scholarly journals Amelogenesis Imperfecta: A Case Series from the Community

2018 ◽  
Vol 56 (214) ◽  
pp. 977-979
Author(s):  
Abanish Singh ◽  
Santosh Kumari Agrawal ◽  
Ashish Shrestha ◽  
Tarakant Bhagat
Keyword(s):  
Oral Hygiene ◽  
Multidisciplinary Approach ◽  
Case Series ◽  
Good Prognosis ◽  
Amelogenesis Imperfecta ◽  
Deciduous Teeth ◽  
Oral Rehabilitation ◽  
Lateral Cephalogram ◽  
Enamel Structure

Amelogenesis Imperfecta is a hereditary disorder affecting the formation of enamel structure. Two female children and one male (11 years, 12 years and 6 years respectively) reported with chief complaint of yellowish discoloration of teeth since their childhood. They reported that they had similar discoloration in their deciduous teeth. Examination showed generalized deposits of plaque and calculus, yellowish discoloration of the teeth with chipping off of the incisal and cuspal enamel structures. OPG revealed thin lining of enamel with thick dentin layer and pulp chamber. PA view revealed unfused anterior fontanels and lateral cephalogram indicated vertebrae in growing phase. The patients were instructed to maintain proper oral hygiene and regular follow up till the growth cessation. Permanent skeletal, functional, esthetic needs is addressed after growth completion. Oral rehabilitation through multidisciplinary approach can certainly provide a good prognosis and patient was counseled and motivated to maintain good oral hygiene.

Early oral rehabilitation of amelogenesis imperfecta: A case series

2018 ◽  
Vol 3 (2) ◽  
pp. 80
Author(s):  
Kashika Arora ◽  
DeepaVinod Bhat ◽  
Malay Mitra ◽  
Subrata Saha
Keyword(s):  
Case Series ◽  
Amelogenesis Imperfecta ◽  
Oral Rehabilitation

The Neurological Compromised Spine Due to Ewing Sarcoma. What First

Neurosurgery ◽  
2015 ◽  
Vol 77 (5) ◽  
pp. 718-725 ◽  
Author(s):  
Lida Mirzaei ◽  
Suzanne E.J. Kaal ◽  
Hendrik W.B. Schreuder ◽  
Ronald H.M.A. Bartels
Keyword(s):  
Ewing Sarcoma ◽  
Neurological Deficit ◽  
Multidisciplinary Approach ◽  
Cauda Equina ◽  
Case Series ◽  
Decompressive Laminectomy ◽  
Cauda Equina Compression ◽  
Before And After ◽  
Frankel Grade

Abstract BACKGROUND: The vertebral column is an infrequent site of primary involvement in Ewing sarcoma. Yet when Ewing sarcoma is found in the spine, the urge for decompression is high because of the often symptomatic compression of neural structures. It is unclear in alleviating a neurological deficit whether chemotherapy is preferred over decompressive laminectomy. OBJECTIVE: To underline, in this case series, the efficiency of initial chemotherapy before upfront surgery in the setting of high-grade spinal cord or cauda equina compression of primary Ewing sarcoma. METHODS: Fifteen patients with Ewing sarcoma primarily located in the spine were treated at our institution between 1983 and 2015. Localization, neurological deficit expressed as Frankel grade, and outcome expressed as Rankin scale before and after initial chemotherapy, the recurrence rate, and overall survival were evaluated. The multidisciplinary approach of 1 case will be discussed in detail. RESULTS: Nine patients (60%) were female. The age at presentation was 15.0 ± 5.5 years (range: 0.9–22.8 years). Ten patients (67%) were initially treated with chemotherapy, and 1 patient (7%) was treated primarily with radiotherapy followed by chemotherapy. The remaining 4 patients (27%) were initially treated with decompressive surgery. All patients treated primarily nonsurgically improved neurologically at follow-up, showing the importance of chemotherapy as an effective initial treatment option. CONCLUSION: Adequate and quick decompression of neural structures with similar results can be achieved by chemotherapy and radiotherapy, avoiding the local spill of malignant cells.

Management of uterine malignancy found incidentally after supracervical hysterectomy or uterine morcellation for presumed benign disease

2008 ◽  
Vol 18 (5) ◽  
pp. 1065-1070 ◽  
Author(s):  
M. H. Einstein ◽  
R. R. Barakat ◽  
D. S. Chi ◽  
Y. Sonoda ◽  
K. M. Alektiar ◽  
...  
Keyword(s):  
Case Series ◽  
Good Prognosis ◽  
Uterine Disease ◽  
Retrospective Case ◽  
Secondary Surgery ◽  
Supracervical Hysterectomy ◽  
Initial Surgery ◽  
Completion Surgery ◽  
Disease Free

Patients who have undergone supracervical hysterectomy or uterine morcellation for presumed benign uterine disease and are found to have malignancy on final pathology represent a management dilemma. Our goal was to analyze our experience and make observations regarding staging, treatment, and outcomes. We performed a retrospective case series of patients referred to our institution with uterine malignancy who previously underwent supracervical hysterectomy or uterine morcellation at the time of original surgery for presumed benign uterine disease. Between January 2000 and March 2006, 17 patients with uterine malignancy were identified. Following initial surgery, 15 (88%) patients had presumed stage I disease and 2 (12%) patients had stage III disease. Two (15%) of 13 patients who underwent completion surgery were upstaged; both had leiomyosarcoma (LMS) originally resected with morcellation. Ten of 11 patients whose stage was confirmed with secondary surgery remain disease free. None of the patients who initially underwent supracervical hysterectomy without morcellation were upstaged by secondary surgery. The median follow-up interval was 30 months (range, 2–90 months). Reoperation for completion surgery and staging is important when uterine malignancy is found incidentally after morcellation or supracervical hysterectomy for presumed benign uterine disease. Approximately 15% of patients will be upstaged by reexploration, particularly those with LMS who underwent morcellation. Patients who undergo completion surgery with restaging and are not upstaged appear to have a good prognosis. Surgical staging is valuable for prognosis and may alter postoperative treatments

scholarly journals Amelogenesis Imperfecta – Case Series and Management

2019 ◽  
pp. 12-17
Author(s):  
Rishi Tyagi ◽  
Namita Kalra ◽  
Amit Khatri ◽  
Harsh Singh ◽  
Mayank Sharma ◽  
...  
Keyword(s):  
Early Intervention ◽  
Preventive Care ◽  
Autosomal Recessive ◽  
Autosomal Dominant ◽  
Case Series ◽  
Amelogenesis Imperfecta ◽  
Hereditary Diseases ◽  
Enamel Defects ◽  
Dental Rehabilitation

Amelogenesis imperfecta (AI) incorporates an assemblage of hereditary diseases that involve the defective formation or calcification of enamel. Also known by varied names such as Hereditary enamel dysplasia, Hereditary brown enamel, Hereditary brown opalescent teeth, this defect is entirely ectodermal, since mesodermal components are unaffected. AI is typically characterized by generalized enamel defects in both primary and permanent dentition. The AI trait can be transmitted by either autosomal dominant, autosomal recessive, or X-linked modes of inheritance.AI has a marked impact on aesthetics, function and psychology of the patient. Early intervention and dental rehabilitation should be carried out with strong emphasis on the preventive care and strict follow up schedule. Key words: Amelogenesis imperfecta, developmental anomaly, Dental Rehabilitation

scholarly journals Peripartum Cardiomyopathy- A Case Series Report in a Tertiery Hospital in Pondicherry for Two Years

2020 ◽  
pp. 9-14
Author(s):  
Dr. Shyamala Shyamala ◽  
Dr. Nina Kate ◽  
Dr. P. Sujatha
Keyword(s):  
Multidisciplinary Approach ◽  
Clinical Presentation ◽  
Case Series ◽  
Peripartum Cardiomyopathy ◽  
Rare Entity ◽  
Mortality And Morbidity ◽  
Increasing Trend ◽  
Case Series Report ◽  
Series Report

Peripartum Cardiomyopathy, a type of dilated cardiomyopathy, is a rare entity with increasing trend. The aetiology and pathogenesis of peripartum cardiomyopathy are still unknown. Although the mortality and morbidity rates are high, recognising this condition earlier and treating it with multidisciplinary approach has brought out a better outcome. We, hereby are reporting a case series of eight cases of peripartum cardiomyopathy reported in our hospital and their clinical presentation, echocardiography findings and their subsequent follow up.

scholarly journals Aesthetic and Functional Rehabilitation of the Primary Dentition Affected by Amelogenesis Imperfecta

2015 ◽  
Vol 2015 ◽  
pp. 1-6 ◽  
Author(s):  
Maria Carolina Salomé Marquezin ◽  
Bruna Raquel Zancopé ◽  
Larissa Ferreira Pacheco ◽  
Maria Beatriz Duarte Gavião ◽  
Fernanda Miori Pascon
Keyword(s):  
Stainless Steel ◽  
Psychosocial Development ◽  
Psychological Impact ◽  
Pediatric Dentistry ◽  
Primary Dentition ◽  
Amelogenesis Imperfecta ◽  
Mixed Dentition ◽  
Functional Rehabilitation ◽  
Oral Rehabilitation ◽  
Enamel Structure

The objective of this case report was to describe the oral rehabilitation of a five-year-old boy patient diagnosed with amelogenesis imperfecta (AI) in the primary dentition. AI is a group of hereditary disorders that affects the enamel structure. The patient was brought to the dental clinic complaining of tooth hypersensitivity during meals. The medical history and clinical examination were used to arrive at the diagnosis of AI. The treatment was oral rehabilitation of the primary molars with stainless steel crowns and resin-filled celluloid forms. The main objectives of the selected treatment were to enhance the esthetics, restore masticatory function, and eliminate the teeth sensitivity. The child was monitored in the pediatric dentistry clinic at four-month intervals until the mixed dentition stage. Treatment not only restored function and esthetic, but also showed a positive psychological impact and thereby improved perceived quality of life. The preventive, psychological, and curative measures of a young child with AI were successful. This result can encourage the clinicians to seek a cost-effective technique such as stainless steel crowns, and resin-filled celluloid forms to reestablish the oral functions and improve the child’s psychosocial development.

Oral rehabilitation of a cleft palate patient with tooth-supported, telescopic magnetic overdenture

2020 ◽  
Vol 13 (11) ◽  
pp. e233777
Author(s):  
Mohammed A Alfarsi ◽  
Sharaz Shaik
Keyword(s):  
Patient Education ◽  
Cleft Palate ◽  
Oral Hygiene ◽  
Oral Rehabilitation ◽  
Posterior Teeth ◽  
And Function ◽  
Palate Patient ◽  
Single Path

A 49-year-old male patient with residual cleft palate and missing pre-maxilla presented with an ill-fitting and unaesthetic maxillary denture. The posterior teeth were periodontally sound but crowded and had defective restorations and secondary caries. We restored the bilateral maxillary canines and first premolars with conical telescopic crowns having magnetic keepers. A metal-reinforced acrylic overdenture with magnetic attachments corresponding to the keepers of the telescopic crowns was fabricated. The telescopic crowns provided a single path of insertion, retention and stability to the prosthesis. The magnetic attachments provided additional retention and self-centring properties. The prosthesis effectively sealed the oronasal communication and enhanced the function, aesthetics and oral hygiene. The 6-month and 1-year follow-ups revealed that the patient was delighted, and the prosthesis provided excellent obturation and function. Periodic follow-up, maintenance, patient education and meticulous oral hygiene are vital for long-term success of such prostheses.

scholarly journals Clinical findings and long-term managements of patients with amelogenesis imperfecta

2014 ◽  
Vol 08 (04) ◽  
pp. 546-552 ◽  
Author(s):  
Mine Koruyucu ◽  
Merve Bayram ◽  
Elif Bahar Tuna ◽  
Koray Gencay ◽  
Figen Seymen
Keyword(s):  
Primary Teeth ◽  
Treatment Plan ◽  
Clinical Care ◽  
Young Patients ◽  
Case Series ◽  
Amelogenesis Imperfecta ◽  
Permanent Teeth ◽  
Radiographic Evaluation ◽  
Prevalence Index

ABSTRACTThe aim of this clinical case series is to present a diagnosis and different treatment methods of patients in different ages with amelogenesis imperfecta (AI) as well as further treatments during a 3-6 years follow-up period. A number of 31 patients (16 female, 15 male with a mean age of 10.77 ± 2.65 years) with AI have been examined for the study group between 2007 and 2010 years. A detailed anamnesis was recorded, followed by a clinical and radiological assessment of oral health. The types of AI classified for each patient according to clinical and radiographic evaluation. The main complaints of patients, presence of dental caries and dental anomalies were noted. Necessary treatments had been planned for the individual cases of AI. A number of 19 patients had hypoplastic (HP) form, and 10 patients showed hypomaturation (HM) form of AI, while one patient showed hypocalcified form of AI and one patient had HM-HP form with taurodontism. Main complaints were chiefly related to dissatisfactory esthetics and dental sensitivity. Caries prevalence index was 93.5%. Mean decayed, missing, filling permanent teeth (DMF) and DMF surface (DMFS) were found as 2.74 ± 1.71 and 6.23 ± 3.99; df (decayed, filling primary teeth) and dfs (decayed, filling primary teeth surface) were found as 3.12 ± 2.85 and 5.24 ± 4.97, respectively. All patients received individual clinical care, including preventive, restorative, and prosthetic treatments. Patients have scheduled for regular follow-up in every 3 months. Composite restorations were used as the most common treatment (25 patients, 80.6%). The treatment plan should be based on patient's age, type of defects and individual needs of the patients. Necessary treatment plan is essential, not only due to functional and aesthetic reasons, but also for the positive psychological impact on young patients.

scholarly journals Free Gingival Graft to Increase Keratinized Mucosa after Placing of Mandibular Fixed Implant-Supported Prosthesis

2017 ◽  
Vol 2017 ◽  
pp. 1-5
Author(s):  
Danny Omar Mendoza Marin ◽  
Andressa Rosa Perin Leite ◽  
Lélis Gustavo Nícoli ◽  
Claudio Marcantonio ◽  
Marco Antonio Compagnoni ◽  
...  
Keyword(s):  
Oral Hygiene ◽  
Patient Comfort ◽  
Edentulous Patient ◽  
Oral Rehabilitation ◽  
Mucogingival Surgery ◽  
Free Gingival Graft ◽  
Keratinized Tissue ◽  
Keratinized Mucosa ◽  
Gingival Graft

Insufficiently keratinized tissue can be increased surgically by free gingival grafting. The presence or reconstruction of keratinized mucosa around the implant can facilitate restorative procedure and allow the maintenance of an oral hygiene routine without irritation or discomfort to the patient. The aim of this clinical case report is to describe an oral rehabilitation procedure of an edentulous patient with absence of keratinized mucosa in the interforaminal area, using a free gingival graft associated with a mandibular fixed implant-supported prosthesis. The treatment included the manufacturing of a maxillary complete denture and a mandibular fixed implant-supported prosthesis followed by a free gingival graft to increase the width of the mandibular keratinized mucosa. Free gingival graft was obtained from the palate and grafted on the buccal side of interforaminal area. The follow-up of 02 and 12 months after mucogingival surgery showed that the free gingival graft promoted peri-implant health, hygiene, and patient comfort.Clinical Significance. The free gingival graft is an effective treatment in increasing the width of mandibular keratinized mucosa on the buccal side of the interforaminal area and provided an improvement in maintaining the health of peri-implant tissues which allows for better oral hygiene.

scholarly journals Closed Chest Convergent Epicardial–Endocardial Ablation of Non-paroxysmal Atrial Fibrillation – A Case Series and Literature Review

2013 ◽  
Vol 2 (1) ◽  
pp. 65 ◽  
Author(s):  
Amit J Thosani ◽  
Paul Gerczuk ◽  
Emerson Liu ◽  
William Belden ◽  
Robert Moraca ◽  
...  
Keyword(s):  
Atrial Fibrillation ◽  
Multidisciplinary Approach ◽  
Case Series ◽  
Closed Chest ◽  
Effective Option ◽  
Long Term Follow Up ◽  
Cardiac Surgeon ◽  
Magnetic Resonance Imaging Mri

The closed chest convergent procedure is a multidisciplinary approach to atrial fibrillation (AF) treatment. Epicardial posterior left atrial (PLA) ablation is performed by a cardiac surgeon using a transdiaphragmatic endoscope, immediately followed by percutaneous pulmonary vein (PV) isolation performed by a cardiac electrophysiologist. Interim outcomes for the treatment of non-paroxysmal AF (NPAF) were evaluated based on peri-procedural safety and complications, freedom from recurrent AF, and need for cardioversion or repeat catheter ablation at three, six and 12 months post-procedure. A total of 43 patients (86 % NPAF) underwent the convergent procedure. Patients were 84 % male, with mean age 58.6 ± 8.7 years. Mean AF duration was 45.4 ± 40.3 months. Pre-procedure left atrium (LA) volumetric data using cardiac magnetic resonance imaging (MRI) or computed tomography (CT) was available for 30 patients (70 %). Average LA volume was 155.5 ± 48.4 millilitres (ml); two-thirds of patients had a LA volume >130 ml. There was no operative or peri-operative mortality. Sinus rhythm (SR) was recorded at three months in 31 of 39 (79 %) patients, at six months in 24 of 27 (89 %) patients and at 12 months in nine patients. The convergent procedure is a safe and effective option for both PV isolation and PLA substrate ablation in NPAF patients. Long-term follow-up is required and randomised clinical trials warranted.

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