scholarly journals Prenatal Sonographic Detection of Ebstein’s Anomaly

2017 ◽  
Vol 33 (3) ◽  
pp. 225-230
Author(s):  
Mariah C. Root ◽  
Kelsy L. Fisher
Keyword(s):  
Tricuspid Valve ◽  
Congenital Heart Defect ◽  
Congenital Heart ◽  
Ebstein’S Anomaly ◽  
Rare Type ◽  
Sonographic Appearance ◽  
Ebstein's Anomaly ◽  
Treatment Characteristic ◽  
The Right

Ebstein’s anomaly is a rare type of congenital heart defect characterized by a malformation of the tricuspid valve and the right side of the heart. This case study presents a well-documented case of Ebstein’s anomaly that was diagnosed prenatally using sonography. The ability of prenatal sonography to detect and accurately diagnosis this case allowed for a change in the management of the pregnancy to properly evaluate the condition and prepare for treatment. In addition, information regarding Ebstein’s anomaly is reviewed and specifically addresses etiology, symptoms, diagnosis, treatment, characteristic sonographic appearance, and common differential diagnoses.

Ebstein’s Anomaly

2007 ◽  
Vol 26 (3) ◽  
pp. 197-208 ◽  
Author(s):  
Sarah Pashia
Keyword(s):  
Heart Failure ◽  
Tricuspid Valve ◽  
Congenital Heart ◽  
Clinical Presentation ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Clinical Presentations ◽  
Wide Range ◽  
Pathologic Findings ◽  
The Right

EBSTEIN’S ANOMALY IS A RARE congenital heart defect characterized by displacement of the tricuspid valve leaflets into the right ventricle.1The defect was first described by Wilhelm Ebstein in 1866.2This anomaly of the tricuspid valve causes the right atrium to thin and become enlarged, resulting in a wide range of clinical presentations.3Clinical presentation depends on the severity of the pathologic findings, which vary considerably from patient to patient. Some infants may present with cyanosis, respiratory distress, heart failure, and even death, whereas others may not present with mild symptoms until adolescence or adulthood.

scholarly journals Ebstein’s Anomaly Corrected by Tissue Valve: Case Report

1970 ◽  
Vol 1 (1) ◽  
pp. 112-114
Author(s):  
SAMA Sabur ◽  
Z Rashid ◽  
A Fazel ◽  
MMG Chowdhury ◽  
M Zaman ◽  
...  
Keyword(s):  
Tricuspid Valve ◽  
Congenital Heart ◽  
Heart Diseases ◽  
Ebstein’S Anomaly ◽  
Tricuspid Valve Repair ◽  
Valve Repair ◽  
Ebstein's Anomaly ◽  
Wpw Syndrome ◽  
Tissue Valve ◽  
Bidirectional Glenn Shunt

Ebstein’s anomaly is a rare form of congenital heart disease with incidence of 1% of all congenital heart diseases. There are two modes of surgical correction of Ebstein’s anomaly: either biventricular repair with or without tricuspid valve replacement, or palliative univentricular repair consisting of bidirectional Glenn shunt or Fontan procedure. We treated a case of severe form of Ebstein’s anomaly with ASD secundum with WPW syndrome. Radiofrequency ablation was done to treat WPW syndrome preoperatively. Celermajer’s index is a prognostic indicator for tricuspid valve repair or replacement. On 04.03.08 tricuspid valve was replaced with 31 mm Carpentier-Edwards bovine pericardial valve under cardiopulmonary bypass. Postoperative period was uneventful. Follow up echo done on 01.06.08 which revealed normally functioning tissue valve found in tricuspid position TR Grade I. So, in conclusion, preoperative evaluation and workout of Celermajer’s index is essential before surgical intervention for decision of tricuspid valve repair or replacement. Last but not the least, any event of arrhythmia should be properly evaluated.Key words: Ebstein’s anomaly, WPW (Wolff- Parkinson-White) Syndrome, Celermajer’s index, Tissue valve. DOI: http://dx.doi.org/10.3329/cardio.v1i1.8213 Cardiovasc. j. 2008; 1(1) : 112-114  

Cor triatriatum dexter masquerading as Ebstein's anomaly

2011 ◽  
Vol 21 (3) ◽  
pp. 354-356 ◽  
Author(s):  
Souheir Salam ◽  
David Gallacher ◽  
Orhan Uzun
Keyword(s):  
Tricuspid Valve ◽  
Transthoracic Echocardiography ◽  
Right Atrium ◽  
Cor Triatriatum ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Cor Triatriatum Dexter ◽  
The Right

AbstractWe report the case of a child with cor triatriatum dexter masquerading as Ebstein's anomaly on transthoracic echocardiography. This was attributed to a floppy membrane arising from the right atrium, protruding into the tricuspid valve and pushing the leaflets downwards, giving an impression of Ebstein's anomaly. The importance of recognising this pitfall will prevent misdiagnosis of Ebstein's anomaly.

Cone repair for Ebstein’s anomaly and atrial fibrillation ablation in an adult patient

2021 ◽  
Keyword(s):  
Atrial Fibrillation ◽  
Tricuspid Valve ◽  
Pulmonary Veins ◽  
Maze Procedure ◽  
Right Atrial ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Previously Treated ◽  
Cone Repair ◽  
The Right

We present a 52-year-old woman with Ebstein’s anomaly not previously treated. In this subset of patients, there are no clear guidelines regarding the best surgical strategy for treating the tricuspid valve: replace it or repair it. In this case, extensive repair of the tricuspid valve and the right ventricle is achieved using the cone repair technique popularized by Dr. José Pedro Da Silva. Because the patient also presented with symptomatic paroxysmal atrial fibrillation, a right atrial maze procedure combined with isolation of the pulmonary veins was performed using both radiofrequency and cryotherapy. At the last follow-up, 2 years after the repair, the patient is asymptomatic and maintains sinus rhythm. The last echocardiogram showed mild tricuspid regurgitation with normal right ventricular function.

scholarly journals Image to Fit the Clinical Picture: Point-of-care Ultrasound Assessment of Ebstein’s Anomaly in Peru

2020 ◽  
Vol 4 (2) ◽  
pp. 222-224
Author(s):  
Ashley Rider ◽  
Andrea Dreyfuss ◽  
Roberto Inga
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart Defect ◽  
Congenital Heart ◽  
Point Of Care ◽  
Ebstein’S Anomaly ◽  
Point Of Care Ultrasound ◽  
Ebstein's Anomaly ◽  
Ultrasound Findings ◽  
Ultrasound Assessment

Ebstein’s anomaly is a congenital heart defect that when left untreated can lead to unique physical exam and ultrasound findings. This case describes a patient who presented with dyspnea and was found to have cyanosis, clubbing, and dilation of right-sided chambers on point-of-care ultrasound. The series of images highlights findings in late-stage Ebstein’s anomaly and serves as a springboard for the discussion of the pathophysiology, diagnosis, and treatment of this rare congenital heart disease.

The Right Ventricular Infundibulum in Ebstein's Anomaly of the Tricuspid Valve

Radiology ◽  
1967 ◽  
Vol 89 (4) ◽  
pp. 694-700 ◽  
Author(s):  
Larry P. Elliott ◽  
Alexis F. Hartmann
Keyword(s):  
Right Ventricular ◽  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
The Right

scholarly journals Successful One and One-half Ventricular Circulation with Bioprosthetic Tricuspid Valve Replacement and Total Chordal Preservation in a Patient with Ebstein’s Anomaly: A Video Presentation

2021 ◽  
Vol 5 (02) ◽  
pp. 147-150
Author(s):  
Ujjwal K. Chowdhury ◽  
Sukhjeet Singh ◽  
Niwin George ◽  
Lakshmi Kumari Sankhyan ◽  
Sandeep Sharan ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Anterior Leaflet ◽  
Tricuspid Annulus ◽  
Tricuspid Valve Replacement ◽  
Rotational Displacement ◽  
Atrioventricular Junction ◽  
Ebstein's Anomaly ◽  
The Right

AbstractEbstein’s anomaly is a rare congenital malformation of the right ventricle and tricuspid valve which is characterized by several features that can exhibit an infinite spectrum of malformation.The abnormalities include: i) adherence of the tricuspid leaflets to the underlying myocardium (failure of delamination); ii) anterior and apical rotational displacement of the functional tricuspid annulus (septal > posterior > anterior leaflet); iii) dilatation of the right atrioventricular junction (the true tricuspid annulus) with variable degrees of hypertrophy and thinning of the wall; iv) dilatation of the “atrialized” portion of the right ventricle; and v) redundancy, fenestration, and tethering of the anterior leaflet.

scholarly journals P843 A rare cause of chest pain: paradoxical embolism in Ebstein"s anomaly

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
H S A Abdelgawad ◽  
N Hisham ◽  
M Shehata ◽  
M A Abdelhay
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Right Ventricle ◽  
Patent Foramen Ovale ◽  
Congenital Heart ◽  
Paradoxical Embolism ◽  
Ebstein’S Anomaly ◽  
Foramen Ovale ◽  
Ebstein's Anomaly ◽  
The Right

Abstract Introduction Ebstein’s anomaly is characterized by displacement of the proximal attachments of the tricuspid valve from the atrioventricular ring into the right ventricle. This structural abnormality divides the right ventricle into an ‘atrialized’ portion and a distal ‘ventricularized’ portion. The severity is variable and accounts for the broad clinical spectrum, from severe disease causing fetal or neonatal death to mild disease compatible with natural survival as late as the eighth decade of life. Ebstein’s anomaly is an uncommon defect occurring in less than 1% of patients with congenital heart disease, but it is disproportionately represented in the adult congenital heart disease population because of its favourable natural history Case report A 55 year old man with no previous cardiac history .He presented to our medical facility complaining of acute retrosternal squeezing retrosternal chest pain few hours before admission. On clinical examination, he had a pansystolic murmur over the tricuspid area .ECG showed right bundle branch block. Laboratory results were unremarkable except elevated cardiac enzymes. 2D Transthoracic Echocardiography revealed a small well-functioning right ventricle, 15 mm/m2 apical displacement of the tricuspid septal leaflet with severe tricuspid regurgitation . 2D and 3D transesophageal echocardiography with intravenous agitated saline injection revealed patent foramen ovale with right to left shunt with immediate crossing of bubbles.Coronary angiography revealed normal coronaries. The patient refused intervention and he was maintained on warfarin treatment . Conclusion The clinical presentation of Ebstein’s anomaly is highly variable—depending on anatomic severity, haemodynamics ,and degree of interatrial shunting. The majority of patients have shunting through a secundum ASD or patent-foramen ovale. Paradoxical embolism maybe an indication for PFO/ ASD closure Abstract P843 Figure.

scholarly journals Tricuspid valve dysplasia and Ebstein's anomaly in dogs: case report

2006 ◽  
Vol 58 (5) ◽  
pp. 762-767 ◽  
Author(s):  
M.G. Sousa ◽  
D.G. Gerardi ◽  
R.O. Alves ◽  
A.A. Camacho
Keyword(s):  
Heart Failure ◽  
Tricuspid Valve ◽  
Medical Therapy ◽  
Diagnostic Methods ◽  
The Other ◽  
Ebstein’S Anomaly ◽  
Post Mortem ◽  
Ebstein's Anomaly ◽  
Tricuspid Insufficiency ◽  
The Right

Two cases of tricuspid valve dysplasia are reported. Dogs were presented for evaluation of weakness and ascites. In both cases, echocardiography disclosed tricuspid insufficiency and, in one of them, tricuspid leaflets also were displaced down into the right ventricle, substantiating Ebstein's anomaly. Medical therapy for congestive heart failure was initiated. One of the dogs suddenly died shortly after diagnosis was established. Although the other dog recovered much better initially, sudden death also occurred. Post-mortem examinations showed right atrioventricular enlargement, and thickened tricuspid leaflets. Clinical features, diagnostic methods and medical therapy are discussed in this paper.

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