Malignant Chondroid Syringoma With Nose and Paranasal Sinus Extension: A Case Report

Chondroid syringoma is a rare, skin appendageal tumor. It is also known as mixed tumor of skin, as it histologically resembles mixed tumor of salivary gland (pleomorphic adenoma). It is most commonly a benign tumor, but a few malignant counterparts have been described in history. It usually presents as a solid, slow-growing, solitary, and painless nodule in the head and neck region. Malignant counterpart is rare and commonly affects trunk and extremities. Early diagnosis and surgery by wide local excision are the most reliable treatments to date. Recurrences are common and hence close follow-up is advised. In this study, we present a case of malignant chondroid syringoma of face with extensive extension into nose and paranasal sinuses, which was recurrent and managed by surgical excision and radiotherapy. To the best of our knowledge, this is the first reported case with extension and bone destruction into nose and sinuses.

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Chondroid syringoma of the upper lip: a rare entity

International Journal of Otorhinolaryngology and Head and Neck Surgery ◽

10.18203/issn.2454-5929.ijohns20204198 ◽

2020 ◽

Vol 6 (10) ◽

pp. 1900

Author(s):

Ashiya Goel ◽

Aman . ◽

Vinny Raheja ◽

Manisha Kumari

Keyword(s):

Differential Diagnosis ◽

Normal Tissue ◽

Neck Region ◽

Rare Entity ◽

Upper Lip ◽

Head And Neck Region ◽

Chondroid Syringoma ◽

The Face ◽

Slow Growing

Chondroid syringomas are uncommon cutaneous neoplasms of sweat gland origin which are slow-growing, nontender, subcutaneous or intracutaneous in location and often occurring in the head and neck region. Chondroid syringoma should be considered in the differential diagnosis of any subcutaneous nodule over the face. The clinician may miss the diagnosis of this lesion and if it is suspected, tumour should be excised with a margin of normal tissue and regular follow up should be done.

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A rare case of a benign giant chondroid syringoma of nose

International Journal of Otorhinolaryngology and Head and Neck Surgery ◽

10.18203/issn.2454-5929.ijohns20203214 ◽

2020 ◽

Vol 6 (8) ◽

pp. 1549

Author(s):

Neemu Hage ◽

Jaimanti Bakshi ◽

Mayank Rampal

Keyword(s):

Neck Region ◽

Needle Aspiration ◽

Disease Entity ◽

Head And Neck Region ◽

Chondroid Syringoma ◽

Large Size ◽

Benign Nature ◽

Slow Growing ◽

Disease Free

Chondroid syringoma (CS) is a rare benign appendageal tumour of the skin, with histological similarities to pleomorphic adenoma of salivary glands. It typically presents as a slow growing nodular mass generally less than 3 cm, arising from the skin, predominantly in the head and neck region. We report a case of a 61-year-old male with a massive nasal mass attained over a period of 2 years. A fine needle aspiration of the lesion was suggestive of CS. It was excised completely under general anaesthesia. The postoperative histopathology was also consistent with CS. The patient was followed up on a regular basis and was rendered disease free till his last follow up at 4 months. Our purpose of reporting this case is to highlight the rarity of the disease entity, as well as the occasion of it acquiring a large size yet, maintaining its benign nature.

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A rare clinical case: schwannoma of tongue

International Journal of Otorhinolaryngology and Head and Neck Surgery ◽

10.18203/issn.2454-5929.ijohns20191464 ◽

2019 ◽

Vol 5 (3) ◽

pp. 789

Author(s):

Chandra Veer Singh ◽

Sheetal Radia ◽

Saalim Sheikh ◽

Vijay Haribhakti

Keyword(s):

Head And Neck ◽

Rare Case ◽

Neck Region ◽

Surgical Excision ◽

Imaging Studies ◽

Head And Neck Tumours ◽

Head And Neck Region ◽

Complete Surgical Excision ◽

Slow Growing ◽

Rule Out

Schwannoma are slow growing tumours, which can arise from any peripheral nerve. 10% of schwannomas that occur in the head and neck region mostly originate from the vagus or sympathetic nervous system. Extracranial schwannomas in the head and neck region are rare neoplasm. Intraoral schwannoma are only 1% of the all head and neck tumours. Diagnosis is established by imaging studies such as magnetic resonance imaging or computed tomography, while FNAC is used to rule out other conditions. We report a rare case of lingual schwannomas generally present as a painless lump schwannoma of the tongue in a 27-year-old male complaining of asymptomatic swelling over a posterolateral surface of the tongue, treated by complete surgical excision. The diagnosis was established on the basis of clinical, histopathological, and immunohistochemical examination. We report a rare case of schwannoma over the posterolateral surface of tongue. Prognosis is good for the patient when this condition is correctly diagnosed as the condition rarely recurs after complete resection.

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Asymptomatic nodule on face: Dermoscopic and histopathological clue for diagnosis

Nepal Journal of Neuroscience ◽

10.3126/njn.v17i1.28369 ◽

2020 ◽

Vol 17 (1) ◽

pp. 63-65

Author(s):

Anisha Joshi ◽

Deeptara Pathak Thapa

Keyword(s):

Head And Neck ◽

Peripheral Nerves ◽

Neck Region ◽

Surgical Excision ◽

Benign Tumors ◽

Complete Excision ◽

Head And Neck Region ◽

The Common ◽

Slow Growing ◽

Rare Diagnosis

Schwannomas/ neurilemmomas are benign tumors of nerve sheath arising from Schwann cells that form myelin sheath around peripheral nerves. They are usually solitary, slow growing and encapsulated lesions. Head and neck are the common sites. We report a case of a 38 years old Nepalese female who had presented with a solitary asymptomatic, slow growing nodule on the left side of the chin for the last three years. Dermoscopy of the lesion revealed arborizing vessels with brownish pigmentation overlying a whitish to pinkish background. Complete excision of the lesion was performed. Histopathological evaluation of the lesion revealed schwannoma. Though schwannomas are a rare diagnosis, they should be considered as a differential diagnosis of any unilateral, asymptomatic, slow growing nodule in the head and neck region. Dermoscopy is a useful tool which helps to differentiate schwannoma from other lesions. Histopathology is the gold standard for diagnosis and the treatment of choice is surgical excision.

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Giant Low-Grade Fibromyxoid Sarcoma in the Neck

Korean Journal of Otorhinolaryngology - Head and Neck Surgery ◽

10.3342/kjorl-hns.2019.00857 ◽

2020 ◽

Vol 63 (9) ◽

pp. 432-435

Author(s):

Jong Min Park ◽

Hye Rin Lim ◽

Jo Heon Kim ◽

Dong Hoon Lee

Keyword(s):

Neck Region ◽

Surgical Excision ◽

Late Recurrence ◽

Low Grade ◽

Head And Neck Region ◽

Long Term Follow Up ◽

Fibromyxoid Sarcoma ◽

Middle Aged Adults

Low-grade fibromyxoid sarcoma (LGFS) is a soft tissue tumor that rarely occurs in the head and neck region. It occurs mainly in the proximal extremities and the trunk and is prevalent in the young and middle-aged adults. In the present case, LGFS was present at an atypical location and at an unusual age. The treatment of choice for LGFS is radical wide surgical excision with a clear margin. Long-term follow-up is essential for all patients with LGFS, as it has the potential for late recurrence or metastasis.

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Chondroid Syringoma of Dorsum of the Nose

Bengal Journal of Otolaryngology and Head Neck Surgery ◽

10.47210/bjohns.2018.v26i3.212 ◽

2018 ◽

Vol 26 (3) ◽

pp. 219-221

Author(s):

Netra Aniruddha Pathak ◽

Vidya Vasant Rokade ◽

Kiran Jayawant Shinde

Keyword(s):

Surgical Excision ◽

Benign Tumors ◽

Adult Males ◽

Seborrheic Keratosis ◽

Chondroid Syringoma ◽

External Nose ◽

Middle Aged Adult ◽

Slow Growing ◽

Mixed Tumors

IntroductionChondroid syrigomas are rare, usually benign tumors occurring predominantly in the head and neck area. These are also known as mixed tumors of skin. Preoperative diagnosis is difficult and generally histopathology examination confirms the diagnosis. The usual presentation is that of a slowly growing mass.Case ReportA rare case of chondroid syringoma on dorsum of external nose in 30 year old female patient is presented.DiscussionChondroid syringoma presents as slow‐growing, painless, subcutaneous or intracutaneous nodule in middle‐aged adult males. The tumor is often initially confused with more common dermatologic skin disorders such as sebaceous cysts, dermoid cysts, neurofibromas, dermatofibromas, basal cell carcinoma, histiocytoma and seborrheic keratosis. The treatment of choice is surgical excision with negative margins with follow-up to detect recurrences.

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Fibromatosis aggressiva of parapharyngeal space – a case report and review of literature.

Polski Przegląd Otorynolaryngologiczny ◽

10.5604/01.3001.0010.0179 ◽

2017 ◽

Vol 6 (2) ◽

pp. 10-15

Author(s):

Angelika Piotrowska ◽

Anna Rzepakowska ◽

Piotr Chęciński ◽

Kazimierz Niemczyk

Keyword(s):

Parapharyngeal Space ◽

Neck Region ◽

Aggressive Fibromatosis ◽

Surgical Excision ◽

Review Of Literature ◽

Head And Neck Region ◽

Desmoid Fibromatosis ◽

Complete Surgical Excision ◽

High Local Recurrence Rate

Desmoid fibromatosis is defined as a rare fibroblastic proliferation. Although histologically benign, desmoids are locally invasive and associated with a high local recurrence rate. When located in the head and neck region, fibromatosis tends to be more aggressive and associated with significant morbidity, which may be attributed to the proximity of the vital structures. We report a case of 33-year-old woman with aggressive fibromatosis of parapharyngeal space. Complete surgical excision of the lesion was performed and the postoperative period was without complications. The patient remains under careful follow-up and there is no recurrence of the disease.

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Palatal Schwannoma: A Rare Case Report

Otorhinolaryngology Clinics - An International Journal ◽

10.5005/jp-journals-10003-1221 ◽

2016 ◽

Vol 8 (1) ◽

pp. 29-31

Author(s):

Nikhil Arora ◽

PS Shahul Hameed

Keyword(s):

Case Report ◽

Oral Cavity ◽

Schwann Cells ◽

Rare Case ◽

Benign Tumor ◽

Neck Region ◽

Head And Neck Region ◽

Nerve Sheath ◽

Rare Case Report ◽

Slow Growing

ABSTRACT Schwannoma is a benign tumor that originates from perineural Schwann cells of nerve sheath. They are solitary, wellencapsulated, slow-growing adjacent to the parental nerve but extrinsic to the nerve fascicles. Approximately 25 to 45% of all schwannomas are seen in the head and neck region and are found rarely in the oral cavity. Most of the intraoral schwannomas are located in the tongue. Palatal schwannoma is very rare as till date and only 16 cases have been reported; one such rare case we came across is reported here. How to cite this article Hameed PSS, Arora N, Malhotra V. Palatal Schwannoma: A Rare Case Report. Int J Otorhinolaryngol Clin 2016;8(1):29-31.

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Schwannoma Located in Nasopharyngeal Region

Case Reports in Otolaryngology ◽

10.1155/2016/8260629 ◽

2016 ◽

Vol 2016 ◽

pp. 1-3

Author(s):

Fadlullah Aksoy ◽

Alper Yenigun ◽

Erol Senturk ◽

Orhan Ozturan

Keyword(s):

Peripheral Nerves ◽

Histopathological Examination ◽

Neck Region ◽

Case Presentation ◽

Head And Neck Region ◽

Nerve Sheath ◽

Swallowing Difficulties ◽

First Time ◽

Slow Growing

Schwannoma is a tumor which has neuroectoderm origins, is hard, well-circumscribed, encapsulated, and slow growing benign cranial tumor, and may autonomously grow out of the nerve sheath of peripheral nerves. It is mostly seen in the head and neck region. In the paranasal sinus and nose areas, it is seen at a rate of 4%. The diagnosis is mostly made after histopathological examination. In this paper, a Schwannoma case observed in the nasopharyngeal region was presented in a 20-year-old female who had complaints of sleeping with open mouth, snoring, foreign body feeling in throat, and swallowing difficulties. The tumor was extracted via transoral approach. No recurrence was observed during follow-up over the next year. This case presentation is presented for the first time in the literature in English.

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Novel surgical technique for management of tongue schwannoma: case report

International Journal of Otorhinolaryngology and Head and Neck Surgery ◽

10.18203/issn.2454-5929.ijohns20191754 ◽

2019 ◽

Vol 5 (3) ◽

pp. 804

Author(s):

Neha Jain ◽

Shama Shishodia ◽

Ruchima Dham ◽

Suparna Roy ◽

Sachin Goel

Keyword(s):

Case Report ◽

Treatment Options ◽

Neck Region ◽

Surgical Excision ◽

Uneventful Recovery ◽

Common Site ◽

Head And Neck Region ◽

Complete Surgical Excision ◽

Oral Approach ◽

Slow Growing

Schwannomas are rare, solitary, slow growing, smooth surfaced and well encapsulated tumors. Schwannomas of head and neck region account for 25-40% of all the cases. Approximately 1%–12% of schwannomas occur intraorally, the tongue being the most common site. Complete surgical excision is the treatment of choice. In this article, we describe a case of tongue schwannoma in a child, along with diagnostic and treatment options of tongue lesions. The tongue mass was completely excised via trans-oral approach using coblation method. The patient followed up for 1 year; he had an uneventful recovery and no recurrence.

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