scholarly journals Congenital Lobar Emphysema with Autosomal Dominance Presenting in Adulthood

Author(s):  
A.O. Azmeen ◽  
J. McArdle
2021 ◽  
Vol 21 (1) ◽  
Author(s):  
Bingchun Lin ◽  
Huitao Li ◽  
Chuanzhong Yang

Abstract Background Congenital lobar emphysema (CLE) is a congenital pulmonary cystic disease, characterized by overinflation of the pulmonary lobe and compression of the surrounding areas. Most patients with symptoms need an urgent surgical intervention. Caution and alertness for CLE is required in cases of local emphysema on chest X-ray images of extremely premature infants with bronchopulmonary dysplasia (BPD). Case presentation Here, we report a case of premature infant with 27 + 4 weeks of gestational age who suddenly presented with severe respiratory distress at 60 days after birth. Chest X-ray and computed tomography (CT) indicated emphysema in the middle lobe of the right lung. The diagnosis of CLE was confirmed by histopathological examinations. Conclusions Although extremely premature infants have high-risk factors of bronchopulmonary dysplasia due to their small gestational age, alertness for CLE is necessary if local emphysema is present. Timely pulmonary CT scan and surgical interventions should be performed to avoid the delay of the diagnosis and treatment.


2010 ◽  
Vol 3 (3) ◽  
pp. 150-152 ◽  
Author(s):  
M. Khalid ◽  
S. Saleemi ◽  
B. Khan

1999 ◽  
Vol 34 (9) ◽  
pp. 1347-1351 ◽  
Author(s):  
Ibrahim Karnak ◽  
Mehmet Emin Şenocak ◽  
Arbay O. Ciftci ◽  
Nebil Büyükpamukçu

2018 ◽  
Vol 47 (4) ◽  
pp. 225-227
Author(s):  
Nizar Khatib ◽  
Ron Beloosesky ◽  
Yuval Ginsberg ◽  
Bentur Lea ◽  
Gur Michal ◽  
...  

2013 ◽  
Vol 2 (3) ◽  
pp. 135
Author(s):  
Hbibi Mohamed ◽  
Bouabdellah Youssef ◽  
Bouharrou Abdelhak ◽  
Oulmaati Abdellah

2018 ◽  
Vol 6 (1) ◽  
pp. 218
Author(s):  
Nishant Mittal ◽  
Ankit Parakh ◽  
Prashant Jain ◽  
N. K. Mittal

Congenital lobar emphysema (CLE) is a congenital condition characterized by distension and air trapping of the affected lobe of the lung. It is one of the causes of infantile respiratory distress, which may require surgical resection of affected lobe. Case characteristics: 3-day-old neonate with ventilation refractory respiratory distress. Imaging was suggestive of decreased lung tissue on the right side with ipsilateral mediastinal shift. Intervention/ outcome: Early surgical lobectomy was done to improve lung functions and the child improved dur to early intervention. Message: An early diagnosis with high index of suspicion helps patients with this rare congenital anomaly. Early intervention is the key to good long-term outcome. More awareness about the entity and treatment options available would greatly help improving the outcome and disease burden.


Thorax ◽  
1959 ◽  
Vol 14 (3) ◽  
pp. 254-262 ◽  
Author(s):  
P. G. I. Stovin

PEDIATRICS ◽  
1951 ◽  
Vol 8 (6) ◽  
pp. 795-804
Author(s):  
ROSS ROBERTSON ◽  
E. STEWART JAMES

Congenital lobar emphysema is a surgical emergency of infancy. It may be diagnosed without much difficulty and treated by lobectomy with gratifying success. The exact nature of the congenital defect in the bronchus should be revealed by a more thorough study of similar cases. If the condition is not suspected, it might readily be missed at routine autopsy, and consequently may occur more frequently than realized.


PEDIATRICS ◽  
1983 ◽  
Vol 71 (5) ◽  
pp. 844-848
Author(s):  
WAYNE J. MORGAN ◽  
RICHARD J. LEMEN ◽  
RODRIGO ROJAS

The degree of respiratory dysfunction and subsequent morbidity of patients with congenital lobar emphysema (CLE) are related to the degree of hyperinflation of the involved lobe.1 Whereas neonates with severe CLE may have marked respiratory distress requiring surgical resection of the hyperinflated lobe, children with mild forms of CLE seldom have a sudden increase in size of the involved lobe leading to respiratory failure.2,3 We report two infants with mild CLE who were clinically stable and developed respiratory distress with increased hyperinflation of the involved lobe associated with an acute respiratory tract infection. Both infants returned to their base line clinical status with conservative therapy alone following resolution of their respiratory illness.


Sign in / Sign up

Export Citation Format

Share Document