scholarly journals Juvenile Psammomatoid Ossifying Fibroma (JPOF) of Proximal Radius: A Rare Entity

2017 ◽  
Vol 11 (1) ◽  
pp. 583-588 ◽  
Author(s):  
Jagadish Prabhu ◽  
Veena Nagaraj ◽  
Iftikhar Ahmed Mukhtar

Background: Juvenile psammomatoid ossifying fibroma (JPOF) is a rare fibro-osseous lesion that usually occurs in the facial bones. The pathognomonic histopathologic feature is the presence of spherical ossicles, which are similar to psammoma bodies. It is considered to be a unique lesion because of its reported tendency to occur in children and adolescents and its tendency for locally aggressive growth. Because this lesion is aggressive in nature with high recurrence rate, early detection and complete surgical excision are essential. Case Report: Herein, we present a case of 11 year old girl, who presented to our clinic with history of gradual onset pain around right elbow associated with limitation of right forearm rotation for 3 months. After getting informed consent, we performed needle biopsy and histopathologically it was diagnosed as Psammomatoid type juvenile ossifying fibroma (JPOF) of proximal radius. We performed extensive debridement, curettage of entire cystic lesion involving the proximal radius and filled the cavity with allograft bone granules and intramedullary titanium elastic nail through fibular strut graft, bridging the cystic lesion. Conclusion: As far as our knowledge there is no reported case of psammomatoid type of juvenile ossifying fibroma of proximal radius. We believe that such tumors in long bones are aggressive and have tendency for recurrence. Definitive diagnosis is utmost important for proper planning, surgical excision and reconstruction of long bones and need regular follow up to look for any recurrence or malignant transformation.

Author(s):  
Vasvani M Dimple ◽  
Irom Urmila ◽  
Tuladhar Alisha ◽  
Neeraj ◽  
Chug Ashi

Juvenile psammomatoid ossifying fibroma is histological variant of juvenile ossifying fibroma, a fibro-osseous tumor of craniofacial bones with benign but potentially aggressive nature. Complete excision of tumor is essential as it is associated with very high recurrence rate. We have reported here a case of juvenile ossifying fibroma- a psammomatoid variety present in right maxilla in a 13-year old male child. Complete excision of tumor was done through intra-oral approach with the 2.5 years of follow up shows no recurrence.Juvenile psammomatoid ossifying fibroma is fibro-osseous tumor of craniofacial bones with benign but potentially aggressive nature. Complete excision of tumor is essential as it is associated with very high recurrence rate.


2020 ◽  
Vol 13 (8) ◽  
pp. e234555
Author(s):  
Rachel L Semus ◽  
Elizabeth Zielinski ◽  
William C Foster

Juvenile ossifying fibromas (JOFs) are a rare group of fibro-osseous lesions, typically of odontogenic origin. Juvenile psammomatoid ossifying fibroma (JPOF) is one variant, that is, histopathologically distinguished by spherical ossicles resembling psammoma bodies. JPOF tumours are most commonly found in craniofacial skeletal structures and can be locally aggressive. Thus, early management by complete surgical excision is crucial for good outcomes, although recurrence is still possible. Secondary aneurysmal bone cyst (ABC) formation has been reported with JOF lesions, but less commonly with the JPOF variant. We describe an unusual case of JPOF that presented in the calcaneus with secondary ABC formation.


2013 ◽  
Vol 4 (1) ◽  
pp. 42-44
Author(s):  
Mohammad Shah Kamal ◽  
Mohammad Ashik Anwar Bahar ◽  
MA Latif ◽  
Mehdi Mohammad Imtiaz Uddin Khan

Juvenile ossifying fibroma (JOF) is a rare fibro-osseous neoplasm that arises within the craniofacial bones in individuals under 15 years of age. It affects both males and females equally. It has the potential for excessive growth, bone destruction, and recurrence. It is more aggressive than ossifying fibroma. Recurrence rate ranges from 30% to 58% .We report a case of 11-year-old male child presented with a painless, progressive swelling of the right face for 8 months. CT scan demonstrated a well-defined, mixed-density mass filling the right maxillary sinus. Under general anaesthesia, surgical excision of the tumour was performed. Histopathologically, excised specimen was identical with fibro-osseous lesion. Juvenile ossifying fibroma (JOF) is aggressive in nature and recurrence rate is high, so early detection and complete surgical excision is essential. DOI: http://dx.doi.org/10.3329/akmmcj.v4i1.13685 AKMMC J 2013: 4(1): 42-44


2016 ◽  
Vol 6 (1) ◽  
pp. 45-51
Author(s):  
Deepa Das Achath ◽  
Abhishek Sanjay Ghule ◽  
Preeti Kanchan-Talreja ◽  
Sunanda Bhatnagar

ABSTRACT Fibroosseous lesions of the jaws, including juvenile ossifying fibroma (JOF), pose diagnostic and therapeutic difficulties due to their clinical, radiological, and histological variability. There are two histological varieties of it, one as psammomatoid type and second as trebacular type; here, we present a trebacular type, which is a rare variety. After the clinical examination, radiological and histological analysis, it was diagnosed as juvenile trebacular ossifying fibroma. Although JOF is an uncommon clinical entity, its aggressive local behavior and high recurrence rate means that it is important to make an early diagnosis, apply the appropriate treatment, and, especially, follow-up the patient over the long term. How to cite this article Ghule AS, Achath DD, Kanchan- Talreja P, Bhatnagar S. Juvenile Aggressive Trabecular Ossifying Fibroma of Mandible: A Rare Case Report. J Contemp Dent 2016;6(1):45-51.


2010 ◽  
Vol 1 (1) ◽  
pp. 59-64
Author(s):  
Jagadish Hosmani ◽  
Sujata M Byahatti ◽  
Ranganath Nayak ◽  
Ramakant Nayak ◽  
Bhushan Jayade

ABSTRACT Juvenile ossifying fibroma (JOF) is a highly aggressive uncommon fibro-osseous lesion occurring in the facial bones. Two histological variants of JOF, i.e. trabecular and psammomatoid have been reported. Here we present a case of a 20-year-old juvenile diabetic patient with massive growth on her left side of the jaw which was diagnosed as juvenile ossifying fibroma. This huge aggressive mass in the left side of the mandible had lead to complete lingual tilting of molars and premolars. After clinical and radiological examination, a biopsy led to the histopathological diagnosis of mixed variant of juvenile ossifying fibroma. The required surgical treatment (hemimandibulectomy) was undertaken under GA. The aggressive local behavior and high recurrence rate of JOF emphasizes the need for an early diagnosis, and appropriate radical treatment with long-term follow-up. One such case is reviewed and discussed in detail in the following article.


Author(s):  
MA Awal

Juvenile ossifying fibroma is a locally aggressive, benign fibro-osseous tumor. It usually occurs in young children and arises in the maxillofacial region. It has a high recurrence rate. This pathology would be diagnosed and treated as early as possible because of its rapidly progressive and osteolytic nature which may complicate the surgical removal if left untreated over a long period. The present case is diagnosed as Juvenile ossifying fibroma involving the maxilla causing facial deformity, proptosis, and nasal obstruction in a 15-year-old female child.


Author(s):  
Henry Aldana ◽  
Martin Orozco ◽  
Leonardo Ordoñez ◽  
Clara Estrada ◽  
Camilo Mosquera

Trabecular juvenile ossifying fibroma is a rare fibro-osseous lesion affecting the craniofacial skeleton occurring commonly in children and young adults. Tumor clinical behavior is highly aggressive with invasion of adjacent anatomic structures. Because of its high recurrence rate complete excision is necessary, but this one could be facial mutilating. This case report presents a 23-year-old female patient with a trabecular juvenile ossifying fibroma of the right maxilla, expanding into the orbit and zygomatic bone. The report also shows the multidisciplinary surgical management of this lesion with successful preservation of optic nerve function and facial aesthetics.


1993 ◽  
Vol 102 (12) ◽  
pp. 917-924 ◽  
Author(s):  
Christopher Trent ◽  
Frederick M. Byl

The aneurysmal bone cyst is a nonmalignant lesion that by expanding disrupts the architecture of the affected bone and destroys surrounding tissue. Developing rarely in the craniofacial region, and more commonly affecting the long bones and the spine, the lesion has characteristic radiographic features but is definitively diagnosed only by pathologic characteristics. Complete surgical excision is used to treat aneurysmal bone cyst, with either curettage or composite resection. Recurrence is common in incompletely excised lesions. Adjunctive cryotherapy reduces the risk of recurrence, and radiotherapy is reserved for nonresectable lesions. The case we report of a young man seen for a large mandibular aneurysmal bone cyst demonstrates the complexity of diagnosing and treating this condition.


Author(s):  
Jayachandran S ◽  
Sophia Jeba Priya ◽  
Archana M

Peripheral ossifying fibroma is one of the common reactive oral lesions which accounts for about 9.6% of all gingival lesions. There is a predilection for females in the second to fourth decade of life. Most lesions are less than 2 cm in size, although larger ones occasionally occur. The raised lesion may appear smooth or ulcerated and most often is caused by constant irritation or trauma. The growth-like clinical presentation may lead to misclassification; however, the histologic appearance is quite diagnostic for this lesion. In this case report we are discussing the case of a young male patient with peripheral ossifying fibroma in the mandibular anterior region which was managed by complete surgical excision. Key Words: Peripheral ossifying fibroma, reactive lesion, mandibular gingiva


2016 ◽  
Vol 10 (1) ◽  
pp. 26-28 ◽  
Author(s):  
Swapan Kumar Paul ◽  
Suprotim Howlader ◽  
Diponker Kumar Saha ◽  
Abdur Rahed Khan

Lymphangiomas are benign hamartomatous lymphatic tumours characterized by multiple communicating lymphatic channels and cystic spaces. Cystic lyphangiomas may be seen anywhere in the body but are common in neck, axilla, mediastinum and groin. Treatment options are surgical resection, radiation, sclerotherapy etc but have got high recurrence rate and complications. In the present study we hypothesized that complete surgical resection along with keeping a drain for 2-3 wks, may reduce recurrence rate. This prospective study was performed from July 2008 to June 2013. Total 21 children treated during this period by the technique of complete surgical excision with keeping drain tube in situ for 2 to 3 weeks. Ultrasound performed in all patients, CT scan and Duplex study performed in some patients, histopathology done in all patients. Patients with intra-abdominal lymphangioma not included in this study. Twenty one patients were operated during the study period and average duration of keeping drain tube was 18.57 days. Among the 21 cases 2 (9.52%) patients developed mild infection, 1 (4.76%) patient developed infection with pus formation and 1 (4.76%) patient developed recurrence. Our success in the treatment warrants further verification of potential benefits of keeping drain tube in situ for 2-3 weeks after surgical excision of lymphangiomas.Faridpur Med. Coll. J. Jan 2015;10(1): 26-28


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