X-linked deafness/incomplete partition type 3: Radiological evaluation of temporal bone and intracranial findings

2021 ◽  
Author(s):  
Safak Parlak ◽  
◽  
Ekim Gumeler ◽  
Levent Sennaroglu ◽  
Burce Ozgen Mocan ◽  
...  
Keyword(s):  
Temporal Bone ◽  
Radiological Evaluation ◽  
Incomplete Partition ◽  
Type 3

scholarly journals Temporal Bone Hyperpneumatization and Tinnitus: Clinico-Radiological Evaluation Using CT Scan

2017 ◽  
Vol 3 (1) ◽  
Author(s):  
Sattar Al-Esawi ◽  
◽  
Ali Hasan ◽  
Deepak Takhtani ◽  
Sarwat Hussain ◽  
...  
Keyword(s):  
Ct Scan ◽  
Temporal Bone ◽  
Radiological Evaluation

scholarly journals Incomplete Partition type I: Radiological Evaluation of the Temporal Bone

Acta Medica ◽  
2021 ◽  
pp. 1-9
Author(s):  
Safak Parlak ◽  
Ayca Akgoz Karaosmanoglu ◽  
Sevtap Arslan ◽  
Levent Sennaroglu
Keyword(s):  
Inner Ear ◽  
Temporal Bone ◽  
Correct Diagnosis ◽  
Semicircular Canals ◽  
Type I ◽  
Vestibular Aqueduct ◽  
Endolymphatic Duct ◽  
Incomplete Partition ◽  
Internal Acoustic Canal ◽  
Large Vestibular Aqueduct

Objective: Incomplete partition type I is an uncommon congenital anomaly of the inner ear, characterized by typical cystic cochleovestibular appearance. Incomplete partition type I was firstly defined as cystic cochlea and vestibule without large vestibular aqueduct; however, large vestibular aqueduct and/or enlarged endolymphatic duct could rarely be seen in incomplete partition type I anomaly. Correct diagnosis of the type of cochlear malformation and differentiation of incomplete partition type I is necessary for patient management and surgical approach. Our aim was to document the temporal bone imaging findings in a series of patients with incomplete partition type I. Materials and Methods: CT (n=85) and/or MRI (n=80) examinations of 99 ears in 59 incomplete partition type I patients were retrospectively evaluated. All structures of the otic capsule were retrospectively assessed. The appearances of cochlea and vestibule, vestibular aqueduct/endolymphatic duct, semicircular canals were qualitatively evaluated by an experienced neuroradiologist. The vertical dimension of vestibular aqueduct and/or endolymphatic duct (from the point where the duct arises from the vestibule) was measured on CT/MRI. Anterior-posterior diameter of the internal acoustic canal and the diameter of cochlear aperture were measured on CT. The cochleovestibular nerves were evaluated on sagittal-oblique high T2-weighted imaging. Results: All 99 ears had defective partition with unpartitioned cochlear basal turn and absent interscalar septae, separated but cystic cochlea. The vestibule was enlarged in all ears except one. Semicircular canals were usually dysplastic (92.9%). A total of 35 incomplete partition type I ears (35.3%) had large vestibular aqueduct and/or enlarged endolymphatic duct. Internal acoustic canal was wide in 21% of ears. Cochlear aperture was wide in 5.9% of ears. Cochlear nerve was either hypoplastic or aplastic in about a quarter of incomplete partition type I ears. Conclusion: In up to one-third of incomplete partition type I patients, an associated large vestibular aqueduct /endolymphatic duct could be seen accompanying typical inner ear findings. Although the cochlear nerves are normal in the majority of cases, auditory brainstem implantation may be necessary in certain cases of incomplete partition type I anomaly.

scholarly journals The Story of Separate Yet Connected Cholesteatomas

2021 ◽  
pp. 014556132110331
Author(s):  
Arvind Kumar Kairo ◽  
Rakesh Kumar ◽  
Smita Manchanda ◽  
Ravneet Ravinder Verma
Keyword(s):  
Temporal Bone ◽  
Growth Model ◽  
Surgical Approach ◽  
Radiological Evaluation ◽  
Congenital Lesions ◽  
Anatomical Knowledge ◽  
Extent Of Disease

Significance Statement Petrous cholesteatoma is rare but frequently leads to complications. A thorough radiological evaluation helps in identifying the pathology and the extent of disease. Sound anatomical knowledge is vital for the planning of surgical approach to get adequate access without damaging important structures. Presentations in congenital lesions are varied due to the uneven growth model of the temporal bone. To the best of our knowledge, the pattern of involvement in this case has never been reported earlier.

scholarly journals The Spectrum and Frequency of Inner Ear Anomalies in Patients with Congenital Hearing Impairment in Yakutia

2020 ◽  
Vol 101 (2) ◽  
pp. 90-102
Author(s):  
L. A. Klarov ◽  
N. A. Barashkov ◽  
F. M. Teryutin ◽  
G. P. Romanov ◽  
M. M. Popov ◽  
...  
Keyword(s):  
Inner Ear ◽  
Hearing Impairment ◽  
Temporal Bone ◽  
Semicircular Canals ◽  
Internal Auditory Meatus ◽  
X Ray ◽  
Vestibular Aqueduct ◽  
Incomplete Partition ◽  
Ear Anomalies ◽  
Congenital Hearing Impairment

Objective. To analyze the spectrum and frequency of inner ear anomalies in patients with congenital hearing impairment in Yakutia.Material and methods. A total of 165 patients with congenital hearing impairment were surveyed. All the patients were examined by an audiologist, an educational audiologist, and a neuropsychiatrist. All the patients underwent X-ray computed tomography (X-ray CT) of temporal bone structures (which was supplemented by magnetic resonance imaging (MRI) in some cases).Results. Based on modern ideas about inner ear anomalies and their classification, the authors first analyzed the spectrum and frequency of inner ear anomalies in patients with congenital hearing impairment in Yakutia. Inner ear malformations were identified in 16 (9.7%) of the 165 patients with hearing impairment, which corresponds to that in the previously studied samples of deaf people in different countries (from 3% to 35%). Of the inner ear structures, the cochlea and vestibule were more commonly affected. Abnormalities of the internal auditory meatus, semicircular canals, and vestibular aqueduct were less common. In general, the spectrum of anomalies was represented by 7 different malformations. Incomplete partition type II (IP-II) (34.3%) came first in incidence among all the abnormalities. Incomplete partition type III (IP-III) (18.7%) ranked second in incidence. The expansion of the internal auditory meatus (12.5%) and vestibular aqueduct (12.5%) occupied the third place. Inner ear anomalies occurred as concurrences that are difficult to interpret and classify in half (50%) of all the cases.Conclusion. Analysis of the spectrum and frequency of temporal bone abnormalities in Yakutia suggests that every 10 patients with congenital hearing impairment have one or another inner ear structural malformation (9.7%) and require accurate and timely diagnosis using up-to-date X-ray CT and MRI techniques.

Hypothalamic malformations in patients with X-linked deafness and incomplete partition type 3

2019 ◽  
Vol 61 (8) ◽  
pp. 949-952 ◽  
Author(s):  
Ata Siddiqui ◽  
Alessandra D’Amico ◽  
Giovanna Stefania Colafati ◽  
Domenico Cicala ◽  
Giacomo Talenti ◽  
...  
Keyword(s):  
Incomplete Partition ◽  
Type 3

scholarly journals Cystic Cochleovestibular Malformation (Incomplete Partition Type 1)

2010 ◽  
Vol 25 (1) ◽  
pp. 41-42 ◽  
Author(s):  
Nathaniel W. Yang
Keyword(s):  
Hearing Loss ◽  
Inner Ear ◽  
Temporal Bone ◽  
Cochlear Implantation ◽  
Type I ◽  
Profound Hearing Loss ◽  
Increased Risk ◽  
Ear Malformations ◽  
Temporal Bone Imaging ◽  
Incomplete Partition

A 5-year old female with bilateral profound hearing loss underwent computerized tomographic imaging of the temporal bone as part of the work-up to determine the etiology of her deafness, and to delineate middle and inner ear anatomy prior to cochlear implantation. The examination revealed an inner ear malformation which, based on the newest classification of cochleovestibular malformations by Sennaroglu and Saatci, is called an incomplete partition type I (IP-1) or cystic cochleovestibular malformation. This condition is characterized by (1) a cochlea that is lacking the entire modiolus and cribriform area, resulting in a cystic appearance, and (2) a large cystic vestibule.1   Temporal bone imaging is among the most useful examinations in the etiological investigation of idiopathic sensorineural hearing loss in children, with up to 30%2 of the imaging studies showing an abnormality. The detection of inner ear malformations is important, as some abnormalities are associated with an increased risk of meningitis or progressive hearing loss following head trauma.3 Likewise, the approach to cochlear implantation may be influenced by the type of malformation. In this particular patient, the use of a cochlear implant with a full-band electrode design may be more appropriate, as the location of the neural elements within the cystic cochlea is not definitely known.

Scanning Electron Microscopy of the Red Pulp of the Spleen

1971 ◽  
Vol 29 ◽  
pp. 496-497
Author(s):  
Masayuki Miyoshi
Keyword(s):  
Electron Microscope ◽  
Ringer Solution ◽  
Conclusive Evidence ◽  
Sinus Wall ◽  
Transmission Electron ◽  
Type 3 ◽  
Cytoplasmic Processes ◽  
Splenic Red Pulp ◽  
Scanning Electron ◽  
Red Pulp

In spite of various attempts, conclusive evidence to explain blood passage in the splenic red pulp does not seem to have been presented. Scanning electron microscope (SEM) observations on the rabbit spleen, originally performed by us, revealed that the sinus was lined by a perforated lattice composed of longitudinally extended rod cells and transverse cytoplasmic processes, and that perforations in the lattice were continuous to the spaces among the stellate reticulum cells of the cord. In the present study the observation was extended to the dog and rat spleens, in which the cord is more developed than in the rabbit in order to clarify the possible differences in the fine structure of the sinus wall. An attempt was also made to examine the development and distribution of macrophage in the blood passage of the red pulp.Spleens were washed and fixed by perfusion with Ringer solution and then with buffered glutaraldehyde. Small tissue cubes were dehydrated with acetone, dried in air and heated with gold. Observations were made by a JEOL SEM Type-3. One air dried tissue cube was cut into small pieces and post fixed with buffered OsO4 for examination under the transmission electron microscope (TEM).

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