct Ligation ◽  
And Control ◽  
Msct Angiography

Background. “Scimitar” syndrome is a rare congenital malformation with a frequency of 2 per 100,000 newborns. The syndrome is manifested by complete abnormal drainage of the pulmonary veins of the right lung into the inferior vena cava. According to the literature, a typical symptom of scimitar syndrome can be detected on radiographs in no more than 1/3 of patients. Only complex radiation diagnostics with the inclusion of multispiral computed tomographic angiography allows to diagnose “scimitar” syndrome, determine all its components, clarify the anatomical features and determine the volume and tactics of further cardiac surgery. Objective of the present clinical case is to assess the role of radiation research methods in the primary diagnosis and control of surgical treatment of scimitar syndrome. Materials and methods. A 39-year-old patient with a history of open arterial duct ligation and complaints of fatigue, shortness of breath arising from household loads was examined. According to the results of the chest x-ray and MSCT angiography of the chest organs, “scimitar” syndrome was diagnosed, the patient underwent a two-stage cardiosurgical treatment with the assessment of the results by MSCT angiography. Results. According to the results of radiation studies, the patient revealed a rare congenital malformation — “scimitar” syndrome. Conclusion. MSCT angiography of the chest is a highly informative, minimally invasive diagnostic method for the scimitar syndrome. MSCT angiography of the chest allows you to visually and accurately visualize the type of abnormal drainage, the course and place of the confluence of the collector, the presence of anastomoses with the left heart, which directly affects the definition of tactics for surgical correction of the disease. MSCT angiography of the chest allows you to evaluate the results of surgical treatment.

scholarly journals A Particular Infantile Scimitar Syndrome Variant with Anomalous Systemic Arterial Supply-Inferior Vena Cava Fistula

2021 ◽  
Vol 7 (1) ◽  
pp. 17-21
Author(s):  
Carmen Corina Șuteu ◽  
Cristina Blesneac ◽  
Marian Pop ◽  
Amalia Făgărășan ◽  
Liliana Gozar ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Abdominal Aorta ◽  
Inferior Vena ◽  
Pulmonary Hypoplasia ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Scimitar Syndrome ◽  
Cardiovascular Malformation ◽  
The Right ◽  
Systemic Arterial Supply

Abstract Scimitar syndrome is a rare congenital cardiovascular malformation that includes a partially anomalous drainage of the pulmonary veins in the inferior vena cava, right pulmonary hypoplasia, and systemic-pulmonary collaterals originating from various segments of the aorta. We present a case of Scimitar syndrome with associated intracardiac lesions and a large arterial conduct supplying the right lung, originating from the abdominal aorta and draining in the inferior vena cava.

scholarly journals PARTICULARITIES OF SCIMITAR SYNDROME IN ADULT PATIENTS

2021 ◽  
Vol 9 (5) ◽  
pp. 1274-1278
Author(s):  
Soumia Faid ◽  
◽  
Amine Maliki Alaoui ◽  
Nadif Maryam ◽  
Liban Ibrahim ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Right Atrium ◽  
Inferior Vena ◽  
Superior Vena ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Chest X Ray ◽  
The Right

Scimitar syndrome or Felsons veno-lobar syndrome is a very rare congenital disease characterized by a combination of cardiopulmonary abnormalities, including partial right-sided pulmonary venous drainage to the inferior vena cava, the inferior cavo-atrial junction, or low on the right atrium. We report the case of a 53-year-old female patient who presented with recent gradually worsening dyspnea. The diagnosis was suspected on the chest x-ray and confirmed on Cardiac echography andComputed Tomography scan that showed a wide collector gathering the three right superior pulmonary veins that joins the lower part of the superior vena cava, thus joining the right atrium while the right inferior pulmonary vein is drained into the inferior vena cava. The patient was treated surgically by performing a derivation of the right superior pulmonary venous collector to the left atrium with a tricuspid annuloplasty with a good outcome.

“Double whammy”: anomalous pulmonary and systemic venous drainage in a patient with scimitar syndrome

2013 ◽  
Vol 23 (5) ◽  
pp. 738-739
Author(s):  
Robert W. Elder ◽  
Brian E. Kogon ◽  
Anurag Sahu
Keyword(s):  
Inferior Vena Cava ◽  
Female Patient ◽  
Unusual Case ◽  
Inferior Vena ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome

AbstractAnomalously draining right pulmonary veins are expected with scimitar syndrome, but systemic venous abnormalities are rare. We present an unusual case of a female patient with scimitar and an interrupted inferior vena cava.

Congenital Horner and Scimitar syndrome in a newborn: a previously unreported combination

2020 ◽  
Vol 13 (11) ◽  
pp. e238018
Author(s):  
Joana Carvalho ◽  
Mariana Maia ◽  
Ágata Mota ◽  
Teresa Martins
Keyword(s):  
Multidisciplinary Approach ◽  
Septal Defect ◽  
Inferior Vena ◽  
Superior Vena ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Scimitar Syndrome ◽  
Left Superior Vena Cava ◽  
Dilated Coronary Sinus ◽  
Rule Out

Here we report a case of a term newborn presenting with left palpebral ptosis, anisocoria and heterochromia as well as cleft palate and heart murmur. Congenital Horner syndrome was suspected and a thoracoabdominal CT scan was performed to rule out neuroblastoma. This revealed an anomalous drainage of right pulmonary veins to a collector that drains to the inferior vena cava, leading to the diagnosis of Scimitar syndrome. Echocardiogram showed an ostium secundum atrial septal defect, enlarged right chambers and a dilated coronary sinus due to a persistent left superior vena cava. The combination of Horner and Scimitar syndrome has never been described before. This case should encourage clinicians to use a multidisciplinary approach in order to guarantee an adequate diagnosis and management.

Anomalous Drainage of Pulmonary Veins into the Inferior Vena Cava

Radiology ◽  
1960 ◽  
Vol 75 (4) ◽  
pp. 592-594 ◽  
Author(s):  
Walter Koch ◽  
Alfredo Silva
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Pulmonary Veins ◽  
Vena Cava

Venous anomalies

2017 ◽  
Author(s):  
Sara Thorne ◽  
Sarah Bowater
Keyword(s):  
Inferior Vena Cava ◽  
Superior Vena Cava ◽  
Inferior Vena ◽  
Superior Vena ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Anomalous Pulmonary Venous Drainage ◽  
Venous Anomalies

This chapster discusses anomalies of systemic venous drainage and anomalies of pulmonary venous drainage. It discusses superior vena cava (SVC) anomalies, inferior vena cava (IVC), total anomalous pulmonary venous drainage (TAPVD), partial anomalous pulmonary venous drainage (PAPVD), and scimitar syndrome.

Agenesis of the Hepatic Vena Cava in a Patient with Scimitar Syndrome

Vascular ◽  
2007 ◽  
Vol 15 (2) ◽  
pp. 109-112 ◽  
Author(s):  
Fatih Ors ◽  
Omer Deniz ◽  
Murat Kocaoglu ◽  
Mustafa Tasar ◽  
Turgay Celik
Keyword(s):  
Inferior Vena Cava ◽  
Congenital Anomalies ◽  
Inferior Vena ◽  
Vena Cava ◽  
Vascular Anomaly ◽  
Scimitar Syndrome ◽  
Imaging Modalities ◽  
The Right ◽  
Cardiovascular Anomalies

With the use of sophisticated imaging modalities, congenital anomalies of the inferior vena cava and its tributaries, such as agenesis of the hepatic vena cava, are becoming more and more commonly encountered. Scimitar syndrome, also called venolobar syndrome and hypogenetic lung syndrome, is a rare pulmonary vascular anomaly of the right lung that can sometimes be associated with some cardiovascular anomalies. We present here a case with agenesis of the hepatic vena cava associated with scimitar syndrome.

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