A Rare Case of Chronic Expanding Intrapericardial Hematoma with Refractory Right-sided Heart Failure 30 Years after the Surgical Repair of Tetralogy of Fallot

Aortopulmonary window (APW) itself is a rare congenital cardiac malformation and its association with Tetralogy of Fallot (TOF) makes it more uncommon. We report a case of APW with TOF who presented at 4-year 10 months of age. As the boy was still in operable state, after thorough preoperative evaluation successful surgical repair was done.

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Left ventricular dysfunction, adverse myocardial and aortic remodeling in patients with tetralogy of Fallot without symptoms of heart failure after surgical repair

Journal of Cardiovascular Magnetic Resonance ◽

10.1186/1532-429x-17-s1-w25 ◽

2015 ◽

Vol 17 (S1) ◽

Author(s):

Ana C Andrade ◽

Michael Jerosch-Herold ◽

Inga Voges ◽

Minh H Pham ◽

Ravi V Shah ◽

...

Keyword(s):

Heart Failure ◽

Tetralogy Of Fallot ◽

Left Ventricular Dysfunction ◽

Ventricular Dysfunction ◽

Surgical Repair ◽

Left Ventricular ◽

Aortic Remodeling

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Left-Sided Bochdalek's Hernia in a Young Adult: A Case Report and Literature Review

The Surgery Journal ◽

10.1055/s-0041-1731443 ◽

2021 ◽

Vol 07 (03) ◽

pp. e124-e126

Author(s):

Mark Portelli ◽

Mark Bugeja ◽

Charles Cini

Keyword(s):

Computed Tomography ◽

Young Adult ◽

Rare Case ◽

Surgical Repair ◽

Bochdalek Hernia ◽

Case Presentation ◽

Atypical Case ◽

Accident And Emergency ◽

History Of ◽

Accident And Emergency Department

Abstract Purpose Bochdalek's hernia is a type of congenital diaphragmatic hernia occurring secondary to a defect in the posterior attachment of diaphragm. This condition commonly presents with respiratory insufficiency in infants. To date, there are less than 100 cases of Bochdalek's hernia presenting in adults published in the literature. The mainstay treatment of Bochdalek's hernia involves reduction of hernial contents back into the peritoneal cavity with a tensionless graft repair closing the diaphragmatic defect. Case Presentation We present an atypical case of the Bochdalek hernia presenting in a previously healthy 16-year-old male who presented to the Accident and Emergency department with a 2-day history of dysphagia and loss of breath. The Bochdalek hernia was confirmed on computed tomography (CT) imaging and the patient underwent surgical repair with Gore-Tex mesh. Conclusion The report shows a rare case of the Bochdalek hernia in a young adult, successfully managed with a laparotomy.

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Tetralogy of Fallot: stent palliation or neonatal repair?

Cardiology in the Young ◽

10.1017/s1047951121000846 ◽

2021 ◽

pp. 1-9

Author(s):

Adeolu Banjoko ◽

Golnoush Seyedzenouzi ◽

James Ashton ◽

Fatemeh Hedayat ◽

Natalia N. Smith ◽

...

Keyword(s):

Pulmonary Artery ◽

Right Ventricular ◽

Tetralogy Of Fallot ◽

Surgical Repair ◽

Right Ventricular Outflow Tract ◽

Ventricular Outflow Tract ◽

Outflow Tract ◽

Hospital Length Of Stay ◽

Mortality And Morbidity

Abstract Surgical repair of Tetralogy of Fallot has excellent outcomes, with over 90% of patients alive at 30 years. The ideal time for surgical repair is between 3 and 11 months of age. However, the symptomatic neonate with Tetralogy of Fallot may require earlier intervention: either a palliative intervention (right ventricular outflow tract stent, ductal stent, balloon pulmonary valvuloplasty, or Blalock-Taussig shunt) followed by a surgical repair later on, or a complete surgical repair in the neonatal period. Indications for palliation include prematurity, complex anatomy, small pulmonary artery size, and comorbidities. Given that outcomes after right ventricular outflow tract stent palliation are particularly promising – there is low mortality and morbidity, and consistently increased oxygen saturations and increased pulmonary artery z-scores – it is now considered the first-line palliative option. Disadvantages of right ventricular outflow tract stenting include increased cardiopulmonary bypass time at later repair and the stent preventing pulmonary valve preservation. However, neonatal surgical repair is associated with increased short-term complications and hospital length of stay compared to staged repair. Both staged repair and primary repair appear to have similar long-term mortality and morbidity, but more evidence is needed assessing long-term outcomes for right ventricular outflow tract stent palliation patients.

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Ablation of atrial tachyarrhythmias late after surgical repair of tetralogy of Fallot

Cardiology in the Young ◽

10.1017/s1047951110001447 ◽

2010 ◽

Vol 21 (1) ◽

pp. 31-38 ◽

Cited By ~ 1

Author(s):

Dan Raine ◽

John O’Sullivan ◽

Milind Chaudhari ◽

Leslie Hamilton ◽

Asif Hasan ◽

...

Keyword(s):

Catheter Ablation ◽

Tetralogy Of Fallot ◽

Surgical Repair ◽

Pulmonary Regurgitation ◽

Clinical Problem ◽

Guidance System ◽

Computer Assisted ◽

Atrial Tachyarrhythmias ◽

Jude Medical ◽

Repaired Tetralogy Of Fallot

AbstractBackgroundPatients with repaired tetralogy of Fallot may develop symptomatic and haemodynamic deterioration for many reasons such as arrhythmia, pulmonary regurgitation, and impairment in ventricular function. We describe a consecutive group of patients whose main clinical problem was atrial tachyarrhythmias.AimsTo describe the clinical outcome of atrial tachyarrhythmias occurring late after surgical repair of tetralogy of Fallot; to define the circuits/foci responsible for these atrial tachyarrhythmias; to evaluate the outcome of computer-assisted mapping and catheter ablation in this patient group.Methods and resultsConsecutive patients with surgically repaired tetralogy of Fallot and atrial tachyarrhythmias, who underwent catheter ablation between January, 2001 and June, 2007, were identified retrospectively from case records. Computer-assisted mapping was performed in all using either EnSite® (St Jude Medical Inc.) arrhythmia mapping and intra-cardiac catheter guidance system or CARTO™ (Biosense Webster Inc.) electroanatomical mapping systems. Ten patients (four males) with a median age of 39 plus or minus 8 years were studied. The total number of atrial tachyarrhythmias identified was 22 (six macro-reentrant, 16 micro-reentrant/focal). In nine patients, catheter ablation led to improvement in arrhythmia episodes and/or symptoms during follow-up of 41 plus or minus 20 months. Following ablation(s), five patients required pacing for pre-existing conduction disease and five needed further surgery for haemodynamic indications. All patients remained on anti-arrhythmic drugs.ConclusionsPatients with surgically repaired tetralogy of Fallot and atrial tachyarrhythmias typically have multiple arrhythmic circuits/foci arising from a scarred right atrium. Catheter ablation reduces arrhythmia frequency and improves symptoms. However, hybrid management is often required, comprising drugs, pacing, and further surgery tailored to the individual.

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Feasibility and safety of on table extubation after corrective surgical repair of tetralogy of Fallot in a developing country: A case series

Annals of Cardiac Anaesthesia ◽

10.4103/0971-9784.154490 ◽

2015 ◽

Vol 18 (2) ◽

pp. 237 ◽

Cited By ~ 7

Author(s):

MohammadIrfan Akhtar ◽

Mohammad Hamid ◽

Anwar-Ul-Haq ◽

Fauzia Minai ◽

Naveed Rehman

Keyword(s):

Developing Country ◽

Tetralogy Of Fallot ◽

Surgical Repair ◽

Case Series

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A rare case of Tetralogy of Fallot with right atrial thrombus presenting with hemiplegia complicating the clinical course

Journal of Cardiac Surgery ◽

10.1111/jocs.15792 ◽

2021 ◽

Author(s):

Parag Sharma ◽

Satyajit Samal ◽

Debmalya Saha ◽

Sayyed E. H. Naqvi ◽

Saket Aggarwal ◽

...

Keyword(s):

Tetralogy Of Fallot ◽

Rare Case ◽

Clinical Course ◽

Right Atrial ◽

Atrial Thrombus ◽

Right Atrial Thrombus

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Regional Wall Motion and Abnormalities of Electrical Depolarization and Repolarization in Patients After Surgical Repair of Tetralogy of Fallot

Circulation ◽

10.1161/01.cir.103.12.1669 ◽

2001 ◽

Vol 103 (12) ◽

pp. 1669-1673 ◽

Cited By ~ 93

Author(s):

Michael Vogel ◽

Julia Sponring ◽

Seamus Cullen ◽

John E. Deanfield ◽

Andrew N. Redington

Keyword(s):

Tetralogy Of Fallot ◽

Wall Motion ◽

Surgical Repair ◽

Regional Wall Motion ◽

Regional Wall

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Abstract 17266: Right Atrial Volumes Changes in Tetralogy of Fallot

Circulation ◽

10.1161/circ.138.suppl_1.17266 ◽

2018 ◽

Vol 138 (Suppl_1) ◽

Author(s):

Ashish Patel ◽

Divya Shakti ◽

Chad Blackshear

Keyword(s):

Diastolic Dysfunction ◽

Diastolic Function ◽

Tetralogy Of Fallot ◽

Surgical Repair ◽

Left Ventricular ◽

Right Atrial ◽

Before And After ◽

Ventricular Diastolic Dysfunction ◽

And Function ◽

Averaged Model

Introduction & Hypothesis: There is limited information on right atrial (RA) function in the congenital heart defects. RA volume and function may give insight into the right ventricle (RV) diastolic function. We sought to assess RA function in tetralogy of Fallot (TOF) patients prior to and after complete surgical repair. Methods: Infants with TOF prior to complete repair were included for retrospective chart review and offline analysis of 2-dimensional echocardiograms (echo) before and after surgical repair. RA phasic volumes and stroke volumes were calculated. All volumes were indexed to body surface area. Results: There were 40 infants with TOF (45% females), of which 70% had pulmonary stenosis, 30% pulmonary atresia. Roughly 85% and 60% had 3, or more, echo available pre- and postoperatively. Table 1 (attached) shows the patient characteristics and phasic RA volumes. The indexed RA phasic volumes were in normal range in initial echo prior to surgery. We used normal index RA phasic volumes published by European Society of Echocardiography. There was the increasing trend of indexed RA phasic volume on follow up echo immediately before TOF repair. These phasic volumes continued to remain elevated after complete surgical repair (Table 1). Trends in RA stroke volumes for all available echos before and after surgery were modeled using a population-averaged model with an exchangeable within-panel correlation structure (Figure 2), showing no statistically significant difference after surgery. But there was statistical significance noted in RA ejection fraction. Please see attached image for statistical analysis and results of the study. Conclusions: The indexed RA phasic volumes in children with TOF are normal initially and increases before TOF repair and it continued to increase after TOF repair. The increase RA phasic volumes suggest RV diastolic dysfunction similar to the findings of LA phasic volumes and left ventricular diastolic dysfunction. Our findings indicate slow worsening RV diastolic function in patients with TOF after surgical repair. RA volume and function can be the novel marker to diagnose and monitor right ventricular diastolic dysfunction.

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