scholarly journals Bilateral Sturge Weber Syndrome- a rare case report

2013 ◽  
Vol 5 (1) ◽  
pp. 129-132 ◽  
Author(s):  
P Singh ◽  
S Singh
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Unusual Case ◽  
The Other ◽  
Advanced Stage ◽  
Weber Syndrome ◽  
Rare Case Report ◽  
The Face ◽  
Bilateral Condition ◽  
Sturge Weber Syndrome

Background: Sturge-Weber syndrome is a rare congenital neuro- oculo- cutaneous disorder. Objective: To report a very rare unusual case of bilateral manifestation of Sturge Weber syndrome. Case: We report an unusual case of a 17-year-old female with advanced stage of bilateral glaucoma associated with facial nevus extending to the other half of the face as well and bilateral intracranial calcification. Conclusion: Sturge -Weber syndrome can manifest as a bilateral condition. Nepal J Ophthalmol 2013; 5(9):129-132 DOI: http://dx.doi.org/10.3126/nepjoph.v5i1.7841

STURGE WEBER SYNDROME- A RARE CASE REPORT ORIGINAL

2021 ◽  
pp. 4-5
Author(s):  
Om Prakash Singh ◽  
Vikas Kumar ◽  
Pushp Kant Tiwari
Keyword(s):  
Rare Case ◽  
Signs And Symptoms ◽  
Port Wine ◽  
Occipital Area ◽  
Weber Syndrome ◽  
Rare Case Report ◽  
The Face ◽  
Sturge Weber Syndrome ◽  
The Brain ◽  
Embryonic Vessels

Sturge-Weber Syndrome (SWS) is one of the encephalotrigeminal angiomatosis and one of the important segmental vascular neurocutaneous disorders .The occurrence is not very uncommon and the prevalence is 1:20000 to 1:50000.(1) SWS occurs due to the presence of residual embryonic vessels . The various signs and symptoms include capillary malformation in the face a port wine birthmark and similar malformation in the brain involving leptomeniges as well as blood vessels of the eye causing glaucoma. The patient presents with seizures , hemiparesis and stroke like symptoms, headaches and developmental delay.(2) The imaging nding in SWS children is the calcication in the parietal and occipital area of the brain. The EEG ndings in SWS are the attenuation and the excess of slow activities.We are presenting here a rare case of , a fourteen year old male child who presented to our emergency department with status epilepticus. The aim of presenting this case is to share the classical presentation and the challenges involved in the management

scholarly journals Sturge-Weber Syndrome– A Rare Case Report

2014 ◽  
Vol 13 (5) ◽  
pp. 39-41
Author(s):  
Divyank Pathak ◽  
◽  
Dhananjay.Y Shrikhande ◽  
Nilesh Maniya ◽  
Somdeepak Reddy ◽  
...  
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Weber Syndrome ◽  
Rare Case Report ◽  
Sturge Weber Syndrome

scholarly journals Solitary Trichoepithelioma of Nose: A Rare Case Report and Review of Literature

2015 ◽  
Vol 6 (3) ◽  
pp. 115-117
Author(s):  
Sachin Lal Shilpakar ◽  
Bivek Aryal ◽  
Shyam Thapa Chettri ◽  
Apar Pokharel ◽  
Deepak Paudel
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Histopathological Examination ◽  
Hair Follicles ◽  
Review Of Literature ◽  
Solitary Lesion ◽  
Biological Potential ◽  
Rare Case Report ◽  
The Face ◽  
Head Neck

ABSTRACT The trichoepithelioma is a benign cutaneous neoplasm which is derived from hair follicles. It is common in the face, but there are only three reports of the solitary occurrence on the nose. It is often not recognized because of its rarity, controversial classification, origin and biological potential. The objective of this paper is to present a case of solitary trichoepithelioma on the nose, histopathological examination and treatment. It should be considered as a differential diagnosis of a solitary lesion of nose which is confused with basal cell carcinoma. The confirmation by histopathological examination is essential. How to cite this article Sah BP, Shilpakar SL, Aryal B, Chettri ST, Pokharel A, Mishra S, Paudel D. Solitary Trichoepithelioma of Nose: A Rare Case Report and Review of Literature. Int J Head Neck Surg 2015;6(3):115-117.

scholarly journals Psoriasiform Mycosis Fungoides Involving the Face- A Rare Case Report

2021 ◽  
pp. 94-99
Author(s):  
N. R. Vignesh ◽  
Shreya Srinivasan ◽  
G. Sukanya ◽  
S. Arun Karthikeyan
Keyword(s):  
Case Report ◽  
Mycosis Fungoides ◽  
Rare Case ◽  
Cell Lymphoma ◽  
Punch Biopsy ◽  
Cutaneous T Cell Lymphoma ◽  
Rare Presentation ◽  
Rare Case Report ◽  
Atypical Cells ◽  
The Face

Mycosis fungoides is represented as the most common epidermotropic cutaneous T-cell lymphoma, which is mainly characterized by the proliferation of atypical cells within the epidermis. We report a rare presentation of mycosis fungoides in a 60-year-old male presenting with chronic psoriasiform plaque involving the face. Punch biopsy of the lesion from the forehead was taken for routine histological examination and immunohistochemical stains. Results of biopsy and immunohistochemical findings were consistent with mycosis fungoides and diagnosed as psoriasiform presentation of mycosis fungoides involving the face.

A Rare Case of Incidentally Detected Sturge-Weber Syndrome: a Case Report and Review of the Current Surgical Procedures

2019 ◽  
Vol 1 (9) ◽  
pp. 655-658
Author(s):  
Moawia Bushra Gameraddin ◽  
Kamal Dahan ◽  
Fathelrehman Alagab ◽  
Mariam Khojali
Keyword(s):  
Case Report ◽  
Surgical Procedures ◽  
Rare Case ◽  
Weber Syndrome ◽  
Sturge Weber Syndrome

scholarly journals Isolated Bilateral Zygomatic Complex and Arch Fracture: A Rare Case Report

2010 ◽  
Vol 3 (4) ◽  
pp. 185-187 ◽  
Author(s):  
Manikandhan Ramanathan ◽  
Mathew Pynumootil Cherian
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Unusual Case ◽  
Rare Case Report

This is an unusual case of isolated bilateral zygomatic complex and arch fracture, which is extremely rare. The literature has no such report of a case.

scholarly journals Pulmonary thromboembolism associated with Klippel Trenaunay Weber Syndrome: A rare case report

2016 ◽  
Vol 15 (10) ◽  
pp. 10-12
Author(s):  
Talib S H ◽  
Bhattu S R ◽  
Punde Gaurav ◽  
Hegde Rohan ◽  
Sarode Vinit ◽  
...  
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Pulmonary Thromboembolism ◽  
Weber Syndrome ◽  
Rare Case Report

scholarly journals Bilateral Total Aplasia of Paranasal Sinuses: A Rare Case Report

2015 ◽  
Vol 8 (3) ◽  
pp. 124-126
Author(s):  
Ankita Joshi ◽  
Chinmay Sundarray ◽  
Krishna Arpita Sahoo
Keyword(s):  
Case Report ◽  
Paranasal Sinus ◽  
Paranasal Sinuses ◽  
Rare Case ◽  
The Other ◽  
High Rate ◽  
Unknown Etiology ◽  
Structural Variations ◽  
The Third ◽  
Rare Case Report

ABSTRACT Paranasal sinus anatomical anomalies with unknown etiology are common. Paranasal sinus-related diseases are associated with so high rate of morbidities, it becomes essential to identify the structure and pathophysiology of the paranasal sinuses. Computed tomography (CT) is a valuable tool in displaying its anatomy, any anatomic variations and diseases. As paranasal sinus development is a complex and long-lasting process, there are great structural variations between individuals. Maxillary and/or frontal sinus aplasia or hypoplasia are more common than the other types. Several degrees and combinations of aplasias and hypoplasias have been reported; however, there is only two case of total paranasal sinus aplasia in the literature. Here, we present the third case of total paranasal sinus aplasia, and the first ever case reported from India. How to cite this article Joshi A, Sundarray C, Sahoo KA. Bilateral Total Aplasia of Paranasal Sinuses: A Rare Case Report. Clin Rhinol An Int J 2015;8(3):124-126.

HECK'S DISEASE – A RARE CASE REPORT

2021 ◽  
pp. 40-43
Author(s):  
Seema Patil ◽  
M. Ekta ◽  
Asha. R. Iyengar ◽  
Revan Kumar Joshi ◽  
Ritika Agarwal ◽  
...  
Keyword(s):  
Case Report ◽  
Oral Mucosa ◽  
Rare Case ◽  
Unusual Case ◽  
Indian Subcontinent ◽  
Case Reports ◽  
Benign Lesion ◽  
Human Papilloma Viruses ◽  
Rare Case Report ◽  
Indian Male

Heck's disease is a familial benign lesion affecting the oral mucosa and skin caused by Human papilloma viruses 13 and 32. This condition is quite rare in the Indian subcontinent and till date less than 10 case reports have been published. Females are predominantly affected. It is important for an oral physician to be aware and possess sufcient knowledge about these lesions as these lesions are highly contagious. Further, the presence of these lesions may indicate an underlying immunodecient state of the patient. This paper reports an unusual case of Heck's disease in a 30 year old Indian male.

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