scholarly journals A clinical case of repeated correction of Ebstein’s anomaly using the ‘cone reconstruction’ method

2020 ◽  
Vol 24 (2) ◽  
pp. 102
Author(s):  
N. M. Troshkinev ◽  
E. A. Svyazov ◽  
O. V. Mochula ◽  
N. A. Shmakova ◽  
I. V. Ivanova ◽  
...  
Keyword(s):  
Informed Consent ◽  
Conflict Of Interest ◽  
Ebstein’S Anomaly ◽  
Reconstruction Method ◽  
Hemodynamic Parameters ◽  
Resonance Imaging ◽  
Ebstein's Anomaly ◽  
Mean Pressure ◽  
Critical Revision ◽  
The Right

<p>We report the case of a 16-year-old child with Ebstein’s anomaly who successfully underwent recorrection via the ‘cone reconstruction’ method using a tricuspid valve-in-ring implant. Because the patient had high-grade atrioventricular block, a pacemaker was implanted. Ultrasound and magnetic resonance imaging were conducted to determine the anatomy of the right ventricle and its hemodynamic parameters. Echocardiography performed at the time of discharge revealed an improvement in the hemodynamic parameters of the patient after the correction: triuspid valve regurgitation is mild and peak/mean pressure gradient 10/5 mmHg.</p><p>Received 9 January 2020. Revised 16 March 2020. Accepted 17 March 2020.</p><p><strong>Informed consent:</strong> The patient’s informed consent to use the records for medical purposes is obtained.</p><p><strong>Funding:</strong> The study did not have sponsorship.</p><p><strong>Conflict of interest:</strong> Authors declare no conflict of interest.</p><p><strong>Author contributions</strong><br />Drafting the article: N.M. Troshkinev, O.V. Mochula, O.A. Egunov<br />Literature review: N.A. Shmakova, I.V. Ivanova<br />Illustrations: N.M. Troshkinev, O.V. Mochula<br />Critical revision of the article: E.V. Krivoshchekov, E.A. Svyazov<br />Surgical treatment: E.V. Krivoshchekov, O.A. Egunov, N.M. Troshkinev<br />Final approval of the version to be published: N.M. Troshkinev, E.A. Svyazov, O.V. Mochula, N.A. Shmakova, I.V. Ivanova, O.A. Egunov, E.V. Krivoshchekov</p>

SUCCESSFUL CORRECTION OF EBSTEIN’S ANOMALY CRITICAL FORM COMPLICATED BY THROMBOSIS OF THE RIGHT VENTRICLE IN 10 MONTH-OLD CHILD

2017 ◽  
Vol 96 (1) ◽  
pp. 206-208
Author(s):  
R. R. Movsesyan ◽  
V. A. Bolsunovskiy ◽  
A. V. Bolsunovskiy ◽  
A. L. Tsytko ◽  
D. R. Yamgurov
Keyword(s):  
Right Ventricle ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Critical Form ◽  
The Right

Two decades of experience on ablation in children with Ebstein’s anomaly

2021 ◽  
pp. 1-7
Author(s):  
Tevfik Karagöz ◽  
İlker Ertuğrul ◽  
Ebru Aypar ◽  
Aydın Adıgüzel ◽  
Hayrettin Hakan Aykan ◽  
...  
Keyword(s):  
Atrial Flutter ◽  
Atrial Tachycardia ◽  
Ebstein’S Anomaly ◽  
Atrioventricular Nodal Reentrant Tachycardia ◽  
Success Rates ◽  
Recurrence Rates ◽  
Ebstein's Anomaly ◽  
Accessory Pathways ◽  
Rare Occasion ◽  
The Right

Abstract Introduction: Accessory pathways are commonly seen due to delamination of tricuspid valve leaflets. In addition to accessory pathways, an enlarged right atrium due to tricuspid regurgitation and incisional scars creates substrates for atrial re-entries and ectopic tachycardia. We sought to describe our experience with catheter ablation in children with Ebstein’s anomaly. Methods and results: During the study period, of 89 patients diagnosed with Ebstein’s anomaly, 26 (30.9%) of them who underwent 33 ablation procedures were included in the study. Accessory pathways were observed in the majority of procedures (n = 27), whereas atrial flutter was observed in five, atrioventricular nodal reentrant tachycardia in five, and atrial tachycardia in two procedures. Accessory pathways were commonly localised in the right posteroseptal (n = 10 patients), right posterolateral (n = 14 patients), septal (n = two patients), and left posteroseptal (n = one patient) areas. Multiple accessory pathways and coexistent arrhythmia were observed in six procedures. All ablation attempts related to the accessory pathways were successful, but recurrence was observed in five (19%) of the ablations. Ablation for atrial flutter was performed in five patients; two of them were ablated successfully. One of the atrial tachycardia cases was ablated successfully. Conclusions: Ablation in patients with Ebstein’s anomaly is challenging, and due to nature of the disease, it is not a rare occasion in this group of patients. Ablation of accessory pathways has high success, but also relatively high recurrence rates, whereas ablation of atrial arrhythmias has lower success rates, especially in operated patients.

scholarly journals Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)

2021 ◽  
Vol 2021 ◽  
pp. 1-5
Author(s):  
Mohammad Mehdi ◽  
Snigdha Bhatia ◽  
Mehul Patel ◽  
Ashraf Aly
Keyword(s):  
Heart Defects ◽  
Fontan Procedure ◽  
Left Ventricular ◽  
Ebstein’S Anomaly ◽  
Left Ventricular Noncompaction ◽  
Fetal Diagnosis ◽  
Ventricular Noncompaction ◽  
Ebstein's Anomaly ◽  
The Right ◽  
Apical Displacement

Ebstein’s anomaly is characterized by the apical displacement of the septal and posterior leaflets of the tricuspid valve with atrialization of the right ventricle (RV). It is commonly associated with other heart defects including left ventricular noncompaction. We describe a case of prenatally diagnosed Ebstein’s anomaly in association with left ventricular noncompaction and a septal defect between the left ventricle and the atrialized portion of the RV (Gerbode-like defect). The patient underwent a modified Blalock−Taussig shunt followed by Glenn procedure because of severe RV hypoplasia and RV outflow tract obstruction. The patient tolerated both procedures and is doing clinically well in anticipation of Fontan procedure for single ventricle palliation.

scholarly journals SURGICAL PALLIATION IN PATIENTS WITH EBSTEIN'S ANOMALY AND CONGENITAL HYPOPLASIA OF THE RIGHT VENTRICLE

1960 ◽  
Vol 40 (3) ◽  
pp. 310-320 ◽  
Author(s):  
Milton Weinberg ◽  
Juan P. Bicoff ◽  
Magnus H. Agustsson ◽  
Zwi Steiger ◽  
Benjamin M. Gasul ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Surgical Palliation ◽  
The Right

Progressive post-traumatic syringomyelia: a clinical case

2019 ◽  
Vol 21 (4) ◽  
pp. 81-88
Author(s):  
F. A. Bushkov ◽  
M. A. Bzhylyanskiy ◽  
A. Yu. Kordonskiy
Keyword(s):  
Spinal Cord ◽  
Spinal Cord Injury ◽  
Informed Consent ◽  
Conflict Of Interest ◽  
Clinical Case ◽  
Spinal Injury ◽  
Spinal Column ◽  
Cord Injury ◽  
Post Traumatic ◽  
The Right

The objective of the present article is to describe a rare clinical case of progressive post-traumatic cervical syringomyelia after spinal cord injury with fracture of proximal metaepiphysis of the right humerus. The patient had a progressive neurological loss after spinal cord injury.Materials and methods. The patient underwent surgical treatment: decompression and stabilization of spinal column, surgical technique of spinal cord detethering, cyst shunting.Results. In the postoperative period the patient had increased spasticity in the lower extremities, increased weakness in the muscles of the upper extremities, aggravation of orthostatic hypotension, and inability to flex the first and the fifth fingers of the right hand. Magnetic resonance imaging of the cervical spine revealed progression of syringomyelia.Conclusion. This case demonstrates differentiation between cervical myelopathy and plexus paresis in a patient with combination spinal injury and reveals the mechanisms underlying late progression of neurological deficit.Conflict of interest. The authors declare no conflict of interest.Informed consent. The patient gave written informed consent to the publication of his data.

scholarly journals Hypereosinophilic Syndrome Leading to Severe Right-Sided Heart Failure in a Patient with Ebstein's Anomaly

2013 ◽  
Vol 2013 ◽  
pp. 1-3 ◽  
Author(s):  
Joas John Kyabonaki ◽  
Bjarne Linde Nørgaard ◽  
Søren Høyer ◽  
Niels Holmark Andersen
Keyword(s):  
Heart Failure ◽  
Right Ventricle ◽  
Tricuspid Regurgitation ◽  
Hypereosinophilic Syndrome ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Long Course ◽  
The Right ◽  
Explanted Heart ◽  
Severe Fibrosis

A 36-year-old male with mild Ebstein's anomaly developed severe right-sided heart failure, following a 5-year-long course of hypereosinophilic syndrome. No regular followups had been done, during the years of antineoplastic therapy. A year after being cured from the hypereosinophilic syndrome, the patient developed right-sided heart failure symptoms and was found to have excessive fibrosis of the right ventricular endocardium and free tricuspid regurgitation. The findings were compatible with substantial scarring of the endocardium caused by the hypereosinophilic syndrome. Over a few years, the patient deteriorated significantly and was finally offered a heart transplant. Examination of the explanted heart revealed severe fibrosis of the right ventricle and almost complete sparing of the left.

Reconstruction of the Right Heart in an Elderly Woman With Ebstein’s Anomaly and Severe Heart Failure

2007 ◽  
Vol 84 (5) ◽  
pp. 1745-1746 ◽  
Author(s):  
Takuya Nakayama ◽  
Miki Asano ◽  
Kozo Matsumoto ◽  
Norikazu Nomura ◽  
Takayuki Saito ◽  
...  
Keyword(s):  
Heart Failure ◽  
Elderly Woman ◽  
Severe Heart Failure ◽  
Ebstein’S Anomaly ◽  
Right Heart ◽  
Ebstein's Anomaly ◽  
The Right
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