Nonketotic Hyperglycemic Chorea in a 10-Year-Old Asian Boy with Diabetes Mellitus

2020 ◽  
Author(s):  
Julia Marian ◽  
Firdous Rizvi ◽  
Lily Q. Lew
Keyword(s):  
Diabetes Mellitus ◽  
Parietal Lobe ◽  
Rare Complication ◽  
Brain Magnetic Resonance Imaging ◽  
Food Allergies ◽  
Developmental Venous Anomaly ◽  
Venous Anomaly ◽  
Resonance Imaging ◽  
Focal Lesions

AbstractNonketotic hyperglycemic chorea-ballism (NKHCB), also known as diabetic striato-pathy (DS) by some, is a rare complication of diabetes mellitus and uncommon in children. We report a case of a 10 11/12-year-old boy of Asian descent with uncontrolled type 1 diabetes mellitus (T1DM), Hashimoto's thyroiditis, and multiple food allergies presenting with bilateral chorea-ballism. His brain magnetic resonance imaging revealed developmental venous anomaly in right parietal lobe and right cerebellum, no focal lesions or abnormal enhancements. Choreiform movements resolved with correction of hyperglycemia. Children and adolescents with a movement disorder should be evaluated for diabetes mellitus, especially with increasing prevalence and insidious nature of T2DM associated with obesity.

scholarly journals Liver disease in children and Adolescents with Type1 Diabetes Mellitus

QJM ◽  
2020 ◽  
Vol 113 (Supplement_1) ◽  
Author(s):  
M H Elsayed ◽  
M T Hamza ◽  
M M Elsaeed ◽  
R A F Thabet
Keyword(s):  
Diabetes Mellitus ◽  
Type 1 Diabetes ◽  
Liver Disease ◽  
Type 1 Diabetes Mellitus ◽  
Children And Adolescents ◽  
Liver Enzymes ◽  
Rare Complication ◽  
Elevated Liver Enzymes ◽  
Liver Transaminases

Abstract Glycogenic hepatopathy (GH) is a very rare complication seen mostly in patients with type 1 diabetes mellitus (T1DM) in whom glycemic control has been poor for a long time. We assessed liver diseases in children and adolescents with type 1 diabetes mellitus by detection of elevated liver transaminases and confirmed by fibro scan and ultrasound. One hundred and seven children and adolescents with T1DM were subjected to detailed history, physical examination, laboratory investigation and radiological investigation. Liver transaminases, mean HbA1c and pelviabdominal ultrasound were done for all patients while fibro scan for those with elevated liver enzymes only. Patients with elevated liver enzymes were reassessed after one year. Only nine of our patients have elevated liver enzymes. HbA1c and fibro scan abnormalities (F stage) were significantly higher in patients with elevated liver enzymes. (p < 0.001) After follow up a significant decrease in liver enzymes, fibro scan abnormalities and HbA1c in the group with elevated liver enzymes initially was detected. (p < 0.001) We concluded that liver disease is not a common complication in patients with long standing uncontrolled diabetes which can be reversed after proper control.

scholarly journals Presentación de un caso de síndrome de Mauriac

2017 ◽  
Vol 3 (3) ◽  
pp. 26-32
Author(s):  
Yessica Agudelo Zapata ◽  
Camilo Andrés Quintero Cadavid ◽  
Héctor Fabio Sandoval Alzate ◽  
Luis Miguel Maldonado ◽  
Roberto Franco Vega
Keyword(s):  
Diabetes Mellitus ◽  
Laboratory Tests ◽  
Rare Complication ◽  
Diabetes Mellitus Type 1 ◽  
Type I ◽  
Mucopolysaccharidosis Type I ◽  
Mauriac Syndrome ◽  
Key Issues ◽  
Rule Out

Se presenta un paciente con diabetes mellitus tipo 1, con una complicación poco frecuente conocida como síndrome de Mauriac. Se realizan ayudas diagnósticas tendientes a descartar diagnósticos diferenciales como la mucopolisacaridosis tipo I, que se consideró una de las enfermedades de depósito más probables en el caso del paciente. Finalmente, se presenta una discusión del caso, resumiendo los aspectos fundamentales que llevaron a la sospecha del síndrome de Mauriac. Abstract This is a case report of a patient with diabetes mellitus type 1 and a rare complication known as Mauriac syndrome. Laboratory tests were performed to rule out differential diagnoses, such as mucopolysaccharidosis type I, which was considered one of the storage diseases, most likely for the patient. Finally, we present a discussion of the case, summarizing the key issues that led to the suspicion of a Mauriac syndrome.

Revisit of a rare complication of type 1 diabetes mellitus: Mauriac syndrome

2017 ◽  
Vol 34 (4) ◽  
pp. 132-134 ◽  
Author(s):  
Umang G Thakkar ◽  
Aruna V Vanikar ◽  
Hargovind L Trivedi
Keyword(s):  
Diabetes Mellitus ◽  
Type 1 Diabetes ◽  
Type 1 Diabetes Mellitus ◽  
Rare Complication ◽  
Mauriac Syndrome
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