The Innermore Ossein- Enchondroma

Preface Frequently, benign bone tumours are an incidental discovery wherein clinical symptoms are contingent to tumour location and magnitude and manifest as localized pain, swelling, skeletal deformities or pathologic fracture. Radiographic imaging is a cogent methodology of discerning the neoplasms.

The Vascular Swirls- Angiomatoid Fibrous Histiocytoma

Angiomatoid fibrous histiocytoma (AFH) is an exceptional, soft tissue neoplasm of indeterminate lineage and intermediate malignancy associated with minimal localized tumour reoccurrence and infrequent distant metastasis. Preliminarily contemplated to be a variant or derivative of malignant fibrous histiocytoma or undifferentiated pleomorphic sarcoma or an unusual fibrohistiocytic sarcoma, angiomatoid fibrous histiocytoma predominantly incriminates young po pulation and superficial sites although several extra-somatic sites can be implicated.

The Minimalistic Malignancy- Low grade Fibromyxoid Sarcoma

Low grade fibromyxoid sarcoma (LGFMS) is an exceptional, low grade, soft tissue sarcoma with indolent biological behaviour, extensive preclinical stage, enhanced localized tumour reoccurrence and delayed, distant metastasis. As the deceptively benign neoplasm was initially scripted by Evans in 1987, the tumefaction is nomenclated as “Evan’s tumour”. Incidence of sarcomas is nearly 1% of adult malignancies wherein low-grade fibromyxoid sarcoma represents roughly beneath <5% of soft tissue sarcomas 1.

The Bairn’s Blain- Fibromatosis Colli

Preface Fibromatosis colli is an exceptional, benign neoplasm of infancy constituted by spindle-shaped cells of sternocleidomastoid muscle. Fibromatosis colli emerges within specific sites such as distal or inferior segment of sternocleidomastoid muscle and is accompanied by diffuse enlargement of the muscle. Although nomenclated as “sternocleidomastoid tumour” or “sternocleidomastoid pseudo-tumour of infancy”, the designation is a misnomer, as the condition is non neoplastic although it may be denominated as a congenital fibrotic disorder.

The Coextensive Circumstance- Parachordoma

Parachordoma is an extremely exceptional, peripherally situated soft tissue neoplasm arising at non axial locations. Also designated as soft tissue “myoepithelioma” or “mixed tumour”, the tumefaction histologically simulates a chordoma of axial skeleton and was referred to as “central chordoma” emerging within non- axial sites. Nevertheless, a distinctive immune profile categorises the lesion as a unique entity.

The Neoplastic Whorls-Soft Tissue Perineurioma

Perineurioma is an exceptional, benign neoplasm entirely composed of neoplastic perineurial cells and arises from the peripheral nerve. Pertaining to location, the neoplasm predominantly demonstrates configurations such as intra-neural or extra-neural, confined to the soft tissue. Perineurioma was initially scripted by Lazarus and Trombetta in 1978 and is additionally nomenclated as localized hypertrophic neuropathy1. Extra-neural soft tissue perineurioma and mucosal (intestinal) perineurioma are frequent, in contrast to intra-neural perineurioma or localized hypertrophic neuropathy subtype1, 2.

The Follicular Benignancy- Desmoplastic Trichoepithelioma

Trichoepithelioma is a benign, cutaneous neoplasm originating from the hair follicle and is categorized into singular trichoepithelioma, multiple trichoepithelioma and desmoplastic trichoepithelioma wherein desmoplastic trichoepithelioma is cogitated as an exceptional, cutaneous adnexal tumour. Desmoplastic trichoepithelioma was initially scripted by Hartzell in 1904 wherein the lesion was described as a benign, cystic epithelioma. Desmoplastic trichoepithelioma can be additionally nomenclated as epithelioma adenoides cysticum, morphea - like epithelioma or sclerosing epithelial hamartoma 1. Familial instances of desmoplastic trichoepithelioma are infrequent and can be misdiagnosed on account of adjunctive benign, cutaneous, adnexal neoplasms depicting subtle clinical features, excepting a nodular basal cell carcinoma. Cogent clinical and histological features can assist the diagnosis of desmoplastic trichoepithelioma 1, 2.