scholarly journals Hypohidrotic Ectodermal Dysplasia: A Clinical Case with a Longitudinal Approach

2014 ◽  
Vol 15 (6) ◽  
pp. 788-791 ◽  
Author(s):  
Fabian Calixto Fraiz ◽  
Renato Cordeiro Gugisch ◽  
Bianca Lopes Cavalcante-Leão ◽  
Liliane Moreira Macedo

ABSTRACT Aim This paper describes a clinical case of a male with hypohidrotic ectodermal dysplasia submitted to rehabilitation and occlusal dental interventions with follow-up from 3 to 14 years of age. Background Due to the severe effects on function and esthetics, the clinical manifestations of ectodermal dysplasia exert a negative impact on quality of life. However, oral rehabilitation in childhood poses a challenge due to growth and development. Case description A male with hypohidrotic ectodermal dysplasia began dental intervention at the age of 3 years. The clinical and radiographic exams revealed the absence of several primary and permanent teeth and abnormal shape of the primary maxillary incisors. The facial characteristics were compatible with hypohidrotic ectodermal dysplasia, such as a prominent brow, everted lips, flattened bridge of the nose and small vertical facial height. The treatment proposed involved rehabilitation through successive temporary partial dentures, functional orthopedics of the jaws, esthetic reconstruction of the anterior teeth, timely occlusal intervention and preventive actions for the control of dental caries and plaque. Conclusion The present case demonstrates that early care plays a fundamental role in minimizing the biopsychosocial consequences of hypohidrotic ectodermal dysplasia and preparing the patient for future oral rehabilitation. Clinical significance Although, the literature offers a number of papers describing dental treatment for ectodermal dysplasia, few cases include long-term follow-up and the use of a functional orthopedic appliance in combination with removable dentures in such patients. How to cite this article Fraiz FC, Gugisch RC, Cavalcante- Leão BL, Macedo LM. Hypohidrotic Ectodermal Dysplasia: A Clinical Case with a Longitudinal Approach. J Contemp Dent Pract 2014;15(6):788-791.

2002 ◽  
Vol 26 (1) ◽  
pp. 5-12 ◽  
Author(s):  
B. Kargül ◽  
T. Alcan ◽  
U. Kabalay ◽  
M. Atasu

Patients with hypohidrotic ectodermal dysplasia (HED) are characterized by the clinical manifestations of hypodontia, hypohidrosis, hypotrichosis and a highly characteristic facial physiognomy. This disorder is inherited as an X- linked trait. This report presents three cases with HED in which the clinical evaluation (intraoral and radiological), genetic findings and SEM examination of hair. Boys 6 to 14 year old and a 11 year old girl were referred to the Marmara University, Faculty of Dentistry, complaining of oligodontia in the maxillary and mandibular arches and delay in eruption of other teeth. Peg-shaped teeth have been observed. The dermatoglyphs of the patients were striking. SEM exmimation of hair demostrated a distinctly abnormal longitudinal groving along the entire length of each hair and a desquamation of the surface cuticles. The treatment was planned in a multidisciplinary odontological group involving pediatric dentistry, orthodontics, prosthodontics and oral surgery and maxillofacial radiology of future dental habilitation. A specially designed overdenture, a removable prosthesis and osseointegrated implants were constructed. Periodic recall visits were advised, to monitor the dentures and implants during periods of growth and development, and eruption of the permanent teeth.


2009 ◽  
Vol 67 (1) ◽  
pp. 189-194 ◽  
Author(s):  
Robert Kirmeier ◽  
Christine Gluhak ◽  
Peter Marada ◽  
Walther A. Wegscheider ◽  
Antranik Eskici ◽  
...  

Author(s):  
Jéssyca Maria França de Oliveira MELO ◽  
Eduardo de Farias BARBOSA

ABSTRACT This study aimed to report treatment of a patient with Kennedy’s class l maxillary and class II mandibular arch with removable partial dentures supported on an external hexagon (HE) anterior type implant of regular diameter fitted with an O’ring type of attachment. This clinical case reports the oral rehabilitation of a senile patient whose clinical examination revealed missing dentition in the upper and lower arches, attrition of the lower anterior teeth, caries, and motor impairment affecting hygiene, mastication, and esthetic functions. Due to few severely impaired teeth, the pre-prosthetic preparation included extractions and restorations, followed by the fabrication of upper and lower removable partial dentures supported by an HE-type implant. This study is important because it addresses the current challenges faced in the implementation of treatment involving removable partial dentures combined with implants, which is a topic that still needs long-term follow-up and research.


2019 ◽  
Vol 32 (10) ◽  
pp. 647 ◽  
Author(s):  
Rosana Maia ◽  
Inês Neves ◽  
António Morais ◽  
Henrique Queiroga

Introduction: The relationship between cancer and thromboembolic events has been known for a long time. Lung and venous thromboembolism are frequent complications of lung cancer and its treatment, being a great cause of morbidity and mortality. We pretend to establish the relationship between lung and venous thromboembolism and lung cancer, describe patient characteristics and analyze the impact in the survival and prognosis.Material and Methods: It was a retrospective study. All research subjects were selected from lung cancer patients with a newly diagnosed lung and venous thromboembolism event admitted to Hospital S. João, between January 2008 and December 2013 and were followed until December 2014. Statistical analysis was performed with SPSS.Results: From the search, we obtained 113 patients. The majority was male, smokers or ex-smokers, and adenocarcinoma was the most frequent histologic type, being diagnosed mostly in advanced stages. We noticed that the median time between lung cancer diagnosis and lung venous thromboembolism was 2.9 months. In 24 patients (21.4%), the lung cancer diagnosis occurred after the lung and venous thromboembolism event and in 86 patients (76.8%), it occurred before the event. After a median follow up of 1.4 months, 107 (94.7%) patients died, 1 (0.9%) was lost to follow-up and 5 (4.4%) were still alive. The median survival rate was 1.5 months.Discussion: The diagnosis of lung and venous thromboembolism in patients with lung cancer is associated with bad prognosis. It occurs most frequently in patients with advanced disease, in the first months after lung cancer diagnosis and after beginning chemotherapy.Conclusion: Disease progression is an independent predictor with negative impact in overall survival.


2017 ◽  
Vol 5 (1) ◽  
pp. 2
Author(s):  
Flavio Warol ◽  
Iony Lopes Bispo ◽  
Rodolfo Carvalho Oliveira ◽  
Roberta Barcelos ◽  
Angela Scarparo

Aim: To present the report of a female patient, 10 years old, referred for treatment in the Dentistry Clinic of a Brazilian public university.Case report: The patient's oral health condition was unfavorable with biofilm accumulation, pain report and chewing difficulty. After anamnesis, clinical and radiographic examination, the treatment plan included removal of infectious foci (54, 55, 64, 65, 74, 75, 85, 16, 36 and 46) followed by prosthetic rehabilitation. At this stage, the functional restoration of the lower arch was restricted by the imminent eruption of the premolars. In the upper arch, the maintenance of the mesio-distal diameters aims to guarantee the chronological sequence of successors irruption and establishment of normal occlusion. During the monthly follow-up consultations the patient presents a more spontaneous smile, although she still needs constant reinforcement in oral hygiene habits.Conclusions: The rehabilitation of patients with loss of permanent teeth during the mixed dentition phase should consider the peculiarities of this period for the restoration of health without altering the normal pattern of occlusal development.


2015 ◽  
Vol 3 (3) ◽  
pp. 697
Author(s):  
Cynthia Weiss Menine ◽  
Juliana Maria Habith Martin ◽  
Halina Massignan Berejuk ◽  
Ivete Aparecida De Mattias Sartori

AIM: The objective of this study was to report a clinical case highlighting the main recommendations of the literature to minimize forces applied on implants. MATERIAL AND METHODS: A decision was made to increase the number and size of implants installed. Screwed and cemented prostheses were used, combined with an occlusal bruxism night guard. RESULTS: Four months after the prosthesis installation, no biological or biomechanical complications were encountered. CONCLUSION: There are cases of patients with parafunctional habit who require oral rehabilitation with implants. There are guidelines that enable planning and rehabilitation. It is important to monitor cases to assess the behavior of implants and their suprastructures.


2018 ◽  
Vol 14 (1) ◽  
pp. 58
Author(s):  
Dr. Muna S. Khalaf ◽  
Dr. Bayan S. Khalaf ◽  
Dr. Shorouq M. Abass

Background: Trauma to the anterior teeth is a common injury in young children. Themaxillary incisors being the most affected. Although root fractures are rare, theydo occur and were previously and often considered hopeless and were extracted.The time between the injury and the initiation of treatment, level of the fractureline, and stage of root development are some criteria to be considered whenchoosing a treatment approach for a complicated tooth fracture. This case reportdescribes the management of a traumatized immature maxillary central incisorwith Elise class IV fracture with vertical oblique subgingival fracture of the root.Materials and method: Apexification was carried out using biodentine followed byremoval of the fractured segment. A fiber post was cemented in the root canalwith resin cement. The coronal portion of the tooth was restored using anteriorlight cured composite material. The tooth was examined and evaluated after 1week and after 2 months by clinical examination and radiographical evaluation ofroot development.Results: The follow up evaluation revealed clinical and radiographical success.Radiographic view showed continued development in the apex of the root andshowed normal periodontal ligament space and dense lamina dura.Conclusion: Extraction should not be the first choice of treatment for extensivelydamaged young permanent teeth in the anterior region; instead, alternativetreatment modalities must be considered. The traumatized immature tooth wassaved and restored.


2015 ◽  
Vol 26 (1) ◽  
pp. 75-78 ◽  
Author(s):  
Bianca Zeponi Fernandes Mello ◽  
Thiago Cruvinel Silva ◽  
Daniela Rios ◽  
Maria Aparecida Andrade Moreira Machado ◽  
Fabrício Pinelli Valarelli ◽  
...  

Ectodermal dysplasia is a rare congenital disease that affects several structures of ectodermal origin. The most commonly related oral characteristics are hypodontia, malformed teeth and underdeveloped alveolar ridges. New alternative treatments are needed due to the failure of the conventional prosthesis retention. This case report outlines the oral rehabilitation treatment of a 9-year-old girl with ectodermal dysplasia. The treatment was performed with conventional prosthesis upon mini-implants. The mini-implants provided prosthetic retention. The patient reported a good adaptation of the dental prosthesis and satisfaction with the treatment. The increased self-esteem improved the socialization skills of the girl. In this case report, use of prosthesis with mini-implants was satisfactory for prosthetic retention. However, clinical studies with long-term follow-up are needed to test the mini-implants as an alternative for oral rehabilitation of children with ectodermal dysplasia.


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