scholarly journals A Case of Vanishing Metastatic Mass: Right Atrial Mass in the Setting of Primary Epithelioid Hemangioendothelioma of the Spine

2018 ◽  
Vol 11 (2) ◽  
pp. 534-540 ◽  
Author(s):  
Eshan Patel ◽  
P. Kancharla ◽  
B.K. Surapaneni ◽  
K. Hennrick ◽  
M. Goldfinger ◽  
...  
Keyword(s):  
Clinical Presentation ◽  
Epithelioid Hemangioendothelioma ◽  
The Body ◽  
Right Atrial ◽  
Low Grade ◽  
Vascular Neoplasm ◽  
Right Atrial Mass ◽  
Progression Of Disease ◽  
The Right ◽  
Age And Sex

Epithelioid hemangioendothelioma (EHE) is a rare low-grade vascular neoplasm that is characterized as intermediate between benign hemangioma and high-grade angiosarcoma affecting 1 in 1,000,000 people worldwide. It has been described throughout the body with lung, liver, skin, and bone being the most frequent sites. Primary EHE of the spine has been reported in 56 cases so far with no correlation of age and sex. Our case highlights a rare clinical presentation, etiopathogenesis, diagnosis, and treatment of EHE of the spine with metastasis to the right atrium. This is the first documented case of EHE of the spine with metastatic spread to the heart treated with bevacizumab leading to resolution of the heart metastatic mass. Further studies are warranted to develop a treatment formula for this rare tumor, to consider combination chemotherapy and new adjuvant targeted immunotherapies to prevent progression of disease.

Cystic hypersecretory ductal carcinoma (CHDC): a rare distinctive variant of ductal carcinoma

2021 ◽  
Vol 14 (7) ◽  
pp. e235488
Author(s):  
Ashley DiPasquale ◽  
Lashan Peiris ◽  
Svetlana Silverman
Keyword(s):  
Clinical Presentation ◽  
Ductal Carcinoma ◽  
Cystic Mass ◽  
Low Grade ◽  
Rare Form ◽  
Breast Malignancy ◽  
The Right

Cystic hypersecretory ductal carcinoma (CHDC) is a rare distinctive variant of ductal carcinoma that behaves in a low-grade fashion. This rare form of breast malignancy has only been reported a handful of times in the surgical literature. This article outlines the clinical presentation, workup and management of a 43-year-old woman who presented with a bilobed cystic mass of the right breast diagnosed as CHDC.

scholarly journals Cardiac Lipoma: An Uncharacteristically Large Intra-Atrial Mass Causing Symptoms

2018 ◽  
Vol 2018 ◽  
pp. 1-3 ◽  
Author(s):  
Fahad Syed Naseerullah ◽  
Hemangkumar Javaiya ◽  
Avinash Murthy
Keyword(s):  
Right Atrial ◽  
Rare Type ◽  
Atrial Mass ◽  
Persistent Symptoms ◽  
Coronary Syndrome ◽  
Cardiac Tumours ◽  
Large Size ◽  
Right Atrial Mass ◽  
Cardiac Lipoma ◽  
The Right

Primary tumours of the heart are often encountered in clinical practice. Different autopsy series estimate the incidence to be anywhere from 0.001% to 0.19%. Cardiac lipoma is a rare type of tumour of the heart and pericardium. It comprises approximately 10–19% of all cardiac tumours. We present a case of a large cardiac lipoma in a fifty-year-old female. She presented with sharp chest pains, palpitations, and dizziness. Acute coronary syndrome was ruled out. A transthoracic echocardiogram showed an abnormal, large, fixed right atrial mass. The mass was noted to be occupying most of the right atrium. It was excised due to its large size and persistent symptoms. On pathophysiology, the mass was definitively diagnosed to be an 80 mm × 70 mm cardiac lipoma. Postoperatively, the patient did well with resolution of her symptoms. This case provides evidence that even large, invasive, symptomatic cardiac lipomas can be successfully resected with good outcomes.

Ping-Pong Ball, Tumor or Thrombus in the Right Atrium? A Case Report

2018 ◽  
Vol 9 (3) ◽  
pp. 350-351
Author(s):  
Stephanie Ghaleb ◽  
Bryant Roosevelt ◽  
James Cnota
Keyword(s):  
Clinical Judgment ◽  
Right Atrium ◽  
Frozen Section ◽  
Noninvasive Imaging ◽  
Neoadjuvant Treatment ◽  
Lower Lobe ◽  
Final Diagnosis ◽  
Right Atrial ◽  
Right Atrial Mass ◽  
The Right

Tumors and thrombi are the most common cardiac masses of the right atrium. The use of noninvasive imaging to differentiate between the two can be deceiving, and the clinical judgment of a cardiologist and the emergency of the situation should be partnered to decide on the next step of the management. We present the case of a 29-year-old lady who was receiving neoadjuvant treatment for her rhabdomyosarcoma and was incidentally found to have a very large, very mobile right atrial mass that was protruding in the right ventricle with each cardiac cycle along with findings of a small segmental right lower lobe pulmonary embolism. Along with noninvasive imaging, frozen section analysis procured the wrong diagnosis, and the mass was ultimately found to be a right atrial thrombus on definite pathology review. Exact management of right atrial masses continues to be not well delineated, and when in doubt, final diagnosis might need to be “a posteriori” and based on the treatment response.

scholarly journals Giant right atrial mass obliterating the right atrium

2015 ◽  
Vol 5 (5) ◽  
pp. 29607 ◽  
Author(s):  
Ahmad Al-Fakhouri ◽  
Inyong Hwang ◽  
Shadwan F. Alsafwah
Keyword(s):  
Right Atrium ◽  
Right Atrial ◽  
Atrial Mass ◽  
Right Atrial Mass ◽  
The Right

scholarly journals Right atrial myxoma presenting as a pulmonary embolism in a 32-year-old female

2019 ◽  
Vol 8 ◽  
pp. 204800401881760 ◽  
Author(s):  
Amitabh C Pandey ◽  
John J Carey ◽  
Jess L Thompson
Keyword(s):  
Pulmonary Embolism ◽  
Median Sternotomy ◽  
Atrial Myxoma ◽  
Atrial Septum ◽  
Right Atrial ◽  
Cardiac Tumors ◽  
Right Atrial Mass ◽  
Sternal Border ◽  
Right Atrial Myxoma ◽  
The Right

Primary cardiac tumors are typically benign, with myxomas being most common. We present a 32-year-old female with a chief complaint of dyspnea and a constant non-radiating chest pressure along the left sternal border. She was found to have a pulmonary embolism that was ultimately caused by embolization of a right atrial myxoma with remnants of a large, highly mobile mass attached to the right inter-atrial septum prolapsing through the tricuspid valve. The patient underwent a median sternotomy, right atrial mass resection, pulmonary embolectomy, and inter-atrial septum reconstruction using the patient’s pericardium. The importance of finding the etiology of initial diagnoses is stressed with long-term outcomes for patients.

scholarly journals Crossed renal ectopia with an unusual form of fusion (inverted U shape) managed by novel approach - laparoscopic ureterocalicostomy. A case report

2021 ◽  
Vol 6 (1) ◽  
pp. 71-75
Author(s):  
Osama Bani Hani ◽  
Omar Halalsheh ◽  
Yazeed Mohammad ◽  
Anas Bani Yaseen ◽  
Ruba Khasawneh ◽  
...  
Keyword(s):  
Case Report ◽  
Clinical Presentation ◽  
The Body ◽  
Published Data ◽  
Renal Ectopia ◽  
Novel Approach ◽  
Crossed Renal Ectopia ◽  
The Right ◽  
Tract Infections ◽  
Unusual Type

Herein we present a case of crossed renal ectopia with an unusual type of fusion, discovered incidentally in a 11-year-old girl presented with recurrent urinary tract infections. Both kidneys were located on the right side of the body fused in their upper poles only, forming an inverted U shape. After reviewing the published data on this topic, we found that most of the described anomalies were within the six well-known types of fusion anomalies. This child had an unusual clinical presentation of severe hydronephrosis of the orthotopic kidney. A unique surgical technique to correct the pathology to be able to preserve the residual mass of that kidney was performed.

scholarly journals Cardiac myxoma: The influence of preoperative clinical presentation and surgical technique on late outcome

2007 ◽  
Vol 135 (7-8) ◽  
pp. 401-406
Author(s):  
Aleksandar Mikic ◽  
Biljana Obrenovic-Kircanski ◽  
Mladen Kocica ◽  
Mile Vranes ◽  
Vesna Lackovic ◽  
...  
Keyword(s):  
Surgical Treatment ◽  
Clinical Presentation ◽  
Cardiac Myxoma ◽  
Surgical Techniques ◽  
Right Atrial ◽  
Functional Improvement ◽  
Primary Tumors ◽  
Cardiac Myxomas ◽  
The Right

Introduction Cardiac myxomas are the most frequent primary tumors of the heart in adults, and they can be found in each of four cardiac chambers. Although biologically benign, due to their unfavorable localization, myxomas are considered "functionally malignant" tumors. Diagnosis of cardiac myxoma necessitates surgical treatment. Objective To analyze: 1) the influence of localization, size and consistency of cardiac myxomas on preoperative symptomatology; 2) the influence of different surgical techniques (left, right, biatrial approach, tumor basis solving) on early, and late outcomes. Method From 1982 to 2000, at the Institute for Cardiovascular Diseases, Clinical Center of Serbia, there were 46 patients with cardiac myxomas operated on, 67.4% of them women, mean age 47.1?16.3 years. The diagnosis was made according to clinical presentation, electrocardiographic and echocardiographic examinations and cardiac catheterization. Follow-up period was 4-18 (mean 7.8) years. Results In 41 (89.1%) patients, myxoma was localized in the left, while in 5 (10.9%), it was found in the right atrium. Average size was 5.8?3.8 cm (range: 1?1 cm to 9?8 cm) and 6?4 cm (range: 3?2 cm to 9?5 cm) for the left and right atrial myxomas, respectively. A racemous form predominated in the left (82.6%) and globous in the right (80%) atrium. Fatigue was the most common general (84.8%) and dyspnoea the most common cardiologic symptom (73.9%). Preoperative embolic events were present in 8 patients (4 pulmonary, 4 systemic). In our series: 1) different localization, size and consistency had no influence on the preoperative symptomatology; 2) surgical treatment applied, regardless of different approaches and basis solving, resulted in excellent functional improvements (63.1% patients in NYHA III and IV class preoperatively vs. 6.7% patients postoperatively) and had no influence on new postoperative rhythm disturbances (8.7% patients preoperatively vs. 24.4% patients postoperatively); 3) early (97.8%), and late survival rates (91.3%) were excellent; 4) there were no relapses during the follow-up period. Conclusion Localization, size and consistency had no influence on the preoperative symptomatology. Excellent survival rate with significant functional improvement, rare postoperative complications and no recurrences, justify the applied strategies of surgical approach and tumor basis solving in our series.

scholarly journals A Rare Case of an Ectopic Liver Presenting as Right Atrial Mass

2019 ◽  
Vol 2019 ◽  
pp. 1-4
Author(s):  
Adhirath Doshi ◽  
Dhaval Shah ◽  
Shradha Gupta ◽  
Deepika Panday ◽  
Arie Farji-Cisneros ◽  
...  
Keyword(s):  
Inferior Vena ◽  
Abdominal Cavity ◽  
Vena Cava ◽  
Surgical Excision ◽  
Right Atrial ◽  
Hepatic Tissue ◽  
Transesophageal Echocardiogram ◽  
Right Atrial Mass ◽  
The Right ◽  
Ectopic Liver

Ectopic liver tissue is commonly observed in the abdominal cavity in adjacent organs. Extension of hepatic tissue into the intrathoracic cavity is rarely reported. We present the case of a 46-year-old woman with a 2.1×1.8 cm mass confirmed by transesophageal echocardiogram to be at the right atrial and inferior vena cava junction that was initially thought to be a myxoma which prompted surgical excision but subsequently identified as ectopic liver by histology.

scholarly journals P1325 Lymphoma encasing the heart: intra-cardiac or extra-cardiac mass?

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
S Ahmad ◽  
M Lashein ◽  
W Khan
Keyword(s):  
Systolic Function ◽  
Contrast Echocardiography ◽  
Vascular Lesion ◽  
Right Atrial ◽  
External Compression ◽  
Cardiac Centre ◽  
Atrioventricular Groove ◽  
Right Atrial Mass ◽  
Night Sweats ◽  
The Right

Abstract A 70-year-old gentleman was referred to our department for atypical chest pains and night sweats. He had an unremarkable past medical history and denied any history of familial disease. There were no complaints of dyspnoea, dizziness or palpitations. A routine echocardiogram showed a suspicious right atrial mass, seemingly extra cardiac in origin. Clinical examination was entirely unremarkable and further investigations were arranged as a matter of urgency. Contrast echocardiography confirmed a lesion wrapping around the right atrium with possible myocardial infiltration. Trans-oesophageal echocardiography showed extension of the mass into the adjacent atrioventricular groove. The appearances were of a compressive, non-vascular lesion measuring 4.8cm x 5.6cm. Overall cardiac systolic function remained preserved with no significant intra-cardiac abnormalities. A CT Thorax with contrast was the next step in investigation. This demonstrated nodular soft tissue infiltration of the entire pericardium, mainly involving the right heart chambers with encasement of the aortic root and coronary arteries. Significant lymphadenopathy was also identified suggesting a malignant process. Cardiac MRI was then performed and this substantiated the findings on CT, raising concern for encasement and external compression of the right coronary artery. Urgent transfer to a tertiary cardiac centre was arranged and subsequent biopsy confirmed histological diagnosis of Stage 4 Lymphoma. After a multi-disciplinary meeting, a non-operative approach was decided. Treatment with steroids and chemotherapy was commenced without delay leading to a significant reduction in the size of the mass. Abstract P1325 Figure.

Crystal-Storing Histiocytosis as a Cause of Symptomatic Cardiac Mass

2009 ◽  
Vol 133 (11) ◽  
pp. 1861-1864 ◽  
Author(s):  
Charles J. Sailey ◽  
Borislav A. Alexiev ◽  
James S. Gammie ◽  
Paula Pinell-Salles ◽  
J. Lawrence Stafford ◽  
...  
Keyword(s):  
Monoclonal Gammopathy ◽  
Plasma Cells ◽  
Periodic Acid ◽  
Right Atrial ◽  
Prior History ◽  
Low Grade ◽  
Periodic Acid Schiff ◽  
Right Atrial Mass ◽  
History Of

Abstract Crystal-storing histiocytosis is a rare disorder that is typically associated with low-grade B-cell lymphomas and monoclonal gammopathy. We present a 64-year-old man with a prior history of weakness and weight loss and hematologic evaluation that had revealed immunoglobulin G κ monoclonal light chains in the serum and negative bone marrow biopsy. He presented with supraventricular tachyarrhythmia and a right atrial mass seen on echocardiogram and excised surgically. Histologically, the tumor was composed of sheets of macrophages infiltrating the atrial myocardium. The histiocytes were filled with multiple needle-shaped, periodic acid-Schiff–negative crystals. These cells and associated plasma cells failed to show clonal light chain restriction by in situ hybridization or immunohistochemistry, and there was no area of lymphoma in the tumor. Ultrastructural examination showed numerous sticklike, trapezoidal, or polygonal dense crystals in the cytoplasm of histiocytes corroborating the diagnosis of crystal-storing histiocytosis. Although rare, crystal-storing histiocytosis should be included in the differential diagnosis of heart masses in patients with hematologic conditions associated with monoclonal gammopathy.

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