scholarly journals Glutaric aciduria type I and methylmalonic aciduria: Simulation of cerebral import and export of accumulating neurotoxic dicarboxylic acids in in vitro models of the blood–brain barrier and the choroid plexus

2010 ◽  
Vol 1802 (6) ◽  
pp. 552-560 ◽  
Author(s):  
Sven W. Sauer ◽  
Silvana Opp ◽  
Anne Mahringer ◽  
Marcin M. Kamiński ◽  
Christian Thiel ◽  
...  
Keyword(s):  
Choroid Plexus ◽  
Blood Brain Barrier ◽  
Dicarboxylic Acids ◽  
Methylmalonic Aciduria ◽  
In Vitro Models ◽  
Glutaric Aciduria Type ◽  
Type I ◽  
Glutaric Aciduria ◽  
Import And Export

scholarly journals Formation of 3-hydroxyglutaric acid in glutaric aciduria type I: in vitro participation of medium chain acyl-CoA dehydrogenase

JIMD Reports ◽  
2019 ◽  
Vol 47 (1) ◽  
pp. 30-34 ◽  
Author(s):  
Verena Peters ◽  
Marina Morath ◽  
Matthias Mack ◽  
Michael Liesert ◽  
Wolfgang Buckel ◽  
...  
Keyword(s):  
Glutaric Aciduria Type ◽  
Type I ◽  
Glutaric Aciduria ◽  
Medium Chain ◽  
Glutaric Aciduria Type I ◽  
Chain Acyl ◽  
Hydroxyglutaric Acid

Use of guidelines improves the neurological outcome in glutaric aciduria type I

2010 ◽  
Vol 41 (02) ◽  
Author(s):  
J Heringer ◽  
SPN Boy ◽  
R Ensenauer ◽  
B Assmann ◽  
J Zschocke ◽  
...  
Keyword(s):  
Neurological Outcome ◽  
Glutaric Aciduria Type ◽  
Type I ◽  
Glutaric Aciduria ◽  
Glutaric Aciduria Type I

Development of Neuropsychological Functions in Patients with Glutaric Aciduria Type I

2014 ◽  
Vol 45 (S 01) ◽  
Author(s):  
N. Boy ◽  
J. Heringer ◽  
G. Haege ◽  
E. Glahn ◽  
G. Hoffmann ◽  
...  
Keyword(s):  
Glutaric Aciduria Type ◽  
Type I ◽  
Glutaric Aciduria ◽  
Glutaric Aciduria Type I ◽  
Neuropsychological Functions

scholarly journals Biochemical‐ and Biophysical‐Induced Barriergenesis in the Blood–Brain Barrier: A Review of Barriergenic Factors for Use in In Vitro Models

2021 ◽  
Vol 1 (5) ◽  
pp. 2170051
Author(s):  
Christina L. Schofield ◽  
Aleixandre Rodrigo-Navarro ◽  
Matthew J. Dalby ◽  
Tom Van Agtmael ◽  
Manuel Salmeron-Sanchez
Keyword(s):  
Blood Brain Barrier ◽  
In Vitro Models ◽  
Brain Barrier ◽  
Blood Brain

scholarly journals Glutaric aciduria type I: Pathomechanisms of neurodegeneration

1999 ◽  
Vol 22 (4) ◽  
pp. 392-403 ◽  
Author(s):  
K. Ullrich ◽  
B. Flott-Rahmel ◽  
P. Schluff ◽  
U. Musshoff ◽  
A. Das ◽  
...  
Keyword(s):  
Glutaric Aciduria Type ◽  
Type I ◽  
Glutaric Aciduria ◽  
Glutaric Aciduria Type I

scholarly journals Early Detection of Glutaric Aciduria Type I by Newborn Screening in Taiwan

2008 ◽  
Vol 107 (2) ◽  
pp. 139-144 ◽  
Author(s):  
Chin-Tung Hsieh ◽  
Wuh-Liang Hwu ◽  
Yuan-Te Huang ◽  
Ai-Chu Huang ◽  
Shiao-Fang Wang ◽  
...  
Keyword(s):  
Early Detection ◽  
Newborn Screening ◽  
Glutaric Aciduria Type ◽  
Type I ◽  
Glutaric Aciduria ◽  
Glutaric Aciduria Type I

scholarly journals Glutaric aciduria (type I): prenatal ultrasonographic findings

2002 ◽  
Vol 20 (3) ◽  
pp. 305-307 ◽  
Author(s):  
S. K. Lin ◽  
S. G. Hsu ◽  
E. S. C. Ho ◽  
C. R. Tsai ◽  
Y. T. Hseih ◽  
...  
Keyword(s):  
Glutaric Aciduria Type ◽  
Type I ◽  
Glutaric Aciduria ◽  
Glutaric Aciduria Type I

Understanding the Physiology of the Blood-Brain Barrier: In Vitro Models

Physiology ◽  
1998 ◽  
Vol 13 (6) ◽  
pp. 287-293 ◽  
Author(s):  
Gerald A. Grant ◽  
N. Joan Abbott ◽  
Damir Janigro
Keyword(s):  
Central Nervous System ◽  
Tissue Culture ◽  
Nervous System ◽  
Blood Brain Barrier ◽  
In Vitro Models ◽  
Brain Barrier ◽  
Blood Brain ◽  
Brain Tissue Culture ◽  
The Brain

Endothelial cells exposed to inductive central nervous system factors differentiate into a blood-brain barrier phenotype. The blood-brain barrier frequently obstructs the passage of chemotherapeutics into the brain. Tissue culture systems have been developed to reproduce key properties of the intact blood-brain barrier and to allow for testing of mechanisms of transendothelial drug permeation.

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