scholarly journals Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya

Author(s):  
Adinda Widita ◽  
Magda Hutagalung ◽  
Indri Lakhsmi Putri

Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder

2021 ◽  
Vol 147 (2) ◽  
pp. AB18
Author(s):  
Natalia Blanca-López ◽  
Ana MarÃa Prieto-Moreno Pfeifer ◽  
Diana Perez Alzate ◽  
Isabel Torres Rojas ◽  
Maria Luisa Somoza Alvarez ◽  
...  

2018 ◽  
Vol 26 (3) ◽  
pp. 145-147 ◽  
Author(s):  
Helene Retrouvey ◽  
Perry Gdalevitch

Gender disparity in plastic surgery in Canada is an important issue. The Women Plastic Surgeons of Canada (WPSC) group was created to highlight the interests and concerns of female members of the Canadian Society of Plastic Surgeons (CSPS). Women Plastic Surgeons of Canada seeks to teach and implement measures to overcome the internal and external factors contributing to “the plastic ceiling.” In addition, the WPSC group was created to raise awareness about the gender gap in our leadership and implement strategies to empower female surgeons to “lean in” and seek out leadership roles in plastic surgery. Education, mentorship, and networking among female CSPS members are first steps in empowering our female surgeons. All members of the CSPS are encouraged to learn about gender disparity in order to work together to address this issue.


2011 ◽  
Vol 8 (5) ◽  
pp. 450-454 ◽  
Author(s):  
Mohammad-Ali Jazayeri ◽  
John N. Jensen ◽  
Sean M. Lew

The authors report on the case of a 6-week-old boy who presented with infantile spasms. At 2.5 months of age, the patient underwent a right hemispherectomy. Approximately 3 months postoperatively, the patient presented with left coronal craniosynostosis. Subsequent cranial vault remodeling resulted in satisfactory cosmesis. Four years after surgery, the patient remains seizure free without the need for anticonvulsant medications. The authors believe this to be the first reported case of iatrogenic craniosynostosis due to hemispherectomy, and they describe 2 potential mechanisms for its development. This case suggests that, in the surgical treatment of infants with intractable epilepsy, minimization of brain volume loss through disconnection techniques should be considered, among other factors, when determining the best course of action.


2002 ◽  
Vol 10 (1) ◽  
pp. 11-14 ◽  
Author(s):  
Raman C Mahabir ◽  
Nicholas J Carr ◽  
Robert P Thompson ◽  
Richard J Warren

2021 ◽  
Vol 50 (4) ◽  
pp. E7
Author(s):  
Arvid Frostell ◽  
Maryam Haghighi ◽  
Jiri Bartek ◽  
Ulrika Sandvik ◽  
Bengt Gustavsson ◽  
...  

OBJECTIVE Isolated nonsyndromic sagittal synostosis (SS) is the most common form of craniosynostosis in children, accounting for approximately 60% of all craniosynostoses. The typical cranial measurement used to define and follow SS is the cephalic index (CI). Several surgical techniques have been suggested, but agreement on type and timing of surgery is lacking. This study aimed to evaluate the authors’ institutional experience of surgically treating SS using a modified subtotal cranial vault remodeling technique in a population-based cohort. Special attention was directed toward the effect of patient age at time of surgery on long-term CI outcome. METHODS A retrospective analysis was conducted on all patients with isolated nonsyndromic SS who were surgically treated from 2003 to 2011. Data from electronic medical records were gathered. Eighty-two patients with SS were identified, 77 fulfilled inclusion criteria, and 72 had sufficient follow-up data and were included. CI during follow-up after surgery was investigated with ANOVA and a linear mixed model. RESULTS In total, 72 patients were analyzed, consisting of 16 females (22%) and 56 males (78%). The mean ± SD age at surgery was 4.1 ± 3.1 months. Blood transfusions were received by 81% of patients (26% intraoperatively, 64% postoperatively, 9% both). The mean ± SD time in the pediatric ICU was 1.1 ± 0.25 days, and the mean ± SD total hospital length of stay was 4.6 ± 2.0 days. No patient required reoperation. The mean ± SD CI increased from 69 ± 3 to 87 ± 5 for patients who underwent surgery before 45 days of age. Surgery resulted in a larger increase in CI for patients who underwent surgery at a younger age compared with older patients (p < 0.05, Tukey’s HSD test). In the comparison of patients who underwent surgery before 45 days of age with patients who underwent surgery at 45–90, 90–180, and more than 180 days of age, the linear mixed model estimated a long-term loss of CI of 3.0, 5.5, and 7.4 points, respectively. CONCLUSIONS The modified subtotal cranial vault remodeling technique used in this study significantly improved CI in patients with SS. The best results were achieved when surgery was performed early in life.


2013 ◽  
Vol 70 (5) ◽  
pp. 655-659 ◽  
Author(s):  
Sarah E. Sasor ◽  
Roberto L. Flores ◽  
William A. Wooden ◽  
Sunil Tholpady

2021 ◽  
Vol 147 (3) ◽  
pp. 661-671
Author(s):  
Michael Alperovich ◽  
Christopher M. Runyan ◽  
Kyle S. Gabrick ◽  
Robin T. Wu ◽  
Chelsea Morgan ◽  
...  

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