Hereditary Haemorrhagic Telangiectasia is a genetic vascular disorder, having ve variants depending
on underlying gene mutations and characterised by aneurysms and arterio-venous malformations.
Larger AVMs present most commonly in the brain, lung, and liver. The diagnosis is mainly clinical based on the Curacao
Criteria. Serious Neurological complications can occur in up to 10% of cases. Pregnancy associated hormonal changes affect
the cardiovascular system manifesting in the second and third trimesters. Majority of the pregnancies are uneventful, but severe
complications and even death can occur. HHT in pregnancy is considered high risk and needs management by a multidisciplinary team. Women with HHT planning pregnancy should be counselled regarding the rare but serious risks. Strict
antenatal surveillance and prior awareness of the diagnosis of HHT is usually associated with good pregnancy outcomes.