Delayed Endolymphatic Hydrops: A Case Study

2008 ◽  
Vol 19 (03) ◽  
pp. 204-209 ◽  
Author(s):  
Rachel Lazaro ◽  
Larry Lundy ◽  
David Zapala
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Endolymphatic Hydrops ◽  
Sensorineural Hearing ◽  
Ménière’S Disease ◽  
Episodic Vertigo ◽  
Delayed Endolymphatic Hydrops ◽  
Patient’S History ◽  
Estudio De Caso

Delayed endolymphatic hydrops (DEH) is an unusual variation of Ménière's disease characterized by episodic vertigo that develops some time after the onset of a profound, typically unilateral sensorineural hearing loss. This case study describes a 48-year-old male who presented with complaints of episodic vertigo and disequilibrium 15 years following the onset of unilateral sensorineural hearing loss. The patient's history, audiologic findings, and vestibular evaluation led to the diagnosis of DEH. The case highlights the diagnostic and treatment challenges associated with this condition and focuses attention on principles that guide the audiologist in collecting evidence that aids in solving these challenges. El hidrops endolinfático retardado (DEH) es una variante inusual de la Enfermedad de Ménière, caracterizada por vértigo episódico que se desarrolla en el tiempo luego del inicio de una hipoacusia sensorineural unilateral típica. Este estudio de caso describe una varón de 48 años que presentó quejas de vértigo episódico y desequilibrio, 15 años después del inicio de una hipoacusia sensorineural unilateral. La historia del paciente, los hallazgos audiológicos y la evaluación vestibular llevaron al diagnóstico de DEH. El caso destaca los retos diagnósticos y terapéuticos asociados con esta condición y concentra su atención en los principios que guían al audiólogo en la recolección de evidencia que ayude a resolver estos retos.

Imaging of endolymphatic hydrops: A comprehensive update in primary and secondary hydropic ear disease

2021 ◽  
pp. 1-8
Author(s):  
Michael Eliezer ◽  
Arnaud Attyé ◽  
Michel Toupet ◽  
Charlotte Hautefort
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Inner Ear ◽  
Endolymphatic Hydrops ◽  
Meniere’S Disease ◽  
Sensorineural Hearing ◽  
Ménière’S Disease ◽  
Clinical Settings ◽  
Technical Developments

BACKGROUND: Since the first description by Hallpike and Cairns, the excess of endolymphatic fluid, also known as endolymphatic hydrops (EH), has been established as being the main biomarker in patients with Menière’s disease. Recently, the concept of primary (PHED) and secondary hydropic ear disease (SHED) has been introduced. PHED corresponded to Menière’s disease while SHED was defined as the presence of EH in patients with pre-existing inner ear disease. OBJECTIVE: In this article, we would like to summarize the methodology of hydrops exploration using MRI and the previously published radiological findings in patients with PHED and SHED. RESULTS: Before the emergence of delayed inner ear MRI, the presence of EH was assumed based on clinical symptoms. However, because of the recent technical developments, inner ear MRI became an important tool in clinical settings for identifying EH in vivo, in patients with PHED and SHED. The presence of EH on MRI is related with the degree of sensorineural hearing loss whether in patients with PHED or SHED. By contrast, in PHED or SHED patients without sensorineural hearing loss, MRI showed no sign of EH. CONCLUSIONS: Thanks to the recent technical developments, inner ear MRI became an important tool in clinical settings for identifying EH in vivo, in patients with PHED and SHED.

Delayed Endolymphatic Hydrops

1978 ◽  
Vol 87 (6) ◽  
pp. 743-748 ◽  
Author(s):  
Harold F. Schuknecht
Keyword(s):  
Hearing Loss ◽  
Endolymphatic Hydrops ◽  
Meniere’S Disease ◽  
Ménière’S Disease ◽  
Disease Entity ◽  
Profound Hearing Loss ◽  
Episodic Vertigo ◽  
Delayed Endolymphatic Hydrops ◽  
Ménière's Disease ◽  
Fluctuating Hearing Loss

Delayed endolymphatic hydrops is a disease entity that can be differentiated from Meniere's disease. Typically it occurs in patients who have sustained a profound hearing loss in one ear, usually from infection or trauma, and then after a prolonged period of time develop either episodic vertigo from the same ear (ipsilateral delayed endolymphatic hydrops) or fluctuating hearing loss, also sometimes with episodic vertigo, in the opposite ear (contralateral delayed endolymphatic hydrops). The ipsilateral form of the disease may be treated by labyrinthectomy but no satisfactory therapy is available for the contralateral form of the disease.

Imaging case study: enlarged superior vestibular nerve canal with sensorineural hearing loss

2008 ◽  
Vol 123 (5) ◽  
pp. 572-574 ◽  
Author(s):  
M I Redleaf ◽  
J M Pinto ◽  
J J Klemens
Keyword(s):  
Computed Tomography ◽  
Hearing Loss ◽  
Case Report ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Male Infant ◽  
Vestibular Nerve ◽  
Sensorineural Hearing ◽  
Inferior Vestibular Nerve

AbstractObjective:We report a new temporal bone anomaly – an enlarged superior vestibular nerve canal – associated with sensorineural hearing loss.Case report:A 10-month-old male infant presented with sensorineural hearing loss together with bilaterally enlarged superior vestibular nerve canals. Compared with published temporal bone computed tomography measurements, our patient's canals were normal in length but approximately double the normal width. In addition, careful review of the imaging did not clearly identify a bony wedge between the superior and inferior vestibular nerve canals.Conclusion:Enlarged superior vestibular nerve canal malformation may be a marker for sensorineural hearing loss. Increased vigilance amongst otologists may establish the prevalence of this anomaly and its possible effects on hearing.

Risk of Progressive Sensorineural Hearing Loss and Meniere's Disease after Breast Implantation

1998 ◽  
Vol 118 (6) ◽  
pp. 747-750 ◽  
Author(s):  
DAVID WOOJIN KIM ◽  
JEFFREY P. HARRIS
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Breast Implants ◽  
Meniere’S Disease ◽  
Sensorineural Hearing ◽  
Meniere's Disease ◽  
Ménière’S Disease ◽  
Menière's Disease ◽  
Silicone Breast Implants ◽  
Ménière's Disease

OBJECTIVE: The association of various immunologic abnormalities with the presence of silicone breast implants in women has been described. In addition, some studies report a correlation between autoimmune disorders and silicone breast implants, whereas other studies indicate no difference in the incidence of disease between women with silicone breast implants and control groups. Until recently, no reports had attempted to identify an association between silicone breast implants and hearing impairment. A recent study suggested a possible correlation between prior silicone breast implants and the development of various forms of hearing loss. This study tried to determine whether such a correlation could be duplicated. METHODS: To determine whether such a correlation could be established, we studied 119 female patients with either Meniere's disease or progressive sensorineural hearing loss and 100 age-matched healthy controls. Subjects completed questionnaires that provided various types of information, including the presence or absence of previous silicone breast implants. Serum from all 119 patients with Meniere's disease and progressive sensorineural hearing loss had been subjected to previous Western blot testing for reactivity to a 68 kD protein associated with certain forms of autoimmune hearing loss. RESULTS: Results indicated no significant difference in frequency of prior silicone breast implants among the patients with Meniere's disease, patients with sensorineural hearing loss, or controls. The presence or absence of the 68 kD protein also was not significantly relevant to the frequency of silicone breast implants. CONCLUSIONS: Our data did not show evidence of a significant relationship between the presence of silicone breast implants and later development of Meniere's disease, progressive sensorineural hearing loss, or positive 68 kD serum. (Otolaryngol Head Neck Surg 1998;118:747-50.)

scholarly journals Sensorineural Hearing Loss following Carbon Monoxide Poisoning

2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
Joseph P. Pillion
Keyword(s):  
Carbon Monoxide ◽  
Hearing Loss ◽  
Brain Injury ◽  
Word Recognition ◽  
Sensorineural Hearing Loss ◽  
Recognition Performance ◽  
Carbon Monoxide Poisoning ◽  
Sensorineural Hearing ◽  
Severe Degree

A case study is presented of a 17-year-old male who sustained an anoxic brain injury and sensorineural hearing loss secondary to carbon monoxide poisoning. Audiological data is presented showing a slightly asymmetrical hearing loss of sensorineural origin and mild-to-severe degree for both ears. Word recognition performance was fair to poor bilaterally for speech presented at normal conversational levels in quiet. Management considerations of the hearing loss are discussed.

Ethmoidal Adenocarcinoma Presenting as Sensorineural Hearing Loss

1993 ◽  
Vol 7 (5) ◽  
pp. 241-244
Author(s):  
Faustino Nuñez ◽  
Ignacio Alvarez ◽  
Carlos Suarez ◽  
Valentin Mateos ◽  
Dulce M. Campos ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Clinical Manifestation ◽  
Relevant Literature ◽  
Meningeal Carcinomatosis ◽  
Sensorineural Hearing ◽  
Histopathological Findings ◽  
Early Stages ◽  
Patient’S History ◽  
Bilateral Deafness

We present a case of ethmoidal adenocarcinoma which in early stages of the disease produced a meningeal carcinomatosis. Its first clinical manifestation, bilateral deafness, is exceptional. The patient's history and endoscopic and histopathological findings are presented and the relevant literature is reviewed.

Reversible hearing loss following cryptococcal meningitis: case study

2016 ◽  
Vol 130 (7) ◽  
pp. 691-695 ◽  
Author(s):  
W L Neo ◽  
N Durisala ◽  
E C Ho
Keyword(s):  
Hearing Loss ◽  
Case Report ◽  
Bacterial Meningitis ◽  
Sensorineural Hearing Loss ◽  
Cochlear Implantation ◽  
Cryptococcal Meningitis ◽  
Sudden Onset ◽  
Sensorineural Hearing ◽  
Labyrinthitis Ossificans

AbstractBackground:Sensorineural hearing loss is a recognised complication of cryptococcal meningitis. The mechanism of hearing loss in patients with cryptococcal meningitis is different from that in bacterial meningitis.Case report:An immune-competent man with cryptococcal meningitis presented with sudden onset, bilateral, severe to profound sensorineural hearing loss and vestibular dysfunction. He was initially evaluated for cochlear implantation. However, he had a significant recovery; he no longer required surgery and was able to cope without a hearing aid.Conclusion:Typically, cochlear implantation is performed with some urgency in patients with hearing loss post-bacterial meningitis, because of the risk of labyrinthitis ossificans. However, this process has not been described in patients with cryptococcal meningitis. Furthermore, patients with hearing loss associated with cryptococcal meningitis have shown varying degrees of reversibility. In this case report, hearing loss from cryptococcal meningitis is compared with that from bacterial meningitis, and the need for cochlear implantation in patients with cryptococcal meningitis is discussed.

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