Ulnar deviation with massive palmar keratoderma in epidermolytic ichthyosis

2021 ◽  
Author(s):  
Takahiro Hamada ◽  
Norito Ishii ◽  
Hiroshi Koga ◽  
Kwesi Teye ◽  
Shuji Nagata ◽  
...  
Keyword(s):  
Ulnar Deviation ◽  
Epidermolytic Ichthyosis

scholarly journals Ichthyoses—A Clinical and Pathological Spectrum from Heterogeneous Cornification Disorders to Inflammation

2021 ◽  
Vol 8 (2) ◽  
pp. 107-123
Author(s):  
Dieter Metze ◽  
Heiko Traupe ◽  
Kira Süßmuth
Keyword(s):  
Stratum Granulosum ◽  
Internal Organs ◽  
Histopathologic Diagnosis ◽  
Epidermolytic Ichthyosis ◽  
Life Threatening ◽  
Keratinization Disorders ◽  
Gene Defects ◽  
Immunohistochemical Methods

Ichthyoses are inborn keratinization disorders affecting the skin only (non-syndromic) or are associated with diseases of internal organs (syndromic). In newborns, they can be life-threatening. The identification of the gene defects resulted in reclassification and a better understanding of the pathophysiology. Histopathologic patterns include orthohyperkeratosis with a reduced or well-developed stratum granulosum, hyperkeratosis with ortho- and parakeratosis with preserved or prominent stratum granulosum, and epidermolytic ichthyosis. Another pattern features “perinuclear vacuoles and binucleated keratinocytes”, which is associated with keratin mutations. Some ichthyoses are histologically defined by psoriasis-like features, and distinct subtypes show follicular hyperkeratosis. In addition to histological and immunohistochemical methods, these patterns allow a better histopathologic diagnosis.

Pronated Grip View With Wrist Deviation: A Pilot Study on the Effect on Ulnocarpal Relationships

Hand ◽  
2021 ◽  
pp. 155894472110289
Author(s):  
Anthony L. Logli ◽  
Beth A. Schueler ◽  
Laurel A. Littrell ◽  
Sanjeev Kakar
Keyword(s):  
Pilot Study ◽  
Surface Area ◽  
Coronal Plane ◽  
Ulnar Deviation ◽  
Radial Deviation ◽  
Wrist Position ◽  
Standardized Protocol ◽  
Ulnar Impaction ◽  
Lunate Surface ◽  
Adult Volunteers

Background We hypothesize that different positions of the wrist in the coronal plane makes the carpus susceptible to ulnar impaction. Methods We prospectively enrolled 10 adult volunteers and obtained fluoroscopic images of each wrist in 12 different positions using a standardized protocol. Distances from the ulna to the lunate (UL) and ulna to the triquetrum (UT) were digitally measured as was the portion of the lunate surface area that was uncovered (LUR) with wrist deviation. Results A wrist position of Pronation, Neutral Deviation, and Grip (P-ND-G) significantly shortened the ulnocarpal distance when compared to a position of Neutral Rotation, Neutral Deviation, and No Grip (NR-ND-NG). Radial deviation during pronation and gripping (Pronated, Radial Deviation, Gripping [P-RD-G]) resulted in the lowest mean UL distance (1.2 mm). UT distance was minimized by a position of ulnar deviation during a pronated grip (Pronated, Ulnar Deviation, Gripping [P-UD-G]) (3.1 mm). The lunate becomes more uncovered with radial deviation. Conclusion Radial deviation minimizes the UL distance while ulnar deviation minimizes the UT distance during a wrist position of pronation and gripping. Further, there is more proximal lunate surface area uncoverage during all positions of radial deviation compared to ulnar deviation.

Avascular Necrosis of the Scaphoid Treated by Total Excision and Radial Advancement Osteotomy

1995 ◽  
Vol 20 (6) ◽  
pp. 736-740 ◽  
Author(s):  
I. GÜNAL ◽  
V. ÖZTUNA ◽  
N. KÖSE ◽  
S. SEBER
Keyword(s):  
Clinical Study ◽  
Avascular Necrosis ◽  
Total Excision ◽  
Active Motion ◽  
Ulnar Deviation ◽  
Extensor Carpi Radialis

Total scaphoid excision and radial advancement osteotomy has been investigated in a eadaverie and clinical study. In three below-elbow fresh amputation specimens, the technique was utilized and stability was checked by radiographs. Instability on ulnar deviation was prevented by extensor carpi radialis longus tenodesis. Four patients were treated in this way. The wrist was immobilized in a below-elbow splint for 45 days, then active motion was encouraged. After 10 months, three patients had excellent results and one patient had good result using the criteria of Cooney et al (1987).

scholarly journals 379 Recessive epidermolytic ichthyosis results from loss of KRT10 expression, regardless of the mutation location

2016 ◽  
Vol 136 (5) ◽  
pp. S67
Author(s):  
D. Vodo ◽  
O. Sarig ◽  
A. Peled ◽  
L. Samuelov ◽  
N. Malchin ◽  
...  
Keyword(s):  
Epidermolytic Ichthyosis

scholarly journals Ulnar Deviation of the Fingers

1952 ◽  
Vol 11 (3) ◽  
pp. 219-221 ◽  
Author(s):  
B. Lush
Keyword(s):  
Ulnar Deviation

scholarly journals Epidermolytic Ichthyosis Sine Epidermolysis

2017 ◽  
Vol 39 (6) ◽  
pp. 440-444 ◽  
Author(s):  
Marina Eskin-Schwartz ◽  
Marianna Drozhdina ◽  
Ofer Sarig ◽  
Andrea Gat ◽  
Tomer Jackman ◽  
...  
Keyword(s):  
Epidermolytic Ichthyosis

Ulnar Neuropathies In Rheumatoid Arthritis

HAND ◽  
1978 ◽  
Vol os-10 (1) ◽  
pp. 77-81 ◽  
Author(s):  
A. R. M. Upton ◽  
J. Darracott ◽  
F. A. Bianchi
Keyword(s):  
Rheumatoid Arthritis ◽  
Ulnar Nerve ◽  
Joint Disease ◽  
Motor Axons ◽  
Ulnar Deviation ◽  
Metacarpophalangeal Joints ◽  
Hand Muscles ◽  
Small Hand ◽  
Selective Impairment

Summary A loss of functional motor axons in the median and ulnar nerves occurred in half of thirty-three patients with rheumatoid arthritis. Weakness of small hand muscles may predispose to the development of ulnar deviation of the fingers in patients with joint disease at the radio-ulnar and metacarpophalangeal joints. There is no evidence that spasm of small hand muscles is a significant cause of ulnar deviation of the fingers in rheumatoid arthritis. Ulnar deviation of the fingers in rheumatoid arthritis is not due to selective impairment of the ulnar nerve or the deep palmar branch of the ulnar nerve even though ulnar deviation of the fingers can occur in association with such lesions and in the absence of joint disease.

Assessment of Muscle Activity and Joint Angles in Small-Handed Pianists: A Pilot Study on the 7/8-Sized Keyboard versus the Full-Sized Keyboard

2006 ◽  
Vol 21 (1) ◽  
pp. 3-9
Author(s):  
B G Wristen ◽  
M C Jung ◽  
A K G Wismer ◽  
M S Hallbeck
Keyword(s):  
Pilot Study ◽  
Research Question ◽  
Wrist Flexion ◽  
Joint Angles ◽  
Ulnar Deviation ◽  
Surface Electrodes ◽  
Musical Excerpt ◽  
Muscle Loading ◽  
Maximal Angle ◽  
Flexion And Extension

This pilot study examined whether the use of a 7/8 keyboard contributed to the physical ease of small-handed pianists as compared with the conventional piano keyboard. A secondary research question focused on the progression of physical ease in pianists making the transition from one keyboard to the other. For the purposes of this study, a hand span of 8 inches or less was used to define a “small-handed” pianist. The goal was to measure muscle loading and hand span during performance of a specified musical excerpt. For data collection, each of the two participants was connected to an 8-channel electromyography system via surface electrodes, which were attached to the upper back/shoulder, parts of the hand and arm, and masseter muscle of the jaw. Subjects also were fitted with electrogoniometers to capture how the span from the first metacarpophalangeal (MCP) joint to the fifth MCP joint moves according to performance demands, as well as wrist flexion and extension and radial and ulnar deviation. We found that small-handed pianists preferred the smaller keyboard and were able to transition between it and the conventional keyboard. The maximal angle of hand span while playing a difficult piece was about 5º smaller radially and 10º smaller ulnarly for the 7/8 keyboard, leading to perceived ease and better performance as rated by the pianists.

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