Ethmoidal Adenocarcinoma Presenting as Sensorineural Hearing Loss

We present a case of ethmoidal adenocarcinoma which in early stages of the disease produced a meningeal carcinomatosis. Its first clinical manifestation, bilateral deafness, is exceptional. The patient's history and endoscopic and histopathological findings are presented and the relevant literature is reviewed.

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Sudden sensorineural hearing loss and vertigo associated with arterial occlusive disease: three case reports and literature review

Sao Paulo Medical Journal ◽

10.1590/s1516-31802007000300012 ◽

2007 ◽

Vol 125 (3) ◽

pp. 191-195 ◽

Cited By ~ 7

Author(s):

Ney Penteado de Castro Junior ◽

Clemente Isnard Ribeiro de Almeida ◽

Carlos Alberto Herrerias de Campos

Keyword(s):

Hearing Loss ◽

Sensorineural Hearing Loss ◽

Case Reports ◽

Relevant Literature ◽

Sudden Sensorineural Hearing Loss ◽

Occlusive Disease ◽

Sensorineural Hearing ◽

Therapeutic Management ◽

Interventional Treatment ◽

Vascular Insufficiency

Sudden sensorineural hearing loss and vertigo (SSNHLV) has multifactorial causes, of which viral, autoimmune and vascular insufficiency are the most common. The therapeutic management for SSNHLV includes antiviral drugs, corticosteroids, vasodilators, normovolemic hemodilution therapy and hyperbaric oxygen therapy. Vertebrobasilar occlusive disease and carotid occlusive disease are seldom related to SSNHLV. Discussions concerning SSNHLV caused by occlusive vascular disease are important and necessary for both neurologists and otolaryngologists, since their therapeutic management and prognosis are very different from other causes of hearing loss and vertigo. Here, we present our experience with three cases managed with interventional treatment and conduct a review and discussion on the relevant literature. We conclude that investigation of vertebrobasilar and carotid occlusive diseases is necessary in patients over 50 years of age who present SSNHLV, mild neurological symptoms and a history of arteriosclerosis, high blood pressure or thrombosis.

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Sudden onset sensorineural hearing loss caused by meningeal carcinomatosis secondary to occult malignancy: Report of two cases

Auris Nasus Larynx ◽

10.1016/j.anl.2009.11.003 ◽

2010 ◽

Vol 37 (4) ◽

pp. 515-518 ◽

Cited By ~ 4

Author(s):

Maria Raffaella Marchese ◽

Carmelo La Greca ◽

Guido Conti ◽

Gaetano Paludetti

Keyword(s):

Hearing Loss ◽

Sensorineural Hearing Loss ◽

Sudden Onset ◽

Meningeal Carcinomatosis ◽

Sensorineural Hearing ◽

Occult Malignancy

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Delayed Endolymphatic Hydrops: A Case Study

Journal of the American Academy of Audiology ◽

10.3766/jaaa.19.3.3 ◽

2008 ◽

Vol 19 (03) ◽

pp. 204-209 ◽

Cited By ~ 2

Author(s):

Rachel Lazaro ◽

Larry Lundy ◽

David Zapala

Keyword(s):

Hearing Loss ◽

Sensorineural Hearing Loss ◽

Endolymphatic Hydrops ◽

Sensorineural Hearing ◽

Ménière’S Disease ◽

Episodic Vertigo ◽

Delayed Endolymphatic Hydrops ◽

Patient’S History ◽

Estudio De Caso

Delayed endolymphatic hydrops (DEH) is an unusual variation of Ménière's disease characterized by episodic vertigo that develops some time after the onset of a profound, typically unilateral sensorineural hearing loss. This case study describes a 48-year-old male who presented with complaints of episodic vertigo and disequilibrium 15 years following the onset of unilateral sensorineural hearing loss. The patient's history, audiologic findings, and vestibular evaluation led to the diagnosis of DEH. The case highlights the diagnostic and treatment challenges associated with this condition and focuses attention on principles that guide the audiologist in collecting evidence that aids in solving these challenges. El hidrops endolinfático retardado (DEH) es una variante inusual de la Enfermedad de Ménière, caracterizada por vértigo episódico que se desarrolla en el tiempo luego del inicio de una hipoacusia sensorineural unilateral típica. Este estudio de caso describe una varón de 48 años que presentó quejas de vértigo episódico y desequilibrio, 15 años después del inicio de una hipoacusia sensorineural unilateral. La historia del paciente, los hallazgos audiológicos y la evaluación vestibular llevaron al diagnóstico de DEH. El caso destaca los retos diagnósticos y terapéuticos asociados con esta condición y concentra su atención en los principios que guían al audiólogo en la recolección de evidencia que ayude a resolver estos retos.

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Sensorineural Hearing Loss as the Prominent Symptom in Meningeal Carcinomatosis

Current Oncology ◽

10.3390/curroncol28050281 ◽

2021 ◽

Vol 28 (5) ◽

pp. 3240-3250

Author(s):

Xiaoqin Huang ◽

Yu Jia ◽

Lidong Jiao

Keyword(s):

Hearing Loss ◽

Sensorineural Hearing Loss ◽

Cranial Nerves ◽

Case Fatality ◽

Whole Brain Radiotherapy ◽

Meningeal Carcinomatosis ◽

Sensorineural Hearing ◽

Initial Symptom ◽

Brain Radiotherapy ◽

Total Deafness

Sensorineural hearing loss (SNHL) has been reported rarely in patients with meningeal carcinomatosis (MC). We summarized the clinical data of eight MC patients with SNHL and 35 patients reported from publications. In the eight patients with SNHL, the medium onset age was 48 (range from 37 to 66) years and six (75%) were male. Seven (87.5%) suffered from headaches as the initial symptom, and they experienced SNHL during the first two months after the occurrence of headaches (0.5 to 2 months, average 1.5 months). The audiogram configuration was flat in three patients (37.5%) and showed total deafness in five patients (62.5%). The damage of cranial nerves VI (abducens) was observed in six patients (75%), and four patients (50%) had cranial nerves VII (facial) injury during the disease course. The percentage of damage of cranial nerves was higher than the patients without SNHL (VIth, 75.0% vs. 13.3%, p = 0.002 and VIIth 50.0% vs. 6.7%, p = 0.012). Four (50%) patients suffered from lung adenocarcinoma as primary tumor, two (25%) experienced stomach adenocarcinoma, one had colon cancer, and one patient was unknown. The symptom of SNHL improved after individualized therapy in four patients (focal radiotherapy and chemotherapy for three patients and whole brain radiotherapy for one patient), but all passed away from 2 to 11 months after diagnosis. Total deafness and flat hearing loss in audiogram were the common types of SNHL resulting from MC. MC patients with SNHL were more likely to suffer from the damage of other cranial nerves, especially to cranial nerves VI and VII. Treatment might improve SNHL, but not improve the case fatality rate.

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A Case of Meningeal Carcinomatosis with Initial Symptoms of Acute Sensorineural Hearing Loss and Rapid Turning Point

Practica oto-rhino-laryngologica Suppl ◽

10.5631/jibirinsuppl.143.107 ◽

2015 ◽

Vol 143 (0) ◽

pp. 107-111

Author(s):

Sawako Minemura ◽

Kouta Wada ◽

Toshihito Suda ◽

Chiaki Arai ◽

Masato Nagaoka ◽

...

Keyword(s):

Hearing Loss ◽

Sensorineural Hearing Loss ◽

Turning Point ◽

Meningeal Carcinomatosis ◽

Sensorineural Hearing ◽

Initial Symptoms

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Sudden bilateral sensorineural hearing loss as the presenting symptom of meningeal carcinomatosis of gastric cancer: Report of a case

Surgery Today ◽

10.1007/s00595-009-4099-1 ◽

2010 ◽

Vol 40 (6) ◽

pp. 561-565 ◽

Cited By ~ 10

Author(s):

Tetsuro Ohno ◽

Yozo Yokoyama ◽

Ryuusuke Aihara ◽

Erito Mochiki ◽

Takayuki Asao ◽

...

Keyword(s):

Gastric Cancer ◽

Hearing Loss ◽

Sensorineural Hearing Loss ◽

Meningeal Carcinomatosis ◽

Sensorineural Hearing ◽

Bilateral Sensorineural Hearing Loss

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Basilar artery occlusion presenting as sudden bilateral deafness: a case report

Journal of Medical Case Reports ◽

10.1186/s13256-020-02574-8 ◽

2021 ◽

Vol 15 (1) ◽

Author(s):

Tomoya Kinouchi ◽

Keisuke Ishitani ◽

Shinichi Uyama ◽

Tadashi Miyamoto ◽

Naomi Fujimoto ◽

...

Keyword(s):

Atrial Fibrillation ◽

Hearing Loss ◽

Sensorineural Hearing Loss ◽

Basilar Artery ◽

Artery Occlusion ◽

Sensorineural Hearing ◽

Basilar Artery Occlusion ◽

Vertebrobasilar Artery ◽

Bilateral Sensorineural Hearing Loss ◽

Bilateral Deafness

Abstract Background Most sudden-onset hearing loss is due to otolaryngologic- and very rarely to cerebrovascular disease. We report a woman with sudden bilateral sensorineural hearing loss. This case suggests that even in the absence of brainstem or cerebellar signs, magnetic resonance imaging (MRI) and MR angiography (MRA) should be performed since such studies may reveal signs of life-threatening vertebrobasilar artery occlusion. Case presentation A 73-year-old Japanese woman with a history of hypertension, hyperlipidemia, and atrial fibrillation who suffered bilateral deafness with vertigo and vomiting was transferred from a local hospital to our department. On admission her consciousness was clear and vertigo was absent. Neurological examination revealed only bilateral sensorineural hearing loss. Head computed tomography (CT) returned no significant findings. The next morning she gradually developed severe drowsiness. Diffusion-weighted MRI demonstrated acute cerebral infarction in the brainstem and bilateral cerebellum; MRA showed basilar artery occlusion due to a cardioembolic thrombus. Revascularization was obtained by endovascular treatment. However, her condition worsened progressively during the following hours. CT revealed new brainstem lesions, massive cerebellar swelling, and obstructive hydrocephalus. She died on the second day after her admission. Conclusions When hearing loss is due to vertebrobasilar occlusive disease, the prognosis is very poor. We suggest that vertebrobasilar stroke be suspected in patients with bilateral sensorineural hearing loss who present with risk factors for stroke such as atrial fibrillation and other neurologic signs.

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Mengenali gangguan pendengaran pada sindrom Waardenburg

Oto Rhino Laryngologica Indonesiana ◽

10.32637/orli.v47i2.226 ◽

2018 ◽

Vol 47 (2) ◽

pp. 171

Author(s):

Semiramis Zizlavsky ◽

Safira Trifani Putri ◽

Ronny Suwento

Keyword(s):

Hearing Loss ◽

Early Detection ◽

Sensorineural Hearing Loss ◽

Hearing Impairment ◽

Clinical Manifestation ◽

Stria Vascularis ◽

Clinical Manifestations ◽

Sensorineural Hearing ◽

Waardenburg Syndrome ◽

Autosomal Dominant Disorder

Latar belakang: Sindrom Waardenburg adalah suatu kelainan yang bersifat autosomal dominan yang ditandai oleh gangguan pendengaran sensorineural dan kelainan pigmen pada mata, rambut, dan kulit. Sindrom auditori-pigmen ini terjadi karena tidak adanya melanosit dari kulit, rambut, mata, serta stria vaskularis pada koklea. Tujuan: Memberikan informasi mengenai manifestasi klinis Sindrom Waardenburg sehingga dapat melakukan deteksi dan penanganan sedini mungkin, terutama untuk gangguan pendengaran. Kasus: Seorang anak laki-laki berusia 7 tahun dengan keterlambatan deteksi gangguan pendengaran. Orang tua anak tidak mengetahui bahwa gangguan pendengaran tersebut merupakan salah satu manifestasi sindrom Waardenburg, sehingga pada anak ini terdapat gangguan perkembangan wicara. Metode: Penelusuran literatur menghasilkan 14 jurnal, dan terdapat 2 jurnal yang relevan. Hasil: Dari 2 jurnal yang didapat, ditemukan 1 artikel penelitian dan 1 laporan kasus sindrom Waardenburg yang memaparkan berbagai manifestasi klinis yang menyertai pasien. Kesimpulan: Deteksi dini dan penatalaksanaan untuk gangguan pendengaran yang merupakan manifestasi klinis tersering dari sindrom Waardenburg, penting dilakukan karena mempengaruhi perkembangan individu dan perkembangan sosial pasien. Kata kunci: Sindrom auditori-pigmentasi, kelainan pigmen, gangguan pendengaran sensorineural, sindrom Waardenburg ABSTRACT Background: Waardenburg Syndrome (WS) is an autosomal-dominant disorder, characterized by sensorineural hearing loss and pigmentary abnormalities of the eyes, hair, and skin. Auditory-pigmentary syndromes are caused by physical absence of melanocytes from the skin, hair, eyes, and the stria vascularis of the cochlea. Purpose: To provide information regarding clinical manifestation of Waardenburg Syndrome for early detection and prompt treatment particularly for hearing impairments. Case: A 7-year-old boy with late detection of hearing impairment. Previously, his parents didn’t recognize that this condition was one manifestation of Waardenburg syndrome, so that this patient developed speech delay. Method: Searching for evidence produced 14 journals and only 2 journals were relevant. Result: Of the 2 relevant journals, there were 1 research article and 1 case report that explained several clinical manifestations of Waardenberg Syndrome. Conclusion: Early detection and management of hearing impairment as one of frequent clinical manifestation of Waardenberg Syndrome is significantly important since this condition could influence patient’s individual and social developments. Keywords: Auditory pigmentary syndrome, pigmentary abnormality, sensorineural hearing loss, Waardenburg syndrome

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Reversible sensorineural hearing loss in Lyme disease

The Journal of Laryngology & Otology ◽

10.1017/s0022215100137910 ◽

1997 ◽

Vol 111 (6) ◽

pp. 562-564 ◽

Cited By ~ 15

Author(s):

S. J. Quinn ◽

B. J. Boucher ◽

J. B. Booth

Keyword(s):

Hearing Loss ◽

Borrelia Burgdorferi ◽

Sensorineural Hearing Loss ◽

Complete Recovery ◽

Target Lesion ◽

Sensorineural Hearing ◽

Oral Antibiotic ◽

Oral Antibiotic Therapy ◽

Bilateral Sensorineural Hearing Loss ◽

Bilateral Deafness

AbstractWe report a case of bilateral sensorineural hearing loss of two years duration which appears to have been due to lateBorrelia burgdorferiinfection. The 39-year-old woman presented with bilateral deafness and multiple other neurological complaints some six months after developing a ‘target’ lesion on the lower leg after walking in the New Forest. Serology forBorrelia burgdorferibecame positive and the patient made a complete recovery from both her deafness and her other neurological problems after a five-week course of oral antibiotic therapy.

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