Retroperitoneal Fibrosis (Ormond's Disease): Clinical Pathologic Study of Eight Cases

2002 ◽  
Vol 9 (5) ◽  
pp. 432-437 ◽  
Author(s):  
Jamie Wu ◽  
Edison Catalano ◽  
Domenico Coppola
Keyword(s):  
Retroperitoneal Fibrosis ◽  
Ormond’S Disease ◽  
Pathologic Study

Ormond's disease: Definizione e cenni anatomici del retroperitoneo: Ormond's disease: Definition and anatomic outlines of the retroperitoneum

1998 ◽  
Vol 65 (2) ◽  
pp. 253-256
Author(s):  
D. Schiavone ◽  
G. Carluccio
Keyword(s):  
Connective Tissue ◽  
Retroperitoneal Fibrosis ◽  
Idiopathic Retroperitoneal Fibrosis ◽  
Ormond’S Disease ◽  
Disease Definition

A presentation is given of the stages through which Ormond in 1962 managed to define Idiopathic Retroperitoneal Fibrosis (RPF), thereby giving it a precise clinical identity while the disease became known with his name. In the following years Ormond examined some etiopathogenetic hypotheses and showed that the etiology of RPF was still unknown, even if in some cases the cause had been traced to some medicines, such as methysergide, which were thought to act as haptens. The anatomical limits of the retroperitoneum and its structures are then outlined, in particular the retroperitoneal connective tissue.

scholarly journals Ormond’s Disease – IgG4-related Disease

2015 ◽  
Vol 116 (3) ◽  
pp. 181-192 ◽  
Author(s):  
Miroslav Průcha ◽  
Ivan Kolombo ◽  
Petr Štádler
Keyword(s):  
Inferior Vena ◽  
Retroperitoneal Fibrosis ◽  
Vena Cava ◽  
Clinical History ◽  
Iliac Arteries ◽  
Ormond’S Disease ◽  
Related Disease ◽  
Igg4 Related Disease ◽  
Diagnostic Approaches ◽  
Unclear Etiology

Ormond’s disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferior vena cava. This disease is currently classed as an IgG4-related disease. In our review we analyse the clinical history, diagnostic approaches, surgical and immunosuppressive therapies.

scholarly journals Retroperitoneal fibrosis (ormond’s disease). Clinical case

2019 ◽  
Vol 9 (2) ◽  
pp. 140-144
Author(s):  
E. N. Skryabina ◽  
N. A. Magdeeva ◽  
I. S. Badurgov
Keyword(s):  
Clinical Case ◽  
Retroperitoneal Fibrosis ◽  
Ormond’S Disease

Ormond's disease: Aspetti anatomo-patologici: Ormond's disease: Histopathological features

1998 ◽  
Vol 65 (2) ◽  
pp. 267-271
Author(s):  
M. Chilosi ◽  
G. Mariuzzi
Keyword(s):  
Differential Diagnosis ◽  
Retroperitoneal Fibrosis ◽  
Idiopathic Retroperitoneal Fibrosis ◽  
Clinical Role ◽  
Ormond’S Disease ◽  
Histopathological Features ◽  
Pathologic Features ◽  
Cell Components ◽  
Histopathological Studies

Histopathological studies have significantly contributed to clarifing the pathogenetic mechanisms of idiopathic retroperitoneal fibrosis (Ormond's disease), confirming in most cases its inflammatory nature. In this review we describe the principal pathologic features of the lesion, describing the different inflammatory and fibrogenic cell components. In addition, the differential diagnosis of Ormond's disease and the clinical role of histopathology and immunophenotypical analysis are briefly discussed.

scholarly journals An atypical presentation of Ormond’s disease

2022 ◽  
Vol 35 (4) ◽  
Author(s):  
João Carvão ◽  
◽  
Carlota Vida ◽  
Luís Resende ◽  
Francisca Silva ◽  
...  
Keyword(s):  
Retroperitoneal Fibrosis ◽  
Immunohistochemical Study ◽  
Rare Condition ◽  
Therapeutic Strategies ◽  
Atypical Presentation ◽  
Ormond’S Disease ◽  
Randomized Controlled ◽  
Adjacent Structures ◽  
The Right ◽  
Inflammatory Tissue

Retroperitoneal fibrosis is a rare condition defined by an overproduction of fibro-inflammatory tissue in the retroperitoneum, usually involving the abdominal aorta, but also managing to invade adjacent structures. We report a case of a 47-year-old female patient with an atypical radiological presentation of retroperitoneal fibrosis, involving predominantly the right kidney. Ultimately, the diagnosis was performed by an immunohistochemical study that identified IgG4+ plasmocytes after kidney nephrectomy, also known as Ormond’s disease. There are no universal guidelines for the treatment of retroperitoneal fibrosis, due to its rarity and lack of randomized controlled trials comparing different therapeutic strategies.

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