Unusual cases of congenital cholesteatoma of the ear

1999 ◽  
Vol 113 (1) ◽  
pp. 52-54 ◽  
Author(s):  
Usama Rashad ◽  
Maurice Hawthorne ◽  
Udhaya Kumar ◽  
Andrée Welsh
Keyword(s):  
Surgical Treatment ◽  
Temporal Bone ◽  
Middle Ear ◽  
External Auditory Canal ◽  
Cerebellopontine Angle ◽  
Mastoid Process ◽  
Petrous Apex ◽  
Common Site ◽  
Radiological Findings ◽  
Congenital Cholesteatoma

AbstractCongenital cholesteatoma may originate at various sites in the temporal bone. For example, in the petrous apex, the cerebellopontine angle, the middle ear cavity, the mastoid process or the external auditory canal. The least common site being the mastoid process. We present two cases of congenital cholesteatoma of the mastoid process, each presenting with different symptoms and at different ages. Both patients underwent surgical treatment, which confirmed the diagnosis and radiological findings.

Congenital cholesteatoma of the mastoid region

2000 ◽  
Vol 114 (10) ◽  
pp. 779-780 ◽  
Author(s):  
Sebahattin Cüreoglu ◽  
Üstün Osma ◽  
M. Faruk Oktay ◽  
Hasan Nazaroglu ◽  
Faruk Meric ◽  
...  
Keyword(s):  
Clinical Examination ◽  
Middle Ear ◽  
External Auditory Canal ◽  
Mastoid Process ◽  
Petrous Apex ◽  
Radiological Evaluation ◽  
Common Site ◽  
Congenital Cholesteatoma ◽  
Mastoid Region

Congenital cholesteatoma may arise in the petrous apex, mastoid, middle ear, or external auditory canal. The least common site being the mastoid process. We present one case of primary mastoid cholesteatoma confirmed by clinical examination, surgical findings and radiological evaluation.

Correlation between temporal bone pneumatization, location of lateral sinus and length of the mastoid process

1992 ◽  
Vol 106 (6) ◽  
pp. 485-489 ◽  
Author(s):  
S. Turgut ◽  
M. Tos
Keyword(s):  
Temporal Bone ◽  
Middle Ear ◽  
External Auditory Canal ◽  
Sigmoid Sinus ◽  
Mastoid Process ◽  
Lateral Sinus ◽  
Gross Pathology ◽  
Significant Difference ◽  
Temporal Bone Pneumatization ◽  
Temporal Bones

AbstractThe relationship between temporal bone pneumatization and the location of the lateral sinus and length of the mastoid process was investigated in 60 fresh frozen adult temporal bones, by plain X-rays, computed tomography and surgical dissection including otomicroscopic findings. Temporal bone pneumatization was classified as small, moderate and large. After drilling, the shortest distances between the middle fossa dura and mastoid tip representing the mastoid length and between the sigmoid sinus and posterior border of external auditory canal were measured and compared to the degree of pneumatization. The distances in the specimens with pathological eardrum and adhesions in the middle ear were compared to the ones without gross pathology. The length of mastoid process was significantly shorter in specimens with small pneumatization than those with large (Mann Whitney P<0.001).The specimens with a pathological eardrum and middle ear adhesions had a significantly shorter mastoid length than those without gross pathology. There was no significant difference between degree of pneumatization and the shortest distance between sigmoid sinus and external auditory canal (Mann Whitney P>0.05). It is demonstrated that the ‘under-developed’ mastoid process can be a consequence of hampered pneumatization.

scholarly journals A rare case of bilateral congenital posterior mesotympanic cholesteatoma

2018 ◽  
Vol 17 (2) ◽  
pp. 307-310
Author(s):  
Ahmad Hafiz Ali ◽  
Zulkiflee Salahuddin ◽  
Mohd Khairi MD Daud ◽  
Rosdan Salim
Keyword(s):  
Soft Tissue ◽  
Tympanic Membrane ◽  
Middle Ear ◽  
Rare Case ◽  
Medical Science ◽  
Canal Wall ◽  
Common Site ◽  
Congenital Cholesteatoma ◽  
Canal Wall Down ◽  
The Common

Bilateral congenital mesotympanic cholesteatoma is a very rare disease. It can present differently from ordinary congenital cholesteatoma. We report a case of bilateral congenital cholesteatoma diagnosed at age of 22 years old. She presented with bilateral intermittent ear discharge since 10 years old that worsening two weeks prior to her presentation to our clinic and associated with bilateral reduced hearing. Clinically there was intact tympanic membrane with retraction of the mesotympanic area with present of mass medial to tympanic membrane. CT scan imaging showed there was soft tissue in the bilateral middle ear cavity with intact scutum and ossicles. Patient undergone canal wall down procedure and the diagnosis of congenital mesotympanic cholesteatoma was confirmed with present of cholesteatoma sac at the posterosuperior part, as opposed to anterosuperior quadrant, where the common site for congenital cholesteatoma.Bangladesh Journal of Medical Science Vol.17(2) 2018 p.307-310

Temporal bone and skull base

2018 ◽  
Author(s):  
Arangasamy Anbarasu ◽  
Jack I. Lane
Keyword(s):  
Skull Base ◽  
Temporal Bone ◽  
External Auditory Canal ◽  
Cerebellopontine Angle

In this section the temporal base is covered in detail. The skull, Cerebellopontine angle, External Auditory Canal, and areas of the ear are all discussed. Various issues and problems are detailed with imagining techniques for each area.

THE VALUE OF NAVIGATION SYSTEM IN COCHLEAR IMPLANTATION IN PATIENTS WITH ABNORMALITIES OF THE INTERNAL AND MIDDLE EAR

2019 ◽  
Vol 25 (3) ◽  
pp. 12-20
Author(s):  
V.I. Fedoseev ◽  
◽  
N.A. Mileshina ◽  
E.V. Kurbatova ◽  
S.S. Osipenkov ◽  
...  
Keyword(s):  
Surgical Treatment ◽  
Inner Ear ◽  
Temporal Bone ◽  
Congenital Malformation ◽  
Middle Ear ◽  
Navigation System ◽  
Cochlear Implantation ◽  
Internal Auditory Canal ◽  
Mondini Dysplasia ◽  
Ct And Mri

The use of navigation system during the coclear implantation (CI) in patients with congenital and acquired malformation of the inner ear is necessary because of surgical difficulties. The purpose of our work is to evaluate the effectiveness of the navigation system in congenital and acquired anomalies of the middle and inner ear. Materials and methods The authors followed-up 27 children with bilateral congenital malformation of the inner ear and 58 patients with acquired cochlea obliteration (12 adults and 46 children with the acquired obliteration were included in the group). 55 patients have the acquired obliteration of the inner ear, 3 patients – the total obliteration of the inner ear. Audiological, CT and MRI were performed. All our patients the CI was performed. Conclusion.The use of navigation system during CI in patients with a combination of malformation of the inner and middle ear to increase the efficiency of surgical treatment. The duration of anesthesia and surgery in children with congenital malformation increases when navigation is applied All patients after meningitis or with the fracture of the temporal bone should be performed MRI The patients with an extension of the internal auditory canal, anomaly of Mondini dysplasia of the cochlear, the partial obliteration of the cochlea have good rehabilitation results after CI. The patients with the total obliteration of the inner ear have unsatisfactory results of rehabilitation.

Congenital cholesteatoma of the infratemporal fossa

2009 ◽  
Vol 124 (1) ◽  
pp. 80-82 ◽  
Author(s):  
Z Chen ◽  
L Tang ◽  
H Zhou ◽  
G Xing
Keyword(s):  
Surgical Treatment ◽  
Rare Case ◽  
Infratemporal Fossa ◽  
Tympanic Cavity ◽  
Middle Ear Effusion ◽  
Radiological Findings ◽  
Congenital Cholesteatoma ◽  
Operative Findings ◽  
Radiological Studies ◽  
Ear Effusion

AbstractObjective:We report an extremely rare case of congenital cholesteatoma of the infratemporal fossa.Method:The clinical, radiological and intra-operative findings of the patient are presented.Results:A five-year-old girl presented to our hospital with symptoms in the left ear consistent with middle-ear effusion. A congenital cholesteatoma was not suspected until an enlarging mass in the anteroinferior quadrant of the tympanic membrane was observed. Radiological studies revealed that the mass was located largely in the infratemporal fossa, with limited extension into the tympanic cavity. The patient underwent surgical treatment, which confirmed the clinical and radiological findings.Conclusion:This patient's clinical, radiological and intra-operative findings strongly suggested the infratemporal fossa as the site of origin of her congenital cholesteatoma.

scholarly journals Ganglioneuroma of the External Auditory Canal and Middle Ear

2017 ◽  
Vol 2017 ◽  
pp. 1-5 ◽  
Author(s):  
Hesham Saleh Almofada ◽  
Michael Steven Timms ◽  
M. Anas Dababo
Keyword(s):  
Bone Marrow ◽  
Temporal Bone ◽  
Middle Ear ◽  
External Auditory Canal ◽  
Rare Case ◽  
Clinical Presentation ◽  
Surgical Intervention ◽  
Stage Iv ◽  
Posterior Mediastinum

Objective. We report an extremely rare case of ganglioneuroma involving the external auditory canal and middle ear. Case Report. Ganglioneuromas are rare benign mature tumors thought to originate from sympathetic ganglions, with the highest incidence in the retroperitoneum, adrenal medulla, and posterior mediastinum. We present a case of ganglioneuroma of the external auditory canal and middle ear. At the age of 12 months, the patient was diagnosed with neuroblastoma stage IV with metastasis to the squamous temporal bone, bone marrow, and skull base. He received a high-risk protocol regimen resulting in complete remission. The patient later presented with recurrent right ear discharge at the age of six years and was diagnosed with ganglioneuroma of external auditory canal and middle ear after appropriate investigations. We report in this article the clinical presentation, investigations, surgical intervention, and follow-up. Conclusion. After the literature review and to our knowledge, this is the first reported case of its kind. Ganglioneuroma maturing from neuroblastoma is one of the theories describing pathophysiology of the disease. Ganglioneuroma should be considered in the differential diagnosis of patients presenting with recurrent ear discharge and decreased hearing in treated cases of neuroblastoma with metastases to temporal bone.

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