Long-term plasma exchange in a case of Refsum's disease

1991 ◽  
Vol 241 (2) ◽  
pp. 82-84 ◽  
Author(s):  
D. Leppert ◽  
U. Schanz ◽  
J. Burger ◽  
J. Gmür ◽  
N. Blau ◽  
...  
Keyword(s):  
Plasma Exchange ◽  
Refsum's Disease

Therapeutic Plasma Exchange Application in Children Requires Individual Decision

2020 ◽  
Author(s):  
Gürkan Atay ◽  
Demet Demirkol
Keyword(s):  
Plasma Exchange ◽  
Vascular Access ◽  
Pediatric Patients ◽  
Demyelinating Disease ◽  
Pediatric Intensive Care ◽  
Therapeutic Plasma Exchange ◽  
Transplantation Rejection ◽  
Access Problems ◽  
Uremic Syndrome

AbstractTherapeutic plasma exchange (TPE) is a treatment administered with the aim of removing a pathogenic material or compound causing morbidity in a variety of neurologic, hematologic, renal, and autoimmune diseases. In this study, we aimed to assess the indications, efficacy, reliability, complications, and treatment response of pediatric patients for TPE. This retrospective study analyzed data from 39 patients aged from 0 to 18 years who underwent a total of 172 TPE sessions from January 2015 to April 2018 in a tertiary pediatric intensive care unit. Indications for TPE were, in order of frequency, macrophage activation syndrome (28.2%, n = 11), renal transplantation rejection (15.4%, n = 6), liver failure (15.4%, n = 6), Guillain–Barre's syndrome (15%, n = 6), hemolytic uremic syndrome (7.7%, n = 3), acute demyelinating disease (7.7%, n = 3), septic shock (5.1%, n = 2), and intoxication (5.1%, n = 2). No patient had any adverse event related to the TPE during the procedure. The TPE session was ended prematurely in one patient due to insufficient vascular access and lack of blood flow (2.6%). In the long term, thrombosis due to the indwelling central catheter occurred (5.1%, n = 2). TPE appears to be an effective first-stage or supplementary treatment in a variety of diseases, may be safely used in pediatric patients, and there are significant findings that its area of use will increase. In experienced hands and when assessed carefully, it appears that the rate of adverse reactions and vascular access problems may be low enough to be negligible.

scholarly journals Plasma exchange in the treatment of Refsum's disease (heredopathia atactica polyneuritiformis).

1991 ◽  
Vol 54 (7) ◽  
pp. 614-617 ◽  
Author(s):  
D Harari ◽  
F B Gibberd ◽  
J P Dick ◽  
M C Sidey
Keyword(s):  
Plasma Exchange ◽  
Refsum's Disease

Treatment of Progressive Systemic Sclerosis by Plasma Exchange: Long-term Results in 40 Patients

1990 ◽  
Vol 13 (2) ◽  
pp. 125-129 ◽  
Author(s):  
L. Guillevin ◽  
Z. Amoura ◽  
Ph. Merviel ◽  
J. Pourrat ◽  
A. Bussel ◽  
...  
Keyword(s):  
Systemic Sclerosis ◽  
Plasma Exchange ◽  
Progressive Systemic Sclerosis ◽  
Long Term Results

Aluminium Bone Deposits in Normal Renal Function Patients after Long-Term Treatment by Plasma Exchange

1989 ◽  
Vol 12 (10) ◽  
pp. 664-667 ◽  
Author(s):  
C. Mousson ◽  
S.A. Charhon ◽  
M. Ammar ◽  
M. Accominotti ◽  
G. Rifle
Keyword(s):  
Renal Function ◽  
Bone Formation ◽  
Plasma Exchange ◽  
Normal Renal Function ◽  
Bone Biopsy ◽  
Term Treatment ◽  
Normal Range ◽  
Non Invasive ◽  
Long Term Treatment

The accumulation of aluminium (AI) can cause AI bone deposits, osteomalacia and encephalopathy. As albumin solutions used as replacement fluid in plasma exchange (PE) are contaminated with AI, we studied AI overload in two symptomless patients with normal renal function, treated by long-term plasma exchange (PE). Total AI loading was calculated at 1750 μmol in patient 1 (178 PE sessions) and 2100 μmol in patient 2 (153 PE sessions). Bone biopsy showed AI deposits and low bone formation without osteomalacia in patient 1 and only osteoporosis in patient 2. Plasma AI levels were useless in detecting early AI overload, because the remained in the normal range, even after PE in both patients. Bone biopsy was the best means of recognizing AI intoxication, but cannot be recommended for frequent evaluations. However, the desferrioxamine mobilization test can be proposed as a repetitive non-invasive investigation method.

Long-term remission of pure red cell aplasia after plasma exchange and lymphocytapheresis

2009 ◽  
Vol 36 (1) ◽  
pp. 121-122 ◽  
Author(s):  
Gosta Berlin ◽  
Gudrun Lieden
Keyword(s):  
Plasma Exchange ◽  
Pure Red Cell Aplasia ◽  
Red Cell ◽  
Red Cell Aplasia

Acute Decompensation and Absence of Brain and Kidney Dysfunction Predict Long-Term Efficacy of Plasma Exchange in Hyper-Bilirubinemic Cirrhotic Patients Awaiting Liver Transplantation

2008 ◽  
Vol 40 (6) ◽  
pp. 1929-1931
Author(s):  
B.E. Annicchiarico ◽  
A.W. Avolio ◽  
M. Siciliano ◽  
S. Passalacqua ◽  
G. Caracciolo ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Plasma Exchange ◽  
Kidney Dysfunction ◽  
Term Efficacy ◽  
Acute Decompensation ◽  
Cirrhotic Patients

scholarly journals Long-term follow-up of patients with severe ANCA-associated vasculitis comparing plasma exchange to intravenous methylprednisolone treatment is unclear

2013 ◽  
Vol 84 (2) ◽  
pp. 397-402 ◽  
Author(s):  
Michael Walsh ◽  
Alina Casian ◽  
Oliver Flossmann ◽  
Kerstin Westman ◽  
Peter Höglund ◽  
...  
Keyword(s):  
Plasma Exchange ◽  
Intravenous Methylprednisolone ◽  
Anca Associated Vasculitis ◽  
Methylprednisolone Treatment ◽  
Long Term Follow Up

scholarly journals Long-term renal function under plasma exchange in atypical hemolytic uremic syndrome

2011 ◽  
Vol 26 (10) ◽  
pp. 1915-1916 ◽  
Author(s):  
Jean-Claude Davin ◽  
Jaap Groothoff ◽  
Valentina Gracchi ◽  
Antonia Bouts
Keyword(s):  
Renal Function ◽  
Hemolytic Uremic Syndrome ◽  
Plasma Exchange ◽  
Atypical Hemolytic Uremic Syndrome ◽  
Uremic Syndrome

Long-term remission in a patient with refractory thrombotic thrombocytopenic purpura treated with rituximab and plasma exchange

2007 ◽  
Vol 87 (4) ◽  
pp. 321-323 ◽  
Author(s):  
A. L. Basquiera ◽  
J. C. Damonte ◽  
P. Abichaín ◽  
A. G. Sturich ◽  
J. J. García
Keyword(s):  
Plasma Exchange ◽  
Thrombotic Thrombocytopenic Purpura ◽  
Thrombocytopenic Purpura
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