Surgical Treatment of a 4-Year-Old Child with Hypertrophic Obstructive Cardiomyopathy: Case Report

2016 ◽  
Vol 19 (1) ◽  
pp. 043
Author(s):  
Jin Chen ◽  
Qingyu Wu ◽  
Zhonghua Xu ◽  
Xiangchen Kong

The incidence of pediatric hypertrophic obstructive cardiomyopathy is low. The lesions usually involve the left ventricle or ventricular septum, leading to either left or right ventricular outflow tract stenosis. However, combined left and right ventricular outflow tract stenosis is rare, and the surgical treatment is limited, especially in children. Surgery to release the obstruction was performed successfully in a 4-year-old child with right and left ventricular outflow tract obstruction together with a hypertrophic cardiomyopathy. The result was excellent.

Author(s):  
B.M. Todurov ◽  
◽  
G.I. Kovtun ◽  
A.V. Khokhlov ◽  
O.V. Pantazi ◽  
...  

Hypertrophic obstructive cardiomyopathy іs a relatively common condition and one of the most common causes of sudden cardiac death in young age. One of the options for the surgical treatment of this pathology is septal myoectomy, which has been the gold standard for decades. However, despite this, surgical treatment is intended for young patients with a low risk of postoperative complications, while patients with concomitant diseases and a higher surgical risk require alternative treatment. Today, alcohol septal ablation is considered an effective, minimally invasive method for treating hypertrophic obstructive cardiomyopathy in patients with a left ventricular outflow tract gradient ≥ 50 mm Hg. The article presents the experience of using alcohol septal ablation in 57 patients with obstruction of the left ventricular outflow tract. Key words: alcoholic septal ablation, hypertrophic cardiomyopathy, left ventricular outflow tract obstruction.


2021 ◽  
Author(s):  
Wanqian Yu ◽  
Hongzhou Zhang ◽  
Pingping Yang ◽  
Lujin Gan ◽  
Chenxi Wang ◽  
...  

Abstract Background: There were no studies on the mechanism of clinical manifestations of straight back syndrome. Our aim was to explore the mechanism of clinical symptoms of straight back syndrome.Methods: From February 2018 to February 2021, we included 4 patients (3 males and 1 female) with straight back syndrome as the experimental group, and 4 normal people matched with sex and BMI as the normal control group. Basic information of patients, laboratory examination, echocardiography in supine and standing position, chest film in positive and lateral position, basic information of control group and echocardiography in supine and standing position were collected. The differences of clinical data between the two groups were compared and analyzed. Results: There were significant differences in left ventricular outflow tract diameter, right ventricular outflow tract diameter and right ventricular outflow tract velocity in the experimental group (their P values were 0.035, 0.011 and 0.015, respectively), but there was no significant difference in left ventricular outflow tract velocity in the standing and supine position (P=0.638). The left ventricular outflow tract diameter, the right ventricular outflow tract diameter and the right ventricular outflow tract velocity in the experimental group were significantly different (P<0.05). The internal diameters of left ventricular outflow tract in upright position, supine position, right ventricular outflow tract, supine position, right ventricular outflow tract were20.50±1.91mm, 18.75±0.96mm;10.00±6.68mm, 15.45±6.06mm;124.25±40.29cm/s and 91.00±28.93cm/s, respectively, in standing position, recumbent position, right ventricular outflow tract, right ventricular outflow tract, supine position, right ventricular outflow tract, supine position, supine position. The velocity of left ventricular outflow tract in upright position was 82.50±2.01 cm/s, and that in supine position was 83.25±2.06 cm/s. There was no significant difference in left ventricular outflow tract velocity in standing and supine position, which may be related to the compression of right ventricular outflow tract.Conclusions: In this study, we got the clinical manifestations of direct-back syndrome patients through comparison of straight back syndrome.


2021 ◽  

Hypertrophic obstructive cardiomyopathy is the most common inherited cardiomyopathy. Septal myectomy is a low-risk operation and remains the first septal reduction therapeutic option. We present a patient with hypertrophic obstructive cardiomyopathy requiring extended septal myectomy and concomitant left ventricular outflow tract intervention. In addition to septal reduction therapy, this patient also underwent anterior mitral valve plication, trigonal release, and secondary chordal division to relieve the obstruction. A tailored approach to hypertrophic obstructive cardiomyopathy with a comprehensive left ventricular outflow tract intervention is necessary to ensure the best hemodynamic outcome. Preoperative heart failure and recurrent syncope fully resolved after this intervention.


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