Congenital scalp defects with distal limb anomalies (Adams-Oliver syndrome): Report of ten cases and review of the literature

Le syndrome de loge sur positionnement prolongé en lithotomie ou en hémilithitomie, est une complication rare en chirurgie. Les dommages neurovasculaires sont souvent permanents. On reporte deux cas d'ostéosynthèse du fémur en position d'hemilithotomie, compliqués d'un syndrome de loge de la jambe controlatérale. Une revue de la littérature sur les 40 cas décrits, jusqu'à ce jour, nous démontre que cette complication est fortement liée au positionnement du patient et à la durée opératoire. Compte tenu du pronostic fonctionnel incertain, une limitation du temps de positionnement en lithotomie doit être recherchée. La surveillance postopératoire doit être rigoureuse et sans hésitation quant à une fasciotomie éventuelle sur simple examen clinique ou après la mesure de la pression dans les loges. Une technique de positionnement sur la table orthopédique est proposée.

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Mitchell-Riley Syndrome Report of Novel Mutation and Review of the Literature

Journal of Biochemical and Clinical Genetics ◽

10.24911/jbcgenetics/183-1529491124 ◽

2018 ◽

pp. 87-92 ◽

Cited By ~ 1

Author(s):

Nourah Alruqaie ◽

Majid Alfadhel

Keyword(s):

Novel Mutation ◽

Review Of The Literature ◽

Syndrome Report

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Faculty Opinions recommendation of Pulmonary arterial hypertension: a rare complication of primary Sjögren syndrome: report of 9 new cases and review of the literature.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.1090986.544353 ◽

2007 ◽

Author(s):

Jay H Ryu

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Rare Complication ◽

Sjögren Syndrome ◽

Sjogren Syndrome ◽

Review Of The Literature ◽

Primary Sjögren Syndrome ◽

Pulmonary Arterial ◽

Syndrome Report

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The Greig cephalopolysyndactyly syndrome: Report of a family and review of the literature

American Journal of Medical Genetics ◽

10.1002/ajmg.1320220106 ◽

1985 ◽

Vol 22 (1) ◽

pp. 59-68 ◽

Cited By ~ 31

Author(s):

Thomaz Rafael Gollop ◽

Luiz Roberto Fontes ◽

John M. Opitz ◽

James F. Reynolds

Keyword(s):

Review Of The Literature ◽

Greig Cephalopolysyndactyly Syndrome ◽

Syndrome Report

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B cell malignant lymphoma in a patient with progressive systemic sclerosis and Sjoegren's syndrome Report of a case and review of the literature.

Japanese Journal of Medicine ◽

10.2169/internalmedicine1962.24.155 ◽

1985 ◽

Vol 24 (2) ◽

pp. 155-163 ◽

Cited By ~ 9

Author(s):

Susumu SUGAI ◽

Tomoo TAKIGUCHI ◽

Yuko HIROSE ◽

Shiro SHIMIZU ◽

Junko TACHIBANA ◽

...

Keyword(s):

Systemic Sclerosis ◽

B Cell ◽

Malignant Lymphoma ◽

Progressive Systemic Sclerosis ◽

Review Of The Literature ◽

Sjoegren’S Syndrome ◽

Syndrome Report

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LINEAR NEVUS SEBACEOUS SYNDROME: REPORT OF TWO CASES AND A REVIEW OF THE LITERATURE

PEDIATRICS ◽

10.1542/peds.52.3.382 ◽

1973 ◽

Vol 52 (3) ◽

pp. 382-387

Author(s):

Frederick H. Lovejoy ◽

William E. Boyle

Keyword(s):

Cerebrospinal Fluid ◽

Neurologic Disease ◽

Review Of The Literature ◽

Cutaneous Lesions ◽

Neurocutaneous Syndromes ◽

Nevus Sebaceous ◽

Cerebrospinal Fluid Protein ◽

Syndrome Report

Two cases of linear nevus sebaceous syndrome are described and a review of the eleven cases now reported in the literature is undertaken. The first patient has retardation, seizures, and classic ectodermal lesions while the second patient manifests typical cutaneous lesions and only an elevated cerebrospinal fluid protein as evidence of neurologic disease. The rationale for defining the syndrome as an entity distinct from other neurocutaneous syndromes is discussed and a pleomorphic presentation of the syndrome is suggested.

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