scholarly journals The First of Congenital Cystic Adenomatoid Lung Malformation in Iraq: A Radiologic and Pathologic Study

2020 ◽  
Vol 1 (1) ◽  
pp. 01-03
Author(s):  
Aamir Mosawi
Keyword(s):  
Respiratory Distress ◽  
Left Lung ◽  
Rare Condition ◽  
Male Infant ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Lung Field ◽  
Microscopical Examination ◽  
Pulmonary Tissue ◽  
Cystic Adenomatoid Malformation ◽  
The Right

Background: Congenital cystic adenomatoid lung malformation is a very rare condition characterized by replacement of normal pulmonary tissue with cysts of variable size and distribution. The condition is usually unilateral. Very few cases of bilateral and congenital cystic adenomatoid malformation with good outcome after resections of the lesions have been reported, and most cases were stillborn or died early during life. Patients and methods: A forty-day male infant presented with progressive respiratory distress since the first week of life observed at the Children Teaching Hospital of Baghdad Medical City was studied. The literature was reviewed with aim of describing the early documentation of the condition in the literature. Results: Clinically, the infant had significant respiratory distress interfering with feeding and evidence of shift of the mediastinum to the right. Chest X ray showed increased translucency of left lung field and mediastinal shit to the right. CT-scan showed large air-filled cyst in the left lung and small air-filled cyst in the right lung. The child was treated successfully by left upper lobecomy. The gross examination of two gray pieces of lung tissue showed on cut section microcysts that were apparent grossly. Microscopical examination showed intercommunicating cysts lined by cuboidal epithelium with gland like appearance confirming the diagnosis of congenital cystic adenomatoid malformation of the lung. Conclusion: A very rare case of bilateral congenital cystic adenomatoid malformation of the lung is reported and the early documentation of the condition in the literature is described.

scholarly journals Congenital cystic adenomatoid malformation: a rare serial case report

2021 ◽  
Vol 9 (1) ◽  
pp. 190
Author(s):  
Dedy C. Haryono ◽  
Muhammad Kartika ◽  
Prima K. Hayuningrat ◽  
Darmawan Ismail
Keyword(s):  
Respiratory Distress ◽  
Lung Resection ◽  
Left Lung ◽  
Chest Ct ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Congenital Lung Malformation ◽  
Cystic Adenomatoid Malformation ◽  
The Right ◽  
Multiple Cysts

Congenital cystic adenomatoid malformation (CCAM) is a rare congenital lung malformation which a part of the lung becomes polycystic. CCAM accounts for 25% of congenital lung malformations and 95% of lung lesions. Case 1 was a 5-month-old female infant who was diagnosed with pneumothorax, with multiple cysts in the right lung, using chest computed tomography (CT). Thoracotomy lung resection was performed. Case 2 was one-day-old newborn infant who had respiratory distress with Downe score 3. Multiple cystic lesions with septations in left lung was observed on chest CT. Lobectomy inferior lobes of left lung was performed. Both patients were diagnosed as CCAM type 1 pathologically. CCAM can be detected in the gestation by ultrasonography or after delivery through the appearance of respiratory distress signs.

Recurrent croup in a young child: look beyond airways disease

2021 ◽  
Vol 14 (2) ◽  
pp. e236605
Author(s):  
Saurav Jain ◽  
Taruna Yadav ◽  
Prawin Kumar ◽  
Jagdish Prasad Goyal
Keyword(s):  
Left Lung ◽  
Rare Condition ◽  
Lung Field ◽  
Ct Angiogram ◽  
Breath Sounds ◽  
Cardiac Apex ◽  
Right Pulmonary Artery ◽  
Chest Examination ◽  
Pulmonary Arterial ◽  
The Right

We reported here a boy aged 5 years who presented for the evaluation of recurrent croup since infancy. On chest examination, breath sounds were reduced throughout the right lung field with a shifting of the trachea and cardiac apex to the right side. The chest radiograph showed a small right lung with decreased vascularity, hyperinflated left lung and mediastinum shifted towards the right side. Flexible bronchoscopy revealed tracheomalacia with left bronchomalacia due to external pulsatile compression. In CT angiogram, the right pulmonary artery (PA) was absent with dilated left PA. Echocardiography did not show any features of pulmonary arterial hypertension (PAH). Since the child was growing well, and there was no limitation of activity and evidence of PAH, he was managed conservatively and kept on follow-up. Though unilateral absent PA is a rare condition, it should be suspected in children with unilateral hypoplastic lung.

scholarly journals Congenital cystic adenomatoid malformation of lung: A case report

2015 ◽  
Vol 10 (1) ◽  
pp. 41-42
Author(s):  
Asish Banerjee ◽  
Sumita Pal ◽  
Anish Chatterjee ◽  
A Pan
Keyword(s):  
Case Report ◽  
Respiratory Distress ◽  
Lung Lesion ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Medical Sciences ◽  
Cystic Lung ◽  
Cystic Adenomatoid Malformation ◽  
Cystic Lung Lesion ◽  
The Right ◽  
Tomography Scan

A term neonate developed respiratory distress after 12 hours of birth which was diagnosed as a case of congenital cystic adenomatoid malformation (CCAM) of the right lung by computerized tomography scan. CCAM of the lung is rare congenital cystic lung lesion. DOI: http://dx.doi.org/10.3126/jcmsn.v10i1.12767 Journal of College of Medical Sciences-Nepal, 2014, Vol.10(1); 41-42

scholarly journals Hydrops fetalis secondary to supradiaphragmatic extrapulmonary sequestration with congenital cystic adenomatoid malformation

2017 ◽  
Vol 7 (1) ◽  
pp. 1130-1132 ◽  
Author(s):  
S Shukla ◽  
H Kini ◽  
ML Ilias ◽  
K Gautam
Keyword(s):  
Left Lung ◽  
Breech Presentation ◽  
Hydrops Fetalis ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Associated Anomalies ◽  
Male Baby ◽  
Pain Abdomen ◽  
Cystic Adenomatoid Malformation ◽  
Mediastinal Shift ◽  
Fetal Movements

Congenital cystic adenomatoid malformation is a hamartomatous lesion. A 30 year old woman, G2P1L1, in the 29th week of gestation presented with pain abdomen, chest pain, cough with expectoration, fever and inability to appreciate fetal movements of 2 days duration. Clinically, she had pneumonia. An ultrasound revealed a single fetus in breech presentation with features of hydrops fetalis, hypoplastic left lung, mediastinal shift to the left and poor diastolic and systolic flow in the umbilical artery.A still born male baby delivered subsequently was found at autopsy to have hydrops fetalis, supradiaphragmatic right sided extralobar sequestration with associated congenital cystic adenomatoid malformation.The right lung also showed congenital cystic adenomatoid malformation. There were no other associated anomalies. We present a rare case of extralobar sequestrationwith congenital cystic adenomatoid malformation.

scholarly journals Congenital Cystic Adenomatoid Malformation Of The Lung: A Case Report And Review Of The Literature

2015 ◽  
Vol 8 (2) ◽  
pp. 160-163
Author(s):  
Doroteya V. Malinova ◽  
Penka L. Kolova ◽  
Radoslav S. Radev
Keyword(s):  
Lung Development ◽  
Incidental Finding ◽  
Ct Scanning ◽  
Final Diagnosis ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Pulmonary Infections ◽  
Cystic Adenomatoid Malformation ◽  
Clinical Presentations ◽  
The Right

Summary Congenital cystic adenomatoid malformation (CCAM) is a rare abnormality of lung development. It was classified into 5 types by Stocker in 2002 and is also known under the name of congenital pulmonary airway malformation (CPAM). Cases are typically identified prenatally by routine ultrasonography screening. CCAM may present in the older child and adult as an incidental finding. The case presented is of a 21-year-old male patient who suffered from pulmonary infections with a recurrent productive cough 3-4 times the last 4 years. CT scanning of the thorax showed multiple cystic lesions in the right middle and lower lobes. The areas with the lesions were resected. The macroscopic and histological findings were typical for congenital cystic adenomatoid malformation type 2, which was the final diagnosis. Clinical presentations and prognosis depend on the type of lesion and its sequelae. The diagnosis is confirmed histologically.

scholarly journals Explosive Pleuritis

2001 ◽  
Vol 12 (2) ◽  
pp. 104-107 ◽  
Author(s):  
Jasdeep K Sharma ◽  
Thomas J Marrie
Keyword(s):  
Computed Tomography ◽  
Pleural Effusion ◽  
Respiratory Distress ◽  
Pleural Fluid ◽  
Case Definition ◽  
Pulmonary Tissue ◽  
X Ray ◽  
Mediastinal Shift ◽  
Chest X Ray ◽  
The Right

The objective of the present paper is to describe the clinical and computed tomography features of 'explosive pleuritis', an entity first named by Braman and Donat in 1986, and to propose a case definition. A case report of a previously healthy, 45-year-old man admitted to hospital with acute onset pleuritic chest pain is presented. The patient arrived at the emergency room at 15:00 in mild respiratory distress; the initial chest x-ray revealed a small right lower lobe effusion. The subsequent clinical course in hospital was dramatic. Within 18 h of admission, he developed severe respiratory distress with oxygen desaturation to 83% on room air and dullness of the right lung field. A repeat chest x-ray, taken the morning after admission, revealed complete opacification of the right hemithorax. A computed tomography scan of the thorax demonstrated a massive pleural effusion with compression of pulmonary tissue and mediastinal shift. Pleural fluid biochemical analysis revealed the following concentrations: glucose 3.5 mmol/L, lactate dehydrogenase 1550 U/L, protein 56.98 g/L, amylase 68 U/L and white blood cell count 600 cells/mL. The pleural fluid cultures demonstrated light growth of coagulase-negative staphylococcus and viridans streptococcus, and very light growth ofCandida albicans. Cytology was negative for malignant cells. Thoracotomy was performed, which demonstrated a loculated parapneumonic effusion that required decortication. The patient responded favourably to the empirical administration of intravenous levofloxacin and ceftriaxone, and conservative surgical methods in the management of the empyema. This report also discusses the patient's rapidly progressing pleural effusion and offers a potential case definition for explosive pleuritis. Explosive pleuritis is a medical emergency defined by the rapid development of a pleural effusion involving more than 90% of the hemithorax over 24 h, which causes compression of pulmonary tissue and mediastinal shift to the contralateral side.

scholarly journals Tension hydrothorax in a patient with SARS-CoV-2 pneumonitis and pleural Mycobacterium tuberculosis

2021 ◽  
Vol 14 (7) ◽  
pp. e243760
Author(s):  
Mohsin F Butt ◽  
Maggie Symonds ◽  
Ruhaid Khurram
Keyword(s):  
Emergency Department ◽  
Mycobacterium Tuberculosis ◽  
Pleural Effusion ◽  
Respiratory Distress ◽  
Chest Radiograph ◽  
Left Lung ◽  
Pleural Effusions ◽  
Mediastinal Shift ◽  
History Of ◽  
The Right

Unilateral pleural effusions are uncommonly reported in patients with SARS-CoV-2 pneumonitis. Herein, we report a case of a 42-year-old woman who presented to hospital with worsening dyspnoea on a background of a 2-week history of typical SARS-CoV-2 symptoms. On admission to the emergency department, the patient was severely hypoxic and hypotensive. A chest radiograph demonstrated a large left-sided pleural effusion with associated contralateral mediastinal shift (tension hydrothorax) and typical SARS-CoV-2 changes within the right lung. She was treated with thoracocentesis in which 2 L of serosanguinous, lymphocyte-rich fluid was drained from the left lung pleura. Following incubation, the pleural aspirate sample tested positive for Mycobacterium tuberculosis. This case demonstrates the need to exclude non-SARS-CoV-2-related causes of pleural effusions, particularly when patients present in an atypical manner, that is, with tension hydrothorax. Given the non-specific symptomatology of SARS-CoV-2 pneumonitis, this case illustrates the importance of excluding other causes of respiratory distress.

scholarly journals An optimistic point in COVID-19 pandemic: a case report of large adult congenital cystic adenomatoid malformation

2021 ◽  
Vol 52 (1) ◽  
Author(s):  
Mohamed rafi Kathar Hussain ◽  
N. Kulasekeran ◽  
A. M. Anand
Keyword(s):  
Case Report ◽  
Cystic Lesion ◽  
Histopathological Examination ◽  
Left Lung ◽  
Lower Lobe ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Unexpected Finding ◽  
Rare Presentation ◽  
Cystic Adenomatoid Malformation ◽  
Large Adult

Abstract Background Covid-19 pandemic is a major health calamity causing global crisis involving every aspect of the society. CT chest has become an essential diagnostic investigation and as a prognostic tool for assessment for COVID-19 bronchopneumonia. This case report is about an incidental unexpected finding in a young female, who underwent CT chest screening with suspicion of COVID-19 bronchopneumonia. Case presentation A 29-year-old female came with the complaints of sore throat, myalgia, and fever for the past 3 days. She was referred to our department for plain screening CT chest to rule out COVID 19 infection. She was an active sports person since childhood. CT chest revealed a large well-defined bullous cystic lesion of size 16 × 9.5 × 9.5 cm in the left lung lower lobe with partial sparing of its superior, anterior, and posterior basal segments. Imaging diagnosis of large bullous cystic lesion with emphysematous changes was made. No features of COVID 19 bronchopneumonia. Thoracoscopy-guided lobectomy was done, and tissue was sent to histopathological examination. Final diagnosis was large type 1 congenital cystic adenomatoid malformation with mucinous metaplasia. Our case is unique in the sense that large adult CCAM with mucinous metaplasia of the epithelium is a rare presentation. Further it was diagnosed as a part of COVID 19 screening. Conclusion CCAM presentation in adult is rare. Asymptomatic CCAM lesion of this size diagnosed during COVID 19 chest CT screening was rarely described.

scholarly journals Congenital Lobar Emphysema in a 17-Day-Old Male Neonate: The Plain Radiographic Features and a Case Report

2022 ◽  
Vol 3 (1) ◽  
pp. 01-03
Author(s):  
Sule MB ◽  
Umar AU ◽  
Gele IH ◽  
Ribah MM ◽  
Aliyu AZ
Keyword(s):  
Left Lung ◽  
Respiratory Disorder ◽  
Lung Field ◽  
Radiographic Findings ◽  
Female Ratio ◽  
Congenital Lobar Emphysema ◽  
Young Infants ◽  
Lobar Emphysema ◽  
Male Neonate ◽  
The Right

Congenital lobar emphysema (CLE) is a rare respiratory disorder which allows air to enter the lungs but can’t escape causing over-inflation of the lobes of the lung. This condition (CLE) is commonly detected in the newborn or young infants but some cases are diagnosed in adulthood. Congenital lobar emphysema is a rare congenital malformation with a prevalence of 1 in 20,000 to 1 in 30, 000, and more prevalent in males, with a male to female ratio of about 3:1. This is a 17 day old male neonate that presented with respiratory difficulty and .had a supine chest radiograph that showed an overinflated left lung field more on the upper and middle zones with flattening of the left hemi diaphragm, marked shift of the heart and mediastinum to the right with some degree of loss of volume involving the right lung. We report the radiographic findings of this case due the rare nature of congenital lobar emphysema.

scholarly journals Congenital Cystic Adenomatoid Malformation of Lung in an Infant

2020 ◽  
Vol 15 (2) ◽  
pp. 235-236
Author(s):  
SM Shahadat Hossain ◽  
Khan Nazmul Haque ◽  
Mahbuba Sultana
Keyword(s):  
General Anaesthesia ◽  
Congenital Cystic Adenomatoid Malformation ◽  
X Ray ◽  
Cystic Adenomatoid Malformation ◽  
Chest X Ray ◽  
The Right ◽  
Excessive Proliferation

Congenital Cystic Adenomatoid Malformation (CCAM) is considered a hamartomatous lesion of lung with excessive proliferation of bronchial structure without alveoli.  We have treated a child of 12 months who presented with difficulty in breathing after birth and chest x-ray PA view shows increase lucency in the right upper zone suggestive of CCAM. Patient underwent right upper lobectomy under general anaesthesia and now she is fine. JAFMC Bangladesh. Vol 15, No 2 (December) 2019: 235-236

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