scholarly journals Large Retroperitoneal Perivascular Epithelioid Cell Neoplasm (PEComa): A Case Report and a Brief Review

2021 ◽  
pp. 1-6
Author(s):  
Giorgio Lucandri ◽  
Giorgio Lucandri ◽  
Marco Maria Lirici ◽  
Alessia Fassari ◽  
Vito Pende ◽  
...  
Keyword(s):  
Case Report ◽  
Immunohistochemical Staining ◽  
Correct Diagnosis ◽  
Distant Metastases ◽  
Complete Removal ◽  
En Bloc Resection ◽  
Epithelioid Cell ◽  
Bloc Resection ◽  
En Bloc ◽  
Perivascular Epithelioid Cell

Objective: To describe a case of retroperitoneal perivascular epithelioid cell tumor (PEComa) and to discuss the main features of this rare pathology. Introduction: PEComas represent a rare cluster of neoplasms with uncertain origin; their precursor cells are spindle-shaped and characterized by a myomelanocytic phenotype, so only immunohistochemical staining makes a definitive diagnosis possible. To date, less than three hundred cases are reported in Literature and retroperitoneal site accounts for 7-8% of overall locations. Case Report: Middle-aged female has visited for abdominal pain and urinary complaints; physical findings and imaging demonstrated a huge inhomogeneous mass occupying right abdomen and arising from renal capsule. After multidisciplinary evaluation, patient has been addressed to open surgery and an en-bloc resection of the mass, with right nephrectomy and adrenalectomy. Immunohistochemical staining made a diagnosis of PEComa possible. After an uneventful postoperative stay, the patient entered a follow up protocol, without signs of local recurrence and distant metastases. Conclusion: Retroperitoneal PEComa often presents as a bulky mass with renal and adrenal involvement. Surgical resection should be aimed to obtain a complete removal with negative margins; this makes compartment surgery and en-bloc resection mandatory. Immunostaining is the key methods for a correct diagnosis.

scholarly journals Primary Leiomyosarcoma of the Lumbar Spine: A Case Report and Literature Review

2021 ◽  
pp. 1-6
Author(s):  
Eric Luis ◽  
Eric Luis ◽  
Vasanthie Balakrishnan ◽  
Zainur Anuar bin Kamarul Bahrin ◽  
Han Sim Lim ◽  
...  
Keyword(s):  
Spinal Cord ◽  
Case Report ◽  
Literature Review ◽  
Immunohistochemical Staining ◽  
Tumor Recurrence ◽  
En Bloc Resection ◽  
Bloc Resection ◽  
En Bloc ◽  
First Case ◽  
Staining Techniques

Primary vertebral leiomyosarcoma of the spine is extremely rare. Due to its rarity, the number of studies on pathology, treatment and prognosis is limited. Tissue Biopsy and Immunohistochemical staining techniques provide unequivocal diagnosis of leiomyosarcoma. The mainstay of treatment of spinal leiomyosarcoma is surgery, with or without radiotherapy and embolization. The principles of surgery comprise resection of tumor, decompression and stabilisation of the spinal cord and prevention of tumor recurrence. The Tomita total en-bloc resection is the preferred surgical technique. We hereby present a literature review of spinal leiomyosarcoma and a case report of the first case of a 56-year-old lady in Malaysia who was diagnosed with L3 vertebral leiomyosarcoma and lung metastasis.

scholarly journals A Giant retroperitoneal liposarcoma encasing entirely the right kidney: A case report and a review of nephrectomy indications

2021 ◽  
Author(s):  
Houssem Harbi ◽  
Amira Akrout ◽  
Mohamed Fourati ◽  
Amine Zouari ◽  
Nozha Toumi
Keyword(s):  
Elderly Patient ◽  
Case Report ◽  
En Bloc Resection ◽  
Bloc Resection ◽  
Resection Margins ◽  
En Bloc ◽  
Retroperitoneal Liposarcoma ◽  
R1 Resection ◽  
The Right

A 68-year-old female was operated for a giant dedifferentiated retroperitoneal liposarcoma (RLS) encasing entirely the right kidney. She had an en-bloc resection of the tumor with right nephrectomy. The en-bloc resection should avoid R1 resection margins. Renal conservation is suggested if the kidney is widely displaced and for elderly patient.

scholarly journals Successful en bloc resection of an esophageal hemangioma by combined EBL & EMR: a case report and technical review

2016 ◽  
Vol 1 ◽  
pp. 45-45 ◽  
Author(s):  
Il Hyun Baek ◽  
Jung Won Jeon ◽  
Hyun Phil Shin ◽  
Jae Myung Cha ◽  
Kwang Ro Joo ◽  
...  
Keyword(s):  
Case Report ◽  
En Bloc Resection ◽  
Bloc Resection ◽  
En Bloc ◽  
Technical Review

scholarly journals En bloc resection of the external iliac vein along with broad ligament leiomyosarcoma: A case report

2019 ◽  
Vol 23 ◽  
pp. e00131 ◽  
Author(s):  
Fatima Ahmed ◽  
Rachel Pounds ◽  
Hong-Giap Teo ◽  
James Nevin ◽  
Kavita Singh ◽  
...  
Keyword(s):  
Case Report ◽  
Broad Ligament ◽  
Iliac Vein ◽  
En Bloc Resection ◽  
Bloc Resection ◽  
En Bloc ◽  
External Iliac Vein

Fracture of the Tarsal Navicular Associated with Calcaneonavicular Coalition: A Case Report

1995 ◽  
Vol 16 (12) ◽  
pp. 800-802 ◽  
Author(s):  
Yasuhito Tanaka ◽  
Yoshinori Takakura ◽  
Kouichi Akiyama ◽  
Shigeru Kamei ◽  
Masato Nukata ◽  
...  
Keyword(s):  
Case Report ◽  
Full Range ◽  
En Bloc Resection ◽  
Bloc Resection ◽  
Truck Driver ◽  
Fracture Line ◽  
Long Distance ◽  
En Bloc ◽  
Calcaneonavicular Coalition ◽  
Level Of Activity

Fracture of the navicular occurred in a 23-year-old male with unilateral cartilaginous calcaneonavicular coalition. Inversion sprain of the left foot caused the longitudinal navicular fracture next to the coalition. En bloc resection from the beak of the calcaneus to the fracture line of the navicular including the calcaneonavicular coalition was performed, and a short leg cast was applied for 10 days. Four weeks after surgery, he returned to his preinjury level of activity and job as a long-distance truck driver. Two years and 3 months after surgery, he was totally asymptomatic and had gained a full range of subtalar motion. He had no peroneal spasm or recurrence of the coalition.

scholarly journals Surgical treatment of desmoplastic fibroma in the jaw using mandibular graft reconstruction – a case report

RSBO ◽  
2018 ◽  
Vol 15 (2) ◽  
pp. 130-04
Author(s):  
Rafaela Savio Melzer ◽  
Daniela Cristina Lunelli ◽  
Cleverson Patussi ◽  
Laurindo Moacir Sassi
Keyword(s):  
Case Report ◽  
Benign Lesion ◽  
Bone Lesion ◽  
En Bloc Resection ◽  
Bloc Resection ◽  
Desmoplastic Fibroma ◽  
En Bloc ◽  
Graft Harvest ◽  
Long Term Follow Up ◽  
Rare Benign Tumour

: Considered a rare benign tumour of fibroblastic origin, desmoplastic fibroma is an injury with aggressive behaviour and local recurrence and unclear aetiology, although trauma and genetic factors are considered. The pathology may develop in the femur, radio, pelvis and tibia, and rarely affects the jaws, characterized as an injury of slow asymptomatic growth that may vary radiographically. The local aggressive resection is the treatment of choice. Objective: To report a case of a desmoplastic fibroma in the mandible, whose treatment was en bloc resection followed by reconstruction with mandibular graft. Case report: Female patient, 33 years old, Caucasian, with a bone lesion discovered in routine x-ray. Images showed hypodense image with discrete destruction of bone cortical, near teeth 36 and 37, with no involvement of the roots. The chosen treatment was en bloc resection followed by reconstruction with mandibular graft harvest from ramus. Conclusion: desmoplastic fibroma is a benign lesion that should be included in the differential diagnosis list of osteolytic lesions. A long-term follow up is required, considering the potential to recurrence.

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