Juvenile psammomatoid ossifying fibroma of the calcaneus

2020 ◽  
Vol 13 (8) ◽  
pp. e234555
Author(s):  
Rachel L Semus ◽  
Elizabeth Zielinski ◽  
William C Foster
Keyword(s):  
Unusual Case ◽  
Bone Cyst ◽  
Surgical Excision ◽  
Ossifying Fibroma ◽  
Early Management ◽  
Complete Surgical Excision ◽  
Odontogenic Origin ◽  
Secondary Aneurysmal Bone Cyst ◽  
Psammomatoid Ossifying Fibroma ◽  
Rare Group

Juvenile ossifying fibromas (JOFs) are a rare group of fibro-osseous lesions, typically of odontogenic origin. Juvenile psammomatoid ossifying fibroma (JPOF) is one variant, that is, histopathologically distinguished by spherical ossicles resembling psammoma bodies. JPOF tumours are most commonly found in craniofacial skeletal structures and can be locally aggressive. Thus, early management by complete surgical excision is crucial for good outcomes, although recurrence is still possible. Secondary aneurysmal bone cyst (ABC) formation has been reported with JOF lesions, but less commonly with the JPOF variant. We describe an unusual case of JPOF that presented in the calcaneus with secondary ABC formation.

scholarly journals Juvenile Psammomatoid Ossifying Fibroma (JPOF) of Proximal Radius: A Rare Entity

2017 ◽  
Vol 11 (1) ◽  
pp. 583-588 ◽  
Author(s):  
Jagadish Prabhu ◽  
Veena Nagaraj ◽  
Iftikhar Ahmed Mukhtar
Keyword(s):  
Cystic Lesion ◽  
Surgical Excision ◽  
High Recurrence Rate ◽  
Ossifying Fibroma ◽  
Long Bones ◽  
Proximal Radius ◽  
Complete Surgical Excision ◽  
Juvenile Ossifying Fibroma ◽  
Gradual Onset ◽  
Psammomatoid Ossifying Fibroma

Background: Juvenile psammomatoid ossifying fibroma (JPOF) is a rare fibro-osseous lesion that usually occurs in the facial bones. The pathognomonic histopathologic feature is the presence of spherical ossicles, which are similar to psammoma bodies. It is considered to be a unique lesion because of its reported tendency to occur in children and adolescents and its tendency for locally aggressive growth. Because this lesion is aggressive in nature with high recurrence rate, early detection and complete surgical excision are essential. Case Report: Herein, we present a case of 11 year old girl, who presented to our clinic with history of gradual onset pain around right elbow associated with limitation of right forearm rotation for 3 months. After getting informed consent, we performed needle biopsy and histopathologically it was diagnosed as Psammomatoid type juvenile ossifying fibroma (JPOF) of proximal radius. We performed extensive debridement, curettage of entire cystic lesion involving the proximal radius and filled the cavity with allograft bone granules and intramedullary titanium elastic nail through fibular strut graft, bridging the cystic lesion. Conclusion: As far as our knowledge there is no reported case of psammomatoid type of juvenile ossifying fibroma of proximal radius. We believe that such tumors in long bones are aggressive and have tendency for recurrence. Definitive diagnosis is utmost important for proper planning, surgical excision and reconstruction of long bones and need regular follow up to look for any recurrence or malignant transformation.

scholarly journals Recurrent juvenile psammomatoid ossifying fibroma with secondary aneurysmal bone cyst of the maxilla: a case report and review of literature

2018 ◽  
Author(s):  
Sachin C. Sarode ◽  
Gargi S. Sarode ◽  
Yashwant Ingale ◽  
Manjusha Ingale ◽  
Barnali Majumdar ◽  
...  
Keyword(s):  
Case Report ◽  
Aneurysmal Bone Cyst ◽  
English Literature ◽  
Bone Cyst ◽  
Growth Potential ◽  
Ossifying Fibroma ◽  
Surgical Removal ◽  
Juvenile Ossifying Fibroma ◽  
Secondary Aneurysmal Bone Cyst ◽  
Psammomatoid Ossifying Fibroma

Juvenile ossifying fibroma is a benign fibro-osseous lesion commonly affecting the extra-gnathic craniofacial skeleton of the young individuals. The psammomatoid and trabecular variants are its two histopathological subtypes having distinctive clinico-pathological characteristics. Secondary aneurysmal bone cysts are frequently reported to arise in the pre-existing fibro-osseous lesions but rarely reported in the psammmomatoid variant of the juvenile ossifying fibroma. Such hybrid lesions, especially massive in size, tend to exhibit a greater aggressive growth potential and higher recurrence rate and mandate complete surgical removal of the lesion along with a long-term follow-up. The objective of this case report was to present a rare incident of recurrent psammomatoid ossifying fibroma associated with a secondary aneurysmal bone cyst in the maxillary jaw bone of a young patient and review the similar published reports in the English literature.

A rare case of psammomatoid ossifying fibroma in the sphenoid bone reconstructed using autologous particulate exchange cranioplasty

2011 ◽  
Vol 7 (3) ◽  
pp. 238-243 ◽  
Author(s):  
Manish K. Kasliwal ◽  
Gary F. Rogers ◽  
Shakti Ramkissoon ◽  
Alexander Moses-Gardner ◽  
Kyle C. Kurek ◽  
...  
Keyword(s):  
Radiation Therapy ◽  
Acute Lymphoblastic Leukemia ◽  
Rare Case ◽  
Lymphoblastic Leukemia ◽  
Bone Cyst ◽  
Ossifying Fibroma ◽  
Clinical Scenario ◽  
Tumor Excision ◽  
Novel Technique ◽  
Psammomatoid Ossifying Fibroma

Psammomatoid ossifying fibroma (POF), a variant of ossifying fibroma, is a benign fibroosseous lesion typically arising within the nasal cavity, paranasal sinuses, and orbit. Cranial vault involvement is exceedingly rare, with very few cases reported in the literature. The authors report a case of POF in the neurocranium of an 11-year-old child, 4 years after chemotherapy and radiation therapy for acute lymphoblastic leukemia. This case is reported in view of its rarity, novelty of presentation, and the difficulty in diagnosis due to its radiological resemblance to aneurysmal bone cyst or monostotic cystic fibrous dysplasia, further aggravated by the clinical scenario. A novel technique of cranial reconstruction called autologous particulate exchange cranioplasty was used following tumor excision.

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