Isolated congenital stapes suprastructure fixation

1999 ◽  
Vol 113 (9) ◽  
pp. 798-802 ◽  
Author(s):  
V. Nandapalan ◽  
M. Tos
Keyword(s):  
Hearing Loss ◽  
Congenital Anomalies ◽  
World Literature ◽  
Rare Case ◽  
Conductive Hearing Loss ◽  
Stapedius Muscle ◽  
The World ◽  
Normal Configuration ◽  
Ear Anomalies ◽  
Conductive Hearing

AbstractIsolated congenital anomalies of the ossicles are rare. The majority of cases of congenital conductive hearing loss secondary to middle-ear anomalies have other associated defects, such as atresia, microtia and craniofacial deformities.We present a rare case of isolated congenital stapes suprastructure fixation, where a monocrural stapes with a mobile footplate was attached to the promontory by bony synostosis. There was no stapedius muscle nor pyramidal process. The incus and malleus were of normal configuration. Mobilization of the stapes from the promontory resulted in improvement in hearing. We believe this is the first reported case of such an abnormality. A review of the world literature of isolated stapes suprastructure ankylosis and the classifications of minor congenital anomalies are discussed.

A rare case of primary otoscleroma of the middle ear

2012 ◽  
Vol 126 (12) ◽  
pp. 1276-1277
Author(s):  
A R Kakeri ◽  
A H Patel
Keyword(s):  
Hearing Loss ◽  
Case Report ◽  
Middle Ear ◽  
World Literature ◽  
Rare Case ◽  
Conductive Hearing Loss ◽  
Histopathological Examination ◽  
Suppurative Otitis Media ◽  
The World ◽  
Conductive Hearing

AbstractObjective:We report an extremely rare case of primary otoscleroma.Method:We present a case report and a review of the world literature concerning otoscleroma.Results:An adult woman presented with chronic suppurative otitis media with tubotympanic disease and conductive hearing loss. On mastoid exploration, dark granulations were seen, which were identified as otoscleroma on histopathological examination. The patient responded well to streptomycin.Conclusion:To the best of our knowledge, this is the first report of primary otoscleroma in the world literature. This case indicates that Frisch's bacillus can also spread to the middle ear.

Congenital Anomalies Limited to the Middle Ear

1992 ◽  
Vol 106 (3) ◽  
pp. 285-287 ◽  
Author(s):  
Howard K. Herman ◽  
Charles P. Kimmelman
Keyword(s):  
New York ◽  
Hearing Loss ◽  
Middle Ear ◽  
Congenital Anomalies ◽  
Conductive Hearing Loss ◽  
Oval Window ◽  
Hearing Improvement ◽  
Surgical Indications ◽  
Ear Anomalies ◽  
Conductive Hearing

Congenital anomalies of the middle ear are occasionally encountered during surgery for conductive hearing loss and are unexpected in patients with no other deformities. We reviewed 12 such patients operated on at The New York Eye and Ear Infirmary from 1985 through 1989. Nine of the patients (75%) had unilateral conductive hearing loss whereas three (25%) had bilateral symptoms. One had bilateral congenital middle ear anomalies. Three patients (25%) had anomalies limited to the malleus and scutum. Five patients (47%) had agenesis of the oval window. After reconstructive surgery, 72% of patients had hearing improvement ranging from 13 to 38 dB. The etiology of these anomalies is discussed and their evaluation and surgical indications are presented.

scholarly journals A Rare Stapes Abnormality

2015 ◽  
Vol 2015 ◽  
pp. 1-4 ◽  
Author(s):  
Hala Kanona ◽  
Jagdeep Singh Virk ◽  
Gaurav Kumar ◽  
Sanjiv Chawda ◽  
Sherif Khalil
Keyword(s):  
Computed Tomography ◽  
Hearing Loss ◽  
High Resolution ◽  
World Literature ◽  
Surgical Intervention ◽  
Conductive Hearing Loss ◽  
High Resolution Computed Tomography ◽  
Stapes Prosthesis ◽  
Diagnostic Difficulties ◽  
Conductive Hearing

The aim of this study is to increase awareness of rare presentations, diagnostic difficulties alongside management of conductive hearing loss and ossicular abnormalities. We report the case of a 13-year-old female reporting progressive left-sided hearing loss and high resolution computed tomography was initially reported as normal. Exploratory tympanotomy revealed an absent stapedius tendon and lack of connection between the stapes superstructure and footplate. The footplate was fixed. Stapedotomy and stapes prosthesis insertion resulted in closure of the air-bone gap by 50 dB. A review of world literature was performed using MedLine. Middle ear ossicular discontinuity can result in significant conductive hearing loss. This can be managed effectively with surgery to help restore hearing. However, some patients may not be suitable or decline surgical intervention and can be managed safely conservatively.

scholarly journals Mild Form of Treacher Collins Syndrome Imitating Juvenile Otosclerosis

2012 ◽  
Vol 2012 ◽  
pp. 1-3
Author(s):  
Karol Zeleník ◽  
Pavel Komínek
Keyword(s):  
Early Childhood ◽  
Hearing Loss ◽  
Middle Ear ◽  
Developmental Disorder ◽  
Conductive Hearing Loss ◽  
Treacher Collins Syndrome ◽  
Mild Form ◽  
Ear Anomalies ◽  
Conductive Hearing ◽  
Surgical Corrections

Treacher Collins syndrome (TCS) is an inherited developmental disorder. More than 40% of individuals with TCS have conductive hearing loss attributed to external and middle ear anomalies. Mild cases of TCS often pass undiagnosed at birth or early childhood. The disease may be manifested as conductive hearing loss in teenagers and may resemble juvenile otosclerosis. Patients could suffer from slight facial variabilities including retrognathia (as in our case) and others, which point out to a possible middle ear anomaly. Surgical corrections of middle ear anomalies including TCS generally lead to poorer outcomes comparing with juvenile otosclerosis, which should be discussed with parents during preoperative counselling.

Inner Ear Anomalies and Conductive Hearing Loss in Children With Apert Syndrome

2009 ◽  
Vol 30 (2) ◽  
pp. 184-189 ◽  
Author(s):  
Guangwei Zhou ◽  
Lynn Thomas Schwartz ◽  
Quinton Gopen
Keyword(s):  
Hearing Loss ◽  
Inner Ear ◽  
Conductive Hearing Loss ◽  
Apert Syndrome ◽  
Ear Anomalies ◽  
Conductive Hearing

Congenital stapedial suprastructure fixation with normal footplate mobility: case report

2009 ◽  
Vol 124 (6) ◽  
pp. 680-683 ◽  
Author(s):  
J H Lee ◽  
S H Jung ◽  
H C Kim ◽  
C H Park ◽  
S M Hong
Keyword(s):  
Hearing Loss ◽  
Case Report ◽  
Rare Case ◽  
Conductive Hearing Loss ◽  
Branchial Arch ◽  
Fallopian Canal ◽  
Stapes Footplate ◽  
The Right ◽  
Conductive Hearing

AbstractObjective:We report a case of bilateral conductive hearing loss caused by stapedial suprastructure fixation with normal footplate mobility.Case report:A 50-year-old woman had suffered hearing loss in both ears since childhood. Exploratory tympanotomy revealed immobility of the stapes due to a bony bridge between the stapedial suprastructure and the fallopian canal. The incus was missing, while the malleus handle was minimally deformed. The mobility of the stapes footplate was normal. Post-operatively, the hearing in the right ear improved both subjectively and audiographically, while that in the left ear did not improve because of footplate subluxation during surgery.Conclusion:This is a rare case of congenital stapedial suprastructure fixation with normal footplate mobility. In this patient, development of the second branchial arch was arrested. When performing exploratory tympanotomy for stapedial fixation, one must keep in mind that normal footplate mobility is possible.

A rare case of conductive hearing loss due to partially ossified chorda tympani

2011 ◽  
Vol 6 (4) ◽  
pp. 198-200
Author(s):  
Ahmet Kutluhan ◽  
Gökhan Yalçıner ◽  
Kazım Bozdemir ◽  
Behçet Tarlak ◽  
Akif Sinan Bilgen
Keyword(s):  
Hearing Loss ◽  
Rare Case ◽  
Conductive Hearing Loss ◽  
Chorda Tympani ◽  
Conductive Hearing

scholarly journals Acute otitis media and Covid-19 symptoms: a case report

2021 ◽  
Author(s):  
Fatemeh Moghadasi Boroujeni ◽  
Mehdi Ghadiri ◽  
Farzaneh Saberi ◽  
Hamed Hashemi-Dezaki
Keyword(s):  
Hearing Loss ◽  
Otitis Media ◽  
Conductive Hearing Loss ◽  
Acute Otitis Media ◽  
Shortness Of Breath ◽  
Muscular Pain ◽  
Medical Tests ◽  
The World ◽  
The Common ◽  
Conductive Hearing

Background: In December 2019, the first Coro­navirus disease 2019 (Covid-19) case was obse­rved in Wuhan, China, and afterward, the world has been exposed to an ongoing pandemic. The Covid-19 has different symptoms, such as fever, coughing, shortness of breath, muscular pain, headache, diarrhea, nose running, and a sore thr­oat. However, the symptoms of Covid-19 are not limited to these ones. The Case: The present study reports a 39-year-old female patient complaining of earache and hearing loss with no other Covid-19 symp­toms. The medical tests and diagnoses finally inferred that she was suffering from the Covid-19. Conclusion: In addition to the common symp­toms of Covid 19, acute otitis media can be con­sidered as another symptom of this disease. Keywords: Acute otitis media; Covid-19; conductive hearing loss

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